PubRank

Biochemical medicine and metabolic biology (Biochem Med Metab Biol)

Journal PubWeight™ 264.16‹?›

Top papers

Rank Title Year PubWeight™‹?›
1 Nonviability of cells with oxidative defects in galactose medium: a screening test for affected patient fibroblasts. 1992 1.75
2 An evaluation of the measurement of the activities of complexes I-IV in the respiratory chain of human skeletal muscle mitochondria. 1994 1.74
3 Minimizing false positive diagnoses in newborn screening for galactosemia. 1992 1.56
4 Is hyperglycemia risky enough to justify the increased risk of hypoglycemia linked with tight diabetes control? 1991 1.53
5 14CO2 production is no adequate measure of [14C]fatty acid oxidation. 1986 1.22
6 Quantification of the content of fluorescent flavoproteins in mitochondria from liver, kidney cortex, skeletal muscle, and brain. 1993 1.21
7 Aldose reductase: congenial and injurious profiles of an enigmatic enzyme. 1992 1.19
8 Porin interaction with hexokinase and glycerol kinase: metabolic microcompartmentation at the outer mitochondrial membrane. 1991 1.18
9 Differential excretion of xenobiotic acyl-esters of carnitine due to administration of pivampicillin and valproate. 1990 1.07
10 Effects of flavonoids on nonenzymatic lipid peroxidation: structure-activity relationship. 1988 1.02
11 Molecular analysis of common aldolase B alleles for hereditary fructose intolerance in North Americans. 1992 1.02
12 The dopamine D2 receptor (DRD2) as a major gene in obesity and height. 1993 1.02
13 Human serum mannose binding protein (MBP): development of an enzyme-linked immunosorbent assay (ELISA) and determination of levels in serum from 1085 normal Japanese and in some body fluids. 1993 1.02
14 Complementation analysis of patients with intact peroxisomes and impaired peroxisomal beta-oxidation. 1993 1.01
15 Biosynthesis and characterization of (S)-and (R)-3-hydroxy-3-methylglutaryl coenzyme A. 1992 1.00
16 Type 1 Gaucher disease: molecular, biochemical, and clinical characterization of patients from northern Portugal. 1993 0.98
17 Parenchymal organ cystine depletion with long-term cysteamine therapy. 1992 0.97
18 Calculation of inhibitor Ki and inhibitor type from the concentration of inhibitor for 50% inhibition for Michaelis-Menten enzymes. 1987 0.97
19 Effect of Withania somnifera on glycosaminoglycan synthesis in carrageenin-induced air pouch granuloma. 1987 0.95
20 Characterization of a novel biochemical abnormality in galactosemia: deficiency of glycolipids containing galactose or N-acetylgalactosamine and accumulation of precursors in brain and lymphocytes. 1991 0.94
21 Determination of inhibition constants, I50 values and the type of inhibition for enzyme-catalyzed reactions. 1988 0.93
22 Expression of recombinant human methylmalonyl-CoA mutase: in primary mut fibroblasts and Saccharomyces cerevisiae. 1993 0.92
23 Pathways of succinate formation and their contribution to improvement of cardiac function in the hypoxic rat heart. 1988 0.91
24 Alterations in membrane fluidity of diabetic polymorphonuclear leukocytes. 1991 0.91
25 Rat mammary arginase: isolation and characterization. 1994 0.91
26 Activities of dipeptidyl peptidase II, dipeptidyl peptidase IV, prolyl endopeptidase, and collagenase-like peptidase in synovial membrane from patients with rheumatoid arthritis and osteoarthritis. 1991 0.91
27 Interchange of amino acids between tumor and host. 1992 0.91
28 Screening for cystic fibrosis: feasibility of molecular genetic analysis of dried blood specimens. 1991 0.90
29 Screening urine of 3-week-old newborns: transient methylmalonic and hydroxyphenyllactic aciduria. 1992 0.90
30 Impaired ketogenesis in carnitine depletion caused by short-term administration of pivalic acid prodrug. 1994 0.90
31 The salivary flow rate and composition of whole and parotid resting and stimulated saliva in young and old healthy subjects. 1986 0.89
32 Decreased cholesterol biosynthesis in fibroblasts from patients with Parkinson disease. 1993 0.89
33 Metabolic responses of the dopaminergic system during hypoxia in newborn brain. 1994 0.89
34 Methylmalonic and propionic acidemias: lipid profiles of normal and affected human skin fibroblasts incubated with [1-14C]propionate. 1986 0.89
35 Glutathione metabolism in Crohn's disease. 1994 0.88
36 Methylenetetrahydrofolate reductase (MR) deficiency: thermolability of residual MR activity, methionine synthase activity, and methylcobalamin levels in cultured fibroblasts. 1992 0.88
37 Studies on human porin. XII. Eight monoclonal mouse anti-"porin 31HL" antibodies discriminate type 1 and type 2 mammalian porin channels/VDACs in western blotting and enzyme-linked immunosorbent assays. 1994 0.88
38 3-Hydroxy-3-methylglutaryldithio-coenzyme A: a potent inhibitor of Pseudomonas mevalonii HMG-CoA reductase. 1991 0.88
39 Ameliorating effect of murine interferon gamma on bleomycin-induced lung collagen fibrosis in mice. 1986 0.88
40 Effect of calcium glucarate on beta-glucuronidase activity and glucarate content of certain vegetables and fruits. 1990 0.88
41 Homozygous presence of the crossover (fusion gene) mutation identified in a type II Gaucher disease fetus: is this analogous to the Gaucher knock-out mouse model? 1994 0.88
42 Immunoprecipitation and electrophoretic analysis of four human acyl-CoA dehydrogenases and electron transfer flavoprotein using antibodies raised against the corresponding rat enzymes. 1987 0.87
43 Application of molecular genetics in public health: improved follow-up in a neonatal hemoglobinopathy screening program. 1994 0.87
44 Thiamin-responsive maple syrup urine disease in a patient antigenically missing dihydrolipoamide acyltransferase. 1993 0.87
45 Occurrence of the purine nucleotide cycle in rat pancreatic islets. 1992 0.87
46 Studies on the effects of the narcotic alkaloids, cocaine, morphine, and codeine on nonenzymatic lipid peroxidation in rat brain mitochondria. 1987 0.87
47 Methylmalonic semialdehyde dehydrogenase deficiency: demonstration of defective valine and beta-alanine metabolism and reduced malonic semialdehyde dehydrogenase activity in cultured fibroblasts. 1987 0.86
48 Acyl-CoA: glycine N-acyltransferase: in vitro studies on the glycine conjugation of straight- and branched-chained acyl-CoA esters in human liver. 1986 0.86
49 Clinical and biochemical studies in an American child with sialuria. 1993 0.86
50 Neonatal screening for cystic fibrosis: addition of molecular diagnostics to increase specificity. 1993 0.86
Next 50