Published in Ann Otol Rhinol Laryngol on June 01, 1992
Clinical overview and treatment options for non-skeletal manifestations of mucopolysaccharidosis type IVA. J Inherit Metab Dis (2012) 1.32
Development of sensory, motor and behavioral deficits in the murine model of Sanfilippo syndrome type B. PLoS One (2007) 1.23
International guidelines for the management and treatment of Morquio A syndrome. Am J Med Genet A (2014) 1.19
Disease correction by combined neonatal intracranial AAV and systemic lentiviral gene therapy in Sanfilippo Syndrome type B mice. Gene Ther (2013) 0.86
Management of otolaryngological manifestations in mucopolysaccharidoses: our experience. Acta Otorhinolaryngol Ital (2013) 0.79
Separation of viable Rickettsia typhi from yolk sac and L cell host components by renografin density gradient centrifugation. Appl Microbiol (1975) 6.55
p53 mutations in colorectal cancer. Proc Natl Acad Sci U S A (1990) 5.43
The Mycobacterium tuberculosis 65-kilodalton antigen is a heat shock protein which corresponds to common antigen and to the Escherichia coli GroEL protein. Infect Immun (1988) 5.03
Energy metabolism of monocytic Ehrlichia. Proc Natl Acad Sci U S A (1989) 4.04
High-resolution EEG mapping of cortical activation related to working memory: effects of task difficulty, type of processing, and practice. Cereb Cortex (1997) 4.00
Biochemical stratagem for obligate parasitism of eukaryotic cells by Coxiella burnetii. Proc Natl Acad Sci U S A (1981) 3.91
Public and biobank participant attitudes toward genetic research participation and data sharing. Public Health Genomics (2010) 3.57
Serological evaluation of O fever in humans: enhanced phase I titers of immunoglobulins G and A are diagnostic for Q fever endocarditis. Infect Immun (1983) 3.18
A heat shock operon in Coxiella burnetti produces a major antigen homologous to a protein in both mycobacteria and Escherichia coli. J Bacteriol (1988) 3.06
Automated follow-up facilities in Canada for monitoring delayed health effects. Am J Public Health (1980) 2.85
Arrays of complementary oligonucleotides for analysing the hybridisation behaviour of nucleic acids. Nucleic Acids Res (1994) 2.75
Immunological and biological characterization of Coxiella burnetii, phases I and II, separated from host components. Infect Immun (1981) 2.71
The specific selection of recirculating lymphocytes by antigen in normal and preimmunized rats. J Exp Med (1972) 2.66
Primary structure of the L subunit of the reaction center from Rhodopseudomonas sphaeroides. Proc Natl Acad Sci U S A (1984) 2.65
Genetic evidence for superoperonal organization of genes for photosynthetic pigments and pigment-binding proteins in Rhodobacter capsulatus. Mol Gen Genet (1989) 2.60
Transgenic mouse mammary tumor virus superantigen expression prevents viral infection. Cell (1992) 2.55
The distribution and differentiation of lymph-borne immunoblasts after intravenous injection into syngeneic recipients. Cell Tissue Kinet (1972) 2.52
Developmental cycle of Coxiella burnetii: structure and morphogenesis of vegetative and sporogenic differentiations. J Bacteriol (1981) 2.50
Seroconversion, sexual activity, and condom use among 2915 HIV seronegative men followed for up to 2 years. J Acquir Immune Defic Syndr (1989) 2.48
Flexible polyimide-based intracortical electrode arrays with bioactive capability. IEEE Trans Biomed Eng (2001) 2.44
Sales of nonprescription cold remedies: a unique method of influenza surveillance. Pediatr Res (1979) 2.22
Biochemical and immunochemical analysis of Rickettsia rickettsii strains of various degrees of virulence. Infect Immun (1984) 2.12
The small-intestinal mucosa in cow's milk allergy. Lancet (1975) 2.07
Facial neurilemmomas. Laryngoscope (1981) 1.91
Placentitis and Abortion in Goats and Sheep in Ontario Caused by Coxiella burnetii. Can Vet J (1983) 1.90
The class II phosphoinositide 3-kinase C2alpha is activated by clathrin and regulates clathrin-mediated membrane trafficking. Mol Cell (2001) 1.87
Effects of long-term electrical stimulation on some contractile and metabolic characteristics of fast rabbit muscles. Pflugers Arch (1973) 1.85
Immunogenicity and toxicity of lipopolysaccharide from Francisella tularensis LVS. FEMS Microbiol Immunol (1992) 1.82
Neurophysiological measures of working memory and individual differences in cognitive ability and cognitive style. Cereb Cortex (2000) 1.81
Energy metabolism of Rickettsia typhi: pools of adenine nucleotides and energy charge in the presence and absence of glutamate. J Bacteriol (1978) 1.81
Chemical and immunological characterization of lipopolysaccharides from phase I and phase II Coxiella burnetii. J Bacteriol (1984) 1.78
Are schools safe? Analysis of 409 student accidents in elementary schools. Clin Pediatr (Phila) (1969) 1.78
Exposure to parturient cats: a risk factor for acquisition of Q fever in Maritime Canada. J Infect Dis (1988) 1.73
Transverse-momentum and pseudorapidity distributions of charged hadrons in pp collisions at square root of s = 7 TeV. Phys Rev Lett (2010) 1.67
Combined rhegmatogenous-traction retinal detachment following successful treatment of Candida chorioretinitis. Arch Ophthalmol (1992) 1.66
Amino terminal sequence of the major component of human lymphoblastoid interferon. Science (1980) 1.66
Accuracies of computer versus manual linkages of routine health records. Methods Inf Med (1979) 1.64
Monoclonal antibodies distinguish phase variants of Coxiella burnetii. Infect Immun (1984) 1.60
Monitoring working memory load during computer-based tasks with EEG pattern recognition methods. Hum Factors (1998) 1.58
Surgical removal of a subretinal proliferating cysticercus of taeniaeformis crassiceps. Arch Ophthalmol (1997) 1.57
Information system linking a medical school with practitioners and hospitals. J Med Educ (1987) 1.57
Aromatization of androstenedione by human adipose tissue stromal cells in monolayer culture. J Clin Endocrinol Metab (1981) 1.55
Preoperative thyroid scanning in presumed thyroglossal duct cysts. Arch Otolaryngol Head Neck Surg (1992) 1.55
Vole agent identified as a strain of the trench fever rickettsia, Rochalimaea quintana. Infect Immun (1978) 1.54
Endogenous Pseudallescheria boydii endophthalmitis. Clinicopathologic findings in two cases. Arch Ophthalmol (1991) 1.54
Ocular complications in Ehlers-Danlos syndrome type IV. Arch Ophthalmol (1997) 1.54
Multilayer PDMS microfluidic chamber for controlling brain slice microenvironment. Lab Chip (2007) 1.52
Peptidoglycan of Legionella pneumophila: apparent resistance to lysozyme hydrolysis correlates with a high degree of peptide cross-linking. J Bacteriol (1983) 1.51
Seroepidemiology of Q fever among domestic animals in Nova Scotia. Am J Public Health (1985) 1.51
Using gadolinium-enhanced magnetic resonance imaging lesions to monitor disease activity in multiple sclerosis. Ann Neurol (1992) 1.50
Biological and immunological properties of Coxiella burnetii vaccines in C57BL/10ScN endotoxin-nonresponder mice. Infect Immun (1982) 1.50
The matrix attachment region-binding protein SATB1 participates in negative regulation of tissue-specific gene expression. Mol Cell Biol (1997) 1.50
The Department of Veterans Affairs medical care system and the people it serves. Med Care (1996) 1.49
High diversity and widespread occurrence of mitotic spore mats in ectomycorrhizal Pezizales. Mol Ecol (2012) 1.49
A comparative study of the value of immunohistochemistry and the polymerase chain reaction in the diagnosis of follicular lymphoma. Histopathology (1995) 1.48
The transport of pteroylglutamic acid across the small intestine of the rat. Biochim Biophys Acta (1970) 1.48
Interstitial laser photocoagulation as a treatment for breast cancer. Br J Surg (1994) 1.48
The role of the linker between the SH2 domain and catalytic domain in the regulation and function of Src. EMBO J (1997) 1.47
A Coxiella burnetti repeated DNA element resembling a bacterial insertion sequence. J Bacteriol (1992) 1.46
Q fever pneumonia associated with exposure to wild rabbits. Lancet (1986) 1.45
Homing of lymph-borne immunoblasts to the gut. Nature (1970) 1.45
Newer Knowledge of Blood Transfusions. Bull N Y Acad Med (1941) 1.44
The effect of hypocholesteremic agents on myelinogenesis. J Neurochem (1969) 1.43
Cadherins in reactive lymph nodes and lymphomas: high expression in anaplastic large cell lymphomas. Histopathology (1996) 1.40
West Nile Virus in the New World: trends in the spread and proliferation of West Nile Virus in the Western Hemisphere. Zoonoses Public Health (2009) 1.39
Echocardiographic abnormalities in the mucopolysaccharide storage diseases. Am J Cardiol (1988) 1.39
A method for the calculation of areas under indicator-dilution curves. J Appl Physiol (1966) 1.38
Enzymatic activities leading to pyrimidine nucleotide biosynthesis from cell-free extracts of Rickettsia typhi. Infect Immun (1976) 1.38
The incidence of genetic disease and the impact on man of an altered mutation rate. Can J Genet Cytol (1977) 1.37
A massive, cooling-flow-induced starburst in the core of a luminous cluster of galaxies. Nature (2012) 1.36
Migration of lymphoblasts in the rat. Preferential localization of DNA-synthesizing lymphocytes in particular lymph nodes and other sties. Monogr Allergy (1980) 1.36
Gaucher cells in chronic myelocytic leukemia: an acquired abnormality. Blood (1969) 1.36
The role of phosphatidate phosphohydrolase in glyceride biosynthesis. Eur J Biochem (1967) 1.36
Seroepidemiology of Q fever in Nova Scotia and Prince Edward Island. Can J Microbiol (1984) 1.36
A phase II trial of nerve growth factor for sensory neuropathy associated with HIV infection. AIDS Clinical Trials Group Team 291. Neurology (2000) 1.35
Poker players' pneumonia. An urban outbreak of Q fever following exposure to a parturient cat. N Engl J Med (1988) 1.34
Repression of enzyme synthesis of the pyrimidine pathway in Salmonella typhimurium. J Bacteriol (1973) 1.34
Fully-automated quantification of regional brain volumes for improved detection of focal atrophy in Alzheimer disease. AJNR Am J Neuroradiol (2008) 1.33
Current and future strategies for the treatment of malignant brain tumors. Pharmacol Ther (2003) 1.33
B and T cells are required for mouse mammary tumor virus spread within the mammary gland. J Immunol (1998) 1.33
Biochemical and immunological properties of Coxiella burnetii cell wall and peptidoglycan-protein complex fractions. J Bacteriol (1984) 1.31
Identification of phase-specific antigenic fractions of Coxiella burnetti by enzyme-linked immunosorbent assay. J Clin Microbiol (1986) 1.31
Mortality and prognosis related to the amyloidosis of Still's disease. Ann Rheum Dis (1968) 1.30
Cellular immunity in Q fever: modulation of responsiveness by a suppressor T cell-monocyte circuit. J Immunol (1985) 1.30
Musculoskeletal changes following non-invasive knee injury using a novel mouse model of post-traumatic osteoarthritis. Osteoarthritis Cartilage (2012) 1.29
Maternal allele loss in Wilms' tumour. Lancet (1989) 1.29
Purification and translation of murine mammary tumor virus mRNA's. J Virol (1981) 1.29
Neurological deterioration in adult phenylketonuria. J Inherit Metab Dis (1989) 1.28
The recirculating lymphocyte pool of the rat: a systematic description of the migratory behaviour of recirculating lymphocytes. Immunology (1983) 1.27
The effect of interferon-beta on blood-brain barrier disruptions demonstrated by contrast-enhanced magnetic resonance imaging in relapsing-remitting multiple sclerosis. Ann Neurol (1995) 1.27
Specific alteration of the oxidation potential of the electron donor in reaction centers from Rhodobacter sphaeroides. Proc Natl Acad Sci U S A (1994) 1.27
Passive protection of mice against lethal Francisella tularensis (live tularemia vaccine strain) infection by the sera of human recipients of the live tularemia vaccine. Am J Med Sci (1994) 1.27
Structure and biological relationships of Coxiella burnetii lipopolysaccharides. J Biol Chem (1987) 1.27
Helical CT of urinary calculi: effect of stone composition, stone size, and scan collimation. AJR Am J Roentgenol (2000) 1.26
Pre-analytical and analytical variables affecting the measurement of plasma-derived microparticle tissue factor activity. Thromb Res (2011) 1.25
Chromosomal DNA deletions explain phenotypic characteristics of two antigenic variants, phase II and RSA 514 (crazy), of the Coxiella burnetii nine mile strain. Infect Immun (2002) 1.25
The class II phosphoinositide 3-kinase PI3K-C2alpha is concentrated in the trans-Golgi network and present in clathrin-coated vesicles. J Biol Chem (2000) 1.25
Low expression of collagen receptors in moderate and poorly differentiated colorectal adenocarcinomas. Br J Cancer (1990) 1.25