Published in Biochem J on August 15, 1992
Free N-linked oligosaccharide chains: formation and degradation. Glycoconj J (2006) 1.05
Man2C1, an alpha-mannosidase, is involved in the trimming of free oligosaccharides in the cytosol. Biochem J (2006) 1.03
Oligomannosides or oligosaccharide-lipids as potential substrates for rat liver cytosolic alpha-D-mannosidase. Biochem J (1996) 0.96
Kex2 protease converts the endoplasmic reticulum alpha1,2-mannosidase of Candida albicans into a soluble cytosolic form. Microbiology (2008) 0.75
Assembly of asparagine-linked oligosaccharides. Annu Rev Biochem (1985) 26.05
Characterization of human liver alpha-D-mannosidase purified by affinity chromatography. Biochem J (1976) 1.94
Evidence for an alpha-mannosidase in endoplasmic reticulum of rat liver. J Biol Chem (1983) 1.83
Human mannosidosis--the enzyme defect. Biochem Biophys Res Commun (1972) 1.79
Separation of neutral oligosaccharides by high-performance liquid chromatography. Anal Biochem (1981) 1.62
The use of 1-deoxymannojirimycin to evaluate the role of various alpha-mannosidases in oligosaccharide processing in intact cells. J Biol Chem (1986) 1.53
Mannosidosis in Angus cattle. The enzymic defect. Biochem J (1974) 1.51
Lysosomal alpha-D-mannosidase of rat liver. Purification and comparison with the golgi and cytosolic alpha-D-mannosidases. J Biol Chem (1978) 1.47
Evidence for a non-lysosomal alpha-mannosidase in rat liver homogenates. Biochim Biophys Acta (1971) 1.39
Biochemical studies on a case of feline mannosidosis. Biochem J (1980) 1.38
Lysosomal degradation of Asn-linked glycoproteins. FASEB J (1989) 1.38
Purification and characterization of the alpha-D-mannosidase of rat liver cytosol. J Biol Chem (1976) 1.32
Urinary oligosaccharides of mannosidosis. J Biol Chem (1980) 1.18
Substrate specificities of rat kidney lysosomal and cytosolic alpha-D-mannosidases and effects of swainsonine suggest a role of the cytosolic enzyme in glycoprotein catabolism. J Biol Chem (1987) 1.12
The soluble form of rat liver alpha-mannosidase is immunologically related to the endoplasmic reticulum membrane alpha-mannosidase. J Biol Chem (1986) 1.11
Structural studies of urinary oligosaccharides from patients with mannosidosis. Arch Biochem Biophys (1981) 1.03
The substrate specificity of bovine and feline lysosomal alpha-D-mannosidases in relation to alpha-mannosidosis. J Biol Chem (1991) 0.93
Chromatographic separation of oligosaccharides from mannosidosis urine. Carbohydr Res (1983) 0.89
Presence of two endo-beta-N-acetylglucosaminidases in human kidney. J Biol Chem (1989) 0.88
Structural analysis of the major urinary oligosaccharides in feline alpha-mannosidosis. Biochem J (1986) 0.87
The structures of oligosaccharides excreted by sheep with swainsonine toxicosis. J Biol Chem (1988) 0.84
Substrate specificity of human liver neutral alpha-mannosidase. Biochem J (1992) 0.82
The accumulation of oligosaccharides in tissues and body fluids of cats with alpha-mannosidosis. Carbohydr Res (1988) 0.82
[Comparative study of lysosomal and cytosolic catabolisms of oligomannosidic-type glycans]. C R Acad Sci III (1991) 0.80
Oligosaccharides from placenta: early diagnosis of feline mannosidosis. FEBS Lett (1986) 0.79
Specificity of lysosomal alpha-mannosidase for natural substrates. Biochem Soc Trans (1989) 0.78
Characterization of human liver alpha-D-mannosidase purified by affinity chromatography. Biochem J (1976) 1.94
Human mannosidosis--the enzyme defect. Biochem Biophys Res Commun (1972) 1.79
Human liver alpha-D-mannosidase activity. Clin Chim Acta (1974) 1.58
Hypertrophic obstructive cardiomyopathy in a neonate with the carbohydrate-deficient glycoprotein syndrome. J Inherit Metab Dis (1992) 1.58
Fucosylated human milk oligosaccharides vary between individuals and over the course of lactation. Glycobiology (2001) 1.56
Mannosidosis in Angus cattle. The enzymic defect. Biochem J (1974) 1.51
Identification of defects in glycosylphosphatidylinositol anchor biosynthesis in the Thy-1 expression mutants. J Biol Chem (1991) 1.41
Biochemical studies on a case of feline mannosidosis. Biochem J (1980) 1.38
Mutational analysis of 85 mucopolysaccharidosis type I families: frequency of known mutations, identification of 17 novel mutations and in vitro expression of missense mutations. Hum Genet (2001) 1.29
Survival of human milk oligosaccharides in the intestine of infants. Adv Exp Med Biol (2001) 1.29
Enzymatic synthesis of mannosyl retinyl phosphate from retinyl phosphate and guanosine diphosphate mannose. J Lipid Res (1975) 1.25
Mammalian alpha-mannosidases--multiple forms but a common purpose? Glycobiology (1994) 1.22
Ligand recognition by purified human mannose receptor. Arch Biochem Biophys (1992) 1.19
Identification of a missing link in glycosylphosphatidylinositol anchor biosynthesis in mammalian cells. J Biol Chem (1992) 1.13
Correction of a defect in mammalian GPI anchor biosynthesis by a transfected yeast gene. Science (1990) 1.11
Enzyme replacement therapy--an experiment of nature in a chimeric mannosidosis calf. Pediatr Res (1976) 1.06
Mannosyltransferase activity in calf pancreas microsomes. Formation from guanosine diphosphate-D-(14C)mannose of a 14C-labeled mannolipid with properties of dolichyl mannopyranosyl phosphate. J Biol Chem (1974) 1.05
Early uterine serous carcinoma: clonal origin of extrauterine disease. Int J Gynecol Pathol (2001) 1.04
Complexity of ethanolamine phosphate addition in the biosynthesis of glycosylphosphatidylinositol anchors in mammalian cells. J Biol Chem (1992) 1.04
Identification of 12 novel mutations in the alpha-N-acetylglucosaminidase gene in 14 patients with Sanfilippo syndrome type B (mucopolysaccharidosis type IIIB). J Med Genet (1998) 1.03
Application of magnetic chromatography to the isolation of lysosomes from fibroblasts of patients with lysosomal storage disorders. FEBS Lett (1998) 1.03
Evidence that the mutant enzyme in fibroblasts of a patient with mannosidosis does not crossreact with antiserum raised against normal acidic alpha-D-mannosidase. FEBS Lett (1978) 1.02
High-performance capillary electrophoresis of sialylated oligosaccharides of human milk. Anal Biochem (2000) 1.01
Biosynthesis of a P1-2-acetamido-2-deoxy-D-glucosyl P2-polyisoprenyl pyrophosphate by calf pancreas microsomes. Biochem Biophys Res Commun (1974) 1.01
Swainsonine affects the processing of glycoproteins in vivo. FEBS Lett (1983) 1.00
Sequence variations in the first exon of alpha-galactosidase A. J Med Genet (1993) 0.96
Neurovisceral and skeletal GM1-gangliosidosis in dogs with beta-galactosidase deficiency. Science (1985) 0.95
Molecular defects in Sanfilippo syndrome type B (mucopolysaccharidosis IIIB). J Inherit Metab Dis (2005) 0.94
Characterization of the mutant alpha-mannosidase in bovine mannosidosis. Biochem J (1978) 0.94
The substrate-specificity of human lysosomal alpha-D-mannosidase in relation to genetic alpha-mannosidosis. Biochem J (1991) 0.94
Mannosyltransferase activity in calf pancreas microsomes. Formation of 14C-labeled lipid-linked oligosaccharides from GDP-D-[14C]mannose and pancreatic dolichyl beta-D-[14C]mannopyranosyl phosphate. J Biol Chem (1977) 0.94
The substrate specificity of bovine and feline lysosomal alpha-D-mannosidases in relation to alpha-mannosidosis. J Biol Chem (1991) 0.93
Enzymatic utilization of P1-di-N-acetylchitobiosyl P2-dolichyl pyrophosphate and its chemical synthesis. Proc Natl Acad Sci U S A (1974) 0.93
Milk oligosaccharide profiles by reversed-phase HPLC of their perbenzoylated derivatives. Anal Biochem (1997) 0.92
A human lysosomal alpha(1----6)-mannosidase active on the branched trimannosyl core of complex glycans. Glycobiology (1992) 0.92
Transfer of sugars from nucleoside diphosphosugar compounds to endogenous and synthetic dolichyl phosphate in human lymphocytes. J Biol Chem (1974) 0.92
Characterization of oligosaccharides from the urine of loco-intoxicated sheep. FEBS Lett (1983) 0.91
Induced mannosidosis-excretion of oligosaccharides by locoweed-intoxicated sheep. FEBS Lett (1983) 0.91
Human and canine fucosidosis: a comparative lectin histochemistry study. Acta Neuropathol (1985) 0.90
Comparison of the N-acetylhexosaminidase components in the ram testis and epididymis by isoelectric focusing. Biochem J (1971) 0.90
Glycosylation of the mammalian alpha 1-adrenergic receptor by complex type N-linked oligosaccharides. Mol Pharmacol (1987) 0.89
Synthesis P1-dolichyl P2-alpha-D-mannopyranosyl pyrophosphate. The acid and alkaline hydrolysis of polyisoprenyl alpha-D-mannopyranosyl mono- and pyrophosphate diesters. Biochemistry (1975) 0.89
Mass spectrometric analysis of glycans in elucidating the pathogenesis of CDG type IIx . J Inherit Metab Dis (2003) 0.89
Chromatographic separation of oligosaccharides from mannosidosis urine. Carbohydr Res (1983) 0.89
Inhibition of glycosylphosphatidylinositol anchor formation by mannosamine. J Biol Chem (1992) 0.89
Lectin histochemistry of gangliosidosis. I. Neural tissue in four mammalian species. Acta Neuropathol (1988) 0.88
Defective glycosylphosphatidylinositol anchor synthesis in paroxysmal nocturnal hemoglobinuria granulocytes. Blood (1992) 0.88
The characterization of glycolipids derived from long-chain polyprenols: chemical synthesis of -D-mannopyranosyl dolichyl phosphate. FEBS Lett (1973) 0.86
Identification of alpha(1)-antitrypsin variants in plasma with the use of proteomic technology. Clin Chem (2001) 0.86
Clinical and molecular features of three patients with congenital disorders of glycosylation type Ih (CDG-Ih) (ALG8 deficiency). J Med Genet (2004) 0.86
The nature of the residual alpha-mannosidase in plasma in bovine mannosidosis. Biochem J (1976) 0.86
Anomeric configuration of the dolichyl D-mannosyl phosphate formed in calf pancreas microsomes. J Biol Chem (1975) 0.85
Measurement of the alpha-mannosidase activities in human plasma by a differential assay. Clin Chim Acta (1977) 0.84
Prenatal diagnosis of lysosomal storage diseases. Brain Pathol (1998) 0.84
Occurrence of a beta-D-mannopyranosyl phosphate residue in the polyprenyl mannosyl phosphate formed in calf pancreas microsomes and in human lymphocytes. FEBS Lett (1974) 0.84
Application of lectin histochemistry and carbohydrate analysis to the characterization of lysosomal storage diseases. Carbohydr Res (1991) 0.84
Strain variation in spermatozoal glycosidases in inbred mice. Genet Res (1978) 0.84
A human lysosomal alpha-mannosidase specific for the core of complex glycans. J Biol Chem (1992) 0.83
The molecular defect underlying canine fucosidosis. J Med Genet (1996) 0.83
GM1-gangliosidosis in a cross-bred dog confirmed by detection of GM1-ganglioside using electrospray ionisation-tandem mass spectrometry. Acta Neuropathol (2000) 0.83
A serological investigation into the acidic alpha-D-mannosidase in normal Angus cattle and in a calf with mannosidosis. Biochem J (1977) 0.83
Mutational analysis of Sanfilippo syndrome type A (MPS IIIA): identification of 13 novel mutations. J Med Genet (2000) 0.83
Animal models for lysosomal storage diseases: their past and future contribution. Hum Pathol (1989) 0.83
Swainsonine-induced oligosaccharide excretion in sheep. Time-dependent changes in the oligosaccharide profile. Biochem J (1984) 0.83
Enzyme analysis for Pompe disease in leukocytes; superior results with natural substrate compared with artificial substrates. J Inherit Metab Dis (2009) 0.83
A new procedure for the preparation of oligosaccharide oxazolines. Carbohydr Res (1986) 0.83
Mutation analysis in patients with the typical form of Anderson-Fabry disease. Hum Mol Genet (1993) 0.82
Chemical synthesis of dolichyl phosphate and dolichyl glycosyl phosphates and pyrophosphates or "dolichol intermediates". Methods Enzymol (1978) 0.81
Biosynthesis of P1-di-N-acetyl-alpha-chitobiosyl P2-dolichyl pyrophosphate in calf pancreas microsomes. J Biol Chem (1978) 0.81
Study of the thermal denaturation of ribonuclease A by differential thermal analysis and susceptibility to proteolysis. Biochem J (1970) 0.81
Enzyme purification by electrodecantation. Biochem J (1971) 0.80
Clinical, neurophysiological, biochemical and morphological features of eyes in Persian cats with mannosidosis. Virchows Arch B Cell Pathol Incl Mol Pathol (1991) 0.80
Immunological characterization of human alpha-D-mannosidases. Biochem Soc Trans (1975) 0.80
Canine GM1-gangliosidosis. A clinical, morphologic, histochemical, and biochemical comparison of two different models. Am J Pathol (1992) 0.80
Chemical synthesis of ficaprenyl alpha-D-mannopyranosyl phosphate. Biochemistry (1973) 0.80
The synthesis and chemical properties of polyisoprenyl beta-D-mannopyranosyl phosphates. J Biol Chem (1975) 0.79
Differential expression of glycosylphosphatidylinositol-anchored proteins in a murine T cell hybridoma mutant producing limiting amounts of the glycolipid core. Implications for paroxysmal nocturnal hemoglobinuria. J Clin Invest (1992) 0.79
Bovine mannosidosis--a model lysosomal storage disease. Birth Defects Orig Artic Ser (1975) 0.79
A new form of ovine GM1-gangliosidosis. Acta Neuropathol (1995) 0.79
Carbohydrate-deficient glycoprotein syndromes: inborn errors of protein glycosylation. Ann Clin Biochem (1999) 0.79
Resolution of structural isomers of sialylated oligosaccharides by capillary electrophoresis. J Chromatogr A (2001) 0.79
Oligosaccharides from placenta: early diagnosis of feline mannosidosis. FEBS Lett (1986) 0.79
Successful treatment of carbohydrate deficient glycoprotein syndrome type 1b with oral mannose. Arch Dis Child (2001) 0.79
GM1 gangliosidosis (type 1) in a cat. Biochem J (1986) 0.79
The preparation of a partially protected heptasaccharide-asparagine intermediate for glycopeptide synthesis. Carbohydr Res (1988) 0.78
The structural basis of the inhibition of human alpha-mannosidases by azafuranose analogues of mannose. Biochem J (1993) 0.78
Specificity of lysosomal alpha-mannosidase for natural substrates. Biochem Soc Trans (1989) 0.78
Pre- and postnatal diagnosis of patients with CLN1 and CLN2 by assay of palmitoyl-protein thioesterase and tripeptidyl-peptidase I activities. Eur J Paediatr Neurol (2001) 0.78
Preliminary characterization of the mutant alpha-mannosidase in bovine mannosidosis [proceedings]. Biochem Soc Trans (1978) 0.78
Chemical synthesis of pyrophosphodiesters of carbohydrates and isoprenoid alcohols. Lipid intermediates of bacterial cell wall and antigenic polysaccharide biosynthesis. Biochemistry (1972) 0.78
Conformation of the complex oligosaccharides of glycoproteins. A vacuum ultraviolet circular dichroism study. J Biol Chem (1982) 0.78
Formation of unusual mannosamine-containing lipid-linked oligosaccharides in Madin-Darby canine kidney cell cultures. J Biol Chem (1992) 0.78
Synthesis of lipid-linked oligosaccharides in Saccharomyces cerevisiae: Man2GlcNAc2 and Man1GlcNAc2 are transferred from dolichol to protein in vivo. Arch Biochem Biophys (1989) 0.78
Biochemical, ultrastructural and histochemical studies of cat placentae deficient in activity of lysosomal alpha-mannosidase. Placenta (1988) 0.77
Mechanism of infertility in t-complex mice. Genet Res (1978) 0.77