Published in Ann Neurol on February 01, 1979
Prions. Proc Natl Acad Sci U S A (1998) 27.80
Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease. Brain (2009) 5.03
Quantifying prion disease penetrance using large population control cohorts. Sci Transl Med (2016) 3.04
A retrospective study of Creutzfeldt-Jakob disease in England and Wales 1970-79. I: Clinical features. J Neurol Neurosurg Psychiatry (1984) 2.68
Genetic prion disease: the EUROCJD experience. Hum Genet (2005) 2.64
Transmissible familial Creutzfeldt-Jakob disease associated with five, seven, and eight extra octapeptide coding repeats in the PRNP gene. Proc Natl Acad Sci U S A (1991) 2.55
Hashimoto's encephalitis as a differential diagnosis of Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (1999) 2.55
Diagnosis of Creutzfeldt-Jakob disease by measurement of S100 protein in serum: prospective case-control study. BMJ (1998) 2.15
Evidence for case-to-case transmission of Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (1982) 2.15
Creutzfeldt-Jakob disease in England and Wales, 1980-1984: a case-control study of potential risk factors. J Neurol Neurosurg Psychiatry (1988) 1.87
Rapidly progressive dementia. Neurol Clin (2007) 1.58
Prion proteins in subpopulations of white blood cells from patients with sporadic Creutzfeldt-Jakob disease. Lab Invest (2009) 1.48
Distinct neuropsychological characteristics in Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (2002) 1.48
Experimental transmission of an autosomal dominant spongiform encephalopathy: does the infectious agent originate in the human genome? Br Med J (Clin Res Ed) (1985) 1.47
Rapidly progressive neurodegenerative dementias. Arch Neurol (2009) 1.46
Ancestral origins and worldwide distribution of the PRNP 200K mutation causing familial Creutzfeldt-Jakob disease. Am J Hum Genet (1999) 1.46
Search for a prion-specific nucleic acid. J Virol (2005) 1.44
Evidence-based guideline: diagnostic accuracy of CSF 14-3-3 protein in sporadic Creutzfeldt-Jakob disease: report of the guideline development subcommittee of the American Academy of Neurology. Neurology (2012) 1.43
Bovine spongiform encephalopathy. Can Vet J (1989) 1.39
Patients with Alzheimer's disease and dementia with Lewy bodies mistaken for Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (2001) 1.39
Bovine spongiform encephalopathy. BMJ (1988) 1.36
Assignment of the human and mouse prion protein genes to homologous chromosomes. Proc Natl Acad Sci U S A (1986) 1.33
A prospective study of CSF markers in 250 patients with possible Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (2003) 1.27
A retrospective study of Creutzfeldt-Jakob disease in England and Wales 1970-1979. II: Epidemiology. J Neurol Neurosurg Psychiatry (1986) 1.25
Cerebrospinal fluid biomarker supported diagnosis of Creutzfeldt-Jakob disease and rapid dementias: a longitudinal multicentre study over 10 years. Brain (2012) 1.24
14-3-3 protein, total tau and phosphorylated tau in cerebrospinal fluid of patients with Creutzfeldt-Jakob disease and neurodegenerative disease in Japan. Cell Mol Neurobiol (2006) 1.23
Is Creutzfeldt-Jakob disease transmitted in blood? Emerg Infect Dis (1997) 1.19
Variant Creutzfeldt-Jakob disease: a summary of current scientific knowledge in relation to public health. CMAJ (2001) 1.18
Inherited prion disease (PrP lysine 200) in Britain: two case reports. BMJ (1993) 1.18
Risk of acquiring Creutzfeldt-Jakob disease from blood transfusions: systematic review of case-control studies. BMJ (2000) 1.11
Creutzfeldt-Jakob disease in the United States, 1979-1994: using national mortality data to assess the possible occurrence of variant cases. Emerg Infect Dis (1997) 1.07
Transmission of Creutzfeldt-Jakob disease to a chimpanzee by electrodes contaminated during neurosurgery. J Neurol Neurosurg Psychiatry (1994) 1.06
Radiological assessment of Creutzfeldt-Jakob disease. Eur Radiol (2006) 1.02
Rapidly progressive dementia due to Mycobacterium neoaurum meningoencephalitis. Emerg Infect Dis (2004) 0.99
Differential diagnosis of Jakob-Creutzfeldt disease. Arch Neurol (2012) 0.98
Medical procedures and risk for sporadic Creutzfeldt-Jakob disease, Japan, 1999-2008. Emerg Infect Dis (2009) 0.90
Diagnosing Creutzfeldt-Jakob disease. BMJ (1996) 0.89
A study of clinical profile, radiological and electroencephalographic characteristics of suspected Creutzfeldt-Jakob disease in a tertiary care centre in South India. J Neurosci Rural Pract (2015) 0.88
Duration of prion disease is longer in Japan than in other countries. J Epidemiol (2011) 0.86
Creutzfeldt-Jakob disease in Austria. J Neurol Neurosurg Psychiatry (1996) 0.86
Multicentre multiobserver study of diffusion-weighted and fluid-attenuated inversion recovery MRI for the diagnosis of sporadic Creutzfeldt-Jakob disease: a reliability and agreement study. BMJ Open (2012) 0.83
Graft-related disease progression in dura mater graft-associated Creutzfeldt-Jakob disease: a cross-sectional study. BMJ Open (2013) 0.83
Specific clinical signs and symptoms are predictive of clinical course in sporadic Creutzfeldt-Jakob disease. Eur J Neurol (2016) 0.82
The effect of stress on the onset and progression of Creutzfeldt-Jakob disease: results of a German pilot case-control study. Eur J Epidemiol (1999) 0.82
Ophthalmic surgery in prion diseases. Emerg Infect Dis (2007) 0.82
Incidence of Creutzfeldt-Jakob disease in Taiwan: a prospective 10-year surveillance. Eur J Epidemiol (2010) 0.81
Akinetic mutism as a classification criterion for the diagnosis of Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry (1998) 0.81
Variant Creutzfeldt-Jakob disease. Eur J Epidemiol (2003) 0.81
Increased incidence of sporadic Creutzfeldt-Jakob disease in the age groups between 70 and 90 years in Belgium. Eur J Epidemiol (2006) 0.80
Transmission of scrapie prions to primate after an extended silent incubation period. Sci Rep (2015) 0.80
Multitracer PET imaging in Heidenhain variant of Creutzfeldt-Jakob disease. J Neurol (2005) 0.79
A case-control study of sporadic Creutzfeldt-Jakob disease in Switzerland: analysis of potential risk factors with regard to an increased CJD incidence in the years 2001-2004. BMC Public Health (2009) 0.79
Heidenhain variant of Creutzfeldt-Jakob disease: An autopsy study from India. Ann Indian Acad Neurol (2009) 0.79
Analysis of the exon 1 polymorphism in the Tau gene in transmissible spongiform encephalopathies. J Neurol (2002) 0.78
Neurodegeneration in humans caused by prions. West J Med (1994) 0.77
A retrospective study of Creutzfeldt-Jakob disease in Belgium. Eur J Epidemiol (1999) 0.77
Are population-genetic mechanisms responsible for clustering of cases of Creutzfeldt-Jakob disease? Br Med J (Clin Res Ed) (1981) 0.76
Slow viruses and chronic disease: the contribution of epidemiology. Public Health Rep (1980) 0.76
A brief history of prions. Pathog Dis (2015) 0.76
A case of Creutzfeldt-Jakob disease: diagnostic dilemmas of a rapidly fatal disease. Infect Dis Rep (2013) 0.75
Creutzfeldt-Jakob disease, new variant Creutzfeldt-Jakob disease and bovine spongiform encephalopathy - An update. Can J Infect Dis (1997) 0.75
Autoclaved, formol-fixed scrapie mouse brain is suitable for histopathological examination, but may still be infective. Acta Neuropathol (1987) 0.75
Dietary Risk Factors for Sporadic Creutzfeldt-Jakob Disease: A Confirmatory Case-Control Study. Br J Med Med Res (2014) 0.75
Development of a dot blot assay with antibodies to recombinant "core" 14-3-3 protein: Evaluation of its usefulness in diagnosis of Creutzfeldt-Jakob disease. Ann Indian Acad Neurol (2016) 0.75
Diagnosis of Creutzfeldt-Jakob disease by measurement of S100 protein in serum. Appropriate study populations must be used. BMJ (1998) 0.75
Prions: Beyond a Single Protein. Clin Microbiol Rev (2016) 0.75
Concurrent variably protease-sensitive prionopathy and amyotrophic lateral sclerosis. Acta Neuropathol (2014) 0.75
Creutzfeldt-Jakob disease: Importance of early magnetic resonance imaging. Ann Indian Acad Neurol (2009) 0.75
Creutzfeldt-Jakob Disease: Analysis of Four Cases. Front Neurol (2016) 0.75
Creutzfeldt-Jakob disease and stress. J Neurol Neurosurg Psychiatry (1997) 0.75
The Gordon Wilson Lecture: viruses and chronic neurological diseases. Trans Am Clin Climatol Assoc (1981) 0.75
Serial Magnetic Resonance Imaging in Creutzfeldt-Jakob Disease: a Case Report and Literature Review. Cureus (2017) 0.75
Creutzfeldt-Jakob disease. Br Med J (Clin Res Ed) (1985) 0.75
Bovine spongiform encephalopathy in the United Kingdom: memorandum from a WHO meeting. Bull World Health Organ (1993) 0.75
The precursor of Alzheimer's disease amyloid A4 protein resembles a cell-surface receptor. Nature (1987) 17.08
Amyloid plaque core protein in Alzheimer disease and Down syndrome. Proc Natl Acad Sci U S A (1985) 16.10
Imaging beta-amyloid burden in aging and dementia. Neurology (2007) 7.70
HTLV-III infection in brains of children and adults with AIDS encephalopathy. Science (1985) 7.70
Soluble pool of Abeta amyloid as a determinant of severity of neurodegeneration in Alzheimer's disease. Ann Neurol (1999) 7.69
Characterization and chromosomal localization of a cDNA encoding brain amyloid of Alzheimer's disease. Science (1987) 6.89
Human immunodeficiency virus type 1 neutralization epitope with conserved architecture elicits early type-specific antibodies in experimentally infected chimpanzees. Proc Natl Acad Sci U S A (1988) 6.74
Unconventional viruses and the origin and disappearance of kuru. Science (1977) 6.38
Neuronal origin of a cerebral amyloid: neurofibrillary tangles of Alzheimer's disease contain the same protein as the amyloid of plaque cores and blood vessels. EMBO J (1985) 6.24
Creutzfeldt-Jakob disease (spongiform encephalopathy): transmission to the chimpanzee. Science (1968) 5.76
Rapid induction of Alzheimer A beta amyloid formation by zinc. Science (1994) 5.34
Human spongiform encephalopathy: the National Institutes of Health series of 300 cases of experimentally transmitted disease. Ann Neurol (1994) 5.20
The 14-3-3 brain protein in cerebrospinal fluid as a marker for transmissible spongiform encephalopathies. N Engl J Med (1996) 5.06
Identification, biogenesis, and localization of precursors of Alzheimer's disease A4 amyloid protein. Cell (1989) 4.99
Treatment with a copper-zinc chelator markedly and rapidly inhibits beta-amyloid accumulation in Alzheimer's disease transgenic mice. Neuron (2001) 4.42
Experimental transmission of a Kuru-like syndrome to chimpanzees. Nature (1966) 4.29
Creutzfeldt-Jakob disease and related transmissible spongiform encephalopathies. N Engl J Med (1998) 3.62
Danger of accidental person-to-person transmission of Creutzfeldt-Jakob disease by surgery. Lancet (1977) 3.58
Aggregation and secondary structure of synthetic amyloid beta A4 peptides of Alzheimer's disease. J Mol Biol (1991) 3.33
A4 amyloid protein deposition and the diagnosis of Alzheimer's disease: prevalence in aged brains determined by immunocytochemistry compared with conventional neuropathologic techniques. Neurology (1988) 3.28
Amyloid A4 protein and its precursor in Down's syndrome and Alzheimer's disease. N Engl J Med (1989) 3.24
Precursor of amyloid protein in Alzheimer disease undergoes fast anterograde axonal transport. Proc Natl Acad Sci U S A (1990) 3.13
Analysis of heterogeneous A4 peptides in human cerebrospinal fluid and blood by a newly developed sensitive Western blot assay. J Biol Chem (1996) 3.10
Localization of amyloid beta protein messenger RNA in brains from patients with Alzheimer's disease. Science (1987) 3.07
Mutations in familial Creutzfeldt-Jakob disease and Gerstmann-Sträussler-Scheinker's syndrome. Exp Neurol (1989) 3.00
Real and imagined clinicopathological limits of "prion dementia". Lancet (1993) 2.96
Distinct sites of intracellular production for Alzheimer's disease A beta40/42 amyloid peptides. Nat Med (1997) 2.95
Human alveolar macrophages: comparison of phagocytic ability, glucose utilization, and ultrastructure in smokers and nonsmokers. J Clin Invest (1970) 2.78
Transmission and passage of experimenal "kuru" to chimpanzees. Science (1967) 2.64
Bovine spongiform encephalopathy and variant Creutzfeldt-Jakob disease: background, evolution, and current concerns. Emerg Infect Dis (2001) 2.62
Conformational transitions, dissociation, and unfolding of scrapie amyloid (prion) protein. J Biol Chem (1993) 2.59
Detection of flaviviruses by reverse-transcriptase polymerase chain reaction. J Med Virol (1991) 2.59
Abeta deposits in older non-demented individuals with cognitive decline are indicative of preclinical Alzheimer's disease. Neuropsychologia (2008) 2.58
Transmissible familial Creutzfeldt-Jakob disease associated with five, seven, and eight extra octapeptide coding repeats in the PRNP gene. Proc Natl Acad Sci U S A (1991) 2.55
Determinants of diagnostic investigation sensitivities across the clinical spectrum of sporadic Creutzfeldt-Jakob disease. Brain (2006) 2.54
The foamy viruses. Bacteriol Rev (1975) 2.53
Subacute spongiform encephalopathy (Creutzfeldt-Jakob disease). The nature and progression of spongiform change. Brain (1978) 2.49
Interleukin 1 regulates synthesis of amyloid beta-protein precursor mRNA in human endothelial cells. Proc Natl Acad Sci U S A (1989) 2.48
The epidemiology of Creutzfeldt-Jakob disease: conclusion of a 15-year investigation in France and review of the world literature. Neurology (1987) 2.46
Experimental infection with Puumala virus, the etiologic agent of nephropathia epidemica, in bank voles (Clethrionomys glareolus). J Virol (1985) 2.39
Infection of chimpanzees by human T-lymphotropic retroviruses in brain and other tissues from AIDS patients. Lancet (1985) 2.35
Infection-specific particle from the unconventional slow virus diseases. Science (1984) 2.34
Packaging of prions into exosomes is associated with a novel pathway of PrP processing. J Pathol (2007) 2.31
Cu(II) potentiation of alzheimer abeta neurotoxicity. Correlation with cell-free hydrogen peroxide production and metal reduction. J Biol Chem (1999) 2.30
The amyloid precursor protein of Alzheimer's disease in the reduction of copper(II) to copper(I) Science (1996) 2.29
Persistent infection of chimpanzees with human immunodeficiency virus: serological responses and properties of reisolated viruses. J Virol (1987) 2.28
Ultrastructural morphology of amyloid fibrils from neuritic and amyloid plaques. Acta Neuropathol (1983) 2.23
Identification, transmembrane orientation and biogenesis of the amyloid A4 precursor of Alzheimer's disease. EMBO J (1988) 2.23
A heparin-binding domain in the amyloid protein precursor of Alzheimer's disease is involved in the regulation of neurite outgrowth. J Neurosci (1994) 2.19
The new biology of spongiform encephalopathy: infectious amyloidoses with a genetic twist. Lancet (1991) 2.16
A modified polyriboinosinic-polyribocytidylic acid complex that induces interferon in primates. J Infect Dis (1975) 2.14
Amyloid load in Parkinson's disease dementia and Lewy body dementia measured with [11C]PIB positron emission tomography. J Neurol Neurosurg Psychiatry (2008) 2.12
Precautions in medical care of, and in handling materials from, patients with transmissible virus dementia (Creutzfeldt-Jakob disease). N Engl J Med (1977) 2.10
Clinical and pathological features and laboratory confirmation of Creutzfeldt-Jakob disease in a recipient of pituitary-derived human growth hormone. N Engl J Med (1985) 2.09
Amyloid, aluminium and the aetiology of Alzheimer's disease. Med J Aust (1995) 2.09
Evidence for widespread infection of wild rats with hepatitis E virus in the United States. Am J Trop Med Hyg (1999) 2.08
HTLV-I and HTLV-III antibodies and tropical spastic paraparesis. Lancet (1985) 2.07
Creutzfeldt-Jakob disease: clinical analysis of a consecutive series of 230 neuropathologically verified cases. Ann Neurol (1986) 2.06
Diagnosis of Creutzfeldt-Jakob disease by Western blot identification of marker protein in human brain tissue. N Engl J Med (1986) 2.06
Survival of scrapie virus after 3 years' interment. Lancet (1991) 1.99
Beta-amyloid burden in the temporal neocortex is related to hippocampal atrophy in elderly subjects without dementia. Neurology (2010) 1.99
Oral transmission of kuru, Creutzfeldt-Jakob disease, and scrapie to nonhuman primates. J Infect Dis (1980) 1.96
Creutzfeldt-Jakob disease. The neuropathology of a transmission experiment. Brain (1969) 1.96
The promoter of Alzheimer's disease amyloid A4 precursor gene. EMBO J (1988) 1.92
Substitutions of hydrophobic amino acids reduce the amyloidogenicity of Alzheimer's disease beta A4 peptides. J Mol Biol (1992) 1.90
Serotypic classification of hantaviruses by indirect immunofluorescent antibody and plaque reduction neutralization tests. J Clin Microbiol (1985) 1.87