Published in J Pediatr on May 01, 1975
Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs. Science (2008) 6.28
Prevalence of liver disease in cystic fibrosis. Arch Dis Child (1991) 1.61
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis. Am J Pathol (2010) 1.60
An approach for treating the hepatobiliary disease of cystic fibrosis by somatic gene transfer. Proc Natl Acad Sci U S A (1993) 1.57
Conjugated bile acids in serum and secretions in response to cholecystokinin/secretin stimulation in children with cystic fibrosis. Gut (1985) 1.18
Current clinical management of hepatic problems in cystic fibrosis. J R Soc Med (1986) 1.14
Development of a porcine model of cystic fibrosis. Trans Am Clin Climatol Assoc (2009) 1.02
Pathophysiological basis of liver disease in cystic fibrosis employing a DeltaF508 mouse model. Am J Physiol Gastrointest Liver Physiol (2008) 0.95
Immune responses to liver membrane antigens in patients with cystic fibrosis and liver disease. Arch Dis Child (1980) 0.90
Neonatal cholestasis as the presenting feature in cystic fibrosis. Arch Dis Child (1996) 0.90
Pathophysiological preconditions promoting mixed "black" pigment plus cholesterol gallstones in a DeltaF508 mouse model of cystic fibrosis. Am J Physiol Gastrointest Liver Physiol (2010) 0.84
Hepatolithiasis and cholangiocarcinoma in cystic fibrosis: a case series and review of the literature. Dig Dis Sci (2007) 0.81
Immunoassay of serum conjugates of cholic acid in cystic fibrosis. J Clin Pathol (1980) 0.79
Ursodeoxycholic acid in cystic fibrosis-related liver disease: a systematic review. J R Soc Med (1997) 0.78
Serum glutathione S-transferase B1 activity as an index of liver function in cystic fibrosis. J Clin Pathol (1995) 0.75
THE CULTIVATION OF THE GRANULES OF VACCINIA VIRUS. J Exp Med (1926) 3.11
Pathology of cystic fibrosis review of the literature and comparison with 146 autopsied cases. Perspect Pediatr Pathol (1975) 3.03
The local nature of immunity in tuberculosis, illustrated histochemically in dermal BCG lesions. J Immunol (1968) 2.71
Unexplained bronchopulmonary disease with inflammatory bowel disease. Arch Intern Med (1976) 2.54
Observations in cystic fibrosis of the pancreas. 3. Pulmonary lesions. Johns Hopkins Med J (1968) 1.50
Failure of penicillin in a newborn with congenital syphilis. JAMA (1970) 1.46
Intravascular haemolysis with experimentally produced vascular thrombi. Br J Haematol (1967) 1.45
Unique anomalies in cephalothoracopagus janiceps conjoined twins with implications for multiple mechanisms in the abnormal embryogenesis. Teratology (1990) 1.44
Ultrastructural changes in the alveolar epithelium in response to Freund's adjuvant. Am J Pathol (1971) 1.30
Cystic fibrosis of the pancreas. Morphologic findings in infants with and without diagnostic pancreatic lesions. Arch Pathol (1973) 1.26
Pulmonary hypoplasia: a morphometric study of the lungs of infants with diaphragmatic hernia, anencephaly, and renal malformations. Pediatrics (1973) 1.25
Pulmonary changes in sickle cell disease. Am Rev Respir Dis (1971) 1.12
Pulmonary alterations in systemic lupus erythematosus. Am Rev Respir Dis (1972) 1.12
A modified apparatus for fixing lungs to study the pathology of emphysema. Am Rev Respir Dis (1967) 1.08
Disseminated BCG in twin boys with presumed chronic granulomatous disease of childhood. Pediatrics (1971) 1.07
Transection of spinal cord. A rare obstetrical complication of cephalic delivery. Arch Dis Child (1971) 1.04
Cervical mucus in cystic fibrosis: a possible cause of infertility. Am J Obstet Gynecol (1970) 1.01
Vascular lesions in infants with congenital rubella. Circulation (1967) 0.99
Thrombosis in the newborn: comparison between infants of diabetic and nondiabetic mothers. J Pediatr (1965) 0.98
Pulmonary lesions associated with busulfan therapy of chronic myelogenous leukemia. Cancer (1971) 0.98
Cystic fibrosis of the pancreas: structural changes in peripheral airways. Thorax (1968) 0.96
Nonbacterial thrombotic vegetations. Occurrence in neonate, infant, and child, and relation to valvular lesions in cardiac defects. Am J Pathol (1968) 0.96
Experimental lung injury. I. Bacterial pneumonia: ultrastructural, autoradiographic and histochemical observations. Am J Pathol (1973) 0.95
Massive pulmonary hemorrhage in the newborn. I. Pathologic considerations. J Pediatr (1966) 0.95
Mucin histochemistry of human gallbladder: changes in adenocarcinoma, cystic fibrosis, and cholecystitis. J Natl Cancer Inst (1968) 0.95
Some aspects of cardiac pathology in infancy and childhood. IV. Myocardial and coronary lesions in cardiac malformations. Pediatrics (1967) 0.95
The granular pneumonocyte. Absence of phagocytic activity. Am Rev Respir Dis (1970) 0.93
Myocardial lesions in patients with cystic fibrosis of the pancreas. Johns Hopkins Med J (1973) 0.93
Lymphangiectasis and other pulmonary lesions in the asplenia syndrome. Arch Pathol (1970) 0.90
Alveolar macrophages in perinatal infants. Pediatrics (1984) 0.90
Medical mucoid lesions of the pulmonary artery in cystic fibrosis, pulmonary hypertension, and other disorders. Lab Invest (1974) 0.90
Pathological lesions due to congenital rubella. Arch Pathol (1969) 0.89
Similarity of the tracheobronchial mucous glands and epithelium in infants with and without cystic fibrosis. Hum Pathol (1981) 0.88
Fetal gonorrhea with deep tissue infection occurring in utero. Pediatrics (1982) 0.88
Observations on cystic fibrosis of the pancreas. VI. The uterine cervix. J Pediatr (1970) 0.87
Metastatic calcification in cystic fibrosis. A report of two cases. Radiology (1970) 0.87
Observations on cystic fibrosis of the pancreas. V. Developmental changes in the male genital system. J Pediatr (1969) 0.86
Easy bruisability and terminal coma in a "normal" 5-month-old infant. J Pediatr (1976) 0.86
Differential pathology of nasal polyps in cystic fibrosis and atopy. Lab Invest (1979) 0.86
Retroperitoneal and periarterial fibrosis. Arch Pathol (1967) 0.85
Development of lymphoid tissues in the human embryo and early fetus. Arch Pathol (1970) 0.84
Jejunal atresia in twins with presumed congenital rubella. Lancet (1969) 0.83
Fetal and neonatal development of lymphoid tissues. Arch Pathol (1971) 0.82
Rheumatic pneumonitis. Chest (1972) 0.82
Cyst formation in the outer adrenal cortex. Studies in the human fetus and newborn. Arch Pathol (1969) 0.81
Reticular cell response to transplants. Reactive changes in the rabbit appendix. Arch Pathol (1969) 0.81
Some aspects of cardiac pathology in infancy and childhood. 3. Coronary embolism. Johns Hopkins Med J (1967) 0.80
Congenital syphilis in the newborn infant: clinical and pathological observations in recent cases. Johns Hopkins Med J (1971) 0.80
Histochemical beta-glucuronidase distribution in mammalian tissue as detected by 5-bromo-4-chloroindol-3-yl-beta-D-glucopyruroniside. Lab Invest (1967) 0.79
Prolonged obstructive jaundice and giant cell hepatitis in an infant with cystic fibrosis. J Pediatr (1977) 0.79
Hepatic lesions in the congenital rubella syndrome. J Pediatr (1967) 0.79
Pulmonary surfactant in the immature infant. Am J Clin Pathol (1966) 0.79
Experimental irradiated arthrospore vaccine against coccidioidomycosis in mice. J Bacteriol (1967) 0.79
Hyaline membranes in full-size infants. Virchows Arch Pathol Anat Physiol Klin Med (1966) 0.79
Cystic fibrosis manifested as focal biliary cirrhosis in a newborn infant with congenital heart disease. Johns Hopkins Med J (1974) 0.79
Intrauterine rubella infection. Perspect Pediatr Pathol (1973) 0.79
Hydrolytic enzymes in the neonatal rat lung. Am Rev Respir Dis (1969) 0.78
Persistence of virulent Treponema pallidum despite penicillin therapy in congenital syphilis. Am J Ophthalmol (1972) 0.78
Morphologic changes in the fetal rabbit kidney after intrauterine ureteral ligation. Invest Urol (1970) 0.78
Changing concepts in the management of intestinal atresia. Surg Clin North Am (1970) 0.78
Congenital rubella syndrome: the late effects and their relation to early lesions. Perspect Pediatr Pathol (1981) 0.77
Letter: Congenital cytomegalovirus infection and bileduct obstruction in newborn infant with cystic fibrosis of pancreas. Lancet (1973) 0.76
Inheritance in epidermolysis bullosa letalis. J Med Genet (1968) 0.75
Ultrastructure of human pulmonary alveolar lesions. N Y State J Med (1976) 0.75
Arterial thrombosis (paradoxical embolism) in association with transposition of the great vessels. Johns Hopkins Med J (1969) 0.75
Mosaic trisomy 7 and renal dysplasia. Am J Med Genet (1987) 0.75
Heterotopic fallopian tube. Am J Obstet Gynecol (1977) 0.75
The histochemical demonstration of beta-D-glucuronidase in the reticuloendothelial system. Experientia (1967) 0.75
Ventricular endocardial fibroelastosis. Basis for its presence or absence in cases of pulmonic and aortic atresia. Arch Pathol (1969) 0.75
Intravascular hematopoiesis in chorionic villi. Am J Clin Pathol (1983) 0.75
Clinical pathological conference. J Pediatr (1968) 0.75
Ontogeny of the inflammatory response in the fetal rat. Biol Neonate (1980) 0.75
Histochemical demonstration of lysosomal hydrolase activity in endometrial mononuclear cells. I. Normal endometrium. Am J Obstet Gynecol (1975) 0.75
Anatomic malformations of the lower respiratory tract. Birth Defects Orig Artic Ser (1974) 0.75
Pathogenesis of biliary atresia. Pediatrics (1986) 0.75
Cardiac lesions in hypertensive infants and children. Arch Pathol (1967) 0.75
Establishment of replicating long-term lines of rabbit macrophages and lymphocytes. J Immunol Methods (1975) 0.75
Observations on the human corpus luteum: histochemical changes during development and involution. Am J Obstet Gynecol (1976) 0.75
Histochemical demonstration of lysosomal hydrolase activity in endometrial mononuclear cells. II. Abnormal endometrium. Am J Obstet Gynecol (1975) 0.75
Mitoses in peripheral pulmonary epithelium: the effect of colchicine. Anat Rec (1979) 0.75