Published in Exp Cell Res on August 01, 2002
ANT2 isoform required for cancer cell glycolysis. J Bioenerg Biomembr (2005) 1.26
New insights into the bioenergetics of mitochondrial disorders using intracellular ATP reporters. Mol Biol Cell (2003) 1.02
Do mitochondria regulate the heat-shock response in Saccharomyces cerevisiae? Curr Genet (2005) 0.82
Generating Rho-0 Cells Using Mesenchymal Stem Cell Lines. PLoS One (2016) 0.75
OPA1 mutations induce mitochondrial DNA instability and optic atrophy 'plus' phenotypes. Brain (2007) 3.35
The MFN2 gene is responsible for mitochondrial DNA instability and optic atrophy 'plus' phenotype. Brain (2011) 3.04
The eIF2α/ATF4 pathway is essential for stress-induced autophagy gene expression. Nucleic Acids Res (2013) 1.79
Adenine nucleotide translocase 2 is a key mitochondrial protein in cancer metabolism. Biochim Biophys Acta (2010) 1.79
Molecular screening of 980 cases of suspected hereditary optic neuropathy with a report on 77 novel OPA1 mutations. Hum Mutat (2009) 1.67
Heterozygous OPA1 mutations in Behr syndrome. Brain (2010) 1.57
Low-dose terlipressin improves systemic and splanchnic hemodynamics in fluid-challenged endotoxic rats. Crit Care Med (2003) 1.55
eOPA1: an online database for OPA1 mutations. Hum Mutat (2005) 1.43
OPA1-associated disorders: phenotypes and pathophysiology. Int J Biochem Cell Biol (2009) 1.40
Mechanisms of azole resistance in petite mutants of Candida glabrata. Antimicrob Agents Chemother (2004) 1.37
Mitochondrial dynamics and disease, OPA1. Biochim Biophys Acta (2006) 1.35
Two-step differential expression analysis reveals a new set of genes involved in thyroid oncocytic tumors. J Clin Endocrinol Metab (2004) 1.35
Melanin is an essential component for the integrity of the cell wall of Aspergillus fumigatus conidia. BMC Microbiol (2009) 1.34
Hereditary optic neuropathies share a common mitochondrial coupling defect. Ann Neurol (2008) 1.33
Hemodynamic and antifibrotic effects of losartan in rats with liver fibrosis and/or portal hypertension. J Hepatol (2002) 1.32
Effects of OPA1 mutations on mitochondrial morphology and apoptosis: relevance to ADOA pathogenesis. J Cell Physiol (2007) 1.30
Structure and chromosomal distribution of human mitochondrial pseudogenes. Genomics (2002) 1.27
ANT2 isoform required for cancer cell glycolysis. J Bioenerg Biomembr (2005) 1.26
Mechanisms of azole resistance in a clinical isolate of Candida tropicalis. Antimicrob Agents Chemother (2005) 1.21
OPA1 functions in mitochondria and dysfunctions in optic nerve. Int J Biochem Cell Biol (2009) 1.19
Transcriptional profiling reveals coordinated up-regulation of oxidative metabolism genes in thyroid oncocytic tumors. J Clin Endocrinol Metab (2004) 1.19
OPA1 R445H mutation in optic atrophy associated with sensorineural deafness. Ann Neurol (2005) 1.18
OPA1 links human mitochondrial genome maintenance to mtDNA replication and distribution. Genome Res (2010) 1.17
Leigh-like encephalopathy complicating Leber's hereditary optic neuropathy. Ann Neurol (2002) 1.14
PGC-1-related coactivator and targets are upregulated in thyroid oncocytoma. Biochem Biophys Res Commun (2003) 1.14
Mitochondrial coupling defect in Charcot-Marie-Tooth type 2A disease. Ann Neurol (2007) 1.13
Mitochondrial dysfunction and pathophysiology of Charcot-Marie-Tooth disease involving GDAP1 mutations. Exp Neurol (2010) 1.12
Dominant optic atrophy. Orphanet J Rare Dis (2012) 1.11
Whole mitochondrial genome screening in maternally inherited non-syndromic hearing impairment using a microarray resequencing mitochondrial DNA chip. Eur J Hum Genet (2007) 1.10
Quantification of mitochondrial DNA deletion, depletion, and overreplication: application to diagnosis. Clin Chem (2003) 1.10
High birth weight and early postnatal weight gain protect obese children and adolescents from truncal adiposity and insulin resistance: metabolically healthy but obese subjects? Diabetes Care (2008) 1.08
Effects of hydrogen sulfide on hemodynamics, inflammatory response and oxidative stress during resuscitated hemorrhagic shock in rats. Crit Care (2010) 1.08
Maternal smoking is associated with mitochondrial DNA depletion and respiratory chain complex III deficiency in placenta. Am J Physiol Endocrinol Metab (2005) 1.03
The human OPA1delTTAG mutation induces premature age-related systemic neurodegeneration in mouse. Brain (2012) 1.03
Estrogen-related receptor alpha modulates lactate dehydrogenase activity in thyroid tumors. PLoS One (2013) 1.00
Fourteen novel OPA1 mutations in autosomal dominant optic atrophy including two de novo mutations in sporadic optic atrophy. Hum Mutat (2003) 0.99
Biological consequences of petite mutations in Candida glabrata. J Antimicrob Chemother (2005) 0.98
Resveratrol induces a mitochondrial complex I-dependent increase in NADH oxidation responsible for sirtuin activation in liver cells. J Biol Chem (2013) 0.98
Low serum testosterone assayed by liquid chromatography-tandem mass spectrometry. Comparison with five immunoassay techniques. Clin Chim Acta (2007) 0.97
Dynamic regulation of mitochondrial network and oxidative functions during 3T3-L1 fat cell differentiation. J Physiol Biochem (2011) 0.97
Mitochondrial DNA in the oocyte and the developing embryo. Curr Top Dev Biol (2007) 0.97
Rare primary mitochondrial DNA mutations and probable synergistic variants in Leber's hereditary optic neuropathy. PLoS One (2012) 0.96
Comparison of spheroids formed by rat glioma stem cells and neural stem cells reveals differences in glucose metabolism and promising therapeutic applications. J Biol Chem (2012) 0.96
Increase of mitochondrial DNA content and transcripts in early bovine embryogenesis associated with upregulation of mtTFA and NRF1 transcription factors. Reprod Biol Endocrinol (2005) 0.94
Quantitative two-dimensional HRMAS 1H-NMR spectroscopy-based metabolite profiling of human cancer cell lines and response to chemotherapy. Magn Reson Med (2010) 0.93
Reversible optic neuropathy with OPA1 exon 5b mutation. Ann Neurol (2008) 0.93
Experimental determination of organelle targeting-peptide cleavage sites using transient expression of green fluorescent protein translational fusions. Anal Biochem (2012) 0.92
Effects of the cannabinoid CB1 antagonist rimonabant on hepatic mitochondrial function in rats fed a high-fat diet. Am J Physiol Endocrinol Metab (2009) 0.92
Dinitrophenol-induced mitochondrial uncoupling in vivo triggers respiratory adaptation in HepG2 cells. Biochim Biophys Acta (2005) 0.92
ANT2 expression under hypoxic conditions produces opposite cell-cycle behavior in 143B and HepG2 cancer cells. Mol Carcinog (2005) 0.92
Papilloedema and MRI enhancement of the prechiasmal optic nerve at the acute stage of Leber hereditary optic neuropathy. J Neurol Neurosurg Psychiatry (2010) 0.91
Gene profiling reveals specific oncogenic mechanisms and signaling pathways in oncocytic and papillary thyroid carcinoma. Oncogene (2005) 0.91
Random mtDNA deletions and functional consequence in aged human skeletal muscle. Biochem Biophys Res Commun (2005) 0.91
The association of autosomal dominant optic atrophy and moderate deafness may be due to the R445H mutation in the OPA1 gene. Am J Ophthalmol (2003) 0.90
Bioenergetic defect associated with mKATP channel opening in a mouse model carrying a mitofusin 2 mutation. FASEB J (2011) 0.89
Genetically determined optic neuropathies. Curr Opin Neurol (2010) 0.89
Diagnosis of myotubular myopathy in the oldest known manifesting female carrier: a clinical and genetic study. Neuromuscul Disord (2007) 0.89
Mitochondrial complex I deficiency in GDAP1-related autosomal dominant Charcot-Marie-Tooth disease (CMT2K). Neurogenetics (2008) 0.89
Mitochondrial bioenergetic background confers a survival advantage to HepG2 cells in response to chemotherapy. Mol Carcinog (2009) 0.89
Metabolically induced heteroplasmy shifting and l-arginine treatment reduce the energetic defect in a neuronal-like model of MELAS. Biochim Biophys Acta (2012) 0.89
Hereditary spastic paraplegia-like disorder due to a mitochondrial ATP6 gene point mutation. Mitochondrion (2010) 0.88
Adenine nucleotide translocator promotes oxidative phosphorylation and mild uncoupling in mitochondria after dexamethasone treatment. Am J Physiol Endocrinol Metab (2007) 0.88
Mitochondrial energy metabolism in a model of undernutrition induced by dexamethasone. Br J Nutr (2003) 0.87
Prevalence of rare mitochondrial DNA mutations in mitochondrial disorders. J Med Genet (2013) 0.87
MFN2, a new gene responsible for mitochondrial DNA depletion. Brain (2012) 0.87