Absence of the alpha6(IV) chain of collagen type IV in Alport syndrome is related to a failure at the protein assembly level and does not result in diffuse leiomyomatosis.

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Published in Am J Pathol on June 01, 1999

Authors

K Zheng1, S Harvey, Y Sado, I Naito, Y Ninomiya, R Jacobs, P S Thorner

Author Affiliations

1: Division of Pathology, Hospital for Sick Children, University of Toronto, Canada.

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