Published in Pediatrics on August 01, 1963
DISORDERS OF AMINO-ACID TRANSPORT. Br Med J (1964) 1.44
Histidinaemia. Study of relation between clinical and biological findings in 7 subjects. Arch Dis Child (1972) 1.41
BIOCHEMICAL INVESTIGATION OF HISTIDINAEMIA. J Clin Pathol (1964) 1.12
Histidinaemia: a child and his family. Arch Dis Child (1968) 0.99
Further case of histidinaemia. Br Med J (1966) 0.87
Histidine metabolism in experimental protein malnutrition in rats. Biochem J (1965) 0.77
Food intolerance in humans. West J Med (1979) 0.75
Histidinaemia in a consanguineous marriage. J Med Genet (1974) 0.75
The enzymatic spectrophotometric method for determination of uric acid. J Lab Clin Med (1959) 6.43
The nature of the defect in tyrosine metabolism in alcaptonuria. J Biol Chem (1958) 4.90
Uric acid production in gout. J Clin Invest (1961) 3.62
A PARADOXICAL EFFECT OF ACTINOMYCIN D: THE MECHANISM OF REGULATION OF ENZYME SYNTHESIS BY HYDROCORTISONE. Proc Natl Acad Sci U S A (1964) 3.48
The synthesis of glucose-6-phosphate and 6-phosphogluconate. J Biol Chem (1951) 3.41
INDUCTION AND MULTI-SENSITIVE END-PRODUCT REPRESSION IN THE ENZYMIC PATHWAY DEGRADING MANDELATE IN PSEUDOMONAS FLUORESCENS. Biochem J (1965) 2.75
The enzymatic conversion of 6-phosphogluconate to ribulose-5-phosphate and ribose-5-phosphate. J Biol Chem (1951) 2.65
The old and new concepts of acute gouty arthritis. Arthritis Rheum (1962) 1.97
Diagnostic significance of hyperuricemia in arthritis. N Engl J Med (1961) 1.78
The plasma ammonia and glutamine content in patients with hepatic coma. J Clin Invest (1954) 1.74
THE EFFECT OF PRETREATMENT WITH COLCHICINE ON THE INFLAMMATORY RESPONSE TO MICROCRYSTALLINE URATE: A MODEL FOR GOUTY INFLAMMATION. Ann Intern Med (1965) 1.71
CLINICAL, PHYSIOLOGICAL AND BIOCHEMICAL STUDIES OF A PATIENT WITH XANTHINURIA AND PHEOCHROMOCYTOMA. Am J Med (1964) 1.65
CHARACTERIZATION OF RIBOSOMAL AGGREGATES ISOLATED FROM LIVER. Proc Natl Acad Sci U S A (1964) 1.61
Determination of histidine alpha-deaminase in human stratum corneum and its absence in histidinaemia. Biochem J (1963) 1.50
RENAL RETENTION OF URIC ACID INDUCED BY INFUSION OF BETA-HYDROXYBUTYRATE AND ACETOACETATE. N Engl J Med (1965) 1.49
Glucose-6-phosphatase deficiency glycogen storage disease. Studies on the interrelationships of carbohydrate, lipid, and purine abnormalities. Pediatrics (1962) 1.44
THE EFFECTIVENESS OF THE XANTHINE OXIDASE INHIBITOR ALLOPURINOL IN THE TREATMENT OF GOUT. Ann Intern Med (1965) 1.43
The tyrosine oxidation system of liver. II. Oxidation of p-hydroxyphenylpyruvic acid to homogentisic acid. J Biol Chem (1955) 1.42
Failure to detect consistent overincorporation of glycine-1-C14 into uric acid in primary gout. Metabolism (1958) 1.37
An enzymatic spectrophotometric method for the determination of homogentisic acid in plasma and urine. J Biol Chem (1961) 1.37
Iron deficiency anemia producing evidence of marrow hyperplasia in the calvarium. Pediatrics (1960) 1.32
Dietary protein in the genesis of hepatic coma. N Engl J Med (1954) 1.32
On the mechanism of peroxidation of uric acids by hemoproteins. J Biol Chem (1960) 1.30
DESTRUCTIVE POLYARTHRITIS DUE TO A PHOTOCHROMOGENIC MYCOBACTERIUM. N Engl J Med (1965) 1.29
Triphosphopyridine nucleotide-linked aldehyde dehydrogenase from yeast. J Biol Chem (1953) 1.28
Biochemistry of uric acid and its relation to gout. N Engl J Med (1963) 1.27
Uric acid metabolism in psoriasis. J Clin Invest (1961) 1.24
Suppression of uric acid synthesis in the gouty human by the use of 6-diazo-5-oxo-L-norleucine. J Clin Invest (1960) 1.23
Properties of acatalasic cells growing in vitro. J Exp Med (1962) 1.22
MAMMALIAN ENZYME INDUCTION BY HYDROCORTISONE: THE POSSIBLE ROLE OF RNA. J Mol Biol (1964) 1.22
THE RENAL EXCRETION OF OXYPURINES. J Clin Invest (1965) 1.21
Studies on the defect in tyrosine metabolism in scorbutic guinea pigs. J Biol Chem (1960) 1.19
The uricosuria and orotic aciduria induced by 6-azauridine. J Clin Invest (1961) 1.19
Utilization of hypoxanthine, adenine and 4-amino-5-imidazole-carboxamide for uric acid synthesis in man. Metabolism (1959) 1.18
STUDIES ON THE SPECIFICITY OF TYROSINE-ALPHA-KETOGLUTARATE TRANSAMINASE. J Biol Chem (1964) 1.18
Biochemistry of uric acid and its relation to gout. N Engl J Med (1963) 1.17
Incorporation of 4-amino-5-imidazolecarboxamide-4-C13 into uric acid in the normal human. J Biol Chem (1955) 1.15
ENZYME DEFECT IN A CASE OF XANTHINURIA. Nature (1964) 1.15
Uricolysis by human leukocytes. Nature (1962) 1.14
The tyrosine oxidation system of liver. IV. Studies on the inhibition of p-hydroxyphenylpyruvic acid oxidase by excess substrate. J Biol Chem (1959) 1.12
The pathogenesis of gout. Metabolism (1957) 1.07
Rectal perforation: a hazard of rectal temperatures. Clin Pediatr (Phila) (1963) 1.03
Biochemistry of uric acid and its relation to gout. N Engl J Med (1963) 1.02
THE INFLAMMATORY RESPONSE TO INJECTED MICROCRYSTALLINE MONOSODIUM URATE IN NORMAL, HYPERURICEMIC, GOUTY, AND UREMIC SUBJECTS. Arthritis Rheum (1965) 1.01
Studies on ochronosis. II. Studies on benzoquinoneacetic acid, a probale intermediate in the connective tissue pigmentation of alcaptonuria. Arthritis Rheum (1962) 0.99
The enzymatic defect in histidinemia. Biochem Biophys Res Commun (1962) 0.99
The role of ascorbic acid in tyrosine metabolism. Ann N Y Acad Sci (1961) 0.98
CATECHOL AMINE METABOLISM AND STORAGE GRANULES IN PHEOCHROMOCYTOMA AND NEUROBLASTOMA. Medicine (Baltimore) (1964) 0.97
Nonspecificity of tyrosine transaminase: an explanation for the simultaneous induction of tyrosine, phenylalanine, and tryptophan transaminase activities in rat liver. Biochem Biophys Res Commun (1962) 0.93
X-ray diffraction studies of the tophaceous deposits in gout. Arthritis Rheum (1963) 0.91
Use of the newer uricosuric agents in the management of gout. JAMA (1960) 0.90
Sudden and unexpected death in childhood. A four year study in a United States Army station hospital in Germany. Mil Med (1963) 0.89
SYNTHESIS OF ANTIGENIC BRANCH-CHAIN COPOLYMERS OF ANGIOTENSIN AND POLY-L-LYSINE. Biochemistry (1965) 0.88
The tyrosine oxidation system of liver. III. Further studies on the oxidation of p-hydroxyphenylpyruvic acid. J Biol Chem (1956) 0.87
Excessive uric acid production in the human induced by 2-ethylamino-1,3,4-thiadiazole. Nature (1959) 0.86
The tyrosine oxidation system of liver. V. The ability of various quinones to reactivate inhibited p-hydroxyphenylpyruvic acid oxidase. J Biol Chem (1962) 0.83
Clinitest-produced esophageal stricture; report of two cases. J Pediatr (1957) 0.82
INTESTINAL OBSTRUCTION IN THE NEWBORN: AN UNUSUAL CASE DUE TO MESENTERIC CYST. Arch Surg (1965) 0.81
The effect of 2-ethylamino-1,3,4-thiadiazole on the incorporation of glycine into urinary purines and uric acid in man. Metabolism (1963) 0.81
A quantitative study of recycling of isotope from glycine-1-C14, alpha-N15 into various subunits of the uric acid molecule in a normal subject. J Clin Invest (1961) 0.80
Central and sensory control of food intake in genetically obese mice. Am J Physiol (1955) 0.78
Alcaptonuria and ochronotic arthritis. Bull Rheum Dis (1958) 0.77
Metabolism of 6-phosphogluconic acid in liver and bone marrow. J Biol Chem (1952) 0.77
Tyrosyluria resulting from inhibition of p-hydroxyphenylpyruvic acid oxidase in vitamin C-deficient guinea pigs. J Biol Chem (1960) 0.77
AN ENZYMATIC SPECTROPHOTOMETRIC METHOD FOR DETERMINATION OF OROTIC ACID. J Lab Clin Med (1964) 0.76
Toxicity of eugenol; determination of LD50 on rats. Proc Soc Exp Biol Med (1950) 0.76
Nature of the defect in alcaptonuria. Nature (1962) 0.75
The effect of folic acid on tyrosine metabolism in guinea pigs. J Biol Chem (1962) 0.75
INBORN ERROR OF METABOLISM. Am J Obstet Gynecol (1964) 0.75
Role of the newer uricosuric agents in management of gout. Bull Rheum Dis (1961) 0.75
A requirement for catalase in tyrosine metabolism: the oxidation of p-hydroxyphenylpyruvic acid to homogentisic acid. Nature (1956) 0.75
The experience of General Motors in developing new techniques for selection, placement and follow-up of employees; a panel discussion. Ind Med Surg (1950) 0.75
Alcaptonuria; clinical staff conference at the National Institutes of Health. Ann Intern Med (1957) 0.75
ULCERATIVE COLITIS IN CHILDREN. Am J Gastroenterol (1964) 0.75
The effect of coenzyme Q-10 on tyrosine metabolism in guinea pigs. Biochem Biophys Res Commun (1962) 0.75
Inert gas eliminator for high altitude oxygen apparatus. No. 2,456,606. J Pat Off Soc (1948) 0.75
Physiologic disposition and uricosuric effect of a keto analog of oxyphenbutazone (G-29701). Arthritis Rheum (1960) 0.75
The effect of nitrogen mustards on the respiration and fertilization of sea urchin sperm and eggs. Biol Bull (1948) 0.75
Clinical brief: a case of cat scratch disease complicated by erythema nodosum. Clin Proc Child Hosp Dist Columbia (1959) 0.75
Effects of electroconvulsive shock on sexual behavior in male rats. J Comp Physiol Psychol (1955) 0.75
The present-day treatment of gout. Med Clin North Am (1961) 0.75
Studies on ochronosis. I. The distribution of homogentisic acid in guinea pigs. Arthritis Rheum (1962) 0.75
IDENTIFICATION OF L-CYSTINE CRYSTALS IN BONE MARROW BY X-RAY DIFFRACTION. J Lab Clin Med (1965) 0.75
CHARCOAL THERAPY OF NEONATAL JAUNDICE: A PRELIMINARY REPORT ON A PROMISING METHOD FOR REDUCING THE NEED FOR EXCHANGE TRANSFUSIONS. Clin Pediatr (Phila) (1965) 0.75
PRIMARY CUTANEOUS TUBERCULOSIS. J Pediatr (1963) 0.75
Challenges ahead in industrial health. AMA Arch Ind Health (1960) 0.75