Published in J Biol Chem on March 15, 1990
Structural, functional, and evolutionary relationships among extracellular solute-binding receptors of bacteria. Microbiol Rev (1993) 5.36
A phosphorylated cytoplasmic autoantigen, GW182, associates with a unique population of human mRNAs within novel cytoplasmic speckles. Mol Biol Cell (2002) 5.34
Genetic analysis of an MDR-like export system: the secretion of colicin V. EMBO J (1990) 2.71
A P-glycoprotein homologue of Plasmodium falciparum is localized on the digestive vacuole. J Cell Biol (1991) 2.68
Genetic transformation in Streptococcus pneumoniae: nucleotide sequence analysis shows comA, a gene required for competence induction, to be a member of the bacterial ATP-dependent transport protein family. J Bacteriol (1991) 2.36
Giant peroxisomes in oleic acid-induced Saccharomyces cerevisiae lacking the peroxisomal membrane protein Pmp27p. J Cell Biol (1995) 2.30
PAS3, a Saccharomyces cerevisiae gene encoding a peroxisomal integral membrane protein essential for peroxisome biogenesis. J Cell Biol (1991) 2.22
Heavy metal tolerance in the fission yeast requires an ATP-binding cassette-type vacuolar membrane transporter. EMBO J (1992) 2.19
PEX19 binds multiple peroxisomal membrane proteins, is predominantly cytoplasmic, and is required for peroxisome membrane synthesis. J Cell Biol (2000) 2.07
Import of proteins into peroxisomes and other microbodies. Biochem J (1992) 1.94
The sorting sequence of the peroxisomal integral membrane protein PMP47 is contained within a short hydrophilic loop. J Cell Biol (1996) 1.71
Association of glyoxylate and beta-oxidation enzymes with peroxisomes of Saccharomyces cerevisiae. J Bacteriol (1990) 1.70
Ascorbate peroxidase. A prominent membrane protein in oilseed glyoxysomes. Plant Physiol (1996) 1.58
Visualization of the peroxisomal compartment in living mammalian cells: dynamic behavior and association with microtubules. J Cell Biol (1997) 1.56
An ABC transporter in the mitochondrial inner membrane is required for normal growth of yeast. EMBO J (1995) 1.51
Human peroxisomal targeting signal-1 receptor restores peroxisomal protein import in cells from patients with fatal peroxisomal disorders. J Cell Biol (1995) 1.45
Brain endothelial dysfunction in cerebral adrenoleukodystrophy. Brain (2015) 1.42
ATP binding cassette transporter G1 (ABCG1) is an intracellular sterol transporter. Proc Natl Acad Sci U S A (2011) 1.41
Two putative subunits of a peptide pump encoded in the human major histocompatibility complex class II region. Proc Natl Acad Sci U S A (1991) 1.40
A close relative of the adrenoleukodystrophy (ALD) gene codes for a peroxisomal protein with a specific expression pattern. Proc Natl Acad Sci U S A (1996) 1.39
Transport of microinjected proteins into peroxisomes of mammalian cells: inability of Zellweger cell lines to import proteins with the SKL tripeptide peroxisomal targeting signal. Mol Cell Biol (1992) 1.39
Involvement of 70-kD heat-shock proteins in peroxisomal import. J Cell Biol (1994) 1.34
Cloning of the cDNA for a human homologue of the Drosophila white gene and mapping to chromosome 21q22.3. Am J Hum Genet (1996) 1.32
Identification of PEX10, the gene defective in complementation group 7 of the peroxisome-biogenesis disorders. Am J Hum Genet (1998) 1.31
An internal region of the peroxisomal membrane protein PMP47 is essential for sorting to peroxisomes. J Cell Biol (1994) 1.26
PXA1, a possible Saccharomyces cerevisiae ortholog of the human adrenoleukodystrophy gene. Proc Natl Acad Sci U S A (1995) 1.22
A Saccharomyces cerevisiae homolog of the human adrenoleukodystrophy transporter is a heterodimer of two half ATP-binding cassette transporters. Proc Natl Acad Sci U S A (1996) 1.22
Identification and characterization of the type-IVA cyclic AMP-specific phosphodiesterase RD1 as a membrane-bound protein expressed in cerebellum. Biochem J (1995) 1.17
Mammalian peroxisomal ABC transporters: from endogenous substrates to pathology and clinical significance. Br J Pharmacol (2011) 1.13
Spectrum of mutations in the gene encoding the adrenoleukodystrophy protein. Am J Hum Genet (1995) 1.13
Identification and characterization of the human orthologue of yeast Pex14p. Mol Cell Biol (1999) 1.12
The absence of Pmp47, a putative yeast peroxisomal transporter, causes a defect in transport and folding of a specific matrix enzyme. J Cell Biol (1996) 1.10
Presence of cytoplasmic factors functional in peroxisomal protein import implicates organelle-associated defects in several human peroxisomal disorders. J Clin Invest (1993) 1.10
Pathophysiology of X-linked adrenoleukodystrophy. Biochimie (2013) 1.09
Transport of microinjected alcohol oxidase from Pichia pastoris into vesicles in mammalian cells: involvement of the peroxisomal targeting signal. J Cell Biol (1992) 1.08
Biogenesis of peroxisomes: isolation and characterization of two distinct peroxisomal populations from normal and regenerating rat liver. J Cell Biol (1993) 1.08
In vitro insertion of the 22-kD peroxisomal membrane protein into isolated rat liver peroxisomes. J Cell Biol (1993) 1.06
The peroxisomal ABC transporter family. Pflugers Arch (2006) 1.05
Fibrates induce mdr2 gene expression and biliary phospholipid secretion in the mouse. Biochem J (1996) 1.04
Gemfibrozil, stretching arms beyond lipid lowering. Immunopharmacol Immunotoxicol (2009) 1.03
Mutational and protein analysis of patients and heterozygous women with X-linked adrenoleukodystrophy. Am J Hum Genet (1996) 0.97
The PAL1 gene product is a peroxisomal ATP-binding cassette transporter in the yeast Saccharomyces cerevisiae. J Cell Biol (1996) 0.96
The Arabidopsis peroxisomal ABC transporter, comatose, complements the Saccharomyces cerevisiae pxa1 pxa2Delta mutant for metabolism of long-chain fatty acids and exhibits fatty acyl-CoA-stimulated ATPase activity. J Biol Chem (2010) 0.96
Phenylbutyrate up-regulates the adrenoleukodystrophy-related gene as a nonclassical peroxisome proliferator. J Cell Biol (2005) 0.93
Identification of mutations in the putative ATP-binding domain of the adrenoleukodystrophy gene. J Clin Invest (1994) 0.92
Impaired very long-chain acyl-CoA β-oxidation in human X-linked adrenoleukodystrophy fibroblasts is a direct consequence of ABCD1 transporter dysfunction. J Biol Chem (2013) 0.90
PEX13 is mutated in complementation group 13 of the peroxisome-biogenesis disorders. Am J Hum Genet (1999) 0.90
Molecular cloning of a peroxisomal Ca2+-dependent member of the mitochondrial carrier superfamily. Proc Natl Acad Sci U S A (1997) 0.88
Peroxisome assembly factor 1: nonsense mutation in a peroxisome-deficient Chinese hamster ovary cell mutant and deletion analysis. Mol Cell Biol (1994) 0.88
Lovastatin does not correct the accumulation of very long-chain fatty acids in tissues of adrenoleukodystrophy protein-deficient mice. J Inherit Metab Dis (2000) 0.87
Monomeric inducible nitric oxide synthase localizes to peroxisomes in hepatocytes. Proc Natl Acad Sci U S A (2005) 0.85
Substrate specificity overlap and interaction between adrenoleukodystrophy protein (ALDP/ABCD1) and adrenoleukodystrophy-related protein (ALDRP/ABCD2). J Biol Chem (2011) 0.84
Peroxisomal dysfunction in inflammatory childhood white matter disorders: an unexpected contributor to neuropathology. J Child Neurol (2009) 0.82
Peroxisomal ABC transporters: functions and mechanism. Biochem Soc Trans (2015) 0.82
Identification of a new fatty acid synthesis-transport machinery at the peroxisomal membrane. J Biol Chem (2011) 0.81
Structure-function analysis of peroxisomal ATP-binding cassette transporters using chimeric dimers. J Biol Chem (2014) 0.80
Demonstration and characterization of phosphate transport in mammalian peroxisomes. Biochem J (2005) 0.80
Identification of a substrate-binding site in a peroxisomal beta-oxidation enzyme by photoaffinity labeling with a novel palmitoyl derivative. J Biol Chem (2010) 0.79
ABCD1 deletion-induced mitochondrial dysfunction is corrected by SAHA: implication for adrenoleukodystrophy. J Neurochem (2015) 0.79
A missense point mutation (Ser515Phe) in the adrenoleukodystrophy gene in a family with adrenomyeloneuropathy: a clinical, biochemical, and genetic study. J Neurol Neurosurg Psychiatry (1995) 0.79
Absence of mutations raises doubts about the role of the 70-kD peroxisomal membrane protein in Zellweger syndrome. Am J Hum Genet (1997) 0.77
Induction of the major integral membrane protein of mouse liver peroxisomes by peroxisome proliferators. Biochem J (1992) 0.77
Translocation of the ABC transporter ABCD4 from the endoplasmic reticulum to lysosomes requires the escort protein LMBD1. Sci Rep (2016) 0.76
ABC Transporter Subfamily D: Distinct Differences in Behavior between ABCD1-3 and ABCD4 in Subcellular Localization, Function, and Human Disease. Biomed Res Int (2016) 0.75
Identification and Characterization of a Large Protein Essential for Degradation of the Crystalline Region of Cellulose by Cytophaga hutchinsonii. Appl Environ Microbiol (2016) 0.75
Clinical or ATPase domain mutations in ABCD4 disrupt the interaction between the vitamin B12-trafficking proteins ABCD4 and LMBD1. J Biol Chem (2017) 0.75
Predictive Structure and Topology of Peroxisomal ATP-Binding Cassette (ABC) Transporters. Int J Mol Sci (2017) 0.75
DNA diagnosis of X-linked adrenoleukodystrophy. J Inherit Metab Dis (1995) 0.75
Brefeldin A causes disassembly of the Golgi complex and accumulation of secretory proteins in the endoplasmic reticulum. J Biol Chem (1988) 5.18
Internal tandem duplication of the flt3 gene found in acute myeloid leukemia. Leukemia (1996) 5.06
High glucose level and free fatty acid stimulate reactive oxygen species production through protein kinase C--dependent activation of NAD(P)H oxidase in cultured vascular cells. Diabetes (2000) 4.55
Cloning and sequencing of two tandem genes involved in degradation of 2,3-dihydroxybiphenyl to benzoic acid in the polychlorinated biphenyl-degrading soil bacterium Pseudomonas sp. strain KKS102. J Bacteriol (1989) 3.83
Altered constitutive expression of fatty acid-metabolizing enzymes in mice lacking the peroxisome proliferator-activated receptor alpha (PPARalpha). J Biol Chem (1998) 3.78
A simple method to estimate populational 24-h urinary sodium and potassium excretion using a casual urine specimen. J Hum Hypertens (2002) 3.67
Peroxisomal beta-oxidation and peroxisome proliferator-activated receptor alpha: an adaptive metabolic system. Annu Rev Nutr (2001) 3.54
Prognostic implication of FLT3 and N-RAS gene mutations in acute myeloid leukemia. Blood (1999) 3.46
Treatment of advanced Parkinson's disease by posterior GPi pallidotomy: 1-year results of a pilot study. Ann Neurol (1996) 3.45
Autophagosome requires specific early Sec proteins for its formation and NSF/SNARE for vacuolar fusion. Mol Biol Cell (2001) 3.41
Etiology of community-acquired pneumonia in hospitalized patients: a 3-year prospective study in Japan. Chest (1998) 3.15
Ribosomal RNA trees misleading? Nature (1993) 3.04
Structural analysis of cDNA for rat peroxisomal 3-ketoacyl-CoA thiolase. J Biol Chem (1987) 2.72
Inositol 1,4,5-trisphosphate releases Ca2+ from intracellular store sites in skinned single cells of porcine coronary artery. Biochem Biophys Res Commun (1984) 2.71
Amino-terminal presequence of the precursor of peroxisomal 3-ketoacyl-CoA thiolase is a cleavable signal peptide for peroxisomal targeting. Biochem Biophys Res Commun (1991) 2.71
Electron microscopic observations on the penetration of Bdellovibrio bacteriovorus into gram-negative bacterial hosts. J Bacteriol (1968) 2.57
Transcription regulation of peroxisomal fatty acyl-CoA oxidase and enoyl-CoA hydratase/3-hydroxyacyl-CoA dehydrogenase in rat liver by peroxisome proliferators. Proc Natl Acad Sci U S A (1986) 2.57
Complete nucleotide sequence of cDNA and predicted amino acid sequence of rat acyl-CoA oxidase. J Biol Chem (1987) 2.51
Internal tandem duplication of the FLT3 gene is a novel modality of elongation mutation which causes constitutive activation of the product. Leukemia (1998) 2.35
Directed disruption of the tobacco ndhB gene impairs cyclic electron flow around photosystem I. Proc Natl Acad Sci U S A (1998) 2.34
Peroxisome targeting signal of rat liver acyl-coenzyme A oxidase resides at the carboxy terminus. Mol Cell Biol (1989) 2.33
Heme mediates derepression of Maf recognition element through direct binding to transcription repressor Bach1. EMBO J (2001) 2.32
Microelectrode-guided pallidotomy: technical approach and its application in medically intractable Parkinson's disease. J Neurosurg (1998) 2.31
Characterization of autoantibodies in pemphigus using antigen-specific enzyme-linked immunosorbent assays with baculovirus-expressed recombinant desmogleins. J Immunol (1997) 2.31
Tumor necrosis factor provokes superoxide anion generation from neutrophils. Biochem Biophys Res Commun (1986) 2.27
A unified nomenclature for peroxisome biogenesis factors. J Cell Biol (1996) 2.25
Acetabular dysplasia and hip osteoarthritis in Britain and Japan. Br J Rheumatol (1998) 2.22
The mechanism of respiratory failure in paraneoplastic pemphigus. N Engl J Med (1999) 2.21
Inositol 1,4,5-trisphosphate activates pharmacomechanical coupling in smooth muscle of the rabbit mesenteric artery. J Physiol (1986) 2.20
Complete nucleotide sequence of cDNA and deduced amino acid sequence of rat liver catalase. Proc Natl Acad Sci U S A (1986) 2.15
Molecular cloning and nucleotide sequence of the cDNA for rat peroxisomal enoyl-CoA: hydratase-3-hydroxyacyl-CoA dehydrogenase bifunctional enzyme. J Biol Chem (1985) 2.12
Regulation of lactose permease activity by the phosphoenolpyruvate:sugar phosphotransferase system: evidence for direct binding of the glucose-specific enzyme III to the lactose permease. Proc Natl Acad Sci U S A (1982) 2.09
Comparison of various submucosal injection solutions for maintaining mucosal elevation during endoscopic mucosal resection. Endoscopy (2004) 2.08
Slow N-acetyltransferase 2 genotype affects the incidence of isoniazid and rifampicin-induced hepatotoxicity. Int J Tuberc Lung Dis (2000) 2.07
Anterior decompression and stabilization with the Kaneda device for thoracolumbar burst fractures associated with neurological deficits. J Bone Joint Surg Am (1997) 2.06
Facultatively parasitic strain of Bdellovibrio bacteriovorus. J Bacteriol (1970) 2.05
Apparent response of subacute sclerosing panencephalitis to intrathecal interferon alpha. Ann Neurol (1991) 2.03
Molecular cloning of hyoscyamine 6 beta-hydroxylase, a 2-oxoglutarate-dependent dioxygenase, from cultured roots of Hyoscyamus niger. J Biol Chem (1991) 2.03
Phosphoglucomutase. II. Preparation and properties of phosphoglucomutases from Micrococcuus lysodeikticus and Bacillus cereus. J Biol Chem (1966) 2.00
Molecular mechanisms contributing to dendritic spine alterations in the prefrontal cortex of subjects with schizophrenia. Mol Psychiatry (2006) 1.99
Agr, an Agravitropic locus of Arabidopsis thaliana, encodes a novel membrane-protein family member. Plant Cell Physiol (1998) 1.98
Human peroxisomal 3-oxoacyl-coenzyme A thiolase deficiency. Proc Natl Acad Sci U S A (1987) 1.98
Novel fatty acid beta-oxidation enzymes in rat liver mitochondria. I. Purification and properties of very-long-chain acyl-coenzyme A dehydrogenase. J Biol Chem (1992) 1.97
Successful nonsurgical management of perforation complicating endoscopic submucosal dissection of gastrointestinal epithelial neoplasms. Endoscopy (2006) 1.97
The SPIRAL genes are required for directional control of cell elongation in Aarabidopsis thaliana. Development (2000) 1.95
A role for inositol 1,4,5-trisphosphate in the initiation of agonist-induced contractions of dog tracheal smooth muscle. Br J Pharmacol (1985) 1.94
Characterization of a novel acidic protein of 38 kDa, A0, in yeast ribosomes which immunologically cross-reacts with the 13 kDa acidic ribosomal proteins, A1/A2. J Biochem (1987) 1.93
Release of Ca2+ from a non-mitochondrial store site in peritoneal macrophages treated with saponin by inositol 1,4,5-trisphosphate. Biochem J (1984) 1.92
Demonstration of mother-to-infant transmission of hepatitis B virus by means of polymerase chain reaction. Lancet (1989) 1.90
A human alpha-fetoprotein enhancer-binding protein, ATBF1, contains four homeodomains and seventeen zinc fingers. Mol Cell Biol (1991) 1.89
Isolation of temperature-sensitive mutants of R plasmid by in vitro mutagenesis with hydroxylamine. J Bacteriol (1976) 1.86
Adjacent-segment morbidity after Graf ligamentoplasty compared with posterolateral lumbar fusion. J Neurosurg (2001) 1.86
Biosynthesis and intracellular transport of enzymes of peroxisomal beta-oxidation. J Biol Chem (1984) 1.85
Multiplex PCR using internal transcribed spacer 1 and 2 regions for rapid detection and identification of yeast strains. J Clin Microbiol (2001) 1.79
A novel disease with deficiency of mitochondrial very-long-chain acyl-CoA dehydrogenase. Biochem Biophys Res Commun (1993) 1.74
Protocadherins: a large family of cadherin-related molecules in central nervous system. EMBO J (1993) 1.72
Prognostic implications of fibrotic focus (scar) in small peripheral lung cancers. Am J Surg Pathol (1980) 1.72
Purification and initial characterization of a protein which facilitates assembly of nucleosome-like structure from mammalian cells. Eur J Biochem (1984) 1.71
Isolation and characterization of Chinese hamster ovary cell mutants defective in assembly of peroxisomes. J Cell Biol (1990) 1.71
Purification and properties of acyl-CoA oxidase from rat liver. J Biochem (1980) 1.70
The treatment of osteoporotic-posttraumatic vertebral collapse using the Kaneda device and a bioactive ceramic vertebral prosthesis. Spine (Phila Pa 1976) (1992) 1.69
Abnormal regional cerebral blood flow in childhood autism. Brain (2000) 1.69
Ultrastructure and cell division of a facultatively parasitic strain of Bdellovibrio bacteriovorus. J Bacteriol (1970) 1.68
Molecular basis of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency: identification of the major disease-causing mutation in the alpha-subunit of the mitochondrial trifunctional protein. Biochim Biophys Acta (1994) 1.68
Structure and regulation of rat long-chain acyl-CoA synthetase. J Biol Chem (1990) 1.68
Hemiballism with hyperglycemia and striatal T1-MRI hyperintensity: an autopsy report. Mov Disord (2001) 1.67
Internal tandem duplication of FLT3 associated with leukocytosis in acute promyelocytic leukemia. Leukemia Study Group of the Ministry of Health and Welfare (Kohseisho). Leukemia (1997) 1.66
Neuronal activity in the basal ganglia in patients with generalized dystonia and hemiballismus. Ann Neurol (1999) 1.64
Deoxyribonucleic acid analyses of five families with familial inherited thyroid stimulating hormone deficiency. J Clin Endocrinol Metab (1990) 1.64
Purification and properties of carnitine octanoyltransferase and carnitine palmitoyltransferase from rat liver. J Biochem (1983) 1.64
Reversal of anemia by erythropoietin therapy retards the progression of chronic renal failure, especially in nondiabetic patients. Nephron (1997) 1.63
Absorption of pathogenic autoantibodies by the extracellular domain of pemphigus vulgaris antigen (Dsg3) produced by baculovirus. J Clin Invest (1994) 1.62
Cholesterol granuloma in the petrous apex: case report and review. Acta Neurochir (Wien) (2001) 1.61
Novel fatty acid beta-oxidation enzymes in rat liver mitochondria. II. Purification and properties of enoyl-coenzyme A (CoA) hydratase/3-hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase trifunctional protein. J Biol Chem (1992) 1.61
Association between genetic variants of mast-cell chymase and eczema. Lancet (1996) 1.57
Clinical and immunological profiles of 25 patients with pemphigoid gestationis. Br J Dermatol (2014) 1.57
Different mixtures of sodium hyaluronate and their ability to create submucosal fluid cushions for endoscopic mucosal resection. Endoscopy (2004) 1.56
Gene expression in tobacco low-nicotine mutants. Plant Cell (1994) 1.54
Isolation and characterization of the rodlet layer of Trichophyton mentagrophytes microconidial wall. J Bacteriol (1976) 1.54
Peroxisome targeting signal type 1 (PTS1) receptor is involved in import of both PTS1 and PTS2: studies with PEX5-defective CHO cell mutants. Mol Cell Biol (1998) 1.53
Usefulness of enzyme-linked immunosorbent assay using recombinant desmogleins 1 and 3 for serodiagnosis of pemphigus. Br J Dermatol (1999) 1.52
Two cis-acting regulatory sequences in the peroxisome proliferator-responsive enhancer region of rat acyl-CoA oxidase gene. Biochem Biophys Res Commun (1991) 1.51
Peroxisomal beta oxidation system of rat liver. Copurification of enoyl-CoA hydratase and 3-hydroxyacyl-CoA dehydrogenase. Biochem Biophys Res Commun (1979) 1.50
Acute disseminated encephalomyelitis associated with poliomyelitis vaccine. Pediatr Neurol (2000) 1.50
Transcatheter oily chemoembolization of hepatocellular carcinoma. Radiology (1989) 1.49
Interactions between collagen-binding stress protein HSP47 and collagen. Analysis of kinetic parameters by surface plasmon resonance biosensor. J Biol Chem (1994) 1.48
Absence of myocardial 123I-BMIPP uptake in the presence of a normal coronary angiogram and normokinetics on a left ventriculogram. Jpn Circ J (1997) 1.48
Clinical features of haemophagocytic syndrome in patients with systemic autoimmune diseases: analysis of 30 cases. Rheumatology (Oxford) (2008) 1.48
Purification and properties of rat liver acyl-CoA dehydrogenases and electron transfer flavoprotein. J Biochem (1981) 1.48
MR appearance of Virchow-Robin spaces along lenticulostriate arteries: spin-echo and two-dimensional fast low-angle shot imaging. AJNR Am J Neuroradiol (1994) 1.48
Antigen-specific immunoadsorption of pathogenic autoantibodies in pemphigus foliaceus. J Invest Dermatol (1995) 1.47