Published in J Korean Med Sci on June 16, 2010
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Clinical diagnosis and differential diagnosis of CJD and vCJD. With special emphasis on laboratory tests. APMIS (2002) 1.10
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Novel PRNP mutation in a patient with a slow progressive dementia syndrome. Med Sci Monit (2008) 0.83
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Patterns of brain atrophy that differentiate corticobasal degeneration syndrome from progressive supranuclear palsy. Arch Neurol (2006) 2.27
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Pseudoneglect in solid-line versus character-line bisection tasks: a test for attention dominance theory. Cogn Behav Neurol (2004) 2.08
Formal protocol for emergency treatment of ruptured intracranial aneurysms to reduce in-hospital rebleeding and improve clinical outcomes. J Neurosurg (2014) 2.04
High prevalence of leukoaraiosis in cerebral magnetic resonance images of patients on peritoneal dialysis. Am J Kidney Dis (2007) 1.88
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Clinical significance of microbleeds in subcortical vascular dementia. Stroke (2007) 1.82
Defining functional SMA and pre-SMA subregions in human MFC using resting state fMRI: functional connectivity-based parcellation method. Neuroimage (2009) 1.69
Seizures and epileptiform activity in the early stages of Alzheimer disease. JAMA Neurol (2013) 1.68
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Cognition impairment in the genetic model of aging klotho gene mutant mice: a role of oxidative stress. FASEB J (2002) 1.52
Exome sequencing identifies ACSF3 as a cause of combined malonic and methylmalonic aciduria. Nat Genet (2011) 1.48
Prion proteins in subpopulations of white blood cells from patients with sporadic Creutzfeldt-Jakob disease. Lab Invest (2009) 1.48
Evidence for a role of the rare p.A152T variant in MAPT in increasing the risk for FTD-spectrum and Alzheimer's diseases. Hum Mol Genet (2012) 1.46
Association between cognitive impairment and bone mineral density in postmenopausal women. Menopause (2012) 1.46
Systematic review of health behavioral risks and cognitive health in older adults. Int Psychogeriatr (2009) 1.44
Brief screening for mild cognitive impairment in elderly outpatient clinic: validation of the Korean version of the Montreal Cognitive Assessment. J Geriatr Psychiatry Neurol (2008) 1.43
Seoul Neuropsychological Screening Battery-dementia version (SNSB-D): a useful tool for assessing and monitoring cognitive impairments in dementia patients. J Korean Med Sci (2010) 1.42
Acute serious rebleeding after angiographically successful coil embolization of ruptured cerebral aneurysms. Acta Neurochir (Wien) (2010) 1.42
Cortical thickness in single- versus multiple-domain amnestic mild cognitive impairment. Neuroimage (2007) 1.42
Additional sex comb-like 1 (ASXL1), in cooperation with SRC-1, acts as a ligand-dependent coactivator for retinoic acid receptor. J Biol Chem (2006) 1.37
The diagnostic utility of brain biopsy procedures in patients with rapidly deteriorating neurological conditions or dementia. J Neurosurg (2007) 1.37
Retracted ASXL1 represses retinoic acid receptor-mediated transcription through associating with HP1 and LSD1. J Biol Chem (2009) 1.35
Early detection of abnormal prion protein in genetic human prion diseases now possible using real-time QUIC assay. PLoS One (2013) 1.30
SORL1 is genetically associated with late-onset Alzheimer's disease in Japanese, Koreans and Caucasians. PLoS One (2013) 1.23
Pathogenesis of cerebral microbleeds: In vivo imaging of amyloid and subcortical ischemic small vessel disease in 226 individuals with cognitive impairment. Ann Neurol (2013) 1.22
Normative data on the Korean version of the Western Aphasia Battery. J Clin Exp Neuropsychol (2004) 1.21
Histopathology and TB-PCR kit analysis in differentiating the diagnosis of intestinal tuberculosis and Crohn's disease. World J Gastroenterol (2010) 1.20
Quantitative evaluation of liver function with MRI Using Gd-EOB-DTPA. Korean J Radiol (2005) 1.17
Induced pluripotent stem cell models of progranulin-deficient frontotemporal dementia uncover specific reversible neuronal defects. Cell Rep (2012) 1.16
Clinical characteristics of patients with spinocerebellar ataxias 1, 2, 3 and 6 in the US; a prospective observational study. Orphanet J Rare Dis (2013) 1.15
Rapidly progressive dementia: prion diseases and other rapid dementias. Continuum (Minneap Minn) (2010) 1.15
MED25 is distinct from TRAP220/MED1 in cooperating with CBP for retinoid receptor activation. EMBO J (2007) 1.14
Generation of monoclonal antibody recognized by the GXXXG motif (glycine zipper) of prion protein. Hybridoma (Larchmt) (2006) 1.13
Additional sex comb-like (ASXL) proteins 1 and 2 play opposite roles in adipogenesis via reciprocal regulation of peroxisome proliferator-activated receptor {gamma}. J Biol Chem (2010) 1.12
Sulcal morphology changes and their relationship with cortical thickness and gyral white matter volume in mild cognitive impairment and Alzheimer's disease. Neuroimage (2008) 1.11
A randomized, placebo-controlled trial of latrepirdine in Huntington disease. Arch Neurol (2010) 1.10
Switching strategy for mechanical thrombectomy of acute large vessel occlusion in the anterior circulation. Stroke (2013) 1.04
The cellular prion protein (PrPC) prevents apoptotic neuronal cell death and mitochondrial dysfunction induced by serum deprivation. Brain Res Mol Brain Res (2004) 1.03
Anti-GAD antibody cerebellar ataxia mimicking Creutzfeldt-Jakob disease. Clin Neurol Neurosurg (2006) 1.03
The prevalence of human endogenous retroviruses in cerebrospinal fluids from patients with sporadic Creutzfeldt-Jakob disease. J Clin Virol (2009) 1.02
Abrogation of IRF-1 response by high-risk HPV E7 protein in vivo. Cancer Lett (2002) 1.01
A 54-year-old man with slowness of movement and confusion. Neurology (2007) 1.01
Prion diseases. Semin Neurol (2013) 1.01
Rapidly Progressive Dementia. Continuum (Minneap Minn) (2016) 0.99
Automatic extraction of sulcal lines on cortical surfaces based on anisotropic geodesic distance. Neuroimage (2009) 0.99
Plasticity of the attentional network after brain injury and cognitive rehabilitation. Neurorehabil Neural Repair (2008) 0.99
Differential diagnosis of Jakob-Creutzfeldt disease. Arch Neurol (2012) 0.98
Cortical thinning in vascular mild cognitive impairment and vascular dementia of subcortical type. J Neuroimaging (2009) 0.98
Association of sporadic Creutzfeldt-Jakob disease with homozygous genotypes at PRNP codons 129 and 219 in the Korean population. Neurogenetics (2005) 0.98
Spectral-based automatic labeling and refining of human cortical sulcal curves using expert-provided examples. Neuroimage (2010) 0.98
Redox metals and oxidative abnormalities in human prion diseases. Acta Neuropathol (2005) 0.98
Accumulation of citrullinated proteins by up-regulated peptidylarginine deiminase 2 in brains of scrapie-infected mice: a possible role in pathogenesis. Am J Pathol (2008) 0.97
Identification of variants in cyclin D1 ( CCND1) and B-Cell CLL/lymphoma 2 ( BCL2). J Hum Genet (2004) 0.95
Cortical thinning related to periventricular and deep white matter hyperintensities. Neurobiol Aging (2011) 0.95
Frontotemporal dementia: what can the behavioral variant teach us about human brain organization? Neuroscientist (2011) 0.95
Activation of mitogen-activated protein kinases in hamster brains infected with 263K scrapie agent. J Neurochem (2005) 0.95
Subcortical aphasia after striatocapsular infarction: quantitative analysis of brain perfusion SPECT using statistical parametric mapping and a statistical probabilistic anatomic map. J Nucl Med (2007) 0.95
Protective effect of anthocyanins in middle cerebral artery occlusion and reperfusion model of cerebral ischemia in rats. Life Sci (2006) 0.94
The pathogenic mechanisms of prion diseases. Mech Ageing Dev (2002) 0.94
Dysphagia in patients with dementia: Alzheimer versus vascular. Alzheimer Dis Assoc Disord (2009) 0.94
Effect of transition metals (Mn, Cu, Fe) and deoxycholic acid (DA) on the conversion of PrPC to PrPres. FASEB J (2005) 0.94
The involvement of cellular prion protein in the autophagy pathway in neuronal cells. Mol Cell Neurosci (2008) 0.93
Variations in cortical thickness with dementia severity in Alzheimer's disease. Neurosci Lett (2008) 0.93
Polymorphisms of the prion protein gene (PRNP) in a Korean population. J Hum Genet (2004) 0.93
Thorough work-up and new diagnostic criteria needed for CJD. Nat Rev Neurol (2011) 0.93
Human prions and plasma lipoproteins. Proc Natl Acad Sci U S A (2006) 0.93
Mechanism of the closing-in phenomenon in a figure copying task in Alzheimer's disease patients. Neurocase (2004) 0.93
JAK-STAT signaling pathway mediates astrogliosis in brains of scrapie-infected mice. J Neurochem (2007) 0.92
Scrapie infection activates the replication of ecotropic, xenotropic, and polytropic murine leukemia virus (MuLV) in brains and spinal cords of senescence-accelerated mice: implication of MuLV in progression of scrapie pathogenesis. Biochem Biophys Res Commun (2006) 0.92
Influence of moving background on line bisection performance in the normal elderly versus patients with hemispatial neglect. Am J Phys Med Rehabil (2007) 0.92
Rescue forced-suction thrombectomy using the reperfusion catheter of the Penumbra System for thromboembolism during coil embolization of ruptured cerebral aneurysms. Neurosurgery (2012) 0.92
Subcortical hypointensity in partial status epilepticus associated with nonketotic hyperglycemia. J Neuroimaging (2003) 0.92
Correlations between neuronal loss, decrease of memory, and decrease expression of brain-derived neurotrophic factor in the gerbil hippocampus during normal aging. Exp Neurol (2006) 0.91
Caregiver-Administered Neuropsychiatric Inventory (CGA-NPI). J Geriatr Psychiatry Neurol (2004) 0.91
Establishment and characterization of Prnp knockdown neuroblastoma cells using dual microRNA-mediated RNA interference. Prion (2011) 0.91
Phospholipase D1 is associated with amyloid precursor protein in Alzheimer's disease. Neurobiol Aging (2006) 0.90
Inclusion body myopathy with Paget disease of bone and frontotemporal dementia linked to VCP p.Arg155Cys in a Korean family. Arch Neurol (2011) 0.90
Effects of demographic factors on cortical thickness in Alzheimer's disease. Neurobiol Aging (2009) 0.90
Clinical trials for prion disease: difficult challenges, but hope for the future. Lancet Neurol (2009) 0.90
Reduction of prion infectivity and levels of scrapie prion protein by lithium aluminum hydride: implications for RNA in prion diseases. J Neuropathol Exp Neurol (2009) 0.90
Mental confusion associated with scopolamine patch in elderly with mild cognitive impairment (MCI). Arch Gerontol Geriatr (2008) 0.90
Oxidative stress impairs autophagic flux in prion protein-deficient hippocampal cells. Autophagy (2012) 0.90
Early ventriculoperitoneal shunt placement after severe aneurysmal subarachnoid hemorrhage: role of intraventricular hemorrhage and shunt function. Neurosurgery (2010) 0.90
Neurodegenerative disease phenotypes in carriers of MAPT p.A152T, a risk factor for frontotemporal dementia spectrum disorders and Alzheimer disease. Alzheimer Dis Assoc Disord (2013) 0.90
Involvement of peptidylarginine deiminase-mediated post-translational citrullination in pathogenesis of sporadic Creutzfeldt-Jakob disease. Acta Neuropathol (2009) 0.90
Follicular stimulating hormone enhances Notch 1 expression in SK-OV-3 ovarian cancer cells. J Gynecol Oncol (2010) 0.90