Monique Fabre

Author PubWeight™ 79.25‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Genotype-phenotype correlation in hepatocellular adenoma: new classification and relationship with HCC. Hepatology 2006 5.46
2 Stem cell-like micro-RNA signature driven by Myc in aggressive liver cancer. Proc Natl Acad Sci U S A 2010 2.91
3 Claudin-1 gene mutations in neonatal sclerosing cholangitis associated with ichthyosis: a tight junction disease. Gastroenterology 2004 1.98
4 Hepatic stem-like phenotype and interplay of Wnt/beta-catenin and Myc signaling in aggressive childhood liver cancer. Cancer Cell 2008 1.70
5 Adams-Oliver syndrome and hepatoportal sclerosis: occasional association or common mechanism? Am J Med Genet A 2005 1.61
6 Corynebacterium ulcerans in an immunocompromised patient with diphtheria and her dog. J Clin Microbiol 2005 1.53
7 Performance of endosonography-guided fine needle aspiration and biopsy in the diagnosis of pancreatic cystic lesions. Am J Gastroenterol 2003 1.51
8 Anti-CD20 monoclonal antibody (Rituximab) treatment for Epstein-Barr virus-associated, B-cell lymphoproliferative disease in pediatric liver transplant recipients. J Pediatr Gastroenterol Nutr 2002 1.47
9 Hepatocyte nuclear factor-1 alpha gene inactivation: cosegregation between liver adenomatosis and diabetes phenotypes in two maturity-onset diabetes of the young (MODY)3 families. J Clin Endocrinol Metab 2004 1.46
10 ATP8B1 and ABCB11 analysis in 62 children with normal gamma-glutamyl transferase progressive familial intrahepatic cholestasis (PFIC): phenotypic differences between PFIC1 and PFIC2 and natural history. Hepatology 2010 1.44
11 Complications of congenital portosystemic shunts in children: therapeutic options and outcomes. J Pediatr Gastroenterol Nutr 2010 1.44
12 Widening spectrum of liver angiosarcoma in children. J Pediatr Gastroenterol Nutr 2011 1.42
13 GNAS-activating mutations define a rare subgroup of inflammatory liver tumors characterized by STAT3 activation. J Hepatol 2011 1.25
14 Familial liver adenomatosis associated with hepatocyte nuclear factor 1alpha inactivation. Gastroenterology 2003 1.22
15 Bone marrow transplantation in mice leads to a minor population of hepatocytes that can be selectively amplified in vivo. Hepatology 2002 1.17
16 Progressive familial intrahepatic cholestasis type 1 and extrahepatic features: no catch-up of stature growth, exacerbation of diarrhea, and appearance of liver steatosis after liver transplantation. J Hepatol 2003 1.15
17 Identification of the leukocyte cell-derived chemotaxin 2 as a direct target gene of beta-catenin in the liver. Hepatology 2004 1.12
18 Oral cholic acid for hereditary defects of primary bile acid synthesis: a safe and effective long-term therapy. Gastroenterology 2009 1.11
19 Conditional cell ablation by tight control of caspase-3 dimerization in transgenic mice. Nat Biotechnol 2002 1.11
20 Over-expression of SERPINB3 in hepatoblastoma: a possible insight into the genesis of this tumour? Eur J Cancer 2011 1.10
21 Macrocystic pancreatic cystadenoma: The role of EUS and cyst fluid analysis in distinguishing mucinous and serous lesions. Gastrointest Endosc 2004 1.09
22 Gastric inflammatory myofibroblastic tumors in children: an unpredictable course. J Pediatr Gastroenterol Nutr 2002 1.02
23 CD133 expression is associated with poor outcome in neuroblastoma via chemoresistance mediated by the AKT pathway. Histopathology 2012 1.00
24 Successful mutation-specific chaperone therapy with 4-phenylbutyrate in a child with progressive familial intrahepatic cholestasis type 2. J Hepatol 2012 0.99
25 Induction of antigen-specific tolerance by intrathymic injection of lentiviral vectors. Blood 2006 0.98
26 Pure and mixed fibrolamellar hepatocellular carcinomas differ in natural history and prognosis after complete surgical resection. Cancer 2012 0.97
27 WNT/beta-catenin pathway activation in Wilms tumors: a unifying mechanism with multiple entries? Genes Chromosomes Cancer 2009 0.96
28 IL-1RA agonist (anakinra) in the treatment of multifocal castleman disease: case report. J Pediatr Hematol Oncol 2008 0.95
29 Transcriptional profiling of pure fibrolamellar hepatocellular carcinoma reveals an endocrine signature. Hepatology 2014 0.94
30 Peripancreatic paraganglioma: a potential diagnostic challenge in cytopathology and surgical pathology. Am J Surg Pathol 2011 0.92
31 Long-term outcome of pediatric liver transplantation for biliary atresia: a 10-year follow-up in a single center. Liver Transpl 2005 0.91
32 Fusarium keratitis and endophthalmitis associated with lens contact wear. Int Ophthalmol 2009 0.91
33 Immunohistochemical markers on needle biopsies are helpful for the diagnosis of focal nodular hyperplasia and hepatocellular adenoma subtypes. Am J Surg Pathol 2012 0.91
34 Prenatal and postnatal Ciliated Hepatic Foregut Cysts in infants. J Pediatr Surg 2010 0.90
35 Features and outcome of autoimmune hepatitis type 2 presenting with isolated positivity for anti-liver cytosol antibody. Clin Gastroenterol Hepatol 2004 0.90
36 Congenital anerythremic erythroleukemia presenting as hepatic failure. Arch Pathol Lab Med 2003 0.89
37 Prognostic value of endoscopy in children with biliary atresia at risk for early development of varices and bleeding. Gastroenterology 2010 0.89
38 ThinPrep-processed fine-needle samples of breast are effective material for RNA- and DNA-based molecular diagnosis: application to p53 mutation analysis. Cancer 2003 0.88
39 EUS-guided FNA of pancreatic metastasis from renal cell carcinoma. Gastrointest Endosc 2003 0.88
40 Relapsing features of bile salt export pump deficiency after liver transplantation in two patients with progressive familial intrahepatic cholestasis type 2. J Hepatol 2010 0.87
41 Prognostic value of portal pressure at the time of Kasai operation in patients with biliary atresia. J Pediatr Gastroenterol Nutr 2006 0.87
42 Abnormal hepatic expression of fibrillin-1 in children with cholestasis. Am J Surg Pathol 2002 0.87
43 Cholestasis in children with portal vein obstruction. J Pediatr 2005 0.85
44 Double pancreatic and gastric adenocarcinomas: a rare association. Clin Res Hepatol Gastroenterol 2012 0.85
45 Giant cell hepatitis with autoimmune hemolytic anemia in early childhood: long-term outcome in 16 children. J Pediatr 2011 0.85
46 Association of Adams-Oliver syndrome and hepatoportal sclerosis: an additional case. Am J Med Genet A 2006 0.84
47 [Pancreatic intraductal tubular carcinoma: a sub-group of intraductal papillary-mucinous tumors or a distinct entity? A case report and review of the literature]. Gastroenterol Clin Biol 2006 0.84
48 Immunohistochemical profile of ezrin and radixin in human liver epithelia during fetal development and pediatric cholestatic diseases. Clin Res Hepatol Gastroenterol 2013 0.84
49 Expression of erythropoietin and its receptor in neuroblastomas. Cancer 2007 0.84
50 Pancreatic haemangioma in infancy: the place of radiology. Pediatr Radiol 2003 0.82
51 Epstein-Barr virus infection and altered control of apoptotic pathways in posttransplant lymphoproliferative disorders. Pathobiology 2012 0.82
52 Adjuvant interleukin-12 gene therapy for the management of colorectal liver metastases. Cancer Gene Ther 2004 0.82
53 [Pancreatic vascular tumours of childhood: a heterogeneous nosologic spectrum]. Ann Pathol 2002 0.82
54 High cyclin E staining index in blastemal, stromal or epithelial cells is correlated with tumor aggressiveness in patients with nephroblastoma. PLoS One 2008 0.82
55 Histopathology of an iliac aneurysm in a case of Menkes disease. Pediatr Dev Pathol 2010 0.81
56 French retrospective multicentric study of neonatal hemochromatosis: importance of autopsy and autoimmune maternal manifestations. Pediatr Dev Pathol 2012 0.81
57 Separate occurrence of extra-adrenal paraganglioma and gastrointestinal stromal tumor in monozygotic twins: probable familial Carney syndrome. Pediatr Dev Pathol 2004 0.81
58 Solid adenoma with exclusive hepatocellular differentiation: a new variant among pancreatic benign neoplasms? Virchows Arch 2002 0.81
59 Erdheim-Chester disease in childhood: a challenging diagnosis and treatment. J Pediatr Hematol Oncol 2009 0.81
60 Importance, mechanisms and limitations of the distant bystander effect in cancer gene therapy of experimental liver tumors. Cancer Lett 2002 0.80
61 Outcome of central hepatectomy for hepatoblastomas. J Pediatr Surg 2010 0.79
62 High level of apoptosis and low AKT activation in mass screening as opposed to standard neuroblastoma. Histopathology 2010 0.79
63 Activation of the phosphatidylinositol 3'-kinase/AKT pathway in neuroblastoma and its regulation by thioredoxin 1. Hum Pathol 2011 0.78
64 Alagille syndrome and nephroblastoma: Unusual coincidence of two rare disorders. Pediatr Blood Cancer 2008 0.78
65 Initial liver transplantation for unresectable hepatoblastoma after chemotherapy. Pediatr Blood Cancer 2011 0.78
66 Tacrolimus dose requirement in pediatric liver transplantation: influence of CYP3A5 gene polymorphism. Pharmacogenomics 2013 0.78
67 Methylome sequencing for fibrolamellar hepatocellular carcinoma depicts distinctive features. Epigenetics 2015 0.78
68 Liver nodules after portal systemic shunt surgery for extrahepatic portal vein obstruction in children. J Pediatr Surg 2009 0.77
69 Clostridium difficile colitis associated with inflammatory pseudotumor in a liver transplant recipient. Pediatr Transplant 2003 0.77
70 [Acinar cell carcinoma of the pancreas with predominant intraductal growth: report of a case]. Gastroenterol Clin Biol 2007 0.77
71 Ciliated hepatic foregut cyst discovered after kidney transplantation in a hepatitis C virus-infected patient: a report of one case and review of the literature. Eur J Gastroenterol Hepatol 2008 0.76
72 Total vascular exclusion of the liver enhances the efficacy of retroviral-mediated associated thymidine kinase and interleukin-2 genes transfer against multiple hepatic tumors in rats. Surgery 2003 0.76
73 Human herpesvirus-6 infection: a prospective study evaluating HHV-6 DNA levels in liver from children with acute liver failure. J Med Virol 2008 0.76
74 Autoimmune pancreatitis with atypical imaging findings that mimicked an endocrine tumor. World J Gastroenterol 2010 0.75
75 p52 Activation in monomorphic B-cell posttransplant lymphoproliferative disorder/diffuse large B-cell lymphoma without BAFF-R expression. Am J Pathol 2011 0.75
76 Transient neonatal liver disease after maternal antenatal intravenous Ig infusions in gestational alloimmune liver disease associated with neonatal haemochromatosis. J Pediatr Gastroenterol Nutr 2014 0.75
77 [Infantile and maternal choriocarcinoma]. Ann Pathol 2003 0.75
78 Intestinal congenital/infantile fibrosarcoma: a new clinico-pathological entity? Pediatr Surg Int 2015 0.75
79 [Poorly differentiated large-cell carcinoma of the rectum]. Gastroenterol Clin Biol 2003 0.75
80 A new feature of the MYH9-related syndrome: chronic transaminase elevation. Hepatology 2012 0.75
81 Irregular narrowing of the main pancreatic duct in association with a wall thickening is a key sign at endoscopic ultrasonography for the diagnosis of autoimmune pancreatitis. Pancreas 2015 0.75
82 Small hepatic vein involvement in IgG multiple myeloma: a very unusual pattern of liver infiltration. Virchows Arch 2006 0.75
83 [Endoscopic ultrasound-guided fine-needle aspiration of pancreatic cystic neoplasms: utility and limitations]. Ann Pathol 2006 0.75