Published in Laryngoscope on December 01, 2006
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A new leukoencephalopathy with brainstem and spinal cord involvement and high lactate. Ann Neurol (2003) 1.57
The natural history of juvenile or subacute GM2 gangliosidosis: 21 new cases and literature review of 134 previously reported. Pediatrics (2006) 1.50
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Neonatal encephalopathy: a prospective comparison of head US and MRI. Pediatr Radiol (2010) 1.15
Imaging of the brain in full-term neonates: does sonography still play a role? Pediatr Radiol (2006) 1.13
A case series of pediatric primary central nervous system lymphoma: favorable outcome without cranial irradiation. Pediatr Blood Cancer (2006) 1.13
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Late onset Leigh syndrome and ataxia due to a T to C mutation at bp 9,185 of mitochondrial DNA. Am J Med Genet A (2007) 1.06
Further expansion of the phenotypic spectrum associated with mutations in ALDH18A1, encoding Δ¹-pyrroline-5-carboxylate synthase (P5CS). Am J Med Genet A (2011) 1.06
Basal ganglia germinoma in children with associated ipsilateral cerebral and brain stem hemiatrophy. Pediatr Radiol (2006) 1.06
Soft tissue complications after small incision pediatric cochlear implantation. Laryngoscope (2009) 1.05
The role of conservative management in congenital tracheal stenosis: an evidence-based long-term follow-up study. J Pediatr Surg (2006) 1.02
Device fixation and small incision access for pediatric cochlear implants. Int J Pediatr Otorhinolaryngol (2004) 1.02
Prenatal US and MR imaging findings of lissencephaly: review of fetal cerebral sulcal development. Radiographics (2006) 1.01
Tone frequency maps and receptive fields in the developing chinchilla auditory cortex. J Neurophysiol (2004) 1.01
Diagnostic approach to childhood-onset cerebellar atrophy: a 10-year retrospective study of 300 patients. J Child Neurol (2012) 1.00
Cochlear implant surgery at 12 months of age or younger. Laryngoscope (2004) 1.00
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Retropharyngeal and parapharyngeal infections in children: the Toronto experience. Int J Pediatr Otorhinolaryngol (2005) 0.97
Late-onset cobalamin-C disorder: a challenging diagnosis. Am J Med Genet A (2007) 0.97
Evidence of vestibular and balance dysfunction in children with profound sensorineural hearing loss using cochlear implants. Laryngoscope (2008) 0.97
Toward a battery of behavioral and objective measures to achieve optimal cochlear implant stimulation levels in children. Ear Hear (2004) 0.96
Corrosion casting of the subglottis following endotracheal tube intubation injury: a pilot study in Yorkshire piglets. J Otolaryngol Head Neck Surg (2013) 0.96
Complex II deficiency--a case report and review of the literature. Am J Med Genet A (2013) 0.96
An evoked potential study of the developmental time course of the auditory nerve and brainstem in children using cochlear implants. Audiol Neurootol (2005) 0.95
Arginase I deficiency: severe infantile presentation with hyperammonemia: more common than reported? Mol Genet Metab (2011) 0.94
Brain abnormalities in patients with Beckwith-Wiedemann syndrome. Am J Med Genet A (2012) 0.93
MUC5AC expression in human middle ear epithelium of patients with otitis media. Arch Otolaryngol Head Neck Surg (2010) 0.93
Abnormal timing delays in auditory brainstem responses evoked by bilateral cochlear implant use in children. Otol Neurotol (2008) 0.93
Recognition of affective speech prosody and facial affect in deaf children with unilateral right cochlear implants. Child Neuropsychol (2009) 0.93
Weight gain in craniopharyngioma--a model for hypothalamic obesity. J Pediatr Endocrinol Metab (2006) 0.93
Partial agenesis of the corpus callosum in spina bifida meningomyelocele and potential compensatory mechanisms. J Clin Exp Neuropsychol (2008) 0.93
Petrified ears in a patient with Keutel syndrome: temporal bone CT findings. Pediatr Radiol (2005) 0.92
Beamformer suppression of cochlear implant artifacts in an electroencephalography dataset. IEEE Trans Biomed Eng (2009) 0.92
A test of static and dynamic balance function in children with cochlear implants: the vestibular olympics. Arch Otolaryngol Head Neck Surg (2008) 0.92
Molar tooth sign in fetal brain magnetic resonance imaging leading to the prenatal diagnosis of Joubert syndrome and related disorders. J Child Neurol (2006) 0.92
Auditory interhemispheric transfer in relation to patterns of partial agenesis and hypoplasia of the corpus callosum in spina bifida meningomyelocele. J Int Neuropsychol Soc (2008) 0.91
Bilateral cochlear implants should be the standard for children with bilateral sensorineural deafness. Curr Opin Otolaryngol Head Neck Surg (2008) 0.91
Children with bilateral cochlear implants identify emotion in speech and music. Cochlear Implants Int (2013) 0.91
Evaluation of subcortical white matter and deep white matter tracts in malformations of cortical development. Epilepsia (2007) 0.91
Benefits and detriments of unilateral cochlear implant use on bilateral auditory development in children who are deaf. Front Psychol (2013) 0.91
Computed tomography and/or magnetic resonance imaging before pediatric cochlear implantation? Developing an investigative strategy. Otol Neurotol (2007) 0.90
Bilateral input protects the cortex from unilaterally-driven reorganization in children who are deaf. Brain (2013) 0.90
Traumatic perilymphatic fistula with pneumolabyrinth: diagnosis and management. Laryngoscope (2011) 0.90
Basilar artery duplication associated with pituitary duplication: a new finding. AJNR Am J Neuroradiol (2003) 0.90
Benefits of short interimplant delays in children receiving bilateral cochlear implants. Otol Neurotol (2009) 0.90
Electrophysiologic and behavioral outcomes of cochlear implantation in children with auditory nerve hypoplasia. Ear Hear (2011) 0.90
Severe cleidocranial dysplasia can mimic hypophosphatasia. Eur J Pediatr (2002) 0.89
Fluid-attenuated inversion recovery ring sign as a marker of dysembryoplastic neuroepithelial tumors. J Comput Assist Tomogr (2007) 0.89
1H MR spectroscopic characteristics of kernicterus: a possible metabolic signature. AJNR Am J Neuroradiol (2005) 0.89
Atypical cortical responses underlie poor speech perception in children using cochlear implants. Neuroreport (2005) 0.89
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Binaural interactions develop in the auditory brainstem of children who are deaf: effects of place and level of bilateral electrical stimulation. J Neurosci (2012) 0.89
Bone-anchored hearing aids in infants and children younger than 5 years. Arch Otolaryngol Head Neck Surg (2007) 0.88
Parents of children with spinal muscular atrophy are not obligate carriers: carrier testing is important for reproductive decision-making. Am J Med Genet (2002) 0.88
Children using cochlear implants capitalize on acoustical hearing for music perception. Front Psychol (2012) 0.88
A recurrent EYA1 mutation causing alternative RNA splicing in branchio-oto-renal syndrome: implications for molecular diagnostics and disease mechanism. Am J Med Genet A (2009) 0.87
Activity-dependent developmental plasticity of the auditory brain stem in children who use cochlear implants. Ear Hear (2003) 0.87
Speech detection in noise and spatial unmasking in children with simultaneous versus sequential bilateral cochlear implants. Otol Neurotol (2011) 0.87
Mycoplasma pneumoniae ecephalitis. Semin Pediatr Infect Dis (2003) 0.86
Lateralization of interimplant timing and level differences in children who use bilateral cochlear implants. Ear Hear (2010) 0.86