Ryoji Kobayashi

Author PubWeight™ 81.12‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 STO-609, a specific inhibitor of the Ca(2+)/calmodulin-dependent protein kinase kinase. J Biol Chem 2002 2.28
2 Mutation of the beta1-tubulin gene associated with congenital macrothrombocytopenia affecting microtubule assembly. Blood 2008 1.73
3 Outcome of 154 patients with severe aplastic anemia who received transplants from unrelated donors: the Japan Marrow Donor Program. Blood 2002 1.55
4 ACTN1 mutations cause congenital macrothrombocytopenia. Am J Hum Genet 2013 1.49
5 Long-term efficacy of hematopoietic stem cell transplantation on brain involvement in patients with mucopolysaccharidosis type II: a nationwide survey in Japan. Mol Genet Metab 2012 1.30
6 Risk-stratified therapy and the intensive use of cytarabine improves the outcome in childhood acute myeloid leukemia: the AML99 trial from the Japanese Childhood AML Cooperative Study Group. J Clin Oncol 2009 1.26
7 Prospective multicenter trial comparing repeated immunosuppressive therapy with stem-cell transplantation from an alternative donor as second-line treatment for children with severe and very severe aplastic anemia. Blood 2007 1.25
8 A CaMK cascade activates CRE-mediated transcription in neurons of Caenorhabditis elegans. EMBO Rep 2002 1.22
9 FBXW7 and NOTCH1 mutations in childhood T cell acute lymphoblastic leukaemia and T cell non-Hodgkin lymphoma. Br J Haematol 2009 1.12
10 Phosphorylation of Numb family proteins. Possible involvement of Ca2+/calmodulin-dependent protein kinases. J Biol Chem 2005 1.09
11 Improved treatment results of children with B-cell non-Hodgkin lymphoma: a report from the Japanese Pediatric Leukemia/Lymphoma Study Group B-NHL03 study. Pediatr Blood Cancer 2014 1.07
12 Prospective study of a pirarubicin, intermediate-dose cytarabine, and etoposide regimen in children with Down syndrome and acute myeloid leukemia: the Japanese Childhood AML Cooperative Study Group. J Clin Oncol 2007 1.03
13 Epstein-Barr virus-associated B-cell lymphoma in a patient with DNA ligase IV (LIG4) syndrome. Am J Med Genet A 2007 1.02
14 A single amino acid difference between alpha and beta Ca2+/calmodulin-dependent protein kinase kinase dictates sensitivity to the specific inhibitor, STO-609. J Biol Chem 2003 1.01
15 Epidemiology and treatment outcome of invasive fungal infections in patients with hematological malignancies. Int J Hematol 2012 0.99
16 Activation of SAD kinase by Ca2+/calmodulin-dependent protein kinase kinase. Biochemistry 2008 0.99
17 Clinical impact of HLA-DR15, a minor population of paroxysmal nocturnal haemoglobinuria-type cells, and an aplastic anaemia-associated autoantibody in children with acquired aplastic anaemia. Br J Haematol 2008 0.98
18 Biologic activity of RANTES in apheresis PLT concentrates and its involvement in nonhemolytic transfusion reactions. Transfusion 2003 0.97
19 Chronic graft-versus-host disease following umbilical cord blood transplantation: retrospective survey involving 1072 patients in Japan. Blood 2008 0.95
20 Identification of a novel erythroid-specific enhancer for the ALAS2 gene and its loss-of-function mutation which is associated with congenital sideroblastic anemia. Haematologica 2013 0.95
21 Mechanism of the generation of autonomous activity of Ca2+/calmodulin-dependent protein kinase IV. J Biol Chem 2004 0.94
22 Haematopoietic stem cell transplantation for relapsed or refractory anaplastic large cell lymphoma: a study of children and adolescents in Japan. Br J Haematol 2014 0.93
23 Interaction of S100 proteins with the antiallergic drugs, olopatadine, amlexanox, and cromolyn: identification of putative drug binding sites on S100A1 protein. Biochem Biophys Res Commun 2002 0.92
24 Identification of intracellular target proteins of the calcium-signaling protein S100A12. Eur J Biochem 2004 0.92
25 Wiskott-Aldrich syndrome presenting with a clinical picture mimicking juvenile myelomonocytic leukaemia. Pediatr Blood Cancer 2012 0.92
26 Interactions of S100A2 and S100A6 with the tetratricopeptide repeat proteins, Hsp90/Hsp70-organizing protein and kinesin light chain. J Biol Chem 2008 0.91
27 Predicting response to immunosuppressive therapy in childhood aplastic anemia. Haematologica 2011 0.90
28 The role of tumor lysis in reversible posterior leukoencephalopathy syndrome. Pediatr Radiol 2005 0.89
29 Treatment of neurodegenerative CNS disease in Langerhans cell histiocytosis with a combination of intravenous immunoglobulin and chemotherapy. Pediatr Blood Cancer 2008 0.89
30 Phosphorylation of Numb regulates its interaction with the clathrin-associated adaptor AP-2. FEBS Lett 2006 0.89
31 S100A1 is a novel molecular chaperone and a member of the Hsp70/Hsp90 multichaperone complex. J Biol Chem 2003 0.88
32 Identification and characterization of wolframin, the product of the wolfram syndrome gene (WFS1), as a novel calmodulin-binding protein. Biochemistry 2009 0.88
33 Identification and characterization of novel components of a Ca2+/calmodulin-dependent protein kinase cascade in HeLa cells. FEBS Lett 2003 0.87
34 36-kDa microfibril-associated glycoprotein (MAGP-36) is an elastin-binding protein increased in chick aortae during development and growth. Exp Cell Res 2005 0.87
35 Acute promyelocytic leukemia after living donor partial orthotopic liver transplantation in two Japanese girls. Leuk Lymphoma 2005 0.87
36 S100 proteins modulate protein phosphatase 5 function: a link between CA2+ signal transduction and protein dephosphorylation. J Biol Chem 2012 0.87
37 S100 proteins regulate the interaction of Hsp90 with Cyclophilin 40 and FKBP52 through their tetratricopeptide repeats. FEBS Lett 2010 0.86
38 The role of calcium/calmodulin-dependent protein kinase cascade in glucose upregulation of insulin gene expression. Diabetes 2004 0.85
39 Prospective study of a therapeutic regimen with all-trans retinoic acid and anthracyclines in combination of cytarabine in children with acute promyelocytic leukaemia: the Japanese childhood acute myeloid leukaemia cooperative study. Br J Haematol 2011 0.85
40 Hematopoietic stem cell transplantation in patients with severe congenital neutropenia: an analysis of 18 Japanese cases. Pediatr Transplant 2010 0.84
41 Identification and characterization of PRG-1 as a neuronal calmodulin-binding protein. Biochem J 2010 0.84
42 A prospective, randomized study comparing cefozopran with piperacillin-tazobactam plus ceftazidime as empirical therapy for febrile neutropenia in children with hematological disorders. Pediatr Blood Cancer 2008 0.84
43 Prognostic significance of the BAALC isoform pattern and CEBPA mutations in pediatric acute myeloid leukemia with normal karyotype: a study by the Japanese Childhood AML Cooperative Study Group. Int J Hematol 2010 0.83
44 Rabbit antithymocyte globulin and cyclosporine as first-line therapy for children with acquired aplastic anemia. Blood 2013 0.83
45 Regulatory mechanism of Dictyostelium myosin light chain kinase A. J Biol Chem 2003 0.82
46 Stem cell transplantation in primary immunodeficiency disease patients. Pediatr Int 2007 0.82
47 Ca2+/S100 proteins act as upstream regulators of the chaperone-associated ubiquitin ligase CHIP (C terminus of Hsc70-interacting protein). J Biol Chem 2013 0.82
48 Risk factor analysis of non-Hodgkin lymphoma-associated haemophagocytic syndromes: a multicentre study. Br J Haematol 2014 0.82
49 Congenital dermatofibrosarcoma protuberans in a newborn infant with a massive back tumor: favorable effects of oral imatinib on the control of residual tumor growth. J Pediatr Hematol Oncol 2011 0.82
50 Differential gene expression of 36-kDa microfibril-associated glycoprotein (MAGP-36/MFAP4) in rat organs. Cell Tissue Res 2008 0.82
51 Cerebellar ataxia in pediatric patients with Langerhans cell histiocytosis. J Pediatr Hematol Oncol 2004 0.81
52 Incidence and risk factors of early bacterial infections after unrelated cord blood transplantation. Biol Blood Marrow Transplant 2009 0.81
53 Neurodegenerative central nervous system disease as late sequelae of Langerhans cell histiocytosis. Report from the Japan LCH Study Group. Haematologica 2008 0.81
54 Expression of 36-kDa microfibril-associated glycoprotein (MAGP-36) in human keratinocytes and its localization in skin. J Dermatol Sci 2002 0.81
55 RAS mutations are frequent in FAB type M4 and M5 of acute myeloid leukemia, and related to late relapse: a study of the Japanese Childhood AML Cooperative Study Group. Int J Hematol 2012 0.81
56 Generation of autonomous activity of Ca(2+)/calmodulin-dependent protein kinase kinase β by autophosphorylation. Biochemistry 2011 0.80
57 The role of calcium/calmodulin-dependent protein kinase cascade on MIP-1alpha gene expression of ATL cells. Exp Hematol 2008 0.80
58 Outcomes in two Japanese adenosine deaminase-deficiency patients treated by stem cell gene therapy with no cytoreductive conditioning. J Clin Immunol 2015 0.80
59 Renal alpha-actinin-4: purification and puromycin aminonucleoside-binding property. Nephron Exp Nephrol 2003 0.79
60 Plasma protein C is a useful clinical marker for hepatic veno-occlusive disease (VOD) in stem cell transplantation. Pediatr Blood Cancer 2010 0.79
61 Wiskott-Aldrich syndrome with unusual clinical features similar to juvenile myelomonocytic leukemia. Int J Hematol 2012 0.79
62 Successful report of reduced-intensity stem cell transplantation from unrelated umbilical cord blood in a girl with chronic active Epstein-Barr virus infection. J Pediatr Hematol Oncol 2006 0.79
63 Association of cigarette smoking with the expression of nuclear survivin in pathological Stage IA lung adenocarcinomas. Med Mol Morphol 2013 0.79
64 Suramin is a novel activator of PP5 and biphasically modulates S100-activated PP5 activity. Appl Biochem Biotechnol 2013 0.79
65 Cord blood transplantation from unrelated donors for children with acute lymphoblastic leukemia in Japan: the impact of methotrexate on clinical outcomes. Biol Blood Marrow Transplant 2011 0.79
66 Neuronal calcium sensor proteins are direct targets of the insulinotropic agent repaglinide. Biochem J 2003 0.79
67 Tumor lysis syndrome as a risk factor for posterior reversible encephalopathy syndrome in children with hematological malignancies. Int J Hematol 2014 0.79
68 A retrospective clinical analysis of Japanese patients with peripheral T-cell lymphoma not otherwise specified: Hokkaido Hematology Study Group. Int J Hematol 2013 0.78
69 Bernard-Soulier syndrome caused by a hemizygous GPIbβ mutation and 22q11.2 deletion. Pediatr Int 2013 0.78
70 Identification of a novel CaMKK substrate. Biochem Biophys Res Commun 2011 0.78
71 Transcriptional regulation of nuclear orphan receptor, NOR-1, by Ca(2+)/calmodulin-dependent protein kinase cascade. FEBS Lett 2002 0.78
72 Progressive glomerulopathy with unusual deposits of striated structures: a new disease entity? Nephrol Dial Transplant 2010 0.78
73 Hsp90 is a direct target of the anti-allergic drugs disodium cromoglycate and amlexanox. Biochem J 2003 0.78
74 Current approaches to management of cerebral fungal infection in pediatric patients with hematologic disorders. J Pediatr Hematol Oncol 2008 0.78
75 Role of calcium-calmodulin-dependent protein kinase cascade in thyrotropin (TSH)-releasing hormone induction of TSH and prolactin gene expression. Endocrinology 2004 0.77
76 Refractory sacrococcygeal germ cell tumor in Schinzel-Giedion syndrome. J Pediatr Hematol Oncol 2015 0.77
77 Outcome of children with relapsed acute myeloid leukemia following initial therapy under the AML99 protocol. Int J Hematol 2014 0.77
78 Exendin-4 regulates pancreatic ABCA1 transcription via CaMKK/CaMKIV pathway. J Cell Mol Med 2009 0.77
79 Risk factors for human herpesvirus 6 reactivation and its relationship with syndrome of inappropriate antidiuretic hormone secretion after stem cell transplantation in pediatric patients. J Pediatr Hematol Oncol 2014 0.77
80 Exendin-4 regulates GLUT2 expression via the CaMKK/CaMKIV pathway in a pancreatic β-cell line. Metabolism 2010 0.77
81 Interaction of the spectrin-like repeats of alpha-actinin-4 with humanin peptide. Clin Exp Nephrol 2004 0.77
82 Incidence and risk of postherpetic neuralgia after varicella zoster virus infection in hematopoietic cell transplantation recipients: Hokkaido Hematology Study Group. Biol Blood Marrow Transplant 2009 0.77
83 Recurrent childhood anaplastic large cell lymphoma: a retrospective analysis of registered cases in Japan. Br J Haematol 2006 0.77
84 [Retrospective analysis of 157 patients with pediatric Hodgkin lymphoma in Japan: investigation by four pediatric cancer study groups]. Rinsho Ketsueki 2012 0.77
85 A randomized trial of cefozopran versus cefepime as empirical antibiotic treatment of febrile neutropenia in pediatric cancer patients. Pediatr Blood Cancer 2014 0.76
86 WT1 mutation in pediatric patients with acute myeloid leukemia: a report from the Japanese Childhood AML Cooperative Study Group. Int J Hematol 2013 0.76
87 Analysis of Japanese registration from the randomized international trial for childhood anaplastic large cell lymphoma (ALCL99-R1). Rinsho Ketsueki 2014 0.76
88 Regulation of nuclear localization signal-importin α interaction by Ca2+/S100A6. FEBS Lett 2010 0.76
89 Ca(2+) /S100 proteins regulate HCV virus NS5A-FKBP8/FKBP38 interaction and HCV virus RNA replication. Liver Int 2013 0.76
90 Risk factor analysis of bloodstream infection in pediatric patients after hematopoietic stem cell transplantation. J Pediatr Hematol Oncol 2013 0.76
91 Impact of reactivation on the sequelae of multi-system Langerhans cell histiocytosis patients. Pediatr Blood Cancer 2008 0.75
92 Risk factors for tumor lysis syndrome in childhood acute myeloid leukemia treated with a uniform protocol without rasburicase prophylaxis. Leuk Lymphoma 2015 0.75
93 In vitro substrate phosphorylation by Ca²⁺/calmodulin-dependent protein kinase kinase using guanosine-5'-triphosphate as a phosphate donor. BMC Biochem 2012 0.75
94 Outcome in 146 patients with paediatric acute myeloid leukaemia treated according to the AML99 protocol in the period 2003-06 from the Japan Association of Childhood Leukaemia Study. Br J Haematol 2012 0.75
95 Follow-up of pediatric patients treated by IVIG for Langerhans cell histiocytosis (LCH)-related neurodegenerative CNS disease. Int J Hematol 2014 0.75
96 Spontaneous remission of 2-chlorodeoxyadenosine (2-CdA)-related secondary myelodysplastic syndrome in a patient with refractory Langerhans cell histiocytosis. Int J Hematol 2013 0.75
97 [Effectiveness of remission induction with high-dose cytarabine for relapsed or refractory pediatric acute leukemia]. Rinsho Ketsueki 2010 0.75
98 Results of the Japan Association of Childhood Leukemia Study (JACLS) NHL-98 protocol for the treatment of B-cell non-Hodgkin lymphoma and mature B-cell acute lymphoblastic leukemia in childhood. Leuk Lymphoma 2011 0.75
99 [Huge brain abscess and invasive pulmonary disease by fungal infection during chemotherapy for infantile acute myeloid leukemia]. Rinsho Ketsueki 2007 0.75
100 Clinicopathological characteristics of erythroblast-rich RAEB and AML M6a in children. Int J Hematol 2008 0.75
101 Immunosuppressive therapy with horse anti-thymocyte globulin and cyclosporine as treatment for fulminant aplastic anemia in children. Ann Hematol 2013 0.75
102 Precursor-T lymphoblastic lymphoma after unrelated bone marrow transplantation in a patient with Fanconi anemia. J Pediatr Hematol Oncol 2011 0.75
103 Population pharmacokinetic modeling and pharmacodynamic assessment of cefozopran in pediatric patients. Jpn J Antibiot 2009 0.75
104 Higher urinary excretion of inorganic phosphate during early induction chemotherapy predicts a good prognosis in childhood acute leukemia. J Pediatr Hematol Oncol 2011 0.75
105 Clinical Features and Prognosis According to Immunophenotypic Subtypes Including the Early T-Cell Precursor Subtype of T-Lymphoblastic Lymphoma in the Japanese Pediatric Leukemia/Lymphoma Study Group ALB-NHL03 Study. J Pediatr Hematol Oncol 2017 0.75
106 Oxidative Stress Impairs the Stimulatory Effect of S100 Proteins on Protein Phosphatase 5 Activity. Tohoku J Exp Med 2016 0.75
107 Extrarenal Nephroblastoma of the Retroperitoneal Space in Children: A Case Report and Review of the Literature. J Pediatr Hematol Oncol 2017 0.75
108 Long-term Results of the Risk-adapted Treatment for Childhood B-Cell Acute Lymphoblastic Leukemia: Report From the Japan Association of Childhood Leukemia Study ALL-97 Trial. J Pediatr Hematol Oncol 2017 0.75
109 [Acute promyelocytic leukemia after living donor partial orthotopic liver transplantation]. Rinsho Ketsueki 2004 0.75
110 Analysis of Risk Factors for Hyponatremia During or Following Chemotherapy in Children With Cancer: A Hospital-based, Retrospective Cohort Study. J Pediatr Hematol Oncol 2016 0.75
111 Bacteremia during neutropenia is a predictive factor for invasive fungal infection in children. Pediatr Int 2013 0.75
112 The International Immune Tolerance Induction Study and its follow-up study on Japanese hemophilia A patients with inhibitors. Int J Hematol 2015 0.75