Published in Agents Actions on October 01, 1978
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Mutations in RAB27A cause Griscelli syndrome associated with haemophagocytic syndrome. Nat Genet (2000) 5.11
Localization of an ataxia-telangiectasia gene to chromosome 11q22-23. Nature (1988) 3.82
Altered apoptotic profiles in irradiated patients with increased toxicity. Int J Radiat Oncol Biol Phys (1999) 1.73
Two genes are responsible for Griscelli syndrome at the same 15q21 locus. Genomics (2000) 1.54
Cyclic neutropenia complicated by renal AA amyloidosis. Turk J Pediatr (2000) 1.46
Common variable immunodeficiency in a patient with neurofibromatosis. Pediatr Int (2001) 1.44
Defective serum opsonization activity in children aged 6-48 months having acute purulent otitis media. Turk J Pediatr (1998) 1.40
Angiotensin tachyphylaxis and its reversal. Circ Res (1966) 1.33
Mutations in Igalpha (CD79a) result in a complete block in B-cell development. J Clin Invest (1999) 1.32
Laparoscopic omental fixation technique versus open surgical placement of peritoneal dialysis catheters. Surg Endosc (2003) 1.20
Epstein-Barr virus-related antibody patterns in ataxia-telangiectasia. Clin Exp Immunol (1979) 1.18
Angiotensin alteration of sodium fluxes in smooth muscle. Arch Int Pharmacodyn Ther (1967) 1.13
Further observations on the pressor action of propranolol. Br J Pharmacol Chemother (1967) 1.09
Presence of histamine H2-receptors in the guinea-pig pulmonary vascular bed. Pharmacology (1973) 1.00
Some properties of prostaglandin E1 action on muscle. Arch Int Pharmacodyn Ther (1967) 0.99
Epstein-Barr-virus-carrying lymphoma in a patient with ataxia-telangiectasia. Br Med J (Clin Res Ed) (1981) 0.98
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Epstein-Barr virus (EBV)-specific cell-mediated and humoral immune responses in ataxia-telangectasia patients. J Clin Immunol (1984) 0.96
Clinical and immunological studies in twenty families with ataxia-telangiectasia. Turk J Pediatr (1974) 0.96
Transient hypogammaglobulinemia of infancy: clinical and immunologic features of 40 new cases. Pediatr Int (2000) 0.96
Impaired IgG antibody production to pneumococcal polysaccharides in patients with ataxia-telangiectasia. J Clin Immunol (1999) 0.93
A study of the histamine H2-receptors in heart muscle and coronary vessels. Eur J Pharmacol (1974) 0.92
The alterations of whole saliva constituents in patients with diabetes mellitus. Aust Dent J (1996) 0.91
The use of IgM-enriched intravenous immunoglobulin for the treatment of neonatal sepsis in preterm infants. Turk J Pediatr (1994) 0.90
A case of chronic severe neutropenia: oral findings and consequences of short-term granulocyte colony-stimulating factor treatment. Aust Dent J (1998) 0.89
Familial Behçet's disease. Eur J Med (1992) 0.89
Increased serum leukotriene B4 level in the active stage of rheumatoid arthritis in children. Prostaglandins Leukot Essent Fatty Acids (1997) 0.89
Twenty-four-hour variations in the sensitivity of rat aorta to vasoactive agents. Chronobiol Int (1996) 0.88
Clinical and immunological studies in a case of selective complete C1q deficiency. Clin Exp Immunol (1979) 0.88
Neutrophil chemotaxis and periodontal status in Down's syndrome patients. J Nihon Univ Sch Dent (1993) 0.88
Congenital erythropoietic porphyria successfully treated by allogeneic bone marrow transplantation. Blood (1998) 0.87
Effect of angiotensin on the response to norepinephrine and peri-arterial stimulation of the isolated perfused cat terminal ileum. Eur J Pharmacol (1973) 0.87
Evidence for muscarinic receptors in the adrenal medulla of the dog. Br J Pharmacol (1969) 0.87
Mutations of chronic granulomatous disease in Turkish families. Eur J Clin Invest (2007) 0.86
Histamine receptors in the vasculature of the rabbit ear. Naunyn Schmiedebergs Arch Pharmacol (1975) 0.86
Inhibitory effect of angiotensin on the intestinal motility of the cat and its relation to sympathetic nervous system. Arch Int Physiol Biochim (1967) 0.86
Effects of varicocele on electrical field stimulation-induced biphasic twitch responses in the ipsilateral and contralateral rat vasa deferentia. Eur Surg Res (2007) 0.86
Iloprost preserves kidney function against anoxia. Prostaglandins Leukot Essent Fatty Acids (1988) 0.85
The gingival crevicular fluid interleukin-1 beta and tumour necrosis factor-alpha levels in patients with rapidly progressive periodontitis. Aust Dent J (1995) 0.85
Possible involvement of endothelium in the responses of various vasoactive agents in rabbit isolated perfused kidney. Gen Pharmacol (1990) 0.84
Histamine receptors in the cat mesenteric circulation. Experientia (1976) 0.84
Effect of lidoflazine on norepinephrine, angiotensin and serotonin responses in isolated smooth muscle preparations. Experientia (1967) 0.84
Oxidative stress and asymmetric dimethylarginine is independently associated with carotid intima media thickness in peritoneal dialysis patients. Am J Nephrol (2007) 0.83
HLA antigens associated with Behçet's disease. Arch Dermatol (1977) 0.83
The mechanism of the relaxing effect of ascorbic acid in guinea pig isolated tracheal muscle. Gen Pharmacol (1997) 0.83
Selective IgA deficiency with unusual features: development of common variable immunodeficiency, Sjögren's syndrome, autoimmune hemolytic anemia and immune thrombocytopenic purpura. Acta Paediatr Jpn (1995) 0.82
The effect of intrathecal sodium nitroprusside on severe chronic vasospasm. Neurol Res (1993) 0.82
Cigarette smoking in renal transplant recipients. Transplant Proc (2004) 0.82
Complement component deficiencies and infection: C5, C8 and C3 deficiencies in three families. Eur J Pediatr (1992) 0.82
The cytoprotective effect of iloprost against carbon tetrachloride induced necrosis in rat liver. Res Commun Mol Pathol Pharmacol (1997) 0.82
Inhibition by nicotine of the vasodilator effect of bradykinin: evidence for a prostacyclin-dependent mechanism. Arch Int Pharmacodyn Ther (1982) 0.81
A new, long-lasting competitive inhibitor of angiotensin. Science (1972) 0.81
Serum IgD concentrations in patients with ataxia telangiectasia and with selective IgA deficiency. Int Arch Allergy Immunol (1998) 0.81
Histamine receptors in the isolated rat stomach fundus and rabbit aortic strips. Pharmacology (1977) 0.81
Ataxia-telangiectasia: linkage analysis of chromosome 11q22-23 markers in Turkish families. FASEB J (1992) 0.81
The presence of histamine H2-receptors in rabbit kidney. Arch Int Pharmacodyn Ther (1974) 0.81
Captopril increases endothelin serum concentrations and preserves intestinal mucosa after mesenteric ischemia-reperfusion injury. Res Exp Med (Berl) (1994) 0.80
The effects of angiotensin I and angiotensin II on the isolated tracheal muscle of the cat. J Pharm Pharmacol (1976) 0.80
Potentiation of the morphine-induced respiratory rate depression by captopril. Eur J Pharmacol (1981) 0.80
HLA antigens in subacute sclerosing panencephalitis. Arch Neurol (1983) 0.80
Alterations by captopril of pain reactions due to thermal stimulation of the mouse foot: interactions with morphine, naloxone and aprotinin. Eur J Pharmacol (1980) 0.80
A case of X linked agammaglobulinaemia complicated with systemic amyloidosis. Arch Dis Child (1998) 0.80
Intravenous single-dose tramadol versus meperidine for pain relief in renal colic. Eur J Anaesthesiol (2002) 0.80
Endothelin-1-induced oedema in rat and guinea-pig isolated perfused lungs. Arch Int Pharmacodyn Ther (1993) 0.80
Skewing of X-chromosome inactivation in three generations of carriers with X-linked chronic granulomatous disease within one family. Eur J Clin Invest (2006) 0.80
Reversal by acetylsalicylic acid of the captopril-induced inhibition of angiotensin converting enzyme in the hindquarters of guinea-pig. Arch Int Pharmacodyn Ther (1982) 0.80
Alopecia universalis in a patient with common variable immunodeficiency. Pediatr Dermatol (1999) 0.80
Seasonal variation in the effect of a fixed dose of heparin on activated clotting time in patients prepared for open-heart surgery. Chronobiol Int (2001) 0.80
Homozygous C2 deficiency: association with defective alternative pathway function and immunoglobulin deficiency. Int Arch Allergy Immunol (1996) 0.80
A comparison between the prostaglandin releasing effects of angiotensin II and angiotensin III. Agents Actions (1977) 0.79
A marked H1-receptor-mediated vasodilator effect of histamine in the isolated perfused rat heart. Eur J Pharmacol (1984) 0.79
Effect of prostaglandin E2 on the pressor response to periarterial stimulation and norepinephrine of the isolated perfused rabbit kidney. Prostaglandins (1975) 0.79
Release of catecholamines from the adrenal medulla by prostaglandin E1. Eur J Pharmacol (1967) 0.79
Assessment and comparison of endothelial function between dialysis and kidney transplant patients. Transplant Proc (2006) 0.79
The incidence of non-classical 21-hydroxylase deficiency in hirsute adolescent girls. Gynecol Endocrinol (1992) 0.79
Isolated cutaneous response to granulocyte-monocyte colony stimulating factor in fatal idiopathic disseminated Bacillus-Calmette-Guerin infection. Eur J Pediatr (2000) 0.79
Studies on lymphocyte cell surface in ataxia-telangiectasia. Clin Exp Immunol (1985) 0.79
Comparison of different de-endothelization procedures in the isolated rat thoracic aorta: a short communication. Res Commun Mol Pathol Pharmacol (2003) 0.79
Superoxide dismutase and allopurinol prevent the pressor effects of angiotensin II and histamine in the guinea-pig isolated perfused lung exposed to hypoxia. Gen Pharmacol (1992) 0.79
Biological-time-dependent differences in effect of verapamil on rat aorta and influence of endothelium. Chronobiol Int (1999) 0.79
High degree of conversion of angiotensin I to angiotensin II in the mesenteric circulation of the isolated perfused terminal ileum of the cat. Arch Int Physiol Biochim (1975) 0.78
Role of endogenous prostaglandins on the conversion of angiotensin I to angiotensin II in the pulmonary circulation. Prostaglandins Med (1979) 0.78
Modulation by endothelium of the vascular effects of angiotensin II. Agents Actions (1987) 0.78
Potentiation of the effect of histamine by PGE2 in the isolated perfused rabbit kidney and guinea-pig lung. Experientia (1975) 0.78
Nicotine is a competitive antagonist for H1-receptors in smooth muscles. Arch Int Pharmacodyn Ther (1985) 0.78