Marie Sissler

Author PubWeight™ 17.99‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Mitochondrial aspartyl-tRNA synthetase deficiency causes leukoencephalopathy with brain stem and spinal cord involvement and lactate elevation. Nat Genet 2007 3.43
2 Mamit-tRNA, a database of mammalian mitochondrial tRNA primary and secondary structures. RNA 2007 1.72
3 Toward the full set of human mitochondrial aminoacyl-tRNA synthetases: characterization of AspRS and TyrRS. Biochemistry 2005 1.50
4 Recognition of human mitochondrial tRNALeu(UUR) by its cognate leucyl-tRNA synthetase. J Mol Biol 2004 0.99
5 Activation of the hetero-octameric ATP phosphoribosyl transferase through subunit interface rearrangement by a tRNA synthetase paralog. J Biol Chem 2005 0.89
6 A human pathology-related mutation prevents import of an aminoacyl-tRNA synthetase into mitochondria. Biochem J 2011 0.86
7 Functional idiosyncrasies of tRNA isoacceptors in cognate and noncognate aminoacylation systems. Biochimie 2004 0.84
8 Thermodynamic properties distinguish human mitochondrial aspartyl-tRNA synthetase from bacterial homolog with same 3D architecture. Nucleic Acids Res 2012 0.83
9 Pathogenic implications of human mitochondrial aminoacyl-tRNA synthetases. Top Curr Chem 2014 0.83
10 Peculiar inhibition of human mitochondrial aspartyl-tRNA synthetase by adenylate analogs. Biochimie 2009 0.83
11 Adaptation of aminoacylation identity rules to mammalian mitochondria. Biochimie 2012 0.82
12 Pathogenic mutations causing LBSL affect mitochondrial aspartyl-tRNA synthetase in diverse ways. Biochem J 2013 0.82
13 Tertiary network in mammalian mitochondrial tRNAAsp revealed by solution probing and phylogeny. Nucleic Acids Res 2009 0.81
14 A yeast arginine specific tRNA is a remnant aspartate acceptor. Nucleic Acids Res 2004 0.81
15 Loss of a primordial identity element for a mammalian mitochondrial aminoacylation system. J Biol Chem 2006 0.79
16 Re-designed N-terminus enhances expression, solubility and crystallizability of mitochondrial protein. Protein Eng Des Sel 2012 0.78
17 Pathology-related mutation A7526G (A9G) helps in the understanding of the 3D structural core of human mitochondrial tRNA(Asp). RNA 2009 0.76