Published in Neurochem Res on March 01, 2007
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Are amygdalar volume alterations in children with Tourette syndrome due to ADHD comorbidity? Dev Med Child Neurol (2008) 2.11
Energy metabolism in amyotrophic lateral sclerosis. Lancet Neurol (2010) 2.00
Two German kindreds with familial amyotrophic lateral sclerosis due to TARDBP mutations. Arch Neurol (2008) 1.78
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IgG antibodies against measles, rubella, and varicella zoster virus predict conversion to multiple sclerosis in clinically isolated syndrome. PLoS One (2009) 1.25
Whole brain-based analysis of regional white matter tract alterations in rare motor neuron diseases by diffusion tensor imaging. Hum Brain Mapp (2010) 1.23
Riluzole in Huntington's disease: a 3-year, randomized controlled study. Ann Neurol (2007) 1.21
Disease severity and progression in progressive supranuclear palsy and multiple system atrophy: validation of the NNIPPS--Parkinson Plus Scale. PLoS One (2011) 1.15
Alternative trial design in amyotrophic lateral sclerosis saves time and patients. Amyotroph Lateral Scler (2007) 1.15
Rsp5p, a new link between the actin cytoskeleton and endocytosis in the yeast Saccharomyces cerevisiae. Mol Cell Biol (2002) 1.14
The modulation of Amyotrophic Lateral Sclerosis risk by ataxin-2 intermediate polyglutamine expansions is a specific effect. Neurobiol Dis (2011) 1.12
Neuroectodermally converted human mesenchymal stromal cells provide cytoprotective effects on neural stem cells and inhibit their glial differentiation. Cytotherapy (2010) 1.10
Accelerated aging phenotype in mice with conditional deficiency for mitochondrial superoxide dismutase in the connective tissue. Aging Cell (2010) 1.09
A randomized, double blind, placebo-controlled trial of pioglitazone in combination with riluzole in amyotrophic lateral sclerosis. PLoS One (2012) 1.09
A point mutation in the dynein heavy chain gene leads to striatal atrophy and compromises neurite outgrowth of striatal neurons. Hum Mol Genet (2010) 1.09
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Phosphoinositide 3-kinases upregulate system xc(-) via eukaryotic initiation factor 2α and activating transcription factor 4 - A pathway active in glioblastomas and epilepsy. Antioxid Redox Signal (2014) 1.05
Mice with a mutation in the dynein heavy chain 1 gene display sensory neuropathy but lack motor neuron disease. Exp Neurol (2008) 1.05
Grey-matter abnormalities in boys with Tourette syndrome: magnetic resonance imaging study using optimised voxel-based morphometry. Br J Psychiatry (2006) 1.04
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Inflammatory dysregulation of blood monocytes in Parkinson's disease patients. Acta Neuropathol (2014) 1.00
MRI-based functional neuroimaging in ALS: an update. Amyotroph Lateral Scler (2009) 0.99
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A novel phosphorylation site mutation in profilin 1 revealed in a large screen of US, Nordic, and German amyotrophic lateral sclerosis/frontotemporal dementia cohorts. Neurobiol Aging (2012) 0.98
CSF concentrations of cAMP and cGMP are lower in patients with Creutzfeldt-Jakob disease but not Parkinson's disease and amyotrophic lateral sclerosis. PLoS One (2012) 0.98
Low stability of Huntington muscle mitochondria against Ca2+ in R6/2 mice. Ann Neurol (2006) 0.97
NIPA1 polyalanine repeat expansions are associated with amyotrophic lateral sclerosis. Hum Mol Genet (2012) 0.97
Dynein mutations associated with hereditary motor neuropathies impair mitochondrial morphology and function with age. Neurobiol Dis (2013) 0.96
PGC-1α is a male-specific disease modifier of human and experimental amyotrophic lateral sclerosis. Hum Mol Genet (2013) 0.96
TDP-43 pathology and neuronal loss in amyotrophic lateral sclerosis spinal cord. Acta Neuropathol (2014) 0.96
Neuroanatomical patterns of cerebral white matter involvement in different motor neuron diseases as studied by diffusion tensor imaging analysis. Amyotroph Lateral Scler (2012) 0.96
Biochemical markers in CSF of ALS patients. Curr Med Chem (2008) 0.95
Proteome analysis of cerebrospinal fluid in amyotrophic lateral sclerosis (ALS). Neurochem Res (2008) 0.95
Brain metabolites in definite amyotrophic lateral sclerosis. A longitudinal proton magnetic resonance spectroscopy study. J Neurol (2007) 0.95
Quantification of brain atrophy in patients with myotonic dystrophy and proximal myotonic myopathy: a controlled 3-dimensional magnetic resonance imaging study. Neurosci Lett (2003) 0.95
Body fat distribution as a risk factor for cerebrovascular disease: an MRI-based body fat quantification study. Cerebrovasc Dis (2013) 0.94
Stages of granulovacuolar degeneration: their relation to Alzheimer's disease and chronic stress response. Acta Neuropathol (2011) 0.93
A novel optineurin truncating mutation and three glaucoma-associated missense variants in patients with familial amyotrophic lateral sclerosis in Germany. Neurobiol Aging (2012) 0.93
Emotional responding in amyotrophic lateral sclerosis. J Neurol (2005) 0.92
Effects of mitochondrial dysfunction on the immunological properties of microglia. J Neuroinflammation (2010) 0.92
Amyotrophic lateral sclerosis: disease stage related changes of tau protein and S100 beta in cerebrospinal fluid and creatine kinase in serum. Neurosci Lett (2003) 0.92
Diffusion tensor imaging and tractwise fractional anisotropy statistics: quantitative analysis in white matter pathology. Biomed Eng Online (2007) 0.92
A large genome scan for rare CNVs in amyotrophic lateral sclerosis. Hum Mol Genet (2010) 0.92
Retinal single-layer analysis in Parkinsonian syndromes: an optical coherence tomography study. J Neural Transm (Vienna) (2013) 0.91
Intersubject variability in the analysis of diffusion tensor images at the group level: fractional anisotropy mapping and fiber tracking techniques. Magn Reson Imaging (2008) 0.91
Quantification of human body fat tissue percentage by MRI. NMR Biomed (2011) 0.91
Whole brain-based computerized neuroimaging in ALS and other motor neuron disorders. Amyotroph Lateral Scler (2008) 0.91
High-caloric food supplements in the treatment of amyotrophic lateral sclerosis: a prospective interventional study. Amyotroph Lateral Scler Frontotemporal Degener (2013) 0.90
Rasagiline alone and in combination with riluzole prolongs survival in an ALS mouse model. J Neurol (2004) 0.90
Extracellular vesicle sorting of α-Synuclein is regulated by sumoylation. Acta Neuropathol (2015) 0.90
Mutual exacerbation of peroxisome proliferator-activated receptor γ coactivator 1α deregulation and α-synuclein oligomerization. Ann Neurol (2014) 0.90
In vivo quantification of spinal and bulbar motor neuron degeneration in the G93A-SOD1 transgenic mouse model of ALS by T2 relaxation time and apparent diffusion coefficient. Exp Neurol (2006) 0.90
Summary of cerebrospinal fluid routine parameters in neurodegenerative diseases. J Neurol (2010) 0.90
Proteome analysis reveals candidate markers of disease progression in amyotrophic lateral sclerosis (ALS). Neurosci Lett (2009) 0.89
The Edinburgh Cognitive and Behavioural Amyotrophic Lateral Sclerosis Screen: a cross-sectional comparison of established screening tools in a German-Swiss population. Amyotroph Lateral Scler Frontotemporal Degener (2014) 0.89
Neuroimaging of multimodal sensory stimulation in amyotrophic lateral sclerosis. J Neurol Neurosurg Psychiatry (2010) 0.89
Systemic dysregulation of TDP-43 binding microRNAs in amyotrophic lateral sclerosis. Acta Neuropathol Commun (2013) 0.89
Emotional adjustment in amyotrophic lateral sclerosis (ALS). J Neurol (2011) 0.89
Levodopa-induced striatal activation in Parkinson's disease: a functional MRI study. Parkinsonism Relat Disord (2009) 0.88
H63D polymorphism in HFE is not associated with amyotrophic lateral sclerosis. Neurobiol Aging (2012) 0.87
Novel mutation in the ALS2 gene in juvenile amyotrophic lateral sclerosis. Ann Neurol (2005) 0.86
Brain responses to emotional stimuli in patients with amyotrophic lateral sclerosis (ALS). J Neurol (2007) 0.86
Soluble beta-amyloid precursor protein is related to disease progression in amyotrophic lateral sclerosis. PLoS One (2011) 0.86
SMN1 gene duplications are more frequent in patients with progressive muscular atrophy. Amyotroph Lateral Scler Frontotemporal Degener (2013) 0.86
Differential diagnostic value of eye movement recording in PSP-parkinsonism, Richardson's syndrome, and idiopathic Parkinson's disease. J Neurol (2009) 0.86
Severe sensorimotor neuropathy after intake of highest dosages of vitamin B6. Neuromuscul Disord (2007) 0.86
Eye movement impairments in Parkinson's disease: possible role of extradopaminergic mechanisms. BMC Neurol (2012) 0.86
On the decline and etiology of high-incidence motor system disease in West Papua (southwest New Guinea). Mov Disord (2005) 0.85
Limited role of free TDP-43 as a diagnostic tool in neurodegenerative diseases. Amyotroph Lateral Scler Frontotemporal Degener (2014) 0.85
Mutations in cytoplasmic dynein lead to a Huntington's disease-like defect in energy metabolism of brown and white adipose tissues. Biochim Biophys Acta (2010) 0.85
Age-dependent changes in MRI of motor brain stem nuclei in a mouse model of ALS. Neuroreport (2004) 0.85
Metabolic progression markers of neurodegeneration in the transgenic G93A-SOD1 mouse model of amyotrophic lateral sclerosis. Eur J Neurosci (2007) 0.85
Cortical plasticity in amyotrophic lateral sclerosis: motor imagery and function. Neurorehabil Neural Repair (2007) 0.84
Can lesions to the motor cortex induce amyotrophic lateral sclerosis? J Neurol (2013) 0.84
A new MRI rating scale for progressive supranuclear palsy and multiple system atrophy: validity and reliability. J Neurol Neurosurg Psychiatry (2011) 0.84
MMP-2 and MMP-9 are elevated in spinal cord and skin in a mouse model of ALS. J Neurol Sci (2010) 0.84
Mechanisms of disease: motoneuron disease aggravated by transgenic expression of a functionally modified AMPA receptor subunit. Ann N Y Acad Sci (2005) 0.84
Enhanced levels of Pis1p (phosphatidylinositol synthase) improve the growth of Saccharomyces cerevisiae cells deficient in Rsp5 ubiquitin ligase. Biochem J (2006) 0.84
Neurofilament heavy-chain NfH(SMI35) in cerebrospinal fluid supports the differential diagnosis of Parkinsonian syndromes. Mov Disord (2006) 0.84
Functional connectivity within the default mode network is associated with saccadic accuracy in Parkinson's disease: a resting-state FMRI and videooculographic study. Brain Connect (2013) 0.84
Comparison of smooth pursuit eye movement deficits in multiple system atrophy and Parkinson's disease. J Neurol (2009) 0.84
Connective tissue disorders in dissections of the carotid or vertebral arteries. J Clin Neurosci (2008) 0.83
Only subtle cognitive deficits in non-bulbar amyotrophic lateral sclerosis patients. J Neurol (2005) 0.83
Quality of life in fatal disease: the flawed judgement of the social environment. J Neurol (2013) 0.83