Published in N Engl J Med on March 19, 2009
The Adult Hemorrhagic Moyamoya Surgery Study (AHMSS) | NCT02319980
Precision Bypass in Patients With Moyamoya Disease (PBM) | NCT03516851
Silent cerebral infarcts occur despite regular blood transfusion therapy after first strokes in children with sickle cell disease. Blood (2010) 2.15
Homozygous mutation in SAMHD1 gene causes cerebral vasculopathy and early onset stroke. Proc Natl Acad Sci U S A (2011) 1.62
De novo ACTA2 mutation causes a novel syndrome of multisystemic smooth muscle dysfunction. Am J Med Genet A (2010) 1.49
Headache associated with moyamoya disease: a case story and literature review. J Headache Pain (2009) 1.41
Vascular remodeling after ischemic stroke: mechanisms and therapeutic potentials. Prog Neurobiol (2013) 1.33
Intracranial atherosclerotic disease associated with moyamoya collateral formation: histopathological findings. J Neurosurg (2013) 1.14
Placenta growth factor in sickle cell disease: association with hemolysis and inflammation. Blood (2009) 1.13
A rare Asian founder polymorphism of Raptor may explain the high prevalence of Moyamoya disease among East Asians and its low prevalence among Caucasians. Environ Health Prev Med (2009) 1.08
RNF213 rare variants in an ethnically diverse population with Moyamoya disease. Stroke (2014) 1.04
Moyamoya disease-associated protein mysterin/RNF213 is a novel AAA+ ATPase, which dynamically changes its oligomeric state. Sci Rep (2014) 1.04
Molecular analysis of RNF213 gene for moyamoya disease in the Chinese Han population. PLoS One (2012) 1.00
Loss of BRCC3 deubiquitinating enzyme leads to abnormal angiogenesis and is associated with syndromic moyamoya. Am J Hum Genet (2011) 0.99
High-resolution Magnetic Resonance Vessel Wall Imaging for Intracranial Arterial Stenosis. Chin Med J (Engl) (2016) 0.99
Moyamoya disease in children. Childs Nerv Syst (2010) 0.95
Loss of α1β1 soluble guanylate cyclase, the major nitric oxide receptor, leads to moyamoya and achalasia. Am J Hum Genet (2014) 0.94
Ischaemic stroke in young adults: risk factors and long-term consequences. Nat Rev Neurol (2014) 0.93
Whole-brain CT perfusion and CT angiography assessment of Moyamoya disease before and after surgical revascularization: preliminary study with 256-slice CT. PLoS One (2013) 0.93
Resolution of bilateral moyamoya associated collateral vessel aneurysms: Rationale for endovascular versus surgical intervention. Surg Neurol Int (2014) 0.92
Noncontrast mapping of arterial delay and functional connectivity using resting-state functional MRI: a study in Moyamoya patients. J Magn Reson Imaging (2014) 0.91
Pediatric stroke: the importance of cerebral arteriopathy and vascular malformations. Childs Nerv Syst (2010) 0.90
Missing relationship of moyamoya and persistent primitive artery in Europeans. Another distinctive feature or artifact? Surg Radiol Anat (2015) 0.88
Vessel Wall Imaging of the Intracranial and Cervical Carotid Arteries. J Stroke (2015) 0.88
A new horizon of moyamoya disease and associated health risks explored through RNF213. Environ Health Prev Med (2015) 0.86
PWI-MRI and contrast extravasation in brain AVM help to estimate angiogenic activity. Neuroradiology (2011) 0.86
Macrovascular involvement in a child with atypical hemolytic uremic syndrome. Pediatr Nephrol (2013) 0.86
Hemorrhage and risk of further hemorrhagic strokes following cerebral revascularization in Moyamoya disease: A review of the literature. Surg Neurol Int (2012) 0.86
Common genetic polymorphisms in moyamoya and atherosclerotic disease in Europeans. Childs Nerv Syst (2010) 0.85
Research Progress of Moyamoya Disease in Children. Int J Med Sci (2015) 0.84
Cerebral angiopathies as a cause of ischemic stroke in children: differential diagnosis and treatment options. Dtsch Arztebl Int (2010) 0.84
Moyamoya syndrome in an adult with essential thrombocythemia. Neurol Int (2011) 0.84
Adult Moyamoya Disease: A Burden of Intracranial Stenosis in East Asians? PLoS One (2015) 0.84
Disease Variant Landscape of a Large Multiethnic Population of Moyamoya Patients by Exome Sequencing. G3 (Bethesda) (2015) 0.84
Immune response profiling identifies autoantibodies specific to Moyamoya patients. Orphanet J Rare Dis (2013) 0.84
Intracranial stent placement in a patient with moyamoya disease. J Neurol (2011) 0.83
Concurrent stenoocclusive disease of intracranial and extracranial arteries in a patient with polycythemia vera. Case Rep Med (2012) 0.83
Neuroimaging of hemorrhage and vascular defects. Neurotherapeutics (2011) 0.82
Moyamoya syndrome associated with Graves' disease: a case series study. Ann Transl Med (2014) 0.82
Moyamoya disease and moyamoya syndrome. N Engl J Med (2009) 0.82
Electroencephalography in pediatric moyamoya disease: reappraisal of clinical value. Childs Nerv Syst (2013) 0.82
CT perfusion assessment of Moyamoya syndrome before and after direct revascularization (superficial temporal artery to middle cerebral artery bypass). Eur Radiol (2015) 0.81
Moyamoya disease mimicking encephalitis. Iran J Med Sci (2014) 0.80
Atypical presentation of moyamoya disease in an infant with a de novo RNF213 variant. Am J Med Genet A (2015) 0.80
Moyamoya disease and moyamoya syndrome. N Engl J Med (2009) 0.80
Case Report: A case report of Moyamoya disease in a 36 year old African American woman. F1000Res (2014) 0.80
Zebrafish models of cerebrovascular disease. J Cereb Blood Flow Metab (2014) 0.80
Natural history and progression factors of unilateral moyamoya disease in pediatric patients. Childs Nerv Syst (2011) 0.80
Cerebral convexity subarachnoid hemorrhage: various causes and role of diagnostic imaging. Emerg Radiol (2014) 0.79
Elevated thyroid autoantibodies and intracranial stenosis in stroke at an early age. Int J Stroke (2013) 0.79
Postpneumococcal Moyamoya syndrome case report and review of the postinfective cases. BMJ Case Rep (2013) 0.79
Pregnancy outcomes in women with moyamoya disease: experiences at a single center in Korea. Yonsei Med J (2015) 0.79
Disrupted nitric oxide signaling due to GUCY1A3 mutations increases risk for moyamoya disease, achalasia and hypertension. Clin Genet (2016) 0.79
A case with unusual stroke and fulminant outcome in a Hispanic male. Am J Case Rep (2013) 0.79
Histopathological Characteristics of Distal Middle Cerebral Artery in Adult and Pediatric Patients with Moyamoya Disease. Neurol Med Chir (Tokyo) (2016) 0.79
Ischemic and hemorrhagic moyamoya disease in adults: CT findings. Int J Clin Exp Med (2015) 0.78
Moyamoya disease and pregnancy: case reports and criteria for successful vaginal delivery. Clin Case Rep (2015) 0.78
Clinicoepidemiological features of asymptomatic moyamoya disease in adult patients. J Cerebrovasc Endovasc Neurosurg (2014) 0.78
The Pathophysiology of Moyamoya Disease: An Update. J Stroke (2016) 0.78
Rare RNF213 variants in the C-terminal region encompassing the RING-finger domain are associated with moyamoya angiopathy in Caucasians. Eur J Hum Genet (2017) 0.77
Vessel wall imaging for intracranial vascular disease evaluation. J Neurointerv Surg (2016) 0.77
Cerebrovascular autoregulation in pediatric moyamoya disease. Paediatr Anaesth (2013) 0.77
Prospective screening of family members with moyamoya disease patients. PLoS One (2014) 0.77
1H-NMR-based metabolomic analysis of cerebrospinal fluid from adult bilateral moyamoya disease: comparison with unilateral moyamoya disease and atherosclerotic stenosis. Medicine (Baltimore) (2015) 0.76
Down syndrome and the molecular pathogenesis resulting from trisomy of human chromosome 21. J Biomed Res (2010) 0.76
Moyamoya syndrome causing stroke in young women with type 1 diabetes. J Diabetes Complications (2016) 0.76
Variant angina in moyamoya disease--a correlative etiology and different presentation: a case report. J Med Case Rep (2015) 0.76
Cerebral-perfusion-based single-photon emission computed tomography (SPECT) staging using NeuroGam® in patients with moyamoya disease. Childs Nerv Syst (2015) 0.76
Cerebrovascular collaterals correlate with disease severity in adult North American patients with Moyamoya disease. AJNR Am J Neuroradiol (2014) 0.76
Role of CT perfusion imaging in evaluating the effects of multiple burr hole surgery on adult ischemic Moyamoya disease. Neuroradiology (2013) 0.76
Moyamoya Biomarkers. J Korean Neurosurg Soc (2015) 0.76
Protein S Deficiency and an Adult Case with Moyamoya Syndrome that Presented with Primary Intraventricular Haemorrhage. Balkan Med J (2014) 0.76
A comment on "Contralateral cerebral hemodynamic changes after unilateral direct revascularization in patients with moyamoya disease". Neurosurg Rev (2011) 0.76
Frequency of RNF213 p.R4810K, a susceptibility variant for moyamoya disease, and health characteristics of carriers in the Japanese population. Environ Health Prev Med (2016) 0.76
Moyamoya disease in pregnancy and delivery planning: A case series and literature review. Obstet Med (2016) 0.75
Symptomatic intracranial arterial disease: incidence, natural history, diagnosis, and management. Neurosurg Focus (2011) 0.75
Angiogenesis in steno-occlusive vasculopathies as a common pathway for intracranial haemorrhage. A report of six cases. Interv Neuroradiol (2014) 0.75
One sided bypass for bilateral Moyamoya disease, a case report and review of the literatures. Int J Surg Case Rep (2016) 0.75
The Contrast Enhancement of Intracranial Arterial Wall on High-resolution MRI and Its Clinical Relevance in Patients with Moyamoya Vasculopathy. Sci Rep (2017) 0.75
Added Value of Vessel Wall Magnetic Resonance Imaging in the Differentiation of Moyamoya Vasculopathies in a Non-Asian Cohort. Stroke (2016) 0.75
Ocular Features and Visual Outcome in Children with Moyamoya Disease and Moyamoya Syndrome: A Case Series. J Clin Diagn Res (2016) 0.75
Neurocognitive Dysfunction According to Hypoperfusion Territory in Patients With Moyamoya Disease. Ann Rehabil Med (2017) 0.75
Adult moyamoya disease in an urban center in the United States is associated with a high burden of watershed ischemia. J Am Heart Assoc (2014) 0.75
Aggressive blood pressure control for chronic kidney disease unmasks moyamoya! Clin Kidney J (2013) 0.75
Moyamoya syndrome in a known case of pulmonary tuberculosis. J Neurosci Rural Pract (2010) 0.75
Moyamoya syndrome in sickle cell anaemia: a cause of recurrent stroke. BMJ Case Rep (2014) 0.75
Moyamoya disease involving anterior and posterior circulation. J Pediatr Neurosci (2017) 0.75
Bilateral Moyamoya Disease in a 2-Year-Old Pakistani Male Treated with Bilateral Encephaloduroarteriosynangiosis: A Positive Outcome. Case Rep Neurol Med (2016) 0.75
Role of Ring Finger Protein 213 in Moyamoya Disease. Chin Med J (Engl) (2016) 0.75
Moyamoya in Hispanics: not Only in Japanese. Neurol Int (2014) 0.75
Characterization of inpatient moyamoya in the United States: 1988-2004. Front Neurol (2011) 0.75
CO2BOLD assessment of moyamoya syndrome: Validation with single photon emission computed tomography and positron emission tomography imaging. World J Radiol (2016) 0.75
Clinical and angiographic findings in Moya Moya. Am J Case Rep (2014) 0.75
Incidence and long-term outcome of postradiotherapy moyamoya syndrome in pediatric patients with primary brain tumors: a single institute experience in Taiwan. Cancer Med (2016) 0.75
Moyamoya Syndrome Associated with Henoch-Schönlein Purpura. Iran J Child Neurol (2016) 0.75
RNF213 Is Associated with Intracranial Aneurysms in the French-Canadian Population. Am J Hum Genet (2016) 0.75
Non-aneurysmal subarachnoid hemorrhage as presentation of moyamoya disease in an adult. Surg Neurol Int (2011) 0.75
Hemiplegic migraine: An atypical presentation of Moyamoya disease. Saudi J Anaesth (2014) 0.75
Moyamoya disease, revascularisation surgery and anaesthetic considerations. BMJ Case Rep (2014) 0.75
Moyamoya Disease with Coexistent Hypertriglyceridemia in Pediatric Patient. Case Rep Endocrinol (2016) 0.75
Occult moyamoya disease causing fulminant infarction after septorhinoplasty. Case Reports Plast Surg Hand Surg (2014) 0.75
Preliminary study of neurocognitive dysfunction in adult moyamoya disease and improvement after superficial temporal artery-middle cerebral artery bypass. J Korean Neurosurg Soc (2014) 0.75
Traumatic pericallosal artery aneurysm: a rare complication of transcallosal surgery. Case report. J Neurosurg (2007) 1.61
Wound complications associated with the use of bovine serum albumin-glutaraldehyde surgical adhesive in pediatric patients. Neurosurgery (2007) 1.47
Fetuin-A is an independent determinant of change of aortic stiffness over 1 year in non-diabetic patients with CKD stages 3 and 4. Nephrol Dial Transplant (2010) 1.39
Moyamoya syndrome associated with Down syndrome: outcome after surgical revascularization. Pediatrics (2005) 1.21
Moyamoya syndrome associated with neurofibromatosis Type 1: perioperative and long-term outcome after surgical revascularization. J Neurosurg Pediatr (2013) 1.12
The value of urinary neutrophil gelatinase-associated lipocalin in risk prediction of renal decline in patients with chronic kidney disease. Kidney Int (2013) 1.09
Tethered cord syndrome. Neurosurg Clin N Am (2007) 1.05
Pial arteriovenous fistulae in pediatric patients: associated syndromes and treatment outcome. J Neurointerv Surg (2012) 0.99
Acute clival and spinal subdural hematoma with spontaneous resolution: clinical and radiographic correlation in support of a proposed pathophysiological mechanism. Case report. J Neurosurg (2005) 0.93
FGF-23 and osteoprotegerin are independently associated with myocardial damage in chronic kidney disease stages 3 and 4. Another link between chronic kidney disease-mineral bone disorder and the heart. Nephrol Dial Transplant (2011) 0.91
Foramen magnum stenosis from overgrowth of the opisthion in a child with achondroplasia. J Neurosurg Pediatr (2008) 0.89
Method-specific differences in plasma fibroblast growth factor 23 measurement using four commercial ELISAs. Clin Chem Lab Med (2013) 0.88
Seckel syndrome and moyamoya. J Neurosurg Pediatr (2009) 0.88
Vertebra plana due to an aneurysmal bone cyst of the lumbar spine. Case report and review of the literature. J Neurosurg (2006) 0.88
Sickle Cell Disease. N Engl J Med (2017) 0.86
Idiopathic syrinx in the pediatric population: a combined center experience. J Neurosurg Pediatr (2011) 0.86
Intraoperative anaphylaxis induced by the gelatin component of thrombin-soaked gelfoam in a pediatric patient. Ann Allergy Asthma Immunol (2012) 0.85
Resection of supratentorial lobar cavernous malformations in children: clinical article.. J Neurosurg Pediatr (2013) 0.84
Moyamoya disease in children with congenital dwarfing conditions. Pediatr Neurosurg (2011) 0.84
Important differences in measurement of fetuin-A. Ann Intern Med (2010) 0.83
Primary gastrointestinal cancers presenting as gynecologic malignancies. Gynecol Oncol (2004) 0.82
Angioarchitectural features associated with hemorrhagic presentation in pediatric cerebral arteriovenous malformations. J Neurointerv Surg (2012) 0.82
Discovery of asymptomatic moyamoya arteriopathy in pediatric syndromic populations: radiographic and clinical progression. Neurosurg Focus (2011) 0.81
Acute hydrocephalus secondary to obstruction of the foramen of monro and cerebral aqueduct caused by a choroid plexus cyst in the lateral ventricle. Case report. J Neurosurg (2007) 0.81
Surviving collapsed structure entrapment after earthquakes: a "time-to-rescue" analysis. Prehosp Disaster Med (2006) 0.81
The importance of klotho in phosphate metabolism and kidney disease. Nephrology (Carlton) (2014) 0.79
Pial synangiosis in patients with moyamoya younger than 2 years of age. J Neurosurg Pediatr (2014) 0.79
Chorea in the clinical presentation of moyamoya disease: results of surgical revascularization and a proposed clinicopathological correlation. J Neurosurg Pediatr (2013) 0.78
Pediatric brain tumors. Adv Pediatr (2009) 0.78
Introduction: moyamoya disease. Neurosurg Focus (2009) 0.78
Lumbar intramedullary spinal schistosomiasis presenting as progressive paraparesis: case report. Neurosurgery (2006) 0.78
Fetuin-A-containing calciprotein particle levels can be reduced by dialysis, sodium thiosulphate and plasma exchange. Potential therapeutic implications for calciphylaxis? Nephrology (Carlton) (2013) 0.77
Use of tranexamic acid in infants undergoing choroid plexus papilloma surgery: a report of two cases. Paediatr Anaesth (2014) 0.77
Multiple pilocytic astrocytomas of the cerebellum in a 17-year-old patient with neurofibromatosis type I. Childs Nerv Syst (2007) 0.77
Visual Field Loss in a Case of Recurrent Cystic Craniopharyngioma During Concomitant Treatment With Pegylated Interferon α-2b. J Pediatr Hematol Oncol (2016) 0.77
Moyamoya disease with mesial temporal sclerosis. J Neurosurg Pediatr (2013) 0.76
Relative abundance of fetuin- A in peritoneal dialysis effluent and its association with in situ formation of calciprotein particles: an observational pilot study. Nephrology (Carlton) (2015) 0.76
Dural arteriovenous fistulae in pediatric patients: associated conditions and treatment outcomes. J Neurointerv Surg (2012) 0.76
Predictors of neoplastic disease in children with isolated pituitary stalk thickening. Pediatr Blood Cancer (2013) 0.76
Identification of an association between Robinow syndrome and moyamoya. Pediatr Neurosurg (2009) 0.76
Dural scalp and intracranial hemangiomas causing hydrocephalus and venous sinus thrombosis in an infant. J Child Neurol (2011) 0.76
Intracranial aneurysms in the youngest patients: characteristics and treatment challenges. Pediatr Neurosurg (2015) 0.76
Analytical considerations in the investigation of mixed cryoglobulinemia. Clin Chem (2009) 0.75
Factors associated with increasing vascular stiffness in PD. Nephrol Dial Transplant (2011) 0.75
FGF23 adds value to risk prediction in patients with chronic kidney disease. Bone (2012) 0.75
Vascular collateralization along ventriculoperitoneal shunt catheters in moyamoya disease. J Neurosurg Pediatr (2013) 0.75
A rare case of psammomatoid ossifying fibroma in the sphenoid bone reconstructed using autologous particulate exchange cranioplasty. J Neurosurg Pediatr (2011) 0.75
913 Moyamoya Associated with Down Syndrome: Outcome after Surgical Revascularization. Neurosurgery (2005) 0.75
Features of the lumbar spine on magnetic resonance images following sectioning of filum terminale. J Neurosurg Pediatr (2011) 0.75
Treatment of Moyamoya disease in the adult population with pial synangiosis. J Neurosurg (2014) 0.75
Intracranial vasospasm with subsequent stroke after traumatic subarachnoid hemorrhage in a 22-month-old child. J Neurosurg Pediatr (2009) 0.75
Assessing the utility of testing aluminum levels in dialysis patients. Hemodial Int (2014) 0.75
Microsurgical treatment of arteriovenous malformations in pediatric patients: the Boston Children's Hospital experience. J Neurosurg Pediatr (2015) 0.75
Cavernous malformations of the basal ganglia in children. J Neurosurg Pediatr (2013) 0.75
Imaging after direct and indirect extracranial-intracranial bypass surgery. AJR Am J Roentgenol (2013) 0.75
A novel TP53 germline mutation in a family with a history of multiple malignancies: case report and review of the literature. Pediatr Neurosurg (2009) 0.75
Occipital pial synangiosis. Acta Neurochir (Wien) (2014) 0.75
Benign triton tumor: multidisciplinary approach to diagnosis and treatment. Pediatr Dev Pathol (2014) 0.75
Management of atypical glandular cells of undetermined significance pap smears: a reappraisal. J Low Genit Tract Dis (2003) 0.75
Real-Time Ultrasound-Guided Catheter Navigation for Approaching Deep-Seated Brain Lesions: Role of Intraoperative Neurosonography with and without Fusion with Magnetic Resonance Imaging. Pediatr Neurosurg (2017) 0.75
Measurement of endometrial stripe thickness by obstetrics and gynecology residents. Am J Obstet Gynecol (2005) 0.75
Incidentally discovered lesions. Neurosurg Focus (2011) 0.75
Hyperparathyroidism in chronic kidney disease: complexities within the commonplace. Clin Med (2012) 0.75
Qualitative and quantitative analysis of fibrosis in the kidney. Nephrology (Carlton) (2014) 0.75
Preface: introduction to pediatric vascular neurosurgery. Neurosurg Clin N Am (2010) 0.75