| Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
|
1
|
Pulmonary hypertension as a risk factor for death in patients with sickle cell disease.
|
N Engl J Med
|
2004
|
10.51
|
|
2
|
Effect of hydroxyurea on mortality and morbidity in adult sickle cell anemia: risks and benefits up to 9 years of treatment.
|
JAMA
|
2003
|
8.18
|
|
3
|
The risks and benefits of long-term use of hydroxyurea in sickle cell anemia: A 17.5 year follow-up.
|
Am J Hematol
|
2010
|
3.78
|
|
4
|
Diastolic dysfunction is an independent risk factor for death in patients with sickle cell disease.
|
J Am Coll Cardiol
|
2007
|
2.76
|
|
5
|
An official American Thoracic Society clinical practice guideline: diagnosis, risk stratification, and management of pulmonary hypertension of sickle cell disease.
|
Am J Respir Crit Care Med
|
2014
|
2.23
|
|
6
|
N-terminal pro-brain natriuretic peptide levels and risk of death in sickle cell disease.
|
JAMA
|
2006
|
2.04
|
|
7
|
Circumstances of death in adult sickle cell disease patients.
|
Am J Hematol
|
2006
|
1.74
|
|
8
|
Hepatitis C virus in sickle cell disease.
|
J Natl Med Assoc
|
2003
|
1.68
|
|
9
|
Efficacy and safety of the Gardos channel blocker, senicapoc (ICA-17043), in patients with sickle cell anemia.
|
Blood
|
2008
|
1.61
|
|
10
|
Severe vaso-occlusive episodes associated with use of systemic corticosteroids in patients with sickle cell disease.
|
J Natl Med Assoc
|
2008
|
1.51
|
|
11
|
Sildenafil therapy in patients with sickle cell disease and pulmonary hypertension.
|
Br J Haematol
|
2005
|
1.47
|
|
12
|
HCV in sickle cell disease.
|
J Natl Med Assoc
|
2003
|
1.39
|
|
13
|
Nitric oxide for inhalation in the acute treatment of sickle cell pain crisis: a randomized controlled trial.
|
JAMA
|
2011
|
1.38
|
|
14
|
Iron overload in Africans and African-Americans and a common mutation in the SCL40A1 (ferroportin 1) gene.
|
Blood Cells Mol Dis
|
2003
|
1.29
|
|
15
|
Genetic screening for iron overload: No evidence of discrimination at 1 year.
|
J Fam Pract
|
2007
|
1.27
|
|
16
|
Exercise capacity and haemodynamics in patients with sickle cell disease with pulmonary hypertension treated with bosentan: results of the ASSET studies.
|
Br J Haematol
|
2010
|
1.25
|
|
17
|
Prospective echocardiography assessment of pulmonary hypertension and its potential etiologies in children with sickle cell disease.
|
Am J Cardiol
|
2009
|
1.22
|
|
18
|
Relationships of serum ferritin, transferrin saturation, and HFE mutations and self-reported diabetes in the Hemochromatosis and Iron Overload Screening (HEIRS) study.
|
Diabetes Care
|
2006
|
1.20
|
|
19
|
Depression in sickle cell disease.
|
J Natl Med Assoc
|
2003
|
1.18
|
|
20
|
Mutations and polymorphisms in hemoglobin genes and the risk of pulmonary hypertension and death in sickle cell disease.
|
Am J Hematol
|
2008
|
1.15
|
|
21
|
Pulmonary hypertension of sickle cell disease beyond classification constraints.
|
J Am Coll Cardiol
|
2014
|
1.09
|
|
22
|
Markers of severe vaso-occlusive painful episode frequency in children and adolescents with sickle cell anemia.
|
J Pediatr
|
2011
|
1.05
|
|
23
|
Hematologic, biochemical, and cardiopulmonary effects of L-arginine supplementation or phosphodiesterase 5 inhibition in patients with sickle cell disease who are on hydroxyurea therapy.
|
Eur J Haematol
|
2008
|
1.04
|
|
24
|
Frequent and prolonged hospitalizations: a risk factor for early mortality in sickle cell disease patients.
|
Am J Hematol
|
2003
|
1.01
|
|
25
|
Long-term outcomes in patients with sickle cell disease and frequent vaso-occlusive crises.
|
Am J Med Sci
|
2003
|
0.99
|
|
26
|
Combination erythropoietin-hydroxyurea therapy in sickle cell disease: experience from the National Institutes of Health and a literature review.
|
Haematologica
|
2006
|
0.99
|
|
27
|
Concordant fetal hemoglobin response to hydroxyurea in siblings with sickle cell disease.
|
Am J Hematol
|
2003
|
0.94
|
|
28
|
Determinants and characteristics of mean corpuscular volume and hemoglobin concentration in white HFE C282Y homozygotes in the hemochromatosis and iron overload screening study.
|
Am J Hematol
|
2007
|
0.94
|
|
29
|
Nitric Oxide Metabolites in Sickle Cell Anemia Patients after Oral Administration of Hydroxyurea; Hemoglobinopathy.
|
Hematology
|
2000
|
0.90
|
|
30
|
Genetic determinants of haemolysis in sickle cell anaemia.
|
Br J Haematol
|
2013
|
0.89
|
|
31
|
Effects of hydroxyurea treatment on cerebral oxygenation in adult patients with sickle cell disease: an open-label pilot study.
|
Clin Ther
|
2005
|
0.89
|
|
32
|
Laboratory and echocardiography markers in sickle cell patients with leg ulcers.
|
Am J Hematol
|
2011
|
0.89
|
|
33
|
Hydroxyurea treatment of sickle cell anemia in hospital-based practices.
|
Am J Hematol
|
2002
|
0.87
|
|
34
|
Fluorescence measurements of the labile iron pool of sickle erythrocytes.
|
Blood
|
2003
|
0.84
|
|
35
|
Nitric oxide and cyclic GMP levels in sickle cell patients receiving hydroxyurea.
|
Br J Haematol
|
2002
|
0.82
|
|
36
|
Accuracy of family history of hemochromatosis or iron overload: the hemochromatosis and iron overload screening study.
|
Clin Gastroenterol Hepatol
|
2008
|
0.82
|
|
37
|
Arterialization of peripheral venous blood in sickle cell disease.
|
J Natl Med Assoc
|
2002
|
0.79
|
|
38
|
Low cobalamin levels in African Americans with and without sickle cell disease.
|
J Natl Med Assoc
|
2006
|
0.79
|
|
39
|
Case 17-2005: acute chest syndrome and ARDS.
|
N Engl J Med
|
2005
|
0.78
|
|
40
|
Bivariate mixture modeling of transferrin saturation and serum ferritin concentration in Asians, African Americans, Hispanics, and whites in the Hemochromatosis and Iron Overload Screening (HEIRS) Study.
|
Transl Res
|
2007
|
0.76
|
|
41
|
Alpha-thalassaemia and response to hydroxyurea in sickle cell anaemia.
|
Eur J Haematol
|
2014
|
0.75
|
|
42
|
Reply: Practice guideline for pulmonary hypertension in sickle cell: direct evidence needed before universal adoption.
|
Am J Respir Crit Care Med
|
2014
|
0.75
|
|
43
|
Physician-assisted suicide.
|
Crit Care Med
|
2009
|
0.75
|
|
44
|
Pulmonary hypertension in sickle cell disease.
|
N Engl J Med
|
2011
|
0.75
|
|
45
|
The celestial fire of conscience.
|
N Engl J Med
|
2005
|
0.75
|
|
46
|
Central retinal vein occlusion in sickle cell disease.
|
South Med J
|
2004
|
0.75
|