PubRank

Akihiro Yachie

Author PubWeight™ 101.29‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Human tyrosine kinase 2 deficiency reveals its requisite roles in multiple cytokine signals involved in innate and acquired immunity. Immunity 2006 4.75
2 Pro-oxidant and cytotoxic effects of circulating heme. Blood 2002 2.45
3 Proposed guidelines for diagnosing chronic active Epstein-Barr virus infection. Am J Hematol 2005 1.65
4 Heme, heme oxygenase, and ferritin: how the vascular endothelium survives (and dies) in an iron-rich environment. Antioxid Redox Signal 2007 1.55
5 Heme oxygenase-1 deficiency: the first autopsy case. Hum Pathol 2002 1.53
6 Prognostic factors for chronic active Epstein-Barr virus infection. J Infect Dis 2003 1.36
7 Tolvaptan therapy for massive edema in a patient with nephrotic syndrome. Pediatr Nephrol 2013 1.19
8 Human heme oxygenase-1 deficiency presenting with hemolysis, nephritis, and asplenia. J Pediatr Hematol Oncol 2011 1.17
9 Cell type specific infection of Epstein-Barr virus (EBV) in EBV-associated hemophagocytic lymphohistiocytosis and chronic active EBV infection. Crit Rev Oncol Hematol 2002 1.15
10 Oligoclonal expansion of T lymphocytes with multiple second-site mutations leads to Omenn syndrome in a patient with RAG1-deficient severe combined immunodeficiency. Blood 2005 1.13
11 Distinct cytokine profiles of systemic-onset juvenile idiopathic arthritis-associated macrophage activation syndrome with particular emphasis on the role of interleukin-18 in its pathogenesis. Rheumatology (Oxford) 2010 1.13
12 Gene transfection of H25A mutant heme oxygenase-1 protects cells against hydroperoxide-induced cytotoxicity. J Biol Chem 2002 1.13
13 CD8alpha alpha memory effector T cells descend directly from clonally expanded CD8alpha +beta high TCRalpha beta T cells in vivo. Blood 2002 1.06
14 Heme, heme oxygenase and ferritin in vascular endothelial cell injury. Mol Nutr Food Res 2005 1.05
15 X-linked ectodermal dysplasia and immunodeficiency caused by reversion mosaicism of NEMO reveals a critical role for NEMO in human T-cell development and/or survival. Blood 2004 1.05
16 Analysis of T-cell repertoire diversity in Wiskott-Aldrich syndrome. Blood 2005 1.04
17 Familial Mediterranean fever in Japan. Medicine (Baltimore) 2012 1.04
18 Sphingosine-1-phosphate receptor type 1 regulates glioma cell proliferation and correlates with patient survival. Int J Cancer 2010 1.02
19 Somatic revertant mosaicism in a patient with leukocyte adhesion deficiency type 1. Blood 2007 1.00
20 Distinct subsets of patients with systemic juvenile idiopathic arthritis based on their cytokine profiles. Cytokine 2012 1.00
21 Tocilizumab masks the clinical symptoms of systemic juvenile idiopathic arthritis-associated macrophage activation syndrome: the diagnostic significance of interleukin-18 and interleukin-6. Cytokine 2012 0.99
22 Clinical significance of cloned expansion and CD5 down-regulation in Epstein-Barr Virus (EBV)-infected CD8+ T lymphocytes in EBV-associated hemophagocytic lymphohistiocytosis. J Infect Dis 2010 0.98
23 Skin infiltration of CD56(bright) CD16(-) natural killer cells in a case of X-SCID with Omenn syndrome-like manifestations. Eur J Haematol 2007 0.95
24 Novel Artemis gene mutations of radiosensitive severe combined immunodeficiency in Japanese families. Hum Genet 2003 0.95
25 Haem, haem oxygenase and ferritin in vascular endothelial cell injury. Nephrol Dial Transplant 2003 0.95
26 Role of activated macrophage and inflammatory cytokines in the development of calcinosis in juvenile dermatomyositis. Rheumatology (Oxford) 2013 0.94
27 Sequentially appearing erythema nodosum, erythema multiforme and Henoch-Schönlein purpura in a patient with Mycoplasma pneumoniae infection: a case report. J Med Case Rep 2012 0.93
28 The first report of adolescent TAFRO syndrome, a unique clinicopathologic variant of multicentric Castleman's disease. BMC Pediatr 2014 0.91
29 Polyclonal hematopoiesis maintained in patients with bone marrow failure harboring a minor population of paroxysmal nocturnal hemoglobinuria-type cells. Blood 2003 0.91
30 Detection of T lymphocytes with a second-site mutation in skin lesions of atypical X-linked severe combined immunodeficiency mimicking Omenn syndrome. Blood 2008 0.90
31 Hepcidin suppression and defective iron recycling account for dysregulation of iron homeostasis in heme oxygenase-1 deficiency. J Cell Mol Med 2009 0.90
32 Expansion of a liver-infiltrating cytotoxic T-lymphocyte clone in concert with the development of hepatitis-associated aplastic anaemia. Br J Haematol 2013 0.90
33 Multiple reversions of an IL2RG mutation restore T cell function in an X-linked severe combined immunodeficiency patient. J Clin Immunol 2012 0.89
34 Analysis of mutations and recombination activity in RAG-deficient patients. Clin Immunol 2010 0.88
35 [A case of Williams syndrome with p47-phox-deficient chronic granulomatous disease]. Nihon Rinsho Meneki Gakkai Kaishi 2003 0.88
36 Urinary heme oxygenase-1 as a sensitive indicator of tubulointerstitial inflammatory damage in various renal diseases. Am J Nephrol 2011 0.88
37 Drug-induced hypersensitivity syndrome associated with human herpesvirus 6 and cytomegalovirus reactivation. J Dermatol 2005 0.88
38 A case of immunoglobulin G4-related chronic sclerosing sialadenitis and dacryoadenitis associated with tuberculosis. Mod Rheumatol 2008 0.87
39 Colchicine-responsive chronic recurrent multifocal osteomyelitis with MEFV mutations: a variant of familial Mediterranean fever? Rheumatology (Oxford) 2010 0.86
40 Sustained elevation of serum interleukin-18 and its association with hemophagocytic lymphohistiocytosis in XIAP deficiency. Cytokine 2013 0.86
41 Paradoxical enhancement of oxidative cell injury by overexpression of heme oxygenase-1 in an anchorage-dependent cell ECV304. J Cell Biochem 2004 0.85
42 Epstein-Barr virus (EBV)-associated post-transplantation lymphoproliferative disorder simultaneously affecting both B and T cells after allogeneic bone marrow transplantation. Am J Hematol 2003 0.85
43 Development of vascular biology over the past 10 years: heme oxygenase-1 in cardiovascular homeostasis. J Endovasc Ther 2004 0.85
44 Cytokine profiles of patients with enterohemorrhagic Escherichia coli O111-induced hemolytic-uremic syndrome. Cytokine 2012 0.85
45 Caffeine activates tumor suppressor PTEN in sarcoma cells. Int J Oncol 2011 0.84
46 Cytokine profiles in children with primary Epstein-Barr virus infection. Pediatr Blood Cancer 2013 0.84
47 Familial Mediterranean fever: genotype-phenotype correlations in Japanese patients. Medicine (Baltimore) 2014 0.84
48 Simultaneous, clonally identical T cell expansion in tonsil and synovium in a patient with rheumatoid arthritis and chronic tonsillitis. Arthritis Rheum 2003 0.83
49 Caffeine induces apoptosis of osteosarcoma cells by inhibiting AKT/mTOR/S6K, NF-κB and MAPK pathways. Anticancer Res 2012 0.83
50 Glomerular proteinuria induces heme oxygenase-1 gene expression within renal epithelial cells. Pediatr Res 2005 0.83
51 RAG1 deficiency may present clinically as selective IgA deficiency. J Clin Immunol 2015 0.83
52 Transducible form of p47phox and p67phox compensate for defective NADPH oxidase activity in neutrophils of patients with chronic granulomatous disease. Biochem Biophys Res Commun 2011 0.82
53 Compensated inflammation in systemic juvenile idiopathic arthritis: role of alternatively activated macrophages. Cytokine 2012 0.82
54 Reactive peripheral blood plasmacytosis in a patient with acute hepatitis A. Int J Hematol 2007 0.82
55 Distinct cytokine profile in juvenile systemic lupus erythematosus-associated macrophage activation syndrome. Clin Immunol 2012 0.82
56 Omenn syndrome--review of several phenotypes of Omenn syndrome and RAG1/RAG2 mutations in Japan. Allergol Int 2006 0.82
57 Cellular heat acclimation regulates cell growth, cell morphology, mitogen-activated protein kinase activation, and expression of aquaporins in mouse fibroblast cells. Cell Physiol Biochem 2012 0.82
58 Immunophenotypic analysis of Epstein-Barr virus (EBV)-infected CD8(+) T cells in a patient with EBV-associated hemophagocytic lymphohistiocytosis. Eur J Haematol 2007 0.82
59 Rotavirus gastroenteritis-associated urinary ammonium acid urate crystals. Pediatr Int 2015 0.81
60 Characterization of Epstein-Barr virus (EBV)-infected cells in EBV-associated hemophagocytic lymphohistiocytosis in two patients with X-linked lymphoproliferative syndrome type 1 and type 2. Herpesviridae 2012 0.81
61 Natural history of medium-sized atrial septal defect in pediatric cases. J Cardiol 2012 0.81
62 Aplastic anemia successfully treated with rituximab: the possible role of aplastic anemia-associated autoantibodies as a marker for response. Eur J Haematol 2011 0.81
63 Down-regulation of CD5 expression on activated CD8+ T cells in familial hemophagocytic lymphohistiocytosis with perforin gene mutations. Hum Immunol 2013 0.81
64 Delayed wound healing in leukocyte adhesion deficiency type 1. J Pediatr 2010 0.81
65 A case series of CAEBV of children and young adults treated with reduced-intensity conditioning and allogeneic bone marrow transplantation: a single-center study. Eur J Haematol 2013 0.81
66 Clinical and mutational features of Vietnamese children with X-linked agammaglobulinemia. BMC Pediatr 2014 0.80
67 Clinical and immunophenotypic features of atypical complete DiGeorge syndrome. Pediatr Int 2012 0.80
68 Carbon monoxide (CO)-releasing molecule-derived CO regulates tissue factor and plasminogen activator inhibitor type 1 in human endothelial cells. Thromb Res 2012 0.80
69 Isolated congenital megacystis without intestinal obstruction: a mild variant of chronic intestinal pseudoobstruction syndrome? J Pediatr Surg 2011 0.80
70 Phosphodiesterase inhibitors suppress Lactobacillus casei cell-wall-induced NF-κB and MAPK activations and cell proliferation through protein kinase A--or exchange protein activated by cAMP-dependent signal pathway. ScientificWorldJournal 2012 0.80
71 Corticosteroid enhances heme oxygenase-1 production by circulating monocytes by up-regulating hemoglobin scavenger receptor and amplifying the receptor-mediated uptake of hemoglobin-haptoglobin complex. Biochem Biophys Res Commun 2007 0.80
72 Expansion of activated eosinophils in infants with severe atopic dermatitis. Pediatr Int 2005 0.80
73 A novel method for determining functional LDL receptor activity in familial hypercholesterolemia: application of the CD3/CD28 assay in lymphocytes. Clin Chim Acta 2008 0.80
74 Aberrant glycosylation of IgA in Wiskott-Aldrich syndrome and X-linked thrombocytopenia. J Allergy Clin Immunol 2012 0.80
75 Intermittent X-linked thrombocytopenia with a novel WAS gene mutation. Pediatr Blood Cancer 2013 0.80
76 Long-term heat exposure prevents hypoxia-induced apoptosis in mouse fibroblast cells. Cell Biochem Biophys 2014 0.80
77 Shiga toxin-2 enhances heat-shock-induced apoptotic cell death in cultured and primary glial cells. Cell Biol Toxicol 2014 0.80
78 Soluble ST2 as a marker of disease activity in systemic juvenile idiopathic arthritis. Cytokine 2013 0.80
79 Urinary neopterin: an immune activation marker in mesangial proliferative glomerulonephritis. Clin Exp Nephrol 2014 0.79
80 Cutaneous calcinosis in juvenile dermatomyositis. J Pediatr 2013 0.79
81 A second-site mutation in the initiation codon of WAS (WASP) results in expansion of subsets of lymphocytes in an Wiskott-Aldrich syndrome patient. Hum Mutat 2006 0.79
82 Activation of tumor suppressor protein PTEN and induction of apoptosis are involved in cAMP-mediated inhibition of cell number in B92 glial cells. Neurosci Lett 2011 0.79
83 Expansion of clonotype-restricted HLA-identical maternal CD4+ T cells in a patient with severe combined immunodeficiency and a homozygous mutation in the Artemis gene. Clin Immunol 2003 0.79
84 Honeycomb appearance of the liver in Wilson's disease. Clin Gastroenterol Hepatol 2011 0.79
85 Thomsen-Friedenreich antigen exposure as a cause of Streptococcus pyogenes-associated hemolytic-uremic syndrome. Clin Nephrol 2012 0.78
86 Serum IL-18 as a potential specific marker for differentiating systemic juvenile idiopathic arthritis from incomplete Kawasaki disease. Rheumatol Int 2014 0.78
87 Novel adopted immunotherapy for mixed chimerism after unrelated cord blood transplantation in Omenn syndrome. Eur J Haematol 2005 0.78
88 Relatively common mutations of the Bloom syndrome gene in the Japanese population. Int J Mol Med 2004 0.78
89 Mollaret meningitis associated with occipital dermal sinus. J Pediatr 2009 0.78
90 Selective protection of renal tubular epithelial cells by heme oxygenase (HO)-1 during stress-induced injury. Kidney Int 2003 0.78
91 Successful treatment of recurrent focal segmental glomerulosclerosis after renal transplantation by lymphocytapheresis and rituximab. Transpl Int 2010 0.78
92 An interesting tetrad of asplenia, inflammation, hemolysis, and nephritis. Pediatr Hematol Oncol 2011 0.78
93 Cannabinoids inhibit peptidoglycan-induced phosphorylation of NF-κB and cell growth in U87MG human malignant glioma cells. Oncol Rep 2012 0.78
94 Dense methylation of types 1 and 2 regulatory regions of the CD10 gene promoter in infant acute lymphoblastic leukemia with MLL/AF4 fusion gene. J Pediatr Hematol Oncol 2010 0.77
95 Theobromine, the primary methylxanthine found in Theobroma cacao, prevents malignant glioblastoma proliferation by negatively regulating phosphodiesterase-4, extracellular signal-regulated kinase, Akt/mammalian target of rapamycin kinase, and nuclear factor-kappa B. Nutr Cancer 2014 0.77
96 Sequential measurement of fecal parameters in a case of non-immunoglobulin E-mediated milk allergy. Pediatr Int 2007 0.77
97 Upregulation of aquaporin expression in the salivary glands of heat-acclimated rats. Sci Rep 2013 0.77
98 Prominent eosinophilia but less eosinophil activation in a patient with Omenn syndrome. Pediatr Int 2010 0.77
99 Massive hyper-reactive hematopoietic nests in bilateral iliac bones in a patient with mild aplastic anemia. Pediatr Blood Cancer 2014 0.77
100 Are regimens containing rituximab effective in the initial treatment of Epstein-Barr virus-positive natural killer cell lymphoproliferative disease-associated hemophagocytic lymphohistiocytosis? Int J Hematol 2013 0.77
101 Successful treatment of primary sclerosing cholangitis with a steroid and a probiotic. Case Rep Gastroenterol 2012 0.77
102 Cytomegalovirus-associated protracted diarrhoea in an immunocompetent boy. J Paediatr Child Health 2006 0.77
103 Relapse of systemic juvenile idiopathic arthritis after influenza vaccination in a patient receiving tocilizumab. Clin Vaccine Immunol 2012 0.77
104 Enhanced exon 2 skipping caused by c.910G>A variant and alternative splicing of MEFV genes in two independent cases of familial Mediterranean fever. Mod Rheumatol 2011 0.76
105 Minimal contribution of severe hypertriglyceridemia in L-asparaginase-associated pancreatitis developed in a child with acute lymphocytic leukemia. Rinsho Ketsueki 2016 0.76
106 Effects of antithrombin III treatment in vascular injury model of mice. Pediatr Int 2011 0.76
107 [Monitoring of Epstein-Barr virus-infected cells by flow cytometer permits early diagnosis and evaluation of disease progression in EBV-associated hemophagocytic lymphohistiocytosis]. Rinsho Ketsueki 2012 0.76
108 Diffusion-weighted MRI of exercise-induced acute renal failure (ALPE). Pediatr Nephrol 2011 0.76
109 Multiple Serum Cytokine Profiling to Identify Combinational Diagnostic Biomarkers in Attacks of Familial Mediterranean Fever. Medicine (Baltimore) 2016 0.76
110 Flow cytometric analysis of skin blister fluid induced by mosquito bites in a patient with chronic active Epstein-Barr virus infection. Int J Hematol 2009 0.76
111 Elevation of fecal eosinophil-derived neurotoxin in infants with food protein-induced enterocolitis syndrome. Pediatr Allergy Immunol 2014 0.76
112 Accumulation of mature B cells in the inflamed muscle tissue of a patient with anti-155/140 antibody-positive juvenile dermatomyositis. Mod Rheumatol 2012 0.76
113 A case of acute encephalopathy with hemophagocytic lymphohistiocytosis and clonal T-cell expansion. Brain Dev 2011 0.76
114 Bicipital synovial cyst in systemic-onset juvenile idiopathic arthritis. J Pediatr 2010 0.75
115 38-year-old woman with recurrent abdominal pain, but no fever. Int J Gen Med 2012 0.75
116 Moth-eaten appearance of tubulointerstitial nephritis and uveitis syndrome on (99m)technetium dimercaptosuccinic acid scintigraphy. J Pediatr 2012 0.75
117 Munc13-4 deficiency with CD5 downregulation on activated CD8+ T cells. Pediatr Int 2014 0.75
118 Anomalous origin with myocardial bridging in coronary artery: stealth images in computed tomography. J Am Coll Cardiol 2012 0.75
119 Clonal expansion of Epstein-Barr virus (EBV)-infected γδ T cells in patients with chronic active EBV disease and hydroa vacciniforme-like eruptions. Int J Hematol 2012 0.75
120 Rituximab therapy for Epstein-Barr virus-related chronic hepatitis following living donor kidney transplantation. Am J Kidney Dis 2006 0.75
121 Successful treatment with bosentan for pulmonary hypertension and reduced peripheral circulation in juvenile systemic sclerosis. Pediatr Cardiol 2011 0.75
122 Extracranial Carotid Aneurysm in Takayasu Arteritis. J Clin Rheumatol 2017 0.75
123 Increased CD69 Expression on Peripheral Eosinophils from Patients with Food Protein-Induced Enterocolitis Syndrome. Int Arch Allergy Immunol 2016 0.75
124 Tubulointerstitial Nephritis and Uveitis Syndrome Associated With Human Papillomavirus Vaccine. J Pediatr Ophthalmol Strabismus 2016 0.75
125 Successful bone marrow transplantation with reduced intensity conditioning in a patient with delayed-onset adenosine deaminase deficiency. Pediatr Transplant 2012 0.75
126 Adult-onset Stills disease with a cellulitis-like eruption. Eur J Dermatol 2009 0.75
127 [Case of systemic-onset juvenile idiopathic arthritis complicated with sepsis --usefulness of cytokine profile for the differentiation between macrophage activation syndrome and sepsis]. Nihon Rinsho Meneki Gakkai Kaishi 2011 0.75
128 Peripheral blood plasmacytosis in severe fever with thrombocytopenia syndrome. Jpn J Infect Dis 2017 0.75
129 An infant with recurrent convulsive seizures of 3 weeks duration: questions. Pediatr Nephrol 2013 0.75
130 Transient impairment of NK cell function in an infant born to a mother with adult-onset Still's disease: perinatal effect of maternal IL-18. Clin Immunol 2012 0.75
131 Lactobacillus casei cell wall extract directly stimulates the expression of COX2 independent of Toll-like receptor 2 in rat glial cells. J Microbiol Immunol Infect 2012 0.75
132 Differential resistance to antiviral drugs in an immunocompromised patient with cytomegalovirus encephalitis. J Clin Virol 2010 0.75
133 Multiple osteonecrosis in a patient with juvenile systemic lupus erythematosus. J Clin Rheumatol 2013 0.75
134 Agranulocytosis after infectious mononucleosis. J Clin Virol 2012 0.75
135 Etanercept-induced lupus accompanied by hemophagocytic syndrome. Intern Med 2011 0.75
136 Increased expression of epidermal thymic stromal lymphopoietin in inflammatory peeling skin syndrome. J Dermatol 2014 0.75
137 [Role of T cells in the pathogenesis of type I diabetes mellitus: structure analysis of complementarity determining region 3 of circulating T cells]. Rinsho Byori 2007 0.75
138 Evaluation of T-Cell receptor diversity in pediatric patients with minimal change nephrotic syndrome. Clin Nephrol 2012 0.75
139 Rapid detection of intracellular p47phox and p67phox by flow cytometry; useful screening tests for chronic granulomatous disease. J Clin Immunol 2013 0.75
140 Delayed onset adenosine deaminase deficiency associated with acute disseminated encephalomyelitis. Int J Hematol 2012 0.75
141 Catastrophic anti-phospholipid syndrome associated with Escherichia coli O157 infection. Rheumatology (Oxford) 2009 0.75