Published in Liver Transpl on August 01, 2003
Suggested guidelines for the diagnosis and management of urea cycle disorders. Orphanet J Rare Dis (2012) 2.46
Characterization and outcomes of young infants with acute liver failure. J Pediatr (2011) 0.98
Predictors of survival following liver transplantation in infants: a single-center analysis of more than 200 cases. Transplantation (2010) 0.92
One hundred thirty-two consecutive pediatric liver transplants without hospital mortality: lessons learned and outlook for the future. Ann Surg (2004) 0.91
Neonatal hemochromatosis. J Clin Exp Hepatol (2013) 0.81
Living Related Liver Transplantation in an Infant with Neonatal Hemochromatosis. Pediatr Gastroenterol Hepatol Nutr (2016) 0.75
Hepatobiliary quiz-9 (2014). J Clin Exp Hepatol (2014) 0.75
A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000. J Pediatr (2006) 3.32
Detection of acetaminophen protein adducts in children with acute liver failure of indeterminate cause. Pediatrics (2006) 2.96
Autologous hematopoietic stem cell transplantation in patients with refractory Crohn's disease. Gastroenterology (2005) 2.85
Biliary atresia is associated with CD4+ Th1 cell-mediated portal tract inflammation. Pediatr Res (2004) 2.38
Osteopontin is induced by hedgehog pathway activation and promotes fibrosis progression in nonalcoholic steatohepatitis. Hepatology (2010) 2.37
Guideline for the evaluation of cholestatic jaundice in infants: recommendations of the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition. J Pediatr Gastroenterol Nutr (2004) 2.16
Obese and diabetic db/db mice develop marked liver fibrosis in a model of nonalcoholic steatohepatitis: role of short-form leptin receptors and osteopontin. Am J Physiol Gastrointest Liver Physiol (2004) 2.10
Glyceroluria and neonatal hemochromatosis. J Pediatr Gastroenterol Nutr (2012) 1.98
Severe bile salt export pump deficiency: 82 different ABCB11 mutations in 109 families. Gastroenterology (2008) 1.95
Upregulation of osteopontin expression is involved in the development of nonalcoholic steatohepatitis in a dietary murine model. Am J Physiol Gastrointest Liver Physiol (2004) 1.86
Extrahepatic anomalies in infants with biliary atresia: results of a large prospective North American multicenter study. Hepatology (2013) 1.80
Hepatocellular carcinoma in ten children under five years of age with bile salt export pump deficiency. Hepatology (2006) 1.80
Growth failure and outcomes in infants with biliary atresia: a report from the Biliary Atresia Research Consortium. Hepatology (2007) 1.68
School outcomes in children registered in the studies for pediatric liver transplant (SPLIT) consortium. Liver Transpl (2010) 1.65
Differences in presentation and progression between severe FIC1 and BSEP deficiencies. J Hepatol (2010) 1.60
Partial external biliary diversion for intractable pruritus and xanthomas in Alagille syndrome. Hepatology (2002) 1.58
Cytokeratin 18, a marker of cell death, is increased in children with suspected nonalcoholic fatty liver disease. J Pediatr Gastroenterol Nutr (2008) 1.54
Novel mechanism of fetal hepatocyte injury in congenital alloimmune hepatitis involves the terminal complement cascade. Hepatology (2010) 1.51
Neonatal iron overload and tissue siderosis due to gestational alloimmune liver disease. J Hepatol (2012) 1.49
Graft histology characteristics in long-term survivors of pediatric liver transplantation. Liver Transpl (2008) 1.49
National survey of adult transplant hepatologists on the pediatric-to-adult care transition after liver transplantation. Liver Transpl (2015) 1.41
EEG abnormalities are associated with increased risk of transplant or poor outcome in children with acute liver failure. J Pediatr Gastroenterol Nutr (2014) 1.38
Nonalcoholic steatohepatitis in children: a multicenter clinicopathological study. Hepatology (2009) 1.37
Complete immunosuppression withdrawal and subsequent allograft function among pediatric recipients of parental living donor liver transplants. JAMA (2012) 1.33
Roles of phosphatidylinositol 3-kinase and osteopontin in steatosis and aminotransferase release by hepatocytes treated with methionine-choline-deficient medium. Am J Physiol Gastrointest Liver Physiol (2006) 1.30
Outcomes and risk factors for failure of radiologic treatment of biliary strictures in pediatric liver transplantation recipients. Liver Transpl (2006) 1.28
The PedsQL™ Infant Scales: feasibility, internal consistency reliability, and validity in healthy and ill infants. Qual Life Res (2010) 1.24
Hedgehog activity, epithelial-mesenchymal transitions, and biliary dysmorphogenesis in biliary atresia. Hepatology (2011) 1.22
Health status of children alive 10 years after pediatric liver transplantation performed in the US and Canada: report of the studies of pediatric liver transplantation experience. J Pediatr (2011) 1.20
Pentoxifylline attenuates steatohepatitis induced by the methionine choline deficient diet. J Hepatol (2004) 1.19
Long-term medical management of the pediatric patient after liver transplantation: 2013 practice guideline by the American Association for the Study of Liver Diseases and the American Society of Transplantation. Liver Transpl (2013) 1.19
Health-related quality of life in pediatric liver transplant recipients compared with other chronic disease groups. Pediatr Transplant (2010) 1.19
Mitochondrial reactive oxygen species signal hepatocyte steatosis by regulating the phosphatidylinositol 3-kinase cell survival pathway. J Biol Chem (2007) 1.17
Surgical restoration of portal flow corrects procoagulant and anticoagulant deficiencies associated with extrahepatic portal vein thrombosis. J Pediatr (2003) 1.10
Fatigue and health-related quality of life in pediatric inflammatory bowel disease. Clin Gastroenterol Hepatol (2009) 1.08
Neonatal hemochromatosis: management, outcome, and prevention. Prenat Diagn (2013) 1.02
Outcomes after liver transplantation in young infants. J Pediatr Gastroenterol Nutr (2008) 1.01
Efficacy of fat-soluble vitamin supplementation in infants with biliary atresia. Pediatrics (2012) 1.00
Carnitine treatment inhibits increases in cerebral carnitine esters and glutamate detected by mass spectrometry after hypoxia-ischemia in newborn rats. Stroke (2005) 0.99
Correction of extrahepatic portal vein thrombosis by the mesenteric to left portal vein bypass. Ann Surg (2006) 0.99
Regional variation and use of exception letters for cadaveric liver allocation in children with chronic liver disease. Am J Transplant (2005) 0.98
Characterization and outcomes of young infants with acute liver failure. J Pediatr (2011) 0.98
Treatment of neonatal hemochromatosis with exchange transfusion and intravenous immunoglobulin. J Pediatr (2009) 0.97
Surgically restoring portal blood flow to the liver in children with primary extrahepatic portal vein thrombosis improves fluid neurocognitive ability. Pediatrics (2006) 0.97
Intracranial vascular abnormalities in patients with Alagille syndrome. J Pediatr Gastroenterol Nutr (2005) 0.97
Design and validation of the biliary atresia research consortium histologic assessment system for cholestasis in infancy. Clin Gastroenterol Hepatol (2011) 0.96
Relative elevations of serum alanine and aspartate aminotransferase in muscular dystrophy. J Pediatr Gastroenterol Nutr (2005) 0.93
Fructose and oxidized low-density lipoprotein in pediatric nonalcoholic fatty liver disease: a pilot study. Arch Pediatr Adolesc Med (2009) 0.93
Pediatric transplantation of the kidney, liver and heart: summary report. Pediatr Transplant (2004) 0.90
Hepatocerebral mitochondrial DNA depletion syndrome: clinical and morphologic features of a nuclear gene mutation. J Pediatr Gastroenterol Nutr (2004) 0.89
Increased hepatic expression is a major determinant of serum alanine aminotransferase elevation in mice with nonalcoholic steatohepatitis. Liver Int (2008) 0.89
Survival after liver transplantation for hepatoblastoma: a 2-center experience. J Pediatr Surg (2008) 0.89
Relations of steatosis type, grade, and zonality to histological features in pediatric nonalcoholic fatty liver disease. J Pediatr Gastroenterol Nutr (2011) 0.89
Steatohepatitis develops rapidly in transgenic mice overexpressing Abcb11 and fed a methionine-choline-deficient diet. Am J Physiol Gastrointest Liver Physiol (2005) 0.88
Neonatal hemochromatosis. Gastroenterol Clin North Am (2003) 0.88
Neonatal liver disease. Pediatr Ann (2006) 0.86
PedsQL™ Cognitive Functioning Scale in pediatric liver transplant recipients: feasibility, reliability, and validity. Qual Life Res (2010) 0.85
Chronic acetaminophen exposure in pediatric acute liver failure. Pediatrics (2013) 0.84
Neonatal liver cirrhosis without iron overload caused by gestational alloimmune liver disease. Pediatrics (2012) 0.84
Health related quality of life in patients with biliary atresia surviving with their native liver. J Pediatr (2013) 0.83
Health status of patients with Alagille syndrome. J Pediatr Gastroenterol Nutr (2010) 0.83
Relationship of proximal renal tubular dysgenesis and fetal liver injury in neonatal hemochromatosis. Pediatr Res (2010) 0.82
Hepatic adenoma in an adolescent with elevated androgen levels. J Pediatr Gastroenterol Nutr (2007) 0.81
Histologic characteristics of late cellular rejection, significance of centrilobular injury, and long-term outcome in pediatric liver transplant recipients. Liver Transpl (2006) 0.80
Improved neurocognitive function after radiologic closure of congenital portosystemic shunts. J Pediatr Gastroenterol Nutr (2004) 0.80
Disparate clinical presentation of neonatal hemochromatosis in twins. Pediatrics (2005) 0.80
Presence of multiple bile ducts in the liver graft increases the incidence of biliary complications in pediatric liver transplantation. Liver Transpl (2005) 0.80
Growth impairment in children with extrahepatic portal vein obstruction is improved by mesenterico-left portal vein bypass. J Pediatr Surg (2009) 0.79
Regression of severe fibrotic liver disease in 2 children with neonatal hemochromatosis. J Pediatr Gastroenterol Nutr (2008) 0.79
Fortune telling in biliary atresia: what is in the tea leaves? Liver Transpl (2009) 0.79
Bile composition in Alagille Syndrome and PFIC patients having Partial External Biliary Diversion. BMC Gastroenterol (2008) 0.78
Neuropsychological functioning and health-related quality of life: pediatric acute liver failure study group results. J Pediatr Gastroenterol Nutr (2015) 0.78
Fetal gender and cocaine exposure as determinants of cord blood gamma-glutamyl transferase activity. J Perinatol (2002) 0.78
Medical and surgical management of portal hypertension in children. Curr Treat Options Gastroenterol (2006) 0.78
NUTORC-a transdisciplinary health services and outcomes research team in transplantation. Transl Behav Med (2012) 0.78
Obesity after pediatric liver transplantation: prevalence and risk factors. J Pediatr Gastroenterol Nutr (2012) 0.77
Long-term linear growth and puberty in pediatric liver transplant recipients. J Pediatr (2013) 0.77
Recombinant factor VIIa improves coagulopathy caused by liver failure. J Pediatr Gastroenterol Nutr (2003) 0.77
Pancreatic adenocarcinoma in type 2 progressive familial intrahepatic cholestasis. BMC Gastroenterol (2010) 0.77
Molecular basis of neonatal cholestasis. Pediatr Clin North Am (2002) 0.77
Factors Determining δ-Bilirubin Levels in Infants With Biliary Atresia. J Pediatr Gastroenterol Nutr (2015) 0.77
Bile acid pool dynamics in progressive familial intrahepatic cholestasis with partial external bile diversion. J Pediatr Gastroenterol Nutr (2015) 0.77
Rituximab as therapy for the recurrence of bile salt export pump deficiency after liver transplantation. Liver Transpl (2013) 0.77
Transition from hospital to home following pediatric solid organ transplant: qualitative findings of parent experience. Pediatr Transplant (2014) 0.77
Recurrent low gamma-glutamyl transpeptidase cholestasis following liver transplantation for bile salt export pump (BSEP) disease (posttransplant recurrent BSEP disease). Liver Transpl (2010) 0.76
Approach to optimizing growth, rehabilitation, and neurodevelopmental outcomes in children after solid-organ transplantation. Pediatr Clin North Am (2010) 0.76
Sirolimus as rescue therapy in pediatric autoimmune hepatitis. J Pediatr Gastroenterol Nutr (2014) 0.76
Giant cell hepatitis and immune thrombocytopenic purpura: reversal of liver failure with rituximab therapy. J Pediatr Gastroenterol Nutr (2012) 0.76
Spectral Electroencephalogram Analysis for the Evaluation of Encephalopathy Grade in Children With Acute Liver Failure. Pediatr Crit Care Med (2016) 0.75
Total serum bilirubin predicts fat-soluble vitamin deficiency better than serum bile acids in infants with biliary atresia. J Pediatr Gastroenterol Nutr (2014) 0.75
Acute liver failure in children: the role of defects in fatty acid oxidation. Hepatology (2005) 0.75
Biliary strictures following living donor liver transplantation: even money on a tight squeeze. Pediatr Transplant (2002) 0.75
Pediatric solid organ transplant recipients: transition to home and chronic illness care. Pediatr Transplant (2014) 0.75
Successful resolution of inflammation and increased regulatory T cells in sirolimus-treated post-transplant allograft hepatitis. Pediatr Transplant (2012) 0.75