C S Dutra-Filho

Author PubWeight™ 16.69‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 The role of oxidative damage in the neuropathology of organic acidurias: insights from animal studies. J Inherit Metab Dis 2004 1.75
2 Inborn errors of metabolism. Sensitivity of screening tests in high risk patients. Clin Pediatr (Phila) 1989 1.38
3 Inhibition of the mitochondrial respiratory chain complex activities in rat cerebral cortex by methylmalonic acid. Neurochem Int 2002 0.92
4 Reduction of large neutral amino acid levels in plasma and brain of hyperleucinemic rats. Neurochem Int 2001 0.92
5 Oxidative stress in patients with phenylketonuria. Biochim Biophys Acta 2005 0.85
6 Propionic and L-methylmalonic acids induce oxidative stress in brain of young rats. Neuroreport 2000 0.85
7 Effects of methylmalonic and propionic acids on glutamate uptake by synaptosomes and synaptic vesicles and on glutamate release by synaptosomes from cerebral cortex of rats. Brain Res 2001 0.82
8 Inhibition of in vitro CO2 production and lipid synthesis by 2-hydroxybutyric acid in rat brain. Braz J Med Biol Res 2001 0.82
9 Na+, K+ ATPase activity is markedly reduced by cis-4-decenoic acid in synaptic plasma membranes from cerebral cortex of rats. Exp Neurol 2005 0.82
10 Inhibition of succinate dehydrogenase and beta-hydroxybutyrate dehydrogenase activities by methylmalonate in brain and liver of developing rats. J Inherit Metab Dis 1993 0.81
11 Inhibition of glutamate uptake into synaptic vesicles of rat brain by the metabolites accumulating in maple syrup urine disease. J Neurol Sci 2000 0.81
12 Promotion of oxidative stress by 3-hydroxyglutaric acid in rat striatum. J Inherit Metab Dis 2005 0.80
13 Quinolinic acid inhibits glutamate uptake into synaptic vesicles from rat brain. Neuroreport 2000 0.79
14 L-pyroglutamic acid inhibits energy production and lipid synthesis in cerebral cortex of young rats in vitro. Neurochem Res 2001 0.79
15 Nitric oxide synthase inhibition by L-NAME prevents the decrease of Na+,K+-ATPase activity in midbrain of rats subjected to arginine administration. Neurochem Res 2001 0.79
16 Inhibition of energy production in vitro by glutaric acid in cerebral cortex of young rats. Metab Brain Dis 2000 0.79
17 Effects of methylmalonate and propionate on uptake of glucose and ketone bodies in vitro by brain of developing rats. Biochem Med Metab Biol 1991 0.78
18 Seven-year experience of a reference laboratory for detection of inborn errors of metabolism in Brazil. J Inherit Metab Dis 1991 0.78
19 Platelet Na+, K+-ATPase activity as a possible peripheral marker for the neurotoxic effects of phenylalanine in phenylketonuria. Metab Brain Dis 2000 0.77
20 Effects of histidine and imidazolelactic acid on various parameters of the oxidative stress in cerebral cortex of young rats. Int J Dev Neurosci 2004 0.76
21 2-Hydroxybutyrate and 4-hydroxybutyrate inhibit CO2 formation from labeled substrates by rat cerebral cortex. Biochem Soc Trans 1995 0.76
22 Investigation of oxidative stress parameters in treated phenylketonuric patients. Metab Brain Dis 2006 0.76
23 Effect of phenylalanine, p-chlorophenylalanine and alpha-methylphenylalanine on glucose uptake in vitro by the brain of young rats. Biochem Soc Trans 1990 0.75
24 [Börjeson-Forssman-Lehmann syndrome: report of a case]. Arq Neuropsiquiatr 1986 0.75
25 Detection of inborn errors of metabolism in unselected patients from pediatric intensive care units in Porto Alegre, Brazil: evaluation of screening techniques. Braz J Med Biol Res 1987 0.75
26 Influence of methylmalonate on the uptake of ketone bodies in vitro by the brain of young rats. Biochem Soc Trans 1990 0.75
27 Chronic postnatal administration of methylmalonic acid provokes a decrease of myelin content and ganglioside N-acetylneuraminic acid concentration in cerebrum of young rats. Braz J Med Biol Res 2001 0.75
28 Inhibition of glutamate uptake into synaptic vesicles from rat brain by 3-nitropropionic acid in vitro. Exp Neurol 2001 0.75
29 Possible high frequency of tetrahydrobiopterin deficiency in south Brazil. J Inherit Metab Dis 1994 0.75
30 Proline administration decreases Na+,K+-ATPase activity in the synaptic plasma membrane from cerebral cortex of rats. Metab Brain Dis 1999 0.75
31 Effect of phenylalanine and p-chlorophenylalanine on Na+, K+-ATPase activity in the synaptic plasma membrane from the cerebral cortex of rats. Metab Brain Dis 2000 0.75
32 Reduced Na(+), K(+)-ATPase activity in erythrocyte membranes from patients with phenylketonuria. Pediatr Res 2001 0.75