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1
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The hepatitis C virus p7 protein forms an ion channel that is inhibited by long-alkyl-chain iminosugar derivatives.
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Proc Natl Acad Sci U S A
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2003
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2.64
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2
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Infantile-onset symptomatic epilepsy syndrome caused by a homozygous loss-of-function mutation of GM3 synthase.
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Nat Genet
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2004
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2.45
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3
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Implications for invariant natural killer T cell ligands due to the restricted presence of isoglobotrihexosylceramide in mammals.
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Proc Natl Acad Sci U S A
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2007
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1.84
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4
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Accumulation of glycosphingolipids in Niemann-Pick C disease disrupts endosomal transport.
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J Biol Chem
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2004
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1.22
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5
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NSAIDs increase survival in the Sandhoff disease mouse: synergy with N-butyldeoxynojirimycin.
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Ann Neurol
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2004
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1.15
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6
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Glucosylated free oligosaccharides are biomarkers of endoplasmic- reticulum alpha-glucosidase inhibition.
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Biochem J
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2008
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1.05
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7
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Activation state and intracellular trafficking contribute to the repertoire of endogenous glycosphingolipids presented by CD1d [corrected].
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Proc Natl Acad Sci U S A
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2010
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1.03
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8
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Recovery of intact 2-aminobenzamide-labeled O-glycans released from glycoproteins by hydrazinolysis.
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Anal Biochem
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2002
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1.01
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9
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Human invariant NKT cells display alloreactivity instructed by invariant TCR-CD1d interaction and killer Ig receptors.
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J Immunol
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2008
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0.88
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10
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Cellular effects of deoxynojirimycin analogues: inhibition of N-linked oligosaccharide processing and generation of free glucosylated oligosaccharides.
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Biochem J
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2004
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0.87
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11
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Lysosomal storage of oligosaccharide and glycosphingolipid in imino sugar treated cells.
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Glycoconj J
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2010
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0.81
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12
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Cellular effects of deoxynojirimycin analogues: uptake, retention and inhibition of glycosphingolipid biosynthesis.
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Biochem J
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2004
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0.81
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