Juan Cabrera-Luque

Author PubWeight™ 7.02‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Long-term correction of ammonia metabolism and prolonged survival in ornithine transcarbamylase-deficient mice following liver-directed treatment with adeno-associated viral vectors. Mol Ther 2006 1.64
2 Acetylornithine transcarbamylase: a novel enzyme in arginine biosynthesis. J Bacteriol 2006 1.06
3 Inversion of allosteric effect of arginine on N-acetylglutamate synthase, a molecular marker for evolution of tetrapods. BMC Biochem 2008 0.97
4 Structure and catalytic mechanism of a novel N-succinyl-L-ornithine transcarbamylase in arginine biosynthesis of Bacteroides fragilis. J Biol Chem 2006 0.89
5 A novel N-acetylglutamate synthase architecture revealed by the crystal structure of the bifunctional enzyme from Maricaulis maris. PLoS One 2011 0.88
6 A single mutation in the active site swaps the substrate specificity of N-acetyl-L-ornithine transcarbamylase and N-succinyl-L-ornithine transcarbamylase. Protein Sci 2007 0.85
7 A novel biochemically salvageable animal model of hyperammonemia devoid of N-acetylglutamate synthase. Mol Genet Metab 2012 0.77