Published in Kidney Int on August 01, 2005
Clinical practice recommendations for the treatment of Alport syndrome: a statement of the Alport Syndrome Research Collaborative. Pediatr Nephrol (2012) 1.17
Familial hematuria. Pediatr Nephrol (2007) 1.04
Chronic kidney disease: a new look at pathogenetic mechanisms and treatment options. Pediatr Nephrol (2013) 0.88
Diagnosis of Alport syndrome without biopsy? Pediatr Nephrol (2006) 0.83
An update on the pathomechanisms and future therapies of Alport syndrome. Pediatr Nephrol (2012) 0.82
Searching for a treatment for Alport syndrome using mouse models. World J Nephrol (2014) 0.77
COL4A6 is dispensable for autosomal recessive Alport syndrome. Sci Rep (2016) 0.75
Alport syndrome: facts and opinions. F1000Res (2017) 0.75
Dual leucine zipper kinase is required for retrograde injury signaling and axonal regeneration. Neuron (2012) 2.88
Early angiotensin-converting enzyme inhibition in Alport syndrome delays renal failure and improves life expectancy. Kidney Int (2011) 2.34
Preemptive ramipril therapy delays renal failure and reduces renal fibrosis in COL4A3-knockout mice with Alport syndrome. Kidney Int (2003) 2.20
X-linked Alport syndrome: natural history and genotype-phenotype correlations in girls and women belonging to 195 families: a "European Community Alport Syndrome Concerted Action" study. J Am Soc Nephrol (2003) 2.12
The Duffy antigen receptor for chemokines transports chemokines and supports their promigratory activity. Nat Immunol (2008) 2.08
Incidence of renal failure and nephroprotection by RAAS inhibition in heterozygous carriers of X-chromosomal and autosomal recessive Alport mutations. Kidney Int (2012) 1.87
Ligands to nucleic acid-specific toll-like receptors and the onset of lupus nephritis. J Am Soc Nephrol (2006) 1.80
Meta-analysis of genotype-phenotype correlation in X-linked Alport syndrome: impact on clinical counselling. Nephrol Dial Transplant (2002) 1.72
Viral double-stranded RNA aggravates lupus nephritis through Toll-like receptor 3 on glomerular mesangial cells and antigen-presenting cells. J Am Soc Nephrol (2005) 1.69
Inhibition of Toll-like receptor-7 (TLR-7) or TLR-7 plus TLR-9 attenuates glomerulonephritis and lung injury in experimental lupus. J Am Soc Nephrol (2007) 1.68
The estrogen receptor-alpha agonist 16alpha-LE2 inhibits cardiac hypertrophy and improves hemodynamic function in estrogen-deficient spontaneously hypertensive rats. Cardiovasc Res (2005) 1.66
Differential regulation of smooth muscle markers in human bone marrow-derived mesenchymal stem cells. J Hypertens (2005) 1.65
Living donor kidney transplantation from relatives with mild urinary abnormalities in Alport syndrome: long-term risk, benefit and outcome. Nephrol Dial Transplant (2008) 1.62
Immune cell-derived c3 is required for autoimmune diabetes induced by multiple low doses of streptozotocin. Diabetes (2010) 1.57
Expression and regulation of Toll-like receptors in lupus-like immune complex glomerulonephritis of MRL-Fas(lpr) mice. Nephrol Dial Transplant (2006) 1.55
Wld S protein requires Nmnat activity and a short N-terminal sequence to protect axons in mice. J Cell Biol (2009) 1.53
Renal tubular PD-L1 (CD274) suppresses alloreactive human T-cell responses. Kidney Int (2010) 1.53
Finding the right position: a three-year, single-center experience with the "self-locating" catheter. Perit Dial Int (2010) 1.49
The slow Wallerian degeneration gene, WldS, inhibits axonal spheroid pathology in gracile axonal dystrophy mice. Brain (2005) 1.46
Spiegelmer inhibition of CCL2/MCP-1 ameliorates lupus nephritis in MRL-(Fas)lpr mice. J Am Soc Nephrol (2007) 1.44
Kidney transplantation in mice using left and right kidney grafts. J Surg Res (2010) 1.44
Lymphotoxin β receptor signaling promotes development of autoimmune pancreatitis. Gastroenterology (2012) 1.43
Chemokine receptor CCR1 but not CCR5 mediates leukocyte recruitment and subsequent renal fibrosis after unilateral ureteral obstruction. J Am Soc Nephrol (2004) 1.41
A rat model of slow Wallerian degeneration (WldS) with improved preservation of neuromuscular synapses. Eur J Neurosci (2005) 1.39
The Phr1 ubiquitin ligase promotes injury-induced axon self-destruction. Cell Rep (2013) 1.39
Renal injury in apolipoprotein E-deficient mice. Lab Invest (2002) 1.36
Toll-like receptor-4: renal cells and bone marrow cells signal for neutrophil recruitment during pyelonephritis. Kidney Int (2005) 1.35
Toll-like receptor-7 modulates immune complex glomerulonephritis. J Am Soc Nephrol (2005) 1.32
Identification of a new tumor suppressor gene located at chromosome 8p21.3-22. FASEB J (2003) 1.31
Resident dendritic cells prevent postischemic acute renal failure by help of single Ig IL-1 receptor-related protein. J Immunol (2009) 1.28
Human nephrosclerosis triggers a hypoxia-related glomerulopathy. Am J Pathol (2009) 1.27
The role of interstitial macrophages in nephropathy of type 2 diabetic db/db mice. Am J Pathol (2007) 1.27
CCR1 blockade reduces interstitial inflammation and fibrosis in mice with glomerulosclerosis and nephrotic syndrome. Kidney Int (2004) 1.24
Late onset of Ccl2 blockade with the Spiegelmer mNOX-E36-3'PEG prevents glomerulosclerosis and improves glomerular filtration rate in db/db mice. Am J Pathol (2008) 1.24
Targeting NMNAT1 to axons and synapses transforms its neuroprotective potency in vivo. J Neurosci (2010) 1.22
Cross-species transcriptional network analysis defines shared inflammatory responses in murine and human lupus nephritis. J Immunol (2012) 1.21
Delayed chemokine receptor 1 blockade prolongs survival in collagen 4A3-deficient mice with Alport disease. J Am Soc Nephrol (2005) 1.19
Periostin is induced in glomerular injury and expressed de novo in interstitial renal fibrosis. Am J Pathol (2011) 1.19
Late onset of treatment with a chemokine receptor CCR1 antagonist prevents progression of lupus nephritis in MRL-Fas(lpr) mice. J Am Soc Nephrol (2004) 1.15
DDR1-deficient mice show localized subepithelial GBM thickening with focal loss of slit diaphragms and proteinuria. Kidney Int (2004) 1.15
The contribution of B cells to renal interstitial inflammation. Am J Pathol (2007) 1.14
The slow Wallerian degeneration protein, WldS, binds directly to VCP/p97 and partially redistributes it within the nucleus. Mol Biol Cell (2005) 1.13
Presence of HSV-1 immediate early genes and clonally expanded T-cells with a memory effector phenotype in human trigeminal ganglia. Brain Pathol (2007) 1.11
Bacterial lipopeptide triggers massive albuminuria in murine lupus nephritis by activating Toll-like receptor 2 at the glomerular filtration barrier. Immunology (2008) 1.09
Loss of collagen-receptor DDR1 delays renal fibrosis in hereditary type IV collagen disease. Matrix Biol (2010) 1.09
Frequency of disease-associated and other nuclear autoantibodies in patients of the German Network for Systemic Scleroderma: correlation with characteristic clinical features. Arthritis Res Ther (2011) 1.09
Stem cell therapy for Alport syndrome: the hope beyond the hype. Nephrol Dial Transplant (2008) 1.07
High frequency of corticosteroid and immunosuppressive therapy in patients with systemic sclerosis despite limited evidence for efficacy. Arthritis Res Ther (2009) 1.05
Chemokine receptor Ccr2 deficiency reduces renal disease and prolongs survival in MRL/lpr lupus-prone mice. J Am Soc Nephrol (2005) 1.03
Antifibrotic, nephroprotective potential of ACE inhibitor vs AT1 antagonist in a murine model of renal fibrosis. Nephrol Dial Transplant (2004) 1.01
Viral 5'-triphosphate RNA and non-CpG DNA aggravate autoimmunity and lupus nephritis via distinct TLR-independent immune responses. Eur J Immunol (2008) 1.00
Human renal cell carcinoma induces a dendritic cell subset that uses T-cell crosstalk for tumor-permissive milieu alterations. Am J Pathol (2011) 1.00
Podoplanin-positive cells are a hallmark of encapsulating peritoneal sclerosis. Nephrol Dial Transplant (2010) 1.00
Intrarenal production of B-cell survival factors in human lupus nephritis. Mod Pathol (2010) 1.00
Anti-Ccl2 Spiegelmer permits 75% dose reduction of cyclophosphamide to control diffuse proliferative lupus nephritis and pneumonitis in MRL-Fas(lpr) mice. J Pharmacol Exp Ther (2008) 0.99
CCR10 is expressed in cutaneous T-cell lymphoma. Int J Cancer (2005) 0.98
Hyperglycemia and hyperlipidemia act synergistically to induce renal disease in LDL receptor-deficient BALB mice. Am J Nephrol (2003) 0.98
Histological criteria for encapsulating peritoneal sclerosis - a standardized approach. PLoS One (2012) 0.96
Coactivation of Toll-like receptor-3 and -7 in immune complex glomerulonephritis. J Autoimmun (2007) 0.96
The chemokine receptor CXCR7 is expressed on lymphatic endothelial cells during renal allograft rejection. Kidney Int (2010) 0.96
Growth factor expression in a murine model of cryoglobulinemia. Kidney Int (2003) 0.95
Enhanced expression of Duffy antigen in the lungs during suppurative pneumonia. J Histochem Cytochem (2003) 0.95
Phenotypes of encapsulating peritoneal sclerosis--macroscopic appearance, histologic findings, and outcome. Perit Dial Int (2013) 0.95
Trif is not required for immune complex glomerulonephritis: dying cells activate mesangial cells via Tlr2/Myd88 rather than Tlr3/Trif. Am J Physiol Renal Physiol (2009) 0.94
Novel COL4A4 splice defect and in-frame deletion in a large consanguine family as a genetic link between benign familial haematuria and autosomal Alport syndrome. Nephrol Dial Transplant (2003) 0.93
Nephroprotective effect of the HMG-CoA-reductase inhibitor cerivastatin in a mouse model of progressive renal fibrosis in Alport syndrome. Nephrol Dial Transplant (2007) 0.93
mTOR regulates vascular smooth muscle cell differentiation from human bone marrow-derived mesenchymal progenitors. Arterioscler Thromb Vasc Biol (2008) 0.92
Deletion of the fcgamma receptor IIb in thymic stromal lymphopoietin transgenic mice aggravates membranoproliferative glomerulonephritis. Am J Pathol (2003) 0.92
Localization of SPARC in developing, mature, and chronically injured human allograft kidneys. Kidney Int (2002) 0.90
Pioglitazone reverses down-regulation of cardiac PPARgamma expression in Zucker diabetic fatty rats. Biochem Biophys Res Commun (2005) 0.89
P2 receptor antagonist PPADS inhibits mesangial cell proliferation in experimental mesangial proliferative glomerulonephritis. Kidney Int (2002) 0.89
[Successful treatment of a severe case of idiopathic pulmonary fibrosis with rapamycin]. Med Klin (Munich) (2005) 0.88
Targeting of sodium-glucose cotransporters with phlorizin inhibits polycystic kidney disease progression in Han:SPRD rats. Kidney Int (2013) 0.88
Ccl2/Mcp-1 blockade reduces glomerular and interstitial macrophages but does not ameliorate renal pathology in collagen4A3-deficient mice with autosomal recessive Alport nephropathy. J Pathol (2009) 0.87
Impact of chemokine receptor CX3CR1 in human renal allograft rejection. Transpl Immunol (2010) 0.86
Cost effectiveness of enoxaparin as prophylaxis against venous thromboembolic complications in acutely ill medical inpatients: modelling study from the hospital perspective in Germany. Pharmacoeconomics (2006) 0.85
Chronic renal failure and shortened lifespan in COL4A3+/- mice: an animal model for thin basement membrane nephropathy. J Am Soc Nephrol (2006) 0.85
A complex pattern of chemokine receptor expression is seen in osteosarcoma. BMC Cancer (2008) 0.84
Dendritic cells in human renal inflammation--Part II. Nephron Exp Nephrol (2011) 0.84
Bone marrow transplantation rescues Alport mice. Nephrol Dial Transplant (2006) 0.84
Developmental expression and functional significance of Kir channel subunits in ureteric bud and nephron epithelia. Pflugers Arch (2002) 0.84
[From the molecular genetics of Alport's syndrome to principles of organo-protection in chronic renal diseases]. Med Klin (Munich) (2005) 0.83
Interstitial inflammation in Alport syndrome. Hum Pathol (2009) 0.83