| Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
|
1
|
Phase II trial of single-agent bevacizumab followed by bevacizumab plus irinotecan at tumor progression in recurrent glioblastoma.
|
J Clin Oncol
|
2008
|
8.79
|
|
2
|
Magnetic resonance imaging and computed tomography in emergency assessment of patients with suspected acute stroke: a prospective comparison.
|
Lancet
|
2007
|
8.68
|
|
3
|
Neonatal-onset multisystem inflammatory disease responsive to interleukin-1beta inhibition.
|
N Engl J Med
|
2006
|
6.17
|
|
4
|
An autoinflammatory disease with deficiency of the interleukin-1-receptor antagonist.
|
N Engl J Med
|
2009
|
4.97
|
|
5
|
Comparison of MRI and CT for detection of acute intracerebral hemorrhage.
|
JAMA
|
2004
|
4.82
|
|
6
|
Pathophysiology of persistent syringomyelia after decompressive craniocervical surgery. Clinical article.
|
J Neurosurg Spine
|
2010
|
2.49
|
|
7
|
Congenital disorder of oxygen sensing: association of the homozygous Chuvash polycythemia VHL mutation with thrombosis and vascular abnormalities but not tumors.
|
Blood
|
2004
|
2.27
|
|
8
|
Hypo-functional SLC26A4 variants associated with nonsyndromic hearing loss and enlargement of the vestibular aqueduct: genotype-phenotype correlation or coincidental polymorphisms?
|
Hum Mutat
|
2009
|
2.25
|
|
9
|
Neurofibromatosis type 2.
|
Lancet
|
2009
|
2.24
|
|
10
|
Pathophysiology of primary spinal syringomyelia.
|
J Neurosurg Spine
|
2012
|
1.92
|
|
11
|
Successful and safe perfusion of the primate brainstem: in vivo magnetic resonance imaging of macromolecular distribution during infusion.
|
J Neurosurg
|
2002
|
1.79
|
|
12
|
User-friendly software for the analysis of brain lesions (ABLe).
|
Comput Methods Programs Biomed
|
2007
|
1.63
|
|
13
|
Long-term natural history of neurofibromatosis Type 2-associated intracranial tumors.
|
J Neurosurg
|
2012
|
1.59
|
|
14
|
Long-term natural history of hemangioblastomas in patients with von Hippel-Lindau disease: implications for treatment.
|
J Neurosurg
|
2006
|
1.55
|
|
15
|
Quantification of brain lesions using interactive automated software.
|
Behav Res Methods Instrum Comput
|
2002
|
1.51
|
|
16
|
West Nile virus: pathogenesis and therapeutic options.
|
Ann Intern Med
|
2004
|
1.51
|
|
17
|
Real-time image-guided direct convective perfusion of intrinsic brainstem lesions. Technical note.
|
J Neurosurg
|
2007
|
1.51
|
|
18
|
The vestibular aqueduct: site of origin of endolymphatic sac tumors.
|
J Neurosurg
|
2008
|
1.49
|
|
19
|
Normal vision despite narrowing of the optic canal in fibrous dysplasia.
|
N Engl J Med
|
2002
|
1.47
|
|
20
|
Increased signal intensity in the pulvinar on T1-weighted images: a pathognomonic MR imaging sign of Fabry disease.
|
AJNR Am J Neuroradiol
|
2003
|
1.44
|
|
21
|
Cochlear implantation for hearing loss associated with bilateral endolymphatic sac tumors in von Hippel-Lindau disease.
|
Otol Neurotol
|
2007
|
1.41
|
|
22
|
Sustained response and prevention of damage progression in patients with neonatal-onset multisystem inflammatory disease treated with anakinra: a cohort study to determine three- and five-year outcomes.
|
Arthritis Rheum
|
2012
|
1.40
|
|
23
|
Tumors of the endolymphatic sac in von Hippel-Lindau disease.
|
N Engl J Med
|
2004
|
1.38
|
|
24
|
Single-trial fMRI shows contralesional activity linked to overt naming errors in chronic aphasic patients.
|
J Cogn Neurosci
|
2010
|
1.38
|
|
25
|
Evaluation of essential tremor with multi-voxel magnetic resonance spectroscopy.
|
Neurology
|
2003
|
1.36
|
|
26
|
Cerebrovascular disease associated with sickle cell pulmonary hypertension.
|
Am J Hematol
|
2006
|
1.35
|
|
27
|
Validation of dynamic contrast-enhanced magnetic resonance imaging-derived vascular permeability measurements using quantitative autoradiography in the RG2 rat brain tumor model.
|
Neoplasia
|
2007
|
1.33
|
|
28
|
Successful treatment of melanoma brain metastases with adoptive cell therapy.
|
Clin Cancer Res
|
2010
|
1.31
|
|
29
|
Surgery versus watchful waiting in patients with craniofacial fibrous dysplasia--a meta-analysis.
|
PLoS One
|
2011
|
1.27
|
|
30
|
Long-term outcome of optic nerve encasement and optic nerve decompression in patients with fibrous dysplasia: risk factors for blindness and safety of observation.
|
Neurosurgery
|
2006
|
1.23
|
|
31
|
Edema is a precursor to central nervous system peritumoral cyst formation.
|
Ann Neurol
|
2005
|
1.23
|
|
32
|
Real-time in vivo imaging of the convective distribution of a low-molecular-weight tracer.
|
J Neurosurg
|
2005
|
1.17
|
|
33
|
Effect of ependymal and pial surfaces on convection-enhanced delivery.
|
J Neurosurg
|
2008
|
1.17
|
|
34
|
Prospective evaluation of radiosurgery for hemangioblastomas in von Hippel-Lindau disease.
|
Neuro Oncol
|
2009
|
1.17
|
|
35
|
Image-guided convection-enhanced delivery of gemcitabine to the brainstem.
|
J Neurosurg
|
2007
|
1.17
|
|
36
|
Cerebrovascular disease in HIV-infected pediatric patients: neuroimaging findings.
|
AJR Am J Roentgenol
|
2002
|
1.17
|
|
37
|
White matter alterations differ in primary lateral sclerosis and amyotrophic lateral sclerosis.
|
Brain
|
2011
|
1.15
|
|
38
|
Iron accumulation in deep cortical layers accounts for MRI signal abnormalities in ALS: correlating 7 tesla MRI and pathology.
|
PLoS One
|
2012
|
1.13
|
|
39
|
Tumors of the endolymphatic sac in patients with von Hippel-Lindau disease: implications for their natural history, diagnosis, and treatment.
|
J Neurosurg
|
2005
|
1.13
|
|
40
|
Optic neuropathy in McCune-Albright syndrome: effects of early diagnosis and treatment of growth hormone excess.
|
J Clin Endocrinol Metab
|
2012
|
1.13
|
|
41
|
Effects of VHL deficiency on endolymphatic duct and sac.
|
Cancer Res
|
2005
|
1.11
|
|
42
|
Pituitary stalk hemangioblastomas in von Hippel-Lindau disease.
|
J Neurosurg
|
2009
|
1.10
|
|
43
|
A phase II trial of single-agent bevacizumab in patients with recurrent anaplastic glioma.
|
Neuro Oncol
|
2011
|
1.09
|
|
44
|
A phase I/II trial of enzastaurin in patients with recurrent high-grade gliomas.
|
Neuro Oncol
|
2010
|
1.08
|
|
45
|
Interferon-beta1a therapy in human T-lymphotropic virus type I-associated neurologic disease.
|
Ann Neurol
|
2005
|
1.05
|
|
46
|
Conventional magnetic resonance imaging features in patients with tropical spastic paraparesis.
|
J Neurovirol
|
2005
|
1.03
|
|
47
|
Nonsyndromic hearing loss DFNA10 and a novel mutation of EYA4: evidence for correlation of normal cardiac phenotype with truncating mutations of the Eya domain.
|
Am J Med Genet A
|
2007
|
1.02
|
|
48
|
Endolymphatic sac tumor demonstrated by intralabyrinthine hemorrhage. Case report.
|
J Neurosurg
|
2007
|
1.02
|
|
49
|
Modulated repetition time look-locker (MORTLL): a method for rapid high resolution three-dimensional T1 mapping.
|
J Magn Reson Imaging
|
2009
|
1.01
|
|
50
|
Surgical resection of endolymphatic sac tumors in von Hippel-Lindau disease: findings, results, and indications.
|
Laryngoscope
|
2012
|
0.98
|
|
51
|
SLC26A4 genotype, but not cochlear radiologic structure, is correlated with hearing loss in ears with an enlarged vestibular aqueduct.
|
Laryngoscope
|
2010
|
0.95
|
|
52
|
Prospective natural history study of central nervous system hemangioblastomas in von Hippel-Lindau disease.
|
J Neurosurg
|
2014
|
0.94
|
|
53
|
Pegvisomant for the treatment of gsp-mediated growth hormone excess in patients with McCune-Albright syndrome.
|
J Clin Endocrinol Metab
|
2006
|
0.94
|
|
54
|
Local distribution and toxicity of prolonged hippocampal infusion of muscimol.
|
J Neurosurg
|
2005
|
0.90
|
|
55
|
Phase 2 trial of talampanel, a glutamate receptor inhibitor, for adults with recurrent malignant gliomas.
|
Cancer
|
2010
|
0.90
|
|
56
|
Investigation of the role of congenital cytomegalovirus infection in the etiology of enlarged vestibular aqueducts.
|
Arch Otolaryngol Head Neck Surg
|
2005
|
0.88
|
|
57
|
Chimeric negative regulation of p14ARF and TBX1 by a t(9;22) translocation associated with melanoma, deafness, and DNA repair deficiency.
|
Hum Mutat
|
2013
|
0.87
|
|
58
|
SLC26A4 genotypes and phenotypes associated with enlargement of the vestibular aqueduct.
|
Cell Physiol Biochem
|
2011
|
0.87
|
|
59
|
Cryopyrin-associated periodic syndromes: otolaryngologic and audiologic manifestations.
|
Otolaryngol Head Neck Surg
|
2011
|
0.86
|
|
60
|
Mechanisms of hearing loss in neurofibromatosis type 2.
|
PLoS One
|
2012
|
0.85
|
|
61
|
A new method for the study of velopharyngeal function using gated magnetic resonance imaging.
|
Plast Reconstr Surg
|
2002
|
0.84
|
|
62
|
Pathogenesis of tumor-associated syringomyelia demonstrated by peritumoral contrast material leakage. Case illustration.
|
J Neurosurg Spine
|
2006
|
0.84
|
|
63
|
Metabolically stable bradykinin B2 receptor agonists enhance transvascular drug delivery into malignant brain tumors by increasing drug half-life.
|
J Transl Med
|
2009
|
0.84
|
|
64
|
Cortical mapping and frameless stereotactic navigation in the high-field intraoperative magnetic resonance imaging suite.
|
J Neurosurg
|
2009
|
0.83
|
|
65
|
Surgical management of lumbosacral nerve root hemangioblastomas in von Hippel-Lindau syndrome.
|
J Neurosurg
|
2003
|
0.83
|
|
66
|
Segmentation of brain tumors in 4D MR images using the hidden Markov model.
|
Comput Methods Programs Biomed
|
2006
|
0.83
|
|
67
|
Integra Foundation Award: Long-term natural history of hemangioblastomas in Von Hippel-Lindau disease: implications for treatment.
|
Clin Neurosurg
|
2006
|
0.83
|
|
68
|
Progressive peritumoral edema defining the optic fibers and resulting in reversible visual loss.
|
J Neurosurg
|
2008
|
0.82
|
|
69
|
Role of edema in peritumoral cyst formation.
|
Neurosurg Focus
|
2007
|
0.82
|
|
70
|
Sacral hemangioblastoma in a patient with von Hippel-Lindau disease. Case report and review of the literature.
|
Neurosurg Focus
|
2003
|
0.82
|
|
71
|
Tracking accuracy of T2- and diffusion-weighted magnetic resonance imaging for infusate distribution by convection-enhanced delivery.
|
J Neurosurg
|
2011
|
0.82
|
|
72
|
Association of brain-derived neurotrophic factor (BDNF) haploinsufficiency with lower adaptive behaviour and reduced cognitive functioning in WAGR/11p13 deletion syndrome.
|
Cortex
|
2013
|
0.81
|
|
73
|
Whole-brain cerebral blood flow mapping using 3D echo planar imaging and pulsed arterial tagging.
|
J Magn Reson Imaging
|
2011
|
0.81
|
|
74
|
Variable expressivity of FGF3 mutations associated with deafness and LAMM syndrome.
|
BMC Med Genet
|
2011
|
0.81
|
|
75
|
Quantitative assessment of susceptibility-weighted imaging processing methods.
|
J Magn Reson Imaging
|
2013
|
0.81
|
|
76
|
Idiopathic intracranial hypertension following kidney transplantation: a case report and review of the literature.
|
Pediatr Transplant
|
2005
|
0.80
|
|
77
|
Thoracic spinal nerve hemangioblastoma. Case illustration.
|
J Neurosurg Spine
|
2004
|
0.80
|
|
78
|
Subarachnoid hemorrhage and the distribution of drugs delivered into the cerebrospinal fluid. Laboratory investigation.
|
J Neurosurg
|
2009
|
0.80
|
|
79
|
Use of SLC26A4 mutation testing for unilateral enlargement of the vestibular aqueduct.
|
JAMA Otolaryngol Head Neck Surg
|
2013
|
0.78
|
|
80
|
Clinical course of retrobulbar hemangioblastomas in von Hippel-Lindau disease.
|
Ophthalmology
|
2008
|
0.78
|
|
81
|
Hereditary hearing loss with thyroid abnormalities.
|
Adv Otorhinolaryngol
|
2011
|
0.78
|
|
82
|
Pineal hypoplasia, reduced melatonin and sleep disturbance in patients with PAX6 haploinsufficiency.
|
J Sleep Res
|
2016
|
0.78
|
|
83
|
Fast T1 mapping determined using incomplete inversion recovery look-locker 3D balanced SSFP acquisition and a simple two-parameter model fit.
|
J Magn Reson Imaging
|
2012
|
0.75
|
|
84
|
Treatment of high-risk venous thrombosis patients using low-dose intraclot injections of recombinant tissue plasminogen activator and regional anticoagulation.
|
J Vasc Interv Radiol
|
2013
|
0.75
|
|
85
|
Reduced scan time three-dimensional FLAIR using modulated inversion and repetition time.
|
J Magn Reson Imaging
|
2014
|
0.75
|
|
86
|
Blast-related traumatic brain injury in U.S. military personnel.
|
N Engl J Med
|
2011
|
0.75
|
|
87
|
Long-term stability after multilevel cervical laminectomy for spinal cord tumor resection in von Hippel-Lindau disease.
|
J Neurosurg Spine
|
2011
|
0.75
|
|
88
|
Granulocytic invasion of the central nervous system after hematopoietic stem cell transplantation for systemic lupus erythematosus.
|
Haematologica
|
2006
|
0.75
|