Published in BMC Neurosci on March 08, 2011
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The ALS disease protein TDP-43 is actively transported in motor neuron axons and regulates axon outgrowth. Hum Mol Genet (2012) 1.25
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Involvement of survival motor neuron (SMN) protein in cell death. Hum Mol Genet (2002) 0.93
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Survival motor neuron protein regulates apoptosis in an in vitro model of spinal muscular atrophy. Neurotox Res (2008) 0.90
SMN protects cells against mutant SOD1 toxicity by increasing chaperone activity. Biochem Biophys Res Commun (2007) 0.90
Valproate and bone loss: iTRAQ proteomics show that valproate reduces collagens and osteonectin in SMA cells. J Proteome Res (2010) 0.86
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Increased susceptibility of spinal muscular atrophy fibroblasts to camptothecin-induced cell death. Mol Genet Metab (2005) 0.86
Ubiquitin carboxyl-terminal hydrolase L1 (UCHL1) regulates the level of SMN expression through ubiquitination in primary spinal muscular atrophy fibroblasts. Clin Chim Acta (2010) 0.84
Increased susceptibility of spinal muscular atrophy fibroblasts to camptothecin is p53-independent. BMC Cell Biol (2009) 0.83
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