| Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
|
1
|
Survival and complications in patients with thalassemia major treated with transfusion and deferoxamine.
|
Haematologica
|
2004
|
5.21
|
|
2
|
Efficacy and safety of sildenafil in the treatment of severe pulmonary hypertension in patients with hemoglobinopathies.
|
Haematologica
|
2005
|
2.64
|
|
3
|
Randomized phase II trial of deferasirox (Exjade, ICL670), a once-daily, orally-administered iron chelator, in comparison to deferoxamine in thalassemia patients with transfusional iron overload.
|
Haematologica
|
2006
|
2.54
|
|
4
|
Cardiac morbidity and mortality in deferoxamine- or deferiprone-treated patients with thalassemia major.
|
Blood
|
2005
|
2.45
|
|
5
|
Phase II clinical evaluation of deferasirox, a once-daily oral chelating agent, in pediatric patients with beta-thalassemia major.
|
Haematologica
|
2006
|
2.14
|
|
6
|
Relative response of patients with myelodysplastic syndromes and other transfusion-dependent anaemias to deferasirox (ICL670): a 1-yr prospective study.
|
Eur J Haematol
|
2007
|
2.14
|
|
7
|
A randomised comparison of deferasirox versus deferoxamine for the treatment of transfusional iron overload in sickle cell disease.
|
Br J Haematol
|
2007
|
1.77
|
|
8
|
Mutational spectrum in congenital dyserythropoietic anemia type II: identification of 19 novel variants in SEC23B gene.
|
Am J Hematol
|
2010
|
1.60
|
|
9
|
A phase 2 study of the safety, tolerability, and pharmacodynamics of FBS0701, a novel oral iron chelator, in transfusional iron overload.
|
Blood
|
2012
|
1.49
|
|
10
|
Long-term safety and efficacy of deferasirox (Exjade) for up to 5 years in transfusional iron-overloaded patients with sickle cell disease.
|
Br J Haematol
|
2011
|
1.45
|
|
11
|
Pregnancy and beta-thalassemia: an Italian multicenter experience.
|
Haematologica
|
2009
|
1.42
|
|
12
|
Hepatocellular carcinoma in thalassaemia: an update of the Italian Registry.
|
Br J Haematol
|
2014
|
1.40
|
|
13
|
Clinical and histological characterization of liver disease in patients with transfusion-dependent beta-thalassemia. A multicenter study of 117 cases.
|
Haematologica
|
2004
|
1.30
|
|
14
|
Changes in the quality of life of people with thalassemia major between 2001 and 2009.
|
Patient Prefer Adherence
|
2013
|
1.13
|
|
15
|
A pilot trial of deferiprone for neurodegeneration with brain iron accumulation.
|
Haematologica
|
2011
|
1.10
|
|
16
|
Genetic and clinical heterogeneity of ferroportin disease.
|
Br J Haematol
|
2005
|
1.07
|
|
17
|
Prevalence and risk factors for pulmonary arterial hypertension in a large group of β-thalassemia patients using right heart catheterization: a Webthal study.
|
Circulation
|
2013
|
1.06
|
|
18
|
Pseudoxanthoma-elasticum-like syndrome and thalassemia: an update.
|
Dermatol Online J
|
2009
|
0.91
|
|
19
|
Daily alternating deferasirox and deferiprone therapy for "hard-to-chelate" beta-thalassemia major patients.
|
Am J Hematol
|
2010
|
0.90
|
|
20
|
CYBRD1 as a modifier gene that modulates iron phenotype in HFE p.C282Y homozygous patients.
|
Haematologica
|
2012
|
0.89
|
|
21
|
Effect of food, type of food, and time of food intake on deferasirox bioavailability: recommendations for an optimal deferasirox administration regimen.
|
J Clin Pharmacol
|
2008
|
0.88
|
|
22
|
Patient-reported outcomes of deferasirox (Exjade, ICL670) versus deferoxamine in sickle cell disease patients with transfusional hemosiderosis. Substudy of a randomized open-label phase II trial.
|
Acta Haematol
|
2008
|
0.88
|
|
23
|
Musculoskeletal manifestations of chronic anemias.
|
Semin Musculoskelet Radiol
|
2011
|
0.87
|
|
24
|
Cholelithiasis in thalassemia major.
|
Eur J Haematol
|
2008
|
0.87
|
|
25
|
The influence of treatment in specialized centers on survival of patients with thalassemia major.
|
Am J Hematol
|
2009
|
0.87
|
|
26
|
New TFR2 mutations in young Italian patients with hemochromatosis.
|
Haematologica
|
2008
|
0.87
|
|
27
|
Sequence variations in mitochondrial ferritin: distribution in healthy controls and different types of patients.
|
Genet Test Mol Biomarkers
|
2010
|
0.80
|
|
28
|
Characterization of ferromagnetic or conductive properties of metallic foreign objects embedded within the human body with magnetic iron detector (MID): Screening patients for MRI.
|
Magn Reson Med
|
2015
|
0.79
|
|
29
|
Therapeutic approaches to pulmonary hypertension in hemoglobinopathies: Efficacy and safety of sildenafil in the treatment of severe pulmonary hypertension in patients with hemoglobinopathy.
|
Ann N Y Acad Sci
|
2005
|
0.79
|
|
30
|
Diagnostic value of real-time elastography in the assessment of hepatic fibrosis in patients with liver iron overload.
|
Eur J Radiol
|
2013
|
0.79
|
|
31
|
Determination of deferasirox plasma concentrations: do gender, physical and genetic differences affect chelation efficacy?
|
Eur J Haematol
|
2014
|
0.78
|
|
32
|
Assessment and management of iron overload in β-thalassaemia major patients during the 21st century: a real-life experience from the Italian WEBTHAL project.
|
Br J Haematol
|
2013
|
0.78
|
|
33
|
Response of iron overload to deferasirox in rare transfusion-dependent anaemias: equivalent effects on serum ferritin and labile plasma iron for haemolytic or production anaemias.
|
Eur J Haematol
|
2011
|
0.78
|
|
34
|
Manual erythroexchange for chronic transfusion therapy in patients with sickle cell syndromes unresponsive to hydroxyurea: a long-term follow-up.
|
Am J Hematol
|
2010
|
0.78
|
|
35
|
Clinical management of cardiovascular complications in patients with thalassaemia major: a large observational multicenter study.
|
Eur J Echocardiogr
|
2011
|
0.77
|
|
36
|
Deferasirox effect on renal haemodynamic parameters in patients with transfusion-dependent β thalassaemia.
|
Br J Haematol
|
2014
|
0.77
|
|
37
|
Development of interactive algorithm for clinical management of acute events related to sickle cell disease in emergency department.
|
Orphanet J Rare Dis
|
2014
|
0.77
|
|
38
|
Venous-like leg ulcers without venous insufficiency in congenital anemia: successful treatment using compression bandages.
|
Dermatol Surg
|
2010
|
0.75
|