Published in Pediatr Res on December 01, 1975
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The biochemistry and clinical features of galactosialidosis. Biochim Biophys Acta (1994) 0.90
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Enzymatic hydrolysis of sphingomyelin liposomes by normal tissues and tissues from patients with Niemann-Pick disease. Biochim Biophys Acta (1983) 0.89
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Selective combination of modalities in soft tissue sarcomas: limb salvage and survival. Semin Surg Oncol (1988) 0.87
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In vitro activation of neuraminidase in the beta-galactosidase-neuraminidase-protective protein complex by cathepsin C. Biochem Biophys Res Commun (1988) 0.87
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Biochemical characterization of yeast RAS2 mutants reveals a new region of ras protein involved in the interaction with GTPase-activating proteins. J Biol Chem (1994) 0.86
Effect of saposins on acid sphingomyelinase. Biochem J (1993) 0.86
Niemann-Pick disease (Crocker's group A). Late onset and pigmentary degeneration resembling Hallervorden-Spatz syndrome. Arch Neurol (1972) 0.86
Early proteolytic cleavage with loss of a C-terminal fragment underlies altered processing of the beta-galactosidase precursor in galactosialidosis. Biochem J (1996) 0.86
Development of a clinical assay for detection of GAA mutations and characterization of the GAA mutation spectrum in a Canadian cohort of individuals with glycogen storage disease, type II. Mol Genet Metab (2007) 0.86
Simultaneous subconjunctival and subscleral mitomycin-C application in trabeculectomy. Ophthalmology (2000) 0.85
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Limb salvage in soft tissue sarcomas with selective combination of modalities. Eur J Surg Oncol (1991) 0.85
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Characteristic localization of gp130 (the signal-transducing receptor component used in common for IL-6/IL-11/CNTF/LIF/OSM) in the rat brain. Eur J Neurosci (1996) 0.84
Type 2 GM1 gangliosidosis with long survival and neuronal ceroid lipofuscinosis. Neurology (1981) 0.84
Cryptosporidiosis in children in Gaza. Ann Trop Paediatr (1991) 0.84
Lymphocytic hypophysitis with normal pituitary function mimicking a pituitary adenoma: a case report and review of literature. Clin Neuropathol (2009) 0.83
Studies on the hydrophobic properties of sphingomyelinase. Biochem J (1981) 0.83
Occupational exposure to staff during endoscopic retrograde cholangiopancreatography in Sudan. Radiat Prot Dosimetry (2010) 0.83
The effect of lipid micelles on mitochondrial malate dehydrogenase. Can J Biochem (1967) 0.83
Purification of G-M-1-ganglioside and ceramide lactoside beta-galactosidase from rabbit brain. Biochim Biophys Acta (1975) 0.83
Induction of hemopoietic chimerism in the caprine fetus by intraperitoneal injection of fetal liver cells. Experientia (1989) 0.82
Behaviour of hepatitis B antigen in bilharzial patients infected with HBs positive viral hepatitis. Egypt J Bilharz (1978) 0.82
Properties and prenatal ontogeny of beta-D-mannosidase in selected goat tissues. Biochem J (1987) 0.82
What keeps hepatocytes on the straight and narrow? Maintaining differentiated function in the liver. Gut (1999) 0.82
Glc7p protein phosphatase inhibits expression of glutamine-fructose-6-phosphate transaminase from GFA1. J Biol Chem (2000) 0.82
Ropivacaine 0.25% compared with bupivacaine 0.25% by the caudal route. Paediatr Anaesth (1999) 0.82
The effect of diarrhoea on low density beta lipoproteins and cholesterol in protein calorie malnutrition. J Trop Med Hyg (1973) 0.82
Studies on the activation of sphingomyelinase activity in Niemann-Pick type A, B, and C fibroblasts: enzymological differentiation of types A and B. Pediatr Res (1984) 0.82
Three dimensional culture upregulates extracellular matrix protein expression in human liver cell lines--a step towards mimicking the liver in vivo? Int J Artif Organs (2000) 0.82
Interferon-beta: the neutralizing antibody (NAb) titre predicts reversion to NAb negativity. Mult Scler (2004) 0.82
The effect of solvents on metal ion adsorption by the alga Chlorella vulgaris. Chemosphere (2005) 0.82
Lysosphingolipids and mitochondrial function. II. Deleterious effects of sphingosylphosphorylcholine. Biochem Cell Biol (1988) 0.81
A fatal thrombotic complication during liver transplantation after aprotinin administration. Transplantation (1994) 0.81
Comparison of duration of neuromuscular blocking effect of atracurium and vecuronium in young and elderly patients. Br J Anaesth (1995) 0.81
Morphological study of levator glandulae thyroidea in Bangladeshi cadaver. Mymensingh Med J (2009) 0.81
Classification performance of the frequency-related parameters derived from uterine EMG signals. Conf Proc IEEE Eng Med Biol Soc (2011) 0.81