PubRank

Aleksander Edelman

Author PubWeight™ 55.72‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 In vitro prediction of stop-codon suppression by intravenous gentamicin in patients with cystic fibrosis: a pilot study. BMC Med 2007 1.82
2 Normal function of the cystic fibrosis conductance regulator protein can be associated with homozygous (Delta)F508 mutation. Pediatr Res 2002 1.61
3 Association between Hsp90 and the ClC-2 chloride channel upregulates channel function. Am J Physiol Cell Physiol 2005 1.56
4 NH3 is involved in the NH4+ transport induced by the functional expression of the human Rh C glycoprotein. J Biol Chem 2004 1.51
5 Evaluation of MRP1-5 gene expression in cystic fibrosis patients homozygous for the delta F508 mutation. Pediatr Res 2003 1.50
6 Distribution of ClC-2 chloride channel in rat and human epithelial tissues. Am J Physiol Cell Physiol 2002 1.44
7 Antibodies for CFTR studies. J Cyst Fibros 2004 1.06
8 Discovery of novel potent ΔF508-CFTR correctors that target the nucleotide binding domain. EMBO Mol Med 2013 1.04
9 Rescue of DeltaF508-CFTR (cystic fibrosis transmembrane conductance regulator) by curcumin: involvement of the keratin 18 network. J Pharmacol Exp Ther 2006 1.04
10 Chloride transport in nasal ciliated cells of cystic fibrosis heterozygotes. Am J Respir Crit Care Med 2005 1.03
11 Neutrophil elastase degrades cystic fibrosis transmembrane conductance regulator via calpains and disables channel function in vitro and in vivo. Am J Respir Crit Care Med 2012 1.03
12 Basic protocol for transepithelial nasal potential difference measurements. J Cyst Fibros 2004 1.01
13 Down-regulation of the anti-inflammatory protein annexin A1 in cystic fibrosis knock-out mice and patients. Mol Cell Proteomics 2005 1.00
14 Cystic fibrosis enters the proteomics scene: new answers to old questions. Proteomics 2006 1.00
15 Biochemical methods to assess CFTR expression and membrane localization. J Cyst Fibros 2004 1.00
16 Cystic fibrosis transmembrane regulator inhibitors CFTR(inh)-172 and GlyH-101 target mitochondrial functions, independently of chloride channel inhibition. J Pharmacol Exp Ther 2010 0.99
17 Expression of the human erythroid Rh glycoprotein (RhAG) enhances both NH3 and NH4+ transport in HeLa cells. Pflugers Arch 2005 0.99
18 Peroxiredoxin 6 fails to limit phospholipid peroxidation in lung from Cftr-knockout mice subjected to oxidative challenge. PLoS One 2009 0.97
19 Cell-specific posttranscriptional regulation of CFTR gene expression via influence of MAPK cascades on 3'UTR part of transcripts. Am J Physiol Cell Physiol 2005 0.96
20 Blue native/SDS-PAGE analysis reveals reduced expression of the mClCA3 protein in cystic fibrosis knock-out mice. Mol Cell Proteomics 2005 0.95
21 TGF-beta 1 downregulates CFTR expression and function in nasal polyps of non-CF patients. Am J Physiol Lung Cell Mol Physiol 2004 0.94
22 Coronin-1 is associated with neutrophil survival and is cleaved during apoptosis: potential implication in neutrophils from cystic fibrosis patients. J Immunol 2009 0.93
23 A neutral variant involved in a complex CFTR allele contributes to a severe cystic fibrosis phenotype. Hum Genet 2005 0.93
24 Lipid mapping of colonic mucosa by cluster TOF-SIMS imaging and multivariate analysis in cftr knockout mice. J Lipid Res 2010 0.92
25 A novel lipidomic strategy reveals plasma phospholipid signatures associated with respiratory disease severity in cystic fibrosis patients. PLoS One 2009 0.90
26 Global proteomic approach unmasks involvement of keratins 8 and 18 in the delivery of cystic fibrosis transmembrane conductance regulator (CFTR)/deltaF508-CFTR to the plasma membrane. Proteomics 2004 0.90
27 Plasma lipidomics reveals potential prognostic signatures within a cohort of cystic fibrosis patients. J Lipid Res 2011 0.90
28 Measurement of halide efflux from cultured and primary airway epithelial cells using fluorescence indicators. J Cyst Fibros 2004 0.89
29 The testis anion transporter TAT1 (SLC26A8) physically and functionally interacts with the cystic fibrosis transmembrane conductance regulator channel: a potential role during sperm capacitation. Hum Mol Genet 2011 0.89
30 Disruption of cytokeratin-8 interaction with F508del-CFTR corrects its functional defect. Hum Mol Genet 2011 0.89
31 Membrane cholesterol content modulates ClC-2 gating and sensitivity to oxidative stress. J Biol Chem 2006 0.89
32 Clinical phenotype and genotype of children with borderline sweat test and abnormal nasal epithelial chloride transport. Am J Respir Crit Care Med 2010 0.88
33 Control of basal CFTR gene expression by bicarbonate-sensitive adenylyl cyclase in human pulmonary cells. Cell Physiol Biochem 2008 0.88
34 Effect of ouabain on CFTR gene expression in human Calu-3 cells. Am J Physiol Cell Physiol 2003 0.87
35 Measurement of nasal potential difference in young children with an equivocal sweat test following newborn screening for cystic fibrosis. Thorax 2010 0.86
36 Resveratrol rescues cAMP-dependent anionic transport in the cystic fibrosis pancreatic cell line CFPAC1. Br J Pharmacol 2011 0.85
37 Immunohistochemistry of CFTR in native tissues and primary epithelial cell cultures. J Cyst Fibros 2004 0.84
38 CFTR inhibition provokes an inflammatory response associated with an imbalance of the annexin A1 pathway. Am J Pathol 2010 0.84
39 GSH monoethyl ester rescues mitochondrial defects in cystic fibrosis models. Hum Mol Genet 2011 0.84
40 Eicosanoid release is increased by membrane destabilization and CFTR inhibition in Calu-3 cells. PLoS One 2009 0.83
41 High sensitivity identification of membrane proteins by MALDI TOF-MASS spectrometry using polystyrene beads. J Proteome Res 2007 0.82
42 Contribution of proteomics to the study of the role of cytokeratins in disease and physiopathology. Proteomics Clin Appl 2008 0.82
43 Lanthanum carbonate, like sevelamer-HCl, retards the progression of vascular calcification and atherosclerosis in uremic apolipoprotein E-deficient mice. Nephrol Dial Transplant 2011 0.81
44 The Gef1 protein of Saccharomyces cerevisiae is associated with chloride channel activity. Biochem Biophys Res Commun 2002 0.81
45 A new workflow for proteomic analysis of urinary exosomes and assessment in cystinuria patients. J Proteome Res 2014 0.81
46 Regulation of interleukin-6 in head and neck squamous cell carcinoma is related to papillomavirus infection. J Proteome Res 2014 0.81
47 Long-term CFTR inhibition modulates 15d-prostaglandin J2 in human pulmonary cells. Int J Biochem Cell Biol 2012 0.79
48 Structural models of CFTR-AMPK and CFTR-PKA interactions: R-domain flexibility is a key factor in CFTR regulation. J Mol Model 2011 0.79
49 New lipidomic approaches in cystic fibrosis. Methods Mol Biol 2011 0.79
50 The functioning of mammalian ClC-2 chloride channel in Saccharomyces cerevisiae cells requires an increased level of Kha1p. Biochem J 2005 0.79
51 Characterization of SLC26A9 in patients with CF-like lung disease. Hum Mutat 2013 0.78
52 Characterization of nasal potential difference in cftr knockout and F508del-CFTR mice. PLoS One 2013 0.77
53 Quantitative differential proteomics of cystic fibrosis cell models by SILAC (stable isotope labelling in cell culture). Methods Mol Biol 2011 0.77
54 Misprocessing of the CFTR protein leads to mild cystic fibrosis phenotype. Hum Mutat 2005 0.77
55 The CF-CIRC study: a French collaborative study to assess the accuracy of cystic fibrosis diagnosis in neonatal screening. BMC Pediatr 2006 0.77
56 Genetic testing to provide targeted treatment for cystic fibrosis patients. Pharmacogenomics 2007 0.76
57 Farnesyltransferase inhibitor R115777 protects against vascular disease in uremic mice. Atherosclerosis 2013 0.76
58 [Pathophysiology in the era of contemporary proteomics]. Med Sci (Paris) 2005 0.75
59 Functional interaction between CFTR and the sodium-phosphate co-transport type 2a in Xenopus laevis oocytes. PLoS One 2012 0.75
60 Nasal potential difference in cystic fibrosis diagnosis of very young children. J Pediatr 2007 0.75
61 Proteomics techniques for cystic fibrosis research. J Cyst Fibros 2004 0.75