Published in Pediatr Pulmonol on August 01, 2006
Outcomes in children treated for persistent bacterial bronchitis. Thorax (2006) 1.57
Bronchodilator responsiveness in wheezy infants and toddlers is not associated with asthma risk factors. Pediatr Pulmonol (2011) 1.41
In young children, persistent wheezing is associated with bronchial bacterial infection: a retrospective analysis. BMC Pediatr (2012) 0.86
Infant pulmonary function testing: overview of technology and practical considerations--new current procedural terminology codes effective 2010. Chest (2011) 0.80
Objective assessment of lung disease in wheezy infants: the time has come. Pediatr Pulmonol (2006) 0.80
The habit cough syndrome and its variations. Lung (2011) 0.77
Persistent and Recurrent Bacterial Bronchitis-A Paradigm Shift in Our Understanding of Chronic Respiratory Disease. Front Pediatr (2017) 0.75
A 2-year-old girl with co-inherited cystic fibrosis and sickle cell-β+ thalassemia presenting with recurrent vaso-occlusive events during cystic fibrosis pulmonary exacerbations: a case report. J Med Case Rep (2013) 0.75
Recurrent wheeze and its relationship with lung function and airway inflammation in preschool children: a cross-sectional study in South Korea. BMJ Open (2017) 0.75
An official ATS clinical practice guideline: interpretation of exhaled nitric oxide levels (FENO) for clinical applications. Am J Respir Crit Care Med (2011) 5.53
Pseudomonas aeruginosa anaerobic respiration in biofilms: relationships to cystic fibrosis pathogenesis. Dev Cell (2002) 4.94
The genome of M. acetivorans reveals extensive metabolic and physiological diversity. Genome Res (2002) 4.58
Primary ciliary dyskinesia: diagnostic and phenotypic features. Am J Respir Crit Care Med (2003) 4.33
Congenital heart disease and other heterotaxic defects in a large cohort of patients with primary ciliary dyskinesia. Circulation (2007) 4.17
An official American Thoracic Society/European Respiratory Society statement: pulmonary function testing in preschool children. Am J Respir Crit Care Med (2007) 4.10
Mutations of DNAH11 in patients with primary ciliary dyskinesia with normal ciliary ultrastructure. Thorax (2011) 2.80
The Comparative Toxicogenomics Database: update 2013. Nucleic Acids Res (2012) 2.72
Clinical and genetic aspects of primary ciliary dyskinesia/Kartagener syndrome. Genet Med (2009) 2.71
Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis. J Pediatr (2009) 2.16
Deletions and point mutations of LRRC50 cause primary ciliary dyskinesia due to dynein arm defects. Am J Hum Genet (2009) 2.10
Primary ciliary dyskinesia. Recent advances in diagnostics, genetics, and characterization of clinical disease. Am J Respir Crit Care Med (2013) 2.09
Variability of a closed, rebreathing setup for multiple breath wash-out testing in children. Pediatr Pulmonol (2012) 2.03
Endotoxin activity and inflammatory markers in the airways of young patients with cystic fibrosis. Am J Respir Crit Care Med (2002) 1.94
Zebrafish Ciliopathy Screen Plus Human Mutational Analysis Identifies C21orf59 and CCDC65 Defects as Causing Primary Ciliary Dyskinesia. Am J Hum Genet (2013) 1.90
Mutations of DNAI1 in primary ciliary dyskinesia: evidence of founder effect in a common mutation. Am J Respir Crit Care Med (2006) 1.80
A bacterial cell to cell signal in the lungs of cystic fibrosis patients. FEMS Microbiol Lett (2002) 1.72
Exome sequencing identifies mutations in CCDC114 as a cause of primary ciliary dyskinesia. Am J Hum Genet (2012) 1.65
A CTD-Pfizer collaboration: manual curation of 88,000 scientific articles text mined for drug-disease and drug-phenotype interactions. Database (Oxford) (2013) 1.59
Computed tomography reflects lower airway inflammation and tracks changes in early cystic fibrosis. Am J Respir Crit Care Med (2007) 1.55
Whole-exome capture and sequencing identifies HEATR2 mutation as a cause of primary ciliary dyskinesia. Am J Hum Genet (2012) 1.53
Standardizing nasal nitric oxide measurement as a test for primary ciliary dyskinesia. Ann Am Thorac Soc (2013) 1.49
Crohn's disease with pulmonary manifestations in children: 2 case reports and review of the literature. J Crohns Colitis (2012) 1.46
DYX1C1 is required for axonemal dynein assembly and ciliary motility. Nat Genet (2013) 1.44
Nontuberculous mycobacterial infection in young children with cystic fibrosis. Pediatr Pulmonol (2005) 1.42
Next generation massively parallel sequencing of targeted exomes to identify genetic mutations in primary ciliary dyskinesia: implications for application to clinical testing. Genet Med (2011) 1.42
Calculating mixed venous saturation during veno-venous extracorporeal membrane oxygenation. Perfusion (2009) 1.42
Mutations in CCDC39 and CCDC40 are the major cause of primary ciliary dyskinesia with axonemal disorganization and absent inner dynein arms. Hum Mutat (2013) 1.31
Reduced expression of IRF7 in nasal epithelial cells from smokers after infection with influenza. Am J Respir Cell Mol Biol (2009) 1.29
High-resolution CT of patients with primary ciliary dyskinesia. AJR Am J Roentgenol (2007) 1.26
Cystic fibrosis airway secretions exhibit mucin hyperconcentration and increased osmotic pressure. J Clin Invest (2014) 1.26
Inhaled hypertonic saline in infants and children younger than 6 years with cystic fibrosis: the ISIS randomized controlled trial. JAMA (2012) 1.25
ZMYND10 is mutated in primary ciliary dyskinesia and interacts with LRRC6. Am J Hum Genet (2013) 1.24
Bronchoalveolar lavage fluid surfactant protein-A and surfactant protein-D are inversely related to inflammation in early cystic fibrosis. Am J Respir Crit Care Med (2003) 1.22
Diagnostic yield of nasal scrape biopsies in primary ciliary dyskinesia: a multicenter experience. Pediatr Pulmonol (2011) 1.22
Mutations in SPAG1 cause primary ciliary dyskinesia associated with defective outer and inner dynein arms. Am J Hum Genet (2013) 1.19
ARMC4 mutations cause primary ciliary dyskinesia with randomization of left/right body asymmetry. Am J Hum Genet (2013) 1.17
Overweight and obese adult humans have a defective cellular immune response to pandemic H1N1 influenza A virus. Obesity (Silver Spring) (2013) 1.17
Mutations in RSPH1 cause primary ciliary dyskinesia with a unique clinical and ciliary phenotype. Am J Respir Crit Care Med (2014) 1.14
Clinical features of childhood primary ciliary dyskinesia by genotype and ultrastructural phenotype. Am J Respir Crit Care Med (2015) 1.09
Early lung disease in young children with primary ciliary dyskinesia. Pediatr Pulmonol (2008) 1.08
Association of lower airway inflammation with physiologic findings in young children with cystic fibrosis. Pediatr Pulmonol (2009) 1.06
Investigation of the possible role of a novel gene, DPCD, in primary ciliary dyskinesia. Am J Respir Cell Mol Biol (2003) 1.05
Nasal lavage natural killer cell function is suppressed in smokers after live attenuated influenza virus. Respir Res (2011) 1.04
Ciliopathies: the central role of cilia in a spectrum of pediatric disorders. J Pediatr (2011) 1.03
Outcomes of children with severe bronchopulmonary dysplasia who were ventilator dependent at home. Pediatrics (2013) 1.02
Quantitative cytokine gene expression in CF airway. Pediatr Pulmonol (2004) 1.01
The effect of respiratory synctial virus on chemokine release by differentiated airway epithelium. Exp Lung Res (2004) 1.00
Temporal microRNA expression during in vitro myogenic progenitor cell proliferation and differentiation: regulation of proliferation by miR-682. Physiol Genomics (2010) 0.99
Update of respiratory tract disease in children with primary ciliary dyskinesia. Proc Am Thorac Soc (2011) 0.98
Plasma TGF-β₁ in pediatric cystic fibrosis: potential biomarker of lung disease and response to therapy. Pediatr Pulmonol (2011) 0.98
Safety and tolerability of inhaled hypertonic saline in young children with cystic fibrosis. Pediatr Pulmonol (2008) 0.95
Survey of clinical infant lung function testing practices. Pediatr Pulmonol (2013) 0.94
Are lower airway or throat cultures predictive of sinus bacteriology in cystic fibrosis? Pediatr Pulmonol (2006) 0.94
Primary ciliary dyskinesia in Amish communities. J Pediatr (2010) 0.92
Cystic fibrosis: NHLBI Workshop on the Primary Prevention of Chronic Lung Diseases. Ann Am Thorac Soc (2014) 0.92
An official American Thoracic Society workshop report: optimal lung function tests for monitoring cystic fibrosis, bronchopulmonary dysplasia, and recurrent wheezing in children less than 6 years of age. Ann Am Thorac Soc (2013) 0.92
Transforming growth factor-beta(1) in bronchoalveolar lavage fluid from children with cystic fibrosis. Pediatr Pulmonol (2009) 0.92
Bronchoscopy-derived correlates of lung injury following inhalational injuries: a prospective observational study. PLoS One (2013) 0.89
Live attenuated influenza virus (LAIV) induces different mucosal T cell function in nonsmokers and smokers. Clin Immunol (2012) 0.89
Founder mutation in RSPH4A identified in patients of Hispanic descent with primary ciliary dyskinesia. Hum Mutat (2013) 0.89
Attenuation of host defense function of lung phagocytes in young cystic fibrosis patients. J Cyst Fibros (2005) 0.88
Combined treatment of rapamycin and dietary restriction has a larger effect on the transcriptome and metabolome of liver. Aging Cell (2013) 0.88
Age of Pseudomonas aeruginosa acquisition and subsequent severity of cystic fibrosis lung disease. Pediatr Pulmonol (2010) 0.87
Population based surveillance in sickle cell disease: methods, findings and implications from the California registry and surveillance system in hemoglobinopathies project (RuSH). Pediatr Blood Cancer (2014) 0.85
Reduced lung function in cystic fibrosis: a primary or secondary phenotype? Am J Respir Crit Care Med (2008) 0.84
Sulforaphane induces SLPI secretion in the nasal mucosa. Respir Med (2012) 0.84
Identifying the origins of cystic fibrosis lung disease. N Engl J Med (2013) 0.83
Inhaled hypertonic saline in infants and toddlers with cystic fibrosis: short-term tolerability, adherence, and safety. Pediatr Pulmonol (2011) 0.83
Release of cytokines by human nasal epithelial cells and peripheral blood mononuclear cells infected with Mycoplasma pneumoniae. Exp Biol Med (Maywood) (2002) 0.83
Inhaled versus systemic antibiotics and airway inflammation in children with cystic fibrosis and Pseudomonas. Pediatr Pulmonol (2010) 0.83
Analysis of the associations between lung function and clinical features in preschool children with cystic fibrosis. Pediatr Pulmonol (2011) 0.82
Improvement in pulmonary function following antibiotics in infants with cystic fibrosis. Pediatr Pulmonol (2011) 0.82
Pulmonary exacerbations and parent-reported outcomes in children <6 years with cystic fibrosis. Pediatr Pulmonol (2014) 0.81
Exhaled breath condensate purines correlate with lung function in infants and preschoolers. Pediatr Pulmonol (2012) 0.81
DNA and inflammatory mediators in bronchoalveolar lavage fluid from children with acute inhalational injuries. J Burn Care Res (2013) 0.81
Diesel exhaust particles modify natural killer cell function and cytokine release. Part Fibre Toxicol (2013) 0.81
Caregiver perspectives on discussions about the use of intensive treatments in cystic fibrosis. J Pain Symptom Manage (2010) 0.81
Cutting edge genetic studies in primary ciliary dyskinesia. Thorax (2012) 0.80