1
|
Functional delineation and differentiation dynamics of human CD4+ T cells expressing the FoxP3 transcription factor.
|
Immunity
|
2009
|
9.01
|
2
|
NOD/SCID/gamma(c)(null) mouse: an excellent recipient mouse model for engraftment of human cells.
|
Blood
|
2002
|
7.78
|
3
|
Generation of pluripotent stem cells from neonatal mouse testis.
|
Cell
|
2004
|
3.95
|
4
|
Complete reconstitution of human lymphocytes from cord blood CD34+ cells using the NOD/SCID/gammacnull mice model.
|
Blood
|
2003
|
2.53
|
5
|
Direct hematological toxicity and illegitimate chromosomal recombination caused by the systemic activation of CreERT2.
|
J Immunol
|
2009
|
2.44
|
6
|
Early-onset sarcoidosis and CARD15 mutations with constitutive nuclear factor-kappaB activation: common genetic etiology with Blau syndrome.
|
Blood
|
2004
|
2.32
|
7
|
Reduced Numbers and Proapoptotic Features of Mucosal-associated Invariant T Cells as a Characteristic Finding in Patients with Inflammatory Bowel Disease.
|
Inflamm Bowel Dis
|
2015
|
2.13
|
8
|
Disease-associated mutations in CIAS1 induce cathepsin B-dependent rapid cell death of human THP-1 monocytic cells.
|
Blood
|
2007
|
2.00
|
9
|
Disease-associated CIAS1 mutations induce monocyte death, revealing low-level mosaicism in mutation-negative cryopyrin-associated periodic syndrome patients.
|
Blood
|
2007
|
1.69
|
10
|
High incidence of NLRP3 somatic mosaicism in patients with chronic infantile neurologic, cutaneous, articular syndrome: results of an International Multicenter Collaborative Study.
|
Arthritis Rheum
|
2011
|
1.61
|
11
|
Somatic mosaicism of CIAS1 in a patient with chronic infantile neurologic, cutaneous, articular syndrome.
|
Arthritis Rheum
|
2005
|
1.59
|
12
|
The effects of cardioactive drugs on cardiomyocytes derived from human induced pluripotent stem cells.
|
Biochem Biophys Res Commun
|
2009
|
1.45
|
13
|
Limited response to CRH stimulation tests at 2 weeks of age in preterm infants born at less than 30 weeks of gestational age.
|
Clin Endocrinol (Oxf)
|
2013
|
1.44
|
14
|
Birth order effect on childhood food allergy.
|
Pediatr Allergy Immunol
|
2012
|
1.41
|
15
|
Acetylation of GATA-4 is involved in the differentiation of embryonic stem cells into cardiac myocytes.
|
J Biol Chem
|
2005
|
1.40
|
16
|
Generation of skeletal muscle stem/progenitor cells from murine induced pluripotent stem cells.
|
FASEB J
|
2010
|
1.38
|
17
|
Role of the NOD2 genotype in the clinical phenotype of Blau syndrome and early-onset sarcoidosis.
|
Arthritis Rheum
|
2009
|
1.33
|
18
|
Cell line-dependent differentiation of induced pluripotent stem cells into cardiomyocytes in mice.
|
Cardiovasc Res
|
2010
|
1.21
|
19
|
Isolation and characterization of bone marrow-derived mesenchymal progenitor cells with myogenic and neuronal properties.
|
Exp Cell Res
|
2007
|
1.20
|
20
|
Detection of base substitution-type somatic mosaicism of the NLRP3 gene with >99.9% statistical confidence by massively parallel sequencing.
|
DNA Res
|
2012
|
1.16
|
21
|
Generation of transplantable, functional satellite-like cells from mouse embryonic stem cells.
|
FASEB J
|
2009
|
1.15
|
22
|
Selective infection of CD4+ effector memory T lymphocytes leads to preferential depletion of memory T lymphocytes in R5 HIV-1-infected humanized NOD/SCID/IL-2Rgammanull mice.
|
Virology
|
2009
|
1.11
|
23
|
Selective development of myogenic mesenchymal cells from human embryonic and induced pluripotent stem cells.
|
PLoS One
|
2012
|
1.10
|
24
|
Prospective characterization of neural stem cells by flow cytometry analysis using a combination of surface markers.
|
J Neurosci Res
|
2005
|
1.07
|
25
|
Development of primitive and definitive hematopoiesis from nonhuman primate embryonic stem cells in vitro.
|
Development
|
2004
|
1.06
|
26
|
X-linked ectodermal dysplasia and immunodeficiency caused by reversion mosaicism of NEMO reveals a critical role for NEMO in human T-cell development and/or survival.
|
Blood
|
2004
|
1.05
|
27
|
Side population cells contribute to the genesis of human endometrium.
|
Fertil Steril
|
2008
|
1.03
|
28
|
Impaired neutrophil maturation in truncated murine G-CSF receptor-transgenic mice.
|
Blood
|
2003
|
1.03
|
29
|
A novel serum-free monolayer culture for orderly hematopoietic differentiation of human pluripotent cells via mesodermal progenitors.
|
PLoS One
|
2011
|
1.02
|
30
|
Induced pluripotent stem cells from CINCA syndrome patients as a model for dissecting somatic mosaicism and drug discovery.
|
Blood
|
2012
|
1.01
|
31
|
Autosomal dominant anhidrotic ectodermal dysplasia with immunodeficiency caused by a novel NFKBIA mutation, p.Ser36Tyr, presents with mild ectodermal dysplasia and non-infectious systemic inflammation.
|
J Clin Immunol
|
2013
|
1.00
|
32
|
Diagnosis and treatment in anhidrotic ectodermal dysplasia with immunodeficiency.
|
Allergol Int
|
2012
|
1.00
|
33
|
Generation of cardiac and endothelial cells from neonatal mouse testis-derived multipotent germline stem cells.
|
Stem Cells
|
2007
|
1.00
|
34
|
Novel method for efficient production of multipotential hematopoietic progenitors from human embryonic stem cells.
|
Int J Hematol
|
2007
|
1.00
|
35
|
Flk1(+) cardiac stem/progenitor cells derived from embryonic stem cells improve cardiac function in a dilated cardiomyopathy mouse model.
|
Cardiovasc Res
|
2007
|
1.00
|
36
|
Long-term extensive expansion of mouse hepatic stem/progenitor cells in a novel serum-free culture system.
|
Gastroenterology
|
2005
|
0.98
|
37
|
Human cord blood CD34+ cells develop into hepatocytes in the livers of NOD/SCID/gamma(c)null mice through cell fusion.
|
FASEB J
|
2007
|
0.98
|
38
|
Human umbilical cord-derived mesenchymal stromal cells differentiate into functional Schwann cells that sustain peripheral nerve regeneration.
|
J Neuropathol Exp Neurol
|
2010
|
0.98
|
39
|
Development of both human connective tissue-type and mucosal-type mast cells in mice from hematopoietic stem cells with identical distribution pattern to human body.
|
Blood
|
2003
|
0.97
|
40
|
Tool-use learning induces BDNF expression in a selective portion of monkey anterior parietal cortex.
|
Brain Res Mol Brain Res
|
2002
|
0.96
|
41
|
Neutrophil differentiation from human-induced pluripotent stem cells.
|
J Cell Physiol
|
2011
|
0.93
|
42
|
Dominant-negative STAT1 SH2 domain mutations in unrelated patients with Mendelian susceptibility to mycobacterial disease.
|
Hum Mutat
|
2012
|
0.93
|
43
|
Orderly hematopoietic development of induced pluripotent stem cells via Flk-1(+) hemoangiogenic progenitors.
|
J Cell Physiol
|
2009
|
0.92
|
44
|
Safety and efficacy of canakinumab in Japanese patients with phenotypes of cryopyrin-associated periodic syndrome as established in the first open-label, phase-3 pivotal study (24-week results).
|
Clin Exp Rheumatol
|
2013
|
0.92
|
45
|
Bone marrow engraftment but limited expansion of hematopoietic cells from multipotent germline stem cells derived from neonatal mouse testis.
|
Exp Hematol
|
2009
|
0.92
|
46
|
Robust and highly-efficient differentiation of functional monocytic cells from human pluripotent stem cells under serum- and feeder cell-free conditions.
|
PLoS One
|
2013
|
0.91
|
47
|
Nationwide survey of patients with primary immunodeficiency diseases in Japan.
|
J Clin Immunol
|
2011
|
0.91
|
48
|
A neurosphere-derived factor, cystatin C, supports differentiation of ES cells into neural stem cells.
|
Proc Natl Acad Sci U S A
|
2006
|
0.90
|
49
|
Mutations in SERPINB7, encoding a member of the serine protease inhibitor superfamily, cause Nagashima-type palmoplantar keratosis.
|
Am J Hum Genet
|
2013
|
0.90
|
50
|
Identification of cardiac stem cells with FLK1, CD31, and VE-cadherin expression during embryonic stem cell differentiation.
|
FASEB J
|
2005
|
0.90
|
51
|
Identification and characterization of hemoangiogenic progenitors during cynomolgus monkey embryonic stem cell differentiation.
|
Stem Cells
|
2006
|
0.90
|
52
|
SPINK5 polymorphism is associated with disease severity and food allergy in children with atopic dermatitis.
|
J Allergy Clin Immunol
|
2005
|
0.90
|
53
|
Multiple reversions of an IL2RG mutation restore T cell function in an X-linked severe combined immunodeficiency patient.
|
J Clin Immunol
|
2012
|
0.89
|
54
|
Tool-use learning selectively induces expression of brain-derived neurotrophic factor, its receptor trkB, and neurotrophin 3 in the intraparietal multisensorycortex of monkeys.
|
Brain Res Cogn Brain Res
|
2002
|
0.89
|
55
|
Rapid diagnosis of FHL3 by flow cytometric detection of intraplatelet Munc13-4 protein.
|
Blood
|
2011
|
0.88
|
56
|
Sequential analysis of alpha- and beta-globin gene expression during erythropoietic differentiation from primate embryonic stem cells.
|
Stem Cells
|
2006
|
0.88
|
57
|
Direct development of functionally mature tryptase/chymase double-positive connective tissue-type mast cells from primate embryonic stem cells.
|
Stem Cells
|
2007
|
0.88
|
58
|
Identification of hepatic niche harboring human acute lymphoblastic leukemic cells via the SDF-1/CXCR4 axis.
|
PLoS One
|
2011
|
0.88
|
59
|
Frequent somatic mosaicism of NEMO in T cells of patients with X-linked anhidrotic ectodermal dysplasia with immunodeficiency.
|
Blood
|
2012
|
0.87
|
60
|
Loss of Borealin/DasraB leads to defective cell proliferation, p53 accumulation and early embryonic lethality.
|
Mech Dev
|
2008
|
0.87
|
61
|
Long-term culture of postnatal mouse hepatic stem/progenitor cells and their relative developmental hierarchy.
|
Stem Cells
|
2007
|
0.85
|
62
|
Changing prevalence and severity of childhood allergic diseases in kyoto, Japan, from 1996 to 2006.
|
Allergol Int
|
2009
|
0.85
|
63
|
Subtypes of familial hemophagocytic lymphohistiocytosis in Japan based on genetic and functional analyses of cytotoxic T lymphocytes.
|
PLoS One
|
2010
|
0.85
|
64
|
Direct visualization of transplanted hematopoietic cell reconstitution in intact mouse organs indicates the presence of a niche.
|
Exp Hematol
|
2003
|
0.85
|
65
|
Ring/marker chromosome derived from chromosome 7 in childhood acute megakaryoblastic leukemia with monosomy 7.
|
Int J Hematol
|
2010
|
0.85
|
66
|
Disseminated BCG infection mimicking metastatic nasopharyngeal carcinoma in an immunodeficient child with a novel hypomorphic NEMO mutation.
|
J Clin Immunol
|
2011
|
0.85
|
67
|
Successful treatment with infliximab for inflammatory colitis in a patient with X-linked anhidrotic ectodermal dysplasia with immunodeficiency.
|
J Clin Immunol
|
2011
|
0.84
|
68
|
Genetic correction of HAX1 in induced pluripotent stem cells from a patient with severe congenital neutropenia improves defective granulopoiesis.
|
Haematologica
|
2013
|
0.84
|
69
|
Obesity and the prevalence of allergic diseases in schoolchildren.
|
Pediatr Allergy Immunol
|
2008
|
0.84
|
70
|
The CD40-CD40L axis and IFN-γ play critical roles in Langhans giant cell formation.
|
Int Immunol
|
2011
|
0.84
|
71
|
Heterozygous TREX1 p.Asp18Asn mutation can cause variable neurological symptoms in a family with Aicardi-Goutieres syndrome/familial chilblain lupus.
|
Rheumatology (Oxford)
|
2012
|
0.84
|
72
|
alpha4-Integrin(+) endothelium derived from primate embryonic stem cells generates primitive and definitive hematopoietic cells.
|
Blood
|
2006
|
0.83
|
73
|
The clinical utility of genetic testing for t(8;16)(p11;p13) in congenital acute myeloid leukemia.
|
J Pediatr Hematol Oncol
|
2014
|
0.83
|
74
|
A nationwide survey of Aicardi-Goutières syndrome patients identifies a strong association between dominant TREX1 mutations and chilblain lesions: Japanese cohort study.
|
Rheumatology (Oxford)
|
2013
|
0.83
|
75
|
Differential requirement for the CD40-CD154 costimulatory pathway during Th cell priming by CD8 alpha+ and CD8 alpha- murine dendritic cell subsets.
|
J Immunol
|
2004
|
0.83
|
76
|
Cyclin-dependent kinase 9 forms a complex with GATA4 and is involved in the differentiation of mouse ES cells into cardiomyocytes.
|
J Cell Physiol
|
2011
|
0.83
|
77
|
Sca-1+ endothelial cells (SPECs) reside in the portal area of the liver and contribute to rapid recovery from acute liver disease.
|
Biochem Biophys Res Commun
|
2007
|
0.83
|
78
|
Breastfeeding and the prevalence of allergic diseases in schoolchildren: Does reverse causation matter?
|
Pediatr Allergy Immunol
|
2010
|
0.83
|
79
|
Patient with neonatal-onset chronic hepatitis presenting with mevalonate kinase deficiency with a novel MVK gene mutation.
|
Mod Rheumatol
|
2011
|
0.83
|
80
|
Ttyh1, a Ca(2+)-binding protein localized to the endoplasmic reticulum, is required for early embryonic development.
|
Dev Dyn
|
2010
|
0.82
|
81
|
Increased susceptibility to severe chronic liver damage in CXCR4 conditional knock-out mice.
|
Dig Dis Sci
|
2012
|
0.82
|
82
|
Cortical muscle control of spontaneous movements in human neonates.
|
Eur J Neurosci
|
2014
|
0.82
|
83
|
Efficient assay for evaluating human thrombopoiesis using NOD/SCID mice transplanted with cord blood CD34+ cells.
|
Eur J Haematol
|
2006
|
0.82
|
84
|
Role of bone marrow-derived progenitor cells in cuff-induced vascular injury in mice.
|
Arterioscler Thromb Vasc Biol
|
2004
|
0.81
|
85
|
The effect of past food avoidance due to allergic symptoms on the growth of children at school age.
|
Allergol Int
|
2010
|
0.81
|
86
|
Hyperthyrotropinemia at 2 weeks of age indicates thyroid dysfunction and predicts the occurrence of delayed elevation of thyrotropin in very low birth weight infants.
|
Clin Endocrinol (Oxf)
|
2012
|
0.81
|
87
|
Diagnostic value of salivary cortisol in the CRH stimulation test in premature infants.
|
J Clin Endocrinol Metab
|
2012
|
0.81
|
88
|
Limited ability of antigen-specific Th1 responses to inhibit Th2 cell development in vivo.
|
J Immunol
|
2005
|
0.80
|
89
|
HOX decoy peptide enhances the ex vivo expansion of human umbilical cord blood CD34+ hematopoietic stem cells/hematopoietic progenitor cells.
|
Stem Cells
|
2006
|
0.80
|
90
|
Salivary biomarkers are not suitable for pain assessment in newborns.
|
Early Hum Dev
|
2013
|
0.80
|
91
|
MEFV Variants in Patients with PFAPA Syndrome in Japan.
|
Open Rheumatol J
|
2013
|
0.80
|
92
|
Familial cases of periodic fever with aphthous stomatitis, pharyngitis, and cervical adenitis syndrome.
|
J Pediatr
|
2010
|
0.80
|
93
|
Enhanced chondrogenesis of induced pluripotent stem cells from patients with neonatal-onset multisystem inflammatory disease occurs via the caspase 1-independent cAMP/protein kinase A/CREB pathway.
|
Arthritis Rheumatol
|
2015
|
0.79
|
94
|
Allergic status of schoolchildren with food allergy to eggs, milk or wheat in infancy.
|
Pediatr Allergy Immunol
|
2009
|
0.79
|
95
|
Paroxysmal gaze deviations as the sole manifestation of occipital lobe epilepsy.
|
Seizure
|
2013
|
0.79
|
96
|
Hypergonadotropic hypogonadism and hypersegmented neutrophils in a patient with ataxia-telangiectasia-like disorder: potential diagnostic clues?
|
Am J Med Genet A
|
2014
|
0.79
|
97
|
[Changes in Japanese cedar sensitization rates of Japanese allergic children during the last 15 years].
|
Arerugi
|
2004
|
0.79
|
98
|
MRI gadolinium enhancement precedes neuroradiological findings in acute necrotizing encephalopathy.
|
Brain Dev
|
2012
|
0.79
|
99
|
A case of early-onset sarcoidosis with a six-base deletion in the NOD2 gene.
|
Rheumatology (Oxford)
|
2009
|
0.78
|
100
|
Guidance on the use of canakinumab in patients with cryopyrin-associated periodic syndrome in Japan.
|
Mod Rheumatol
|
2012
|
0.78
|
101
|
Inactivation of fibroblast growth factor binding protein 3 causes anxiety-related behaviors.
|
Mol Cell Neurosci
|
2010
|
0.78
|
102
|
Two different roles of purified CD45+c-Kit+Sca-1+Lin- cells after transplantation in muscles.
|
Stem Cells
|
2005
|
0.78
|
103
|
Derivation of engraftable myogenic precursors from murine ES/iPS cells and generation of disease-specific iPS cells from patients with Duchenne muscular dystrophy (DMD) and other diseases.
|
Rinsho Shinkeigaku
|
2010
|
0.78
|
104
|
Plasma homocysteine, methionine and S-adenosylhomocysteine levels following high-dose methotrexate treatment in pediatric patients with acute lymphoblastic leukemia or Burkitt lymphoma: association with hepatotoxicity.
|
Leuk Lymphoma
|
2013
|
0.78
|
105
|
Effect of eczema on the association between season of birth and food allergy in Japanese children.
|
Pediatr Int
|
2012
|
0.77
|
106
|
[Heterogeneity of HLH pathophysiology and treatment strategies].
|
Rinsho Ketsueki
|
2015
|
0.77
|
107
|
[Epileptic encephalopathy associated with human herpes virus 6 (HHV-6) encephalitis after the second cord blood transplantation in a patient with pediatric acute lymphoblastic leukemia].
|
Rinsho Ketsueki
|
2014
|
0.77
|
108
|
High prevalence of severe circulatory complications with diazoxide in premature infants.
|
Neonatology
|
2014
|
0.77
|
109
|
Neonatal mouse testis-derived multipotent germline stem cells improve the cardiac function of acute ischemic heart mouse model.
|
Biochem Biophys Res Commun
|
2010
|
0.76
|
110
|
Hematopoietic stem cell transplantation with reduced intensity conditioning from a family haploidentical donor in an infant with familial hemophagocytic lymphohistocytosis.
|
Int J Hematol
|
2011
|
0.76
|
111
|
Clonal selection in xenografted TAM recapitulates the evolutionary process of myeloid leukemia in Down syndrome.
|
Blood
|
2013
|
0.76
|
112
|
Reply.
|
Inflamm Bowel Dis
|
2015
|
0.75
|
113
|
Total and low-density lipoprotein cholesterol levels are associated with atopy in schoolchildren.
|
J Pediatr
|
2010
|
0.75
|
114
|
Primary immunodeficiency and related diseases.
|
Allergol Int
|
2012
|
0.75
|
115
|
Obvious optic disc swelling in a patient with cryopyrin-associated periodic syndrome.
|
Clin Ophthalmol
|
2013
|
0.75
|
116
|
Development of CMV retinitis in an antigenemia-negative infant after cord blood transplantation.
|
Rinsho Ketsueki
|
2015
|
0.75
|
117
|
[Hyperimmunoglobulinemia D and periodic fever syndrome].
|
Nihon Rinsho Meneki Gakkai Kaishi
|
2011
|
0.75
|
118
|
Effective cardiac resynchronization therapy for an adolescent patient with dilated cardiomyopathy seven years after mitral valve replacement and septal anterior ventricular exclusion.
|
J Cardiothorac Surg
|
2010
|
0.75
|
119
|
Munc13-4 deficiency with CD5 downregulation on activated CD8+ T cells.
|
Pediatr Int
|
2014
|
0.75
|
120
|
Expression profile analysis of aorta-gonad-mesonephros region-derived stromal cells reveals genes that regulate hematopoiesis.
|
Biochem Biophys Res Commun
|
2008
|
0.75
|
121
|
Pediatric idiopathic TTP diagnosed with decreased ADAMTS13 activity.
|
Pediatr Int
|
2012
|
0.75
|
122
|
Chronic immune-mediated axonal polyneuropathy following umbilical cord blood transplant for childhood-onset cerebral adrenoleukodystrophy.
|
Pediatr Transplant
|
2012
|
0.75
|
123
|
[An approach to the patients with cryopyrin-associated periodic syndrome (CAPS) : a new biologic response modifier, canakinumab].
|
Nihon Rinsho Meneki Gakkai Kaishi
|
2012
|
0.75
|
124
|
Long-term outcome of sirolimus-eluting stent implantation for left main coronary artery stenosis in infancy.
|
Pediatr Cardiol
|
2010
|
0.75
|
125
|
[Efficacy and tolerability of topiramate, lamotrigine, and levetiracetam in children with refractory epilepsy].
|
No To Hattatsu
|
2015
|
0.75
|
126
|
Long-term efficacy of bevacizumab and irinotecan in recurrent pediatric glioblastoma.
|
Pediatr Int
|
2015
|
0.75
|
127
|
Perforation of enteric duplication during chemotherapy for osteosarcoma.
|
Pediatr Int
|
2014
|
0.75
|
128
|
[Diagnosis and consultation rates of allergic diseases in 11-year old schoolchildren, and usefulness of allergy screening test at school].
|
Arerugi
|
2012
|
0.75
|
129
|
Acute lymphoblastic leukemia in a girl with Wilson's disease.
|
Pediatr Int
|
2014
|
0.75
|
130
|
Maturational sequence of neuroblastoma revealed by molecular analysis on cDNA microarrays.
|
Int J Oncol
|
2002
|
0.75
|
131
|
Good response to chemotherapy spares irradiation for extrarenal rhabdoid tumor conferring better activities of daily living.
|
J Pediatr Hematol Oncol
|
2015
|
0.75
|
132
|
Efficacy of Ifosfamide-Cisplatin-Etoposide (ICE) Chemotherapy for a CNS Germinoma in a Child With Down Syndrome.
|
J Pediatr Hematol Oncol
|
2016
|
0.75
|
133
|
[Comparative study on the efficacy and safety of continuous versus twice-daily 3-hour infusion of cyclosporine A in pediatric hematopoietic stem cell transplantation].
|
Rinsho Ketsueki
|
2012
|
0.75
|
134
|
Successful treatment of refractory donor lymphocyte infusion-induced immune-mediated pancytopenia with rituximab.
|
Pediatr Blood Cancer
|
2010
|
0.75
|
135
|
Gastric ulcer and gastroenteritis caused by Epstein-Barr virus during immunosuppressive therapy for a child with systemic juvenile idiopathic arthritis.
|
Rheumatology (Oxford)
|
2012
|
0.75
|
136
|
[Utility of endoscopic ultrasound-guided fine needle aspiration for diagnosis of Burkitt lymphoma in two pediatric cases].
|
Rinsho Ketsueki
|
2013
|
0.75
|
137
|
The NOD/Shi-scid/IL-2Rγ(null) mice xenograft model recapitulates anaplastic large cell lymphoma dissemination to the bladder.
|
Leuk Lymphoma
|
2014
|
0.75
|
138
|
Rituximab-combination chemotherapy achieves a 10th cycle of remission for Burkitt's lymphoma.
|
Pediatr Int
|
2015
|
0.75
|
139
|
[Changes in food allergen sensitization rates of Japanese allergic children during the last 15 years].
|
Arerugi
|
2004
|
0.75
|
140
|
[A girl with dyslexia suspected to have Irlen syndrome, completely relieved by wearing tinted lenses].
|
No To Hattatsu
|
2015
|
0.75
|