Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease.

PubWeight™: 5.03‹?› | Rank: Top 1%

🔗 View Article (PMC 2759336)

Published in Brain on September 22, 2009

Authors

I Zerr1, K Kallenberg, D M Summers, C Romero, A Taratuto, U Heinemann, M Breithaupt, D Varges, B Meissner, A Ladogana, M Schuur, S Haik, S J Collins, Gerard H Jansen, G B Stokin, J Pimentel, E Hewer, D Collie, P Smith, H Roberts, J P Brandel, C van Duijn, M Pocchiari, C Begue, P Cras, R G Will, P Sanchez-Juan

Author Affiliations

1: National TSE Reference Center, Department of Neurology, Georg-August University Goettingen, Robert-Koch-Strasse 40, Goettingen, Germany.

Articles citing this

(truncated to the top 100)

A test for Creutzfeldt-Jakob disease using nasal brushings. N Engl J Med (2014) 3.58

Quantifying prion disease penetrance using large population control cohorts. Sci Transl Med (2016) 3.04

Determination of neuronal antibodies in suspected and definite Creutzfeldt-Jakob disease. JAMA Neurol (2014) 2.56

Diffusion-weighted MRI hyperintensity patterns differentiate CJD from other rapid dementias. Neurology (2011) 2.42

Real time quaking-induced conversion analysis of cerebrospinal fluid in sporadic Creutzfeldt-Jakob disease. Ann Neurol (2012) 2.18

Population screening for variant Creutzfeldt-Jakob disease using a novel blood test: diagnostic accuracy and feasibility study. JAMA Neurol (2014) 2.08

Treatable neurological disorders misdiagnosed as Creutzfeldt-Jakob disease. Ann Neurol (2011) 1.86

Cerebrospinal fluid biomarker supported diagnosis of Creutzfeldt-Jakob disease and rapid dementias: a longitudinal multicentre study over 10 years. Brain (2012) 1.24

Diagnostic accuracy of cerebrospinal fluid protein markers for sporadic Creutzfeldt-Jakob disease in Canada: a 6-year prospective study. BMC Neurol (2011) 1.24

NMDA receptor autoantibodies in sporadic Creutzfeldt-Jakob disease. J Neurol (2012) 1.21

The epidemiological, clinical, and laboratory features of sporadic Creutzfeldt-Jakob disease patients in China: surveillance data from 2006 to 2010. PLoS One (2011) 1.21

Characteristic CSF prion seeding efficiency in humans with prion diseases. Mol Neurobiol (2014) 1.19

Rapidly progressive dementias and the treatment of human prion diseases. Expert Opin Pharmacother (2010) 1.00

Differential diagnosis of Jakob-Creutzfeldt disease. Arch Neurol (2012) 0.98

Case series of probable sporadic Creutzfeldt-Jakob disease from Eastern India. Ann Indian Acad Neurol (2013) 0.98

Role of magnetic resonance imaging, cerebrospinal fluid, and electroencephalogram in diagnosis of sporadic Creutzfeldt-Jakob disease. J Neurol (2012) 0.96

Cerebrospinal fluid real-time quaking-induced conversion is a robust and reliable test for sporadic creutzfeldt-jakob disease: An international study. Ann Neurol (2016) 0.93

Thorough work-up and new diagnostic criteria needed for CJD. Nat Rev Neurol (2011) 0.93

Neuronal antibodies in patients with suspected or confirmed sporadic Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (2014) 0.92

Natural compounds may open new routes to treatment of amyloid diseases. Neurotherapeutics (2013) 0.92

A study of clinical profile, radiological and electroencephalographic characteristics of suspected Creutzfeldt-Jakob disease in a tertiary care centre in South India. J Neurosci Rural Pract (2015) 0.88

The Features of Genetic Prion Diseases Based on Chinese Surveillance Program. PLoS One (2015) 0.88

A proposal of new diagnostic pathway for fatal familial insomnia. J Neurol Neurosurg Psychiatry (2013) 0.87

Glucose metabolism in sporadic Creutzfeldt-Jakob disease: a statistical parametric mapping analysis of (18) F-FDG PET. Eur J Neurol (2011) 0.87

Recent US Case of Variant Creutzfeldt-Jakob Disease-Global Implications. Emerg Infect Dis (2015) 0.86

Application of quantitative DTI metrics in sporadic CJD. Neuroimage Clin (2014) 0.86

Cerebrospinal fluid markers in sporadic Creutzfeldt-Jakob disease. Int J Mol Sci (2011) 0.84

Ethics in prion disease. Prog Neurobiol (2013) 0.83

Prion disease: diagnostic value of cerebrospinal fluid markers. Nat Rev Neurol (2012) 0.83

MRI findings are often missed in the diagnosis of Creutzfeldt-Jakob disease. BMC Neurol (2012) 0.83

Multicentre multiobserver study of diffusion-weighted and fluid-attenuated inversion recovery MRI for the diagnosis of sporadic Creutzfeldt-Jakob disease: a reliability and agreement study. BMJ Open (2012) 0.83

Assessing dementia in resource-poor regions. Curr Neurol Neurosci Rep (2012) 0.82

Small-molecule theranostic probes: a promising future in neurodegenerative diseases. Int J Cell Biol (2013) 0.82

Overview and evaluation of 15 years of Creutzfeldt-Jakob disease surveillance in Belgium, 1998-2012. BMC Neurol (2015) 0.82

A low-molecular-weight ferroxidase is increased in the CSF of sCJD cases: CSF ferroxidase and transferrin as diagnostic biomarkers for sCJD. Antioxid Redox Signal (2013) 0.82

Detection of the GPI-anchorless prion protein fragment PrP226* in human brain. BMC Neurol (2013) 0.81

Unusual deterioration in a patient with multiple sclerosis on natalizumab therapy. Neurol Neuroimmunol Neuroinflamm (2014) 0.81

Immune responses in rapidly progressive dementia: a comparative study of neuroinflammatory markers in Creutzfeldt-Jakob disease, Alzheimer's disease and multiple sclerosis. J Neuroinflammation (2014) 0.81

Glucose metabolism in nine patients with probable sporadic Creutzfeldt-Jakob disease: FDG-PET study using SPM and individual patient analysis. J Neurol (2013) 0.80

Quantification of CSF biomarkers using an electrochemiluminescence-based detection system in the differential diagnosis of AD and sCJD. J Neurol (2015) 0.80

Comparing CSF biomarkers and brain MRI in the diagnosis of sporadic Creutzfeldt-Jakob disease. Neurol Clin Pract (2015) 0.80

First symptom and initial diagnosis in sporadic CJD patients in Germany. J Neurol (2014) 0.80

Analyses of the survival time and the influencing factors of chinese patients with prion diseases based on the surveillance data from 2008-2011. PLoS One (2013) 0.80

Pathologic evidence that the T188R mutation in PRNP is associated with prion disease. J Neuropathol Exp Neurol (2010) 0.80

Diffusion imaging changes in grey matter in Alzheimer's disease: a potential marker of early neurodegeneration. Alzheimers Res Ther (2015) 0.80

Diagnostic and Prognostic Value of Human Prion Detection in Cerebrospinal Fluid. Ann Neurol (2016) 0.80

Ascertainment bias causes false signal of anticipation in genetic prion disease. Am J Hum Genet (2014) 0.79

Clinical findings and diagnosis in genetic prion diseases in Germany. Eur J Epidemiol (2015) 0.79

Diffusion-weighted MRI findings and clinical correlations in sporadic Creutzfeldt-Jakob disease. J Neurol (2015) 0.79

Chinese specific characteristics of sporadic Creutzfeldt-Jakob disease: a retrospective analysis of 57 cases. PLoS One (2013) 0.79

Sporadic Creutzfeldt-Jakob disease with focal findings: caveats to current diagnostic criteria. Neurol Int (2013) 0.78

Olfactory Receptors in Non-Chemosensory Organs: The Nervous System in Health and Disease. Front Aging Neurosci (2016) 0.78

An update on the diagnosis and management of dementing conditions. Rev Neurol Dis (2011) 0.78

Interpretation of cerebrospinal fluid protein tests in the diagnosis of sporadic Creutzfeldt-Jakob disease: an evidence-based approach. CMAJ (2014) 0.78

Spongiform encephalopathy in siblings with no evidence of protease-resistant prion protein or a mutation in the prion protein gene. J Neurol (2013) 0.78

Prion Diseases. Continuum (Minneap Minn) (2015) 0.78

Revisiting the Heidenhain Variant of Creutzfeldt-Jakob Disease: Evidence for Prion Type Variability Influencing Clinical Course and Laboratory Findings. J Alzheimers Dis (2015) 0.78

Creutzfeldt-jakob disease as a cause of cognitive decline and seizures in the elderly: diagnostic pointers and strategy for investigation. Case Rep Med (2011) 0.77

Symptomatic aggravation after corticosteroid pulse therapy in definite sporadic Creutzfeldt-Jakob disease with the feature of Hashimoto's encephalopathy. BMC Neurol (2014) 0.77

Investigating the association of ApoE genotypes with blood-brain barrier dysfunction measured by cerebrospinal fluid-serum albumin ratio in a cohort of patients with different types of dementia. PLoS One (2013) 0.77

White matter involvement in sporadic Creutzfeldt-Jakob disease. Brain (2014) 0.77

Clinical, biological, and imaging features of monogenic Alzheimer's Disease. Biomed Res Int (2013) 0.77

Rapidly progressive corticobasal degeneration syndrome. Case Rep Neurol (2011) 0.77

Diagnostic profiles of patients with late-onset Creutzfeldt-Jakob disease differ from those of younger Creutzfeldt-Jakob patients: a historical cohort study using data from the German National Reference Center. J Neurol (2014) 0.77

Mathematical models for the diffusion magnetic resonance signal abnormality in patients with prion diseases. Neuroimage Clin (2014) 0.76

Diagnostic Accuracy of a Combined Analysis of Cerebrospinal Fluid t-PrP, t-tau, p-tau, and Aβ42 in the Differential Diagnosis of Creutzfeldt-Jakob Disease from Alzheimer's Disease with Emphasis on Atypical Disease Variants. J Alzheimers Dis (2016) 0.76

Metabolic disorders with clinical and radiologic features of sporadic Creutzfeldt-Jakob disease. Neurol Clin Pract (2015) 0.76

Whipple's disease masquerades as dementia with Lewy bodies. Alzheimer Dis Assoc Disord (2015) 0.76

Unusual features of Creutzfeldt-Jakob disease followed-up in a memory clinic. J Neurol (2014) 0.76

The use of cerebrospinal fluid and neuropathologic studies in neuropsychiatry practice and research. Psychiatr Clin North Am (2015) 0.76

Alternative application of Tau protein in Creutzfeldt-Jakob disease diagnosis: Improvement for weakly positive 14-3-3 protein in the laboratory. Sci Rep (2015) 0.76

Thalamic lesions: a radiological review. Behav Neurol (2014) 0.76

CJD mimics and chameleons. Pract Neurol (2017) 0.76

Temporal evolution of sporadic Creutzfeldt-Jakob disease monitored by 3-Tesla MR spectroscopy. J Neurol (2011) 0.75

Stereotypic Movements in Case of Sporadic Creutzfeldt-Jakob Disease: Possible Role of Anti-NMDA Receptor Antibodies. Case Rep Neurol (2012) 0.75

Sleep Pathology in Creutzfeldt-Jakob Disease. J Clin Sleep Med (2016) 0.75

Sporadic Creutzfeldt-Jakob disease (sCJD) with asymmetric findings. BMJ Case Rep (2014) 0.75

Diagnosing sporadic creutzfeldt-jakob disease in a patient with a suspected status epilepticus in the intensive care unit. Case Rep Neurol Med (2013) 0.75

Case report of Lewy body disease mimicking Creutzfeldt-Jakob disease in a 44-year-old man. BMC Neurol (2016) 0.75

A case of Creutzfeldt-Jakob disease: diagnostic dilemmas of a rapidly fatal disease. Infect Dis Rep (2013) 0.75

Gerstmann-Sträussler-Scheinker disease and "anchorless prion protein" mice share prion conformational properties diverging from sporadic Creutzfeldt-Jakob disease. J Biol Chem (2014) 0.75

Generalized myoclonus as a prominent symptom in a patient with FTLD-TDP. J Neurol (2013) 0.75

EEG-EMG polygraphic study of dystonia and myoclonus in a case of Creutzfeldt-Jakob disease. Epilepsy Behav Case Rep (2015) 0.75

Illustrating the relevance of updated diagnostic criteria for sporadic Creutzfeldt-Jakob disease: a teaching neurocase. BMJ Case Rep (2013) 0.75

Atypical creutzfeldt-jakob disease evolution after electroconvulsive therapy for catatonic depression. Case Rep Psychiatry (2011) 0.75

Creutzfeldt-Jakob Disease in a Tertiary Care Hospital in Thailand: A Case Series and Review of the Literature. J Mov Disord (2015) 0.75

Response to the article by adanipar et Al.: the first report of a patient with probable variant creutzfeldt-jakob disease in Turkey, dement geriatr cogn disord extra 2011;1:429-432. Dement Geriatr Cogn Dis Extra (2012) 0.75

Creutzfeldt-Jakob Disease-Like Periodic Sharp Wave Complexes in Voltage-Gated Potassium Channel-Complex Antibodies Encephalitis: A Case Report. J Clin Neurophysiol (2016) 0.75

Racial and ethnic differences in individuals with sporadic Creutzfeldt-jakob disease in the United States of America. PLoS One (2012) 0.75

Magnetic resonance imaging findings in probable Creutzfeld-Jacob disease: comparison with electroencephalography and cerebrospinal fluid characteristics. Acta Radiol Short Rep (2014) 0.75

Prions: Beyond a Single Protein. Clin Microbiol Rev (2016) 0.75

Wait and see: a 5 year history of 'recurrent dementia'. BMJ Case Rep (2014) 0.75

Genome-wide association study of behavioural and psychiatric features in human prion disease. Transl Psychiatry (2015) 0.75

The value of magnetic resonance imaging in the early diagnosis of Creutzfeldt-Jakob disease - own experience. Pol J Radiol (2012) 0.75

Role of the biomarkers for the diagnosis of Creutzfeldt-Jakob disease. J Med Life (2016) 0.75

Biomarkers for sporadic Creutzfeldt-Jakob disease. Ann Clin Transl Neurol (2016) 0.75

Alien hand and leg as the presenting feature of probable sporadic Creutzfeldt-Jakob disease: A rare presentation of a rare disease. Ann Indian Acad Neurol (2015) 0.75

Creutzfeldt-Jakob Disease Presenting With Dizziness and Gaze-Evoked Nystagmus: A Case Report. Medicine (Baltimore) (2016) 0.75

Creutzfeldt-Jakob disease: typical imaging findings. BMJ Case Rep (2014) 0.75

Severe depression masquerading as Creutzfeldt-Jakob disease. BMJ Case Rep (2014) 0.75

Articles cited by this

Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects. Ann Neurol (1999) 6.98

Creutzfeldt-Jakob disease: patterns of worldwide occurrence and the significance of familial and sporadic clustering. Ann Neurol (1979) 5.53

Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease. Ann Neurol (1996) 4.10

Sporadic and familial CJD: classification and characterisation. Br Med Bull (2003) 3.66

Diffusion-weighted and fluid-attenuated inversion recovery imaging in Creutzfeldt-Jakob disease: high sensitivity and specificity for diagnosis. AJNR Am J Neuroradiol (2005) 3.11

Analysis of EEG and CSF 14-3-3 proteins as aids to the diagnosis of Creutzfeldt-Jakob disease. Neurology (2000) 3.03

Voltage-gated potassium channel autoimmunity mimicking creutzfeldt-jakob disease. Arch Neurol (2008) 2.80

Hashimoto's encephalitis as a differential diagnosis of Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (1999) 2.55

Determinants of diagnostic investigation sensitivities across the clinical spectrum of sporadic Creutzfeldt-Jakob disease. Brain (2006) 2.54

CSF tests in the differential diagnosis of Creutzfeldt-Jakob disease. Neurology (2006) 2.19

Diagnosing variant Creutzfeldt-Jakob disease with the pulvinar sign: MR imaging findings in 86 neuropathologically confirmed cases. AJNR Am J Neuroradiol (2003) 2.05

Total tau protein in cerebrospinal fluid and diffusion-weighted MRI as an early diagnostic marker for Creutzfeldt-Jakob disease. Dement Geriatr Cogn Disord (2007) 1.72

How to improve the clinical diagnosis of Creutzfeldt-Jakob disease. Brain (1999) 1.71

Sporadic Creutzfeldt-Jakob disease: clinical and diagnostic characteristics of the rare VV1 type. Neurology (2005) 1.65

MRI lesion profiles in sporadic Creutzfeldt-Jakob disease. Neurology (2009) 1.61

Creutzfeldt-Jakob disease in Germany: a prospective 12-year surveillance. Brain (2007) 1.56

Autoimmune encephalopathies. Neurologist (2007) 1.50

Sensitivity of 14-3-3 protein test varies in subtypes of sporadic Creutzfeldt-Jakob disease. Neurology (2004) 1.49

Current clinical diagnosis in Creutzfeldt-Jakob disease: identification of uncommon variants. Ann Neurol (2000) 1.49

Rapidly progressive neurodegenerative dementias. Arch Neurol (2009) 1.46

Patients with Alzheimer's disease and dementia with Lewy bodies mistaken for Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (2001) 1.39

Clinical findings and diagnostic tests in the MV2 subtype of sporadic CJD. Brain (2006) 1.35

Pattern of cortical changes in sporadic Creutzfeldt-Jakob disease. AJNR Am J Neuroradiol (2007) 1.24

Creutzfeldt-Jakob disease: comparative analysis of MR imaging sequences. AJNR Am J Neuroradiol (2006) 1.19

14-3-3 CSF levels in sporadic Creutzfeldt-Jakob disease differ across molecular subtypes. Neurobiol Aging (2008) 1.18

MRI in the diagnosis of sporadic Creutzfeldt-Jakob disease: a study on inter-observer agreement. Brain (2005) 1.18

Dementia with Lewy bodies in a neuropathologic series of suspected Creutzfeldt-Jakob disease. Neurology (2000) 1.16

Clinical features and diagnosis of the MM2 cortical subtype of sporadic Creutzfeldt-Jakob disease. Arch Neurol (2006) 1.15

Correlating DWI MRI with pathologic and other features of Jakob-Creutzfeldt disease. Alzheimer Dis Assoc Disord (2009) 1.13

Influence of timing on CSF tests value for Creutzfeldt-Jakob disease diagnosis. J Neurol (2007) 1.12

Anti-GAD antibody cerebellar ataxia mimicking Creutzfeldt-Jakob disease. Clin Neurol Neurosurg (2006) 1.03

Isolated cortical signal increase on MR imaging as a frequent lesion pattern in sporadic Creutzfeldt-Jakob disease. AJNR Am J Neuroradiol (2008) 1.01

CSF analysis in patients with sporadic CJD and other transmissible spongiform encephalopathies. Eur J Neurol (2007) 0.95

MRI in the classical MM1 and the atypical MV2 subtypes of sporadic CJD: an inter-observer agreement study. Eur J Neurol (2008) 0.92

Immunoglobulins and virus-specific antibodies in patients with Creutzfeldt-Jakob disease. Acta Neurol Scand (2005) 0.90

Diffusion tensor imaging in patients with Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (2008) 0.89

MM1-type sporadic Creutzfeldt-Jakob disease with unusually prolonged disease duration presenting with panencephalopathic-type pathology. Neuropathology (2008) 0.87

Differences of apparent diffusion coefficient values in patients with Creutzfeldt-Jakob disease according to the codon 129 genotype. AJNR Am J Neuroradiol (2008) 0.86

Articles by these authors

A new variant of Creutzfeldt-Jakob disease in the UK. Lancet (1996) 20.15

Mild cognitive impairment--beyond controversies, towards a consensus: report of the International Working Group on Mild Cognitive Impairment. J Intern Med (2004) 16.58

Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent. Nature (1997) 15.73

Continuous growth and differentiation of human myeloid leukaemic cells in suspension culture. Nature (1977) 12.57

Terminal differentiation of human promyelocytic leukemia cells induced by dimethyl sulfoxide and other polar compounds. Proc Natl Acad Sci U S A (1978) 9.59

Induction of differentiation of the human promyelocytic leukemia cell line (HL-60) by retinoic acid. Proc Natl Acad Sci U S A (1980) 6.65

An exceptionally conserved transcriptional repressor, CTCF, employs different combinations of zinc fingers to bind diverged promoter sequences of avian and mammalian c-myc oncogenes. Mol Cell Biol (1996) 5.74

Phytochrome and Seed Germination. I. Temperature Dependence and Relative P(FR) Levels in the Germination of Dark-germinating Tomato Seeds. Plant Physiol (1967) 5.14

Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion. Lancet (2004) 4.85

Equity of access to health care services: theory and evidence from the UK. Soc Sci Med (2001) 4.83

Concordance of the toxicity of pharmaceuticals in humans and in animals. Regul Toxicol Pharmacol (2000) 4.58

Mutations in UBQLN2 cause dominant X-linked juvenile and adult-onset ALS and ALS/dementia. Nature (2011) 4.56

A standard reference frame for the description of nucleic acid base-pair geometry. J Mol Biol (2001) 4.29

Attempt at deriving a formula for setting general practitioner fundholding budgets. BMJ (1994) 4.19

The BOADICEA model of genetic susceptibility to breast and ovarian cancer. Br J Cancer (2004) 4.06

Allocating resources to health authorities: development of method for small area analysis of use of inpatient services. BMJ (1994) 3.88

Abnormal dendritic spine characteristics in the temporal and visual cortices of patients with fragile-X syndrome: a quantitative examination. Am J Med Genet (2001) 3.77

"Friendly fire" in medicine: hormones, homografts, and Creutzfeldt-Jakob disease. Lancet (1992) 3.74

Genome of Geobacter sulfurreducens: metal reduction in subsurface environments. Science (2003) 3.68

Geographical distribution of variant CJD in the UK (excluding Northern Ireland). Lancet (1999) 3.39

Bone density in women receiving depot medroxyprogesterone acetate for contraception. BMJ (1991) 3.34

Persistent infection with Chlamydia pneumoniae following acute respiratory illness. Clin Infect Dis (1992) 3.30

Predicting susceptibility and incubation time of human-to-human transmission of vCJD. Lancet Neurol (2006) 3.29

Two exposed amino acid residues confer thermostability on a cold shock protein. Nat Struct Biol (2000) 3.27

Agriculture. Sustainable intensification in agriculture: premises and policies. Science (2013) 3.24

Iatrogenic Creutzfeldt-Jakob disease at the millennium. Neurology (2000) 3.23

Axo-axonal coupling. a novel mechanism for ultrafast neuronal communication. Neuron (2001) 3.19

Predicting the CJD epidemic in humans. Nature (1997) 3.04

Acceptability, benefit and costs of early screening for hearing disability: a study of potential screening tests and models. Health Technol Assess (2007) 3.04

Analysis of EEG and CSF 14-3-3 proteins as aids to the diagnosis of Creutzfeldt-Jakob disease. Neurology (2000) 3.03

The human cytomegalovirus chemokine receptor US28 mediates vascular smooth muscle cell migration. Cell (1999) 2.97

Creutzfeldt-Jakob disease and blood transfusion. Lancet (1993) 2.97

Axonal transport of amyloid precursor protein is mediated by direct binding to the kinesin light chain subunit of kinesin-I. Neuron (2000) 2.94

The pulvinar sign on magnetic resonance imaging in variant Creutzfeldt-Jakob disease. Lancet (2000) 2.92

The influence on survival of delay in the presentation and treatment of symptomatic breast cancer. Br J Cancer (1999) 2.89

Crystal structure of CspA, the major cold shock protein of Escherichia coli. Proc Natl Acad Sci U S A (1994) 2.89

How is mechanical ventilation employed in the intensive care unit? An international utilization review. Am J Respir Crit Care Med (2000) 2.87

Molecular assessment of the potential transmissibilities of BSE and scrapie to humans. Nature (1997) 2.80

Normal functional characteristics of cultured human promyelocytic leukemia cells (HL-60) after induction of differentiation by dimethylsulfoxide. J Exp Med (1979) 2.80

Helix geometry, hydration, and G.A mismatch in a B-DNA decamer. Science (1987) 2.77

IL-9-deficient mice establish fundamental roles for IL-9 in pulmonary mastocytosis and goblet cell hyperplasia but not T cell development. Immunity (2000) 2.74

Improved discrimination of AD patients using beta-amyloid(1-42) and tau levels in CSF. Neurology (1999) 2.74

A retrospective study of Creutzfeldt-Jakob disease in England and Wales 1970-79. I: Clinical features. J Neurol Neurosurg Psychiatry (1984) 2.68

Bovine spongiform encephalopathy and variant Creutzfeldt-Jakob disease: background, evolution, and current concerns. Emerg Infect Dis (2001) 2.62

Mutagenesis identifies new signals for beta-amyloid precursor protein endocytosis, turnover, and the generation of secreted fragments, including Abeta42. J Biol Chem (1999) 2.57

Determinants of diagnostic investigation sensitivities across the clinical spectrum of sporadic Creutzfeldt-Jakob disease. Brain (2006) 2.54

Phytochrome and Seed Germination. III. Action of Prolonged Far Red Irradiation on the Germination of Tomato and Cucumber Seeds. Plant Physiol (1967) 2.54

Widespread West Nile virus activity, eastern United States, 2000. Emerg Infect Dis (2001) 2.52

Osteoprotegerin inhibits prostate cancer-induced osteoclastogenesis and prevents prostate tumor growth in the bone. J Clin Invest (2001) 2.49

Development of minimum criteria for the initiation of antibiotics in residents of long-term-care facilities: results of a consensus conference. Infect Control Hosp Epidemiol (2001) 2.45

Evidence, hierarchies, and typologies: horses for courses. J Epidemiol Community Health (2003) 2.45

Consensus meeting: monosodium glutamate - an update. Eur J Clin Nutr (2006) 2.44

Effect of maximizing oxygen delivery on morbidity and mortality rates in critically ill patients: a prospective, randomized, controlled study. Crit Care Med (1993) 2.42

Universal nucleic acid-binding domain revealed by crystal structure of the B. subtilis major cold-shock protein. Nature (1993) 2.40

Presenile dementia and cerebral haemorrhage linked to a mutation at codon 692 of the beta-amyloid precursor protein gene. Nat Genet (1992) 2.40

One year's treatment with propranolol after myocardial infarction: preliminary report of Norwegian multicentre trial. Br Med J (Clin Res Ed) (1982) 2.39

The role of cerebrospinal fluid 14-3-3 and other proteins in the diagnosis of sporadic Creutzfeldt-Jakob disease in the UK: a 10-year review. J Neurol Neurosurg Psychiatry (2010) 2.29

Immunohistochemical determination of oestrogen receptor: comparison of different methods of assessment of staining and correlation with clinical outcome of breast cancer patients. Br J Cancer (1996) 2.28

The emergence of West Nile virus in North America: ecology, epidemiology, and surveillance. Curr Top Microbiol Immunol (2002) 2.27

The effect of brief halothane anesthesia during daily gavage on complications and body weight in rats. Contemp Top Lab Anim Sci (2001) 2.25

Antiphospholipid antibodies after myocardial infarction and their relation to mortality, reinfarction, and non-haemorrhagic stroke. Lancet (1992) 2.22

Increasing cataract surgery to meet Vision 2020 targets; experience from two rural programmes in east Africa. Br J Ophthalmol (2005) 2.22

Clinical course and prognostic factors following bone recurrence from breast cancer. Br J Cancer (1998) 2.20

CSF tests in the differential diagnosis of Creutzfeldt-Jakob disease. Neurology (2006) 2.19

Detection of tau proteins in normal and Alzheimer's disease cerebrospinal fluid with a sensitive sandwich enzyme-linked immunosorbent assay. J Neurochem (1993) 2.18

Sporadic Creutzfeldt-Jakob disease mimicking nonconvulsive status epilepticus. Neurology (2010) 2.17

Terminal differentiation of human promyelocytic leukemic cells in primary culture in response to retinoic acid. Blood (1981) 2.16

Evidence for case-to-case transmission of Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (1982) 2.15

Evaluation of the relatedness of Brucella spp. and Ochrobactrum anthropi and description of Ochrobactrum intermedium sp. nov., a new species with a closer relationship to Brucella spp. Int J Syst Bacteriol (1998) 2.11

Amphotericin B treatment dissociates in vivo replication of the scrapie agent from PrP accumulation. Nature (1992) 2.11

Cyclin D1 and prognosis in human breast cancer. Int J Cancer (1996) 2.11

Infection control for home health. Infect Control Hosp Epidemiol (1990) 2.09

Rearrangement and amplification of c-abl sequences in the human chronic myelogenous leukemia cell line K-562. Proc Natl Acad Sci U S A (1983) 2.08

Low extracellular magnesium induces epileptiform activity and spreading depression in rat hippocampal slices. J Neurophysiol (1987) 2.07

Pneumococcal diversity: considerations for new vaccine strategies with emphasis on pneumococcal surface protein A (PspA). Clin Microbiol Rev (1998) 2.06

Deaths from variant Creutzfeldt-Jakob disease. Lancet (1999) 2.04

Structure of the DLM-1-Z-DNA complex reveals a conserved family of Z-DNA-binding proteins. Nat Struct Biol (2001) 2.04

Yes-associated protein (YAP) functions as a tumor suppressor in breast. Cell Death Differ (2008) 2.03

Comparison of sensitivities to two commercially available tuberculin skin test reagents in persons with recent tuberculosis. Clin Infect Dis (1997) 2.02

[Long-term study of psychological effects in clinical rehabilitation (VESPER-study)]. Dtsch Med Wochenschr (2003) 2.02

Expression of the ERBB3 gene product in breast cancer. Br J Cancer (1992) 2.01

Attenuated stroke severity after prodromal TIA: a role for ischemic tolerance in the brain? Stroke (1999) 2.00

The abnormal phosphorylation of tau protein at Ser-202 in Alzheimer disease recapitulates phosphorylation during development. Proc Natl Acad Sci U S A (1993) 1.99

Insights into interfacial activation from an open structure of Candida rugosa lipase. J Biol Chem (1993) 1.99

Natural history of autoimmune thyroiditis. Br Med J (Clin Res Ed) (1981) 1.99

Geographical distribution of variant Creutzfeldt-Jakob disease in Great Britain, 1994-2000. Lancet (2001) 1.97

Predictors of survival in sporadic Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies. Brain (2004) 1.96