Published in Pediatr Int on June 01, 2007
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Sudden infant death syndrome due to parainfluenza virus 2 associated with hemophagocytic syndrome. J Infect (2004) 1.39
Distinguishing between cooperative and unimodal downhill protein folding. Proc Natl Acad Sci U S A (2007) 1.35
The landscape of somatic mutations in Down syndrome-related myeloid disorders. Nat Genet (2013) 1.31
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Incidence of ANCA-associated primary renal vasculitis in the Miyazaki Prefecture: the first population-based, retrospective, epidemiologic survey in Japan. Clin J Am Soc Nephrol (2006) 1.16
Cytomegalovirus infection mimicking juvenile myelomonocytic leukemia showing hypersensitivity to granulocyte-macrophage colony stimulating factor. Pediatr Blood Cancer (2009) 1.16
Abnormally high levels of virus-infected IFN-gamma+ CCR4+ CD4+ CD25+ T cells in a retrovirus-associated neuroinflammatory disorder. PLoS One (2009) 1.15
Usefulness of beta-catenin immunostaining for the differential diagnosis of solid-pseudopapillary neoplasm of the pancreas. Am J Surg Pathol (2002) 1.13
A missense mutation of the Toll-like receptor 3 gene in a patient with influenza-associated encephalopathy. Clin Immunol (2006) 1.13
Conformational entropy of alanine versus glycine in protein denatured states. Proc Natl Acad Sci U S A (2007) 1.13
Poly(ADP-ribose) polymerase-1 is a component of the oncogenic T-cell factor-4/beta-catenin complex. Gastroenterology (2005) 1.12
Fine structure analysis of a protein folding transition state; distinguishing between hydrophobic stabilization and specific packing. J Mol Biol (2005) 1.12
Cytochrome c and tumor necrosis factor-alpha values in serum and cerebrospinal fluid of patients with influenza-associated encephalopathy. Pediatr Infect Dis J (2005) 1.11
Beta-catenin interacts with the FUS proto-oncogene product and regulates pre-mRNA splicing. Gastroenterology (2005) 1.07
Nephrotic syndrome complicated by idiopathic central diabetes insipidus. Pediatr Nephrol (2014) 1.07
Combined treatment of steroids and cyclosporine in Kimura disease. Pediatrics (2006) 1.07
Serum and cerebrospinal fluid nitrite/nitrate levels in patients with rotavirus gastroenteritis induced convulsion. Life Sci (2004) 1.03
Risk parameters of fulminant acute respiratory distress syndrome and avian influenza (H5N1) infection in Vietnamese children. J Infect Dis (2009) 1.03
Electrostatic interactions in the denatured state ensemble: their effect upon protein folding and protein stability. Arch Biochem Biophys (2007) 1.01
A new proposal for a clinical-oriented subclassification of baboon syndrome and a review of baboon syndrome. Asian Pac J Allergy Immunol (2011) 1.00
Fungal metabolite gliotoxin targets flavocytochrome b558 in the activation of the human neutrophil NADPH oxidase. Infect Immun (2005) 0.99
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Evaluation of dystrophic dog pathology by fat-suppressed T2-weighted imaging. Muscle Nerve (2009) 0.98
Chalcones and other compounds from the exudates of Angelica keiskei and their cancer chemopreventive effects. J Nat Prod (2006) 0.98
Bullous exudative retinal detachment due to infiltration of leukemic cells in a child with acute lymphoblastic leukemia. Int J Hematol (2010) 0.98
Relationship between self-reported sleep quality and metabolic syndrome in general population. BMC Public Health (2014) 0.96
Diurnal variation in febrile convulsions. Pediatr Neurol (2010) 0.96
Highly efficient bioethanol production by a Saccharomyces cerevisiae strain with multiple stress tolerance to high temperature, acid and ethanol. N Biotechnol (2011) 0.95
Cytomegalovirus retinitis as an adverse immunological effect of pulses of vincristine and dexamethasone in maintenance therapy for childhood acute lymphoblastic leukemia. Pediatr Blood Cancer (2012) 0.94
Umbilical cord milking stabilizes cerebral oxygenation and perfusion in infants born before 29 weeks of gestation. J Pediatr (2012) 0.94
Severe loss of invariant NKT cells exhibiting anti-HTLV-1 activity in patients with HTLV-1-associated disorders. Blood (2009) 0.94
Effect of xenon binding to a hydrophobic cavity on the proton pumping cycle in bacteriorhodopsin. J Mol Biol (2008) 0.93
Isoleucine, a blood glucose-lowering amino acid, increases glucose uptake in rat skeletal muscle in the absence of increases in AMP-activated protein kinase activity. J Nutr (2005) 0.92
Fucoidan therapy decreases the proviral load in patients with human T-lymphotropic virus type-1-associated neurological disease. Antivir Ther (2011) 0.92
Neuronal ceroid lipofuscinosis in Border Collie dogs in Japan: clinical and molecular epidemiological study (2000-2011). ScientificWorldJournal (2012) 0.90
Refraction contrast 11x-magnified X-ray imaging of large objects by MIRRORCLE-type table-top synchrotron. J Synchrotron Radiat (2006) 0.90
Two brothers with ataxia-telangiectasia-like disorder with lung adenocarcinoma. J Pediatr (2009) 0.89
A region C-terminal to the proline-rich core of p47phox regulates activation of the phagocyte NADPH oxidase by interacting with the C-terminal SH3 domain of p67phox. Arch Biochem Biophys (2005) 0.89
Cerebrospinal fluid biomarkers showing neurodegeneration in dogs with GM1 gangliosidosis: possible use for assessment of a therapeutic regimen. Brain Res (2006) 0.89
Clinical application of rapid assay of serum interleukin-6 in Kawasaki disease. Pediatr Int (2008) 0.89
Wnt3a stimulates maturation of impaired neutrophils developed from severe congenital neutropenia patient-derived pluripotent stem cells. Proc Natl Acad Sci U S A (2013) 0.88
Methylation status of the p15 and p16 genes in paediatric myelodysplastic syndrome and juvenile myelomonocytic leukaemia. Br J Haematol (2005) 0.88
CBL mutation in chronic myelomonocytic leukemia secondary to familial platelet disorder with propensity to develop acute myeloid leukemia (FPD/AML). Blood (2011) 0.88
Involvement of cholesterol-enriched microdomains in class A scavenger receptor-mediated responses in human macrophages. Atherosclerosis (2010) 0.88
Frequent somatic mosaicism of NEMO in T cells of patients with X-linked anhidrotic ectodermal dysplasia with immunodeficiency. Blood (2012) 0.87
Primary biomarkers in cerebral spinal fluid obtained from patients with influenza-associated encephalopathy analyzed by metabolomics. Int J Neurosci (2006) 0.87
Production of chemokines in respiratory syncytial virus infection with central nervous system manifestations. J Infect Chemother (2012) 0.87
Efficacy of prolonged valganciclovir therapy for congenital cytomegalovirus infection. J Infect Chemother (2011) 0.87
Inflammatory cytokines as predictors of resistance to intravenous immunoglobulin therapy in Kawasaki disease patients. Int J Rheum Dis (2013) 0.87
A novel mutation of the PHKA2 gene in a patient with X-linked liver glycogenosis type 1. Pediatr Int (2005) 0.86
National survey of pandemic influenza A (H1N1) 2009-associated encephalopathy in Japanese children. J Med Virol (2012) 0.86
Adult onset X-linked chronic granulomatous disease in a woman patient caused by a de novo mutation in paternal-origin CYBB gene and skewed inactivation of normal maternal X chromosome. Intern Med (2008) 0.86
Newly established Askin tumor cell line and overexpression of focal adhesion kinase in Ewing sarcoma family of tumors cell lines. Cancer Genet Cytogenet (2003) 0.86
Case series of pediatric acute leukemia without a peripheral blood abnormality, detected by magnetic resonance imaging. Int J Hematol (2011) 0.86
Interferon-alpha induces transient upregulation of c-FLIP through NF-kappaB activation. Exp Cell Res (2007) 0.85
Clinical magnetic resonance volumetry of the hippocampus in 58 epileptic dogs. Vet Radiol Ultrasound (2010) 0.85
Significance of aberrant (cytoplasmic/nuclear) expression of beta-catenin in pancreatoblastoma. J Pathol (2003) 0.85
Xanthoangelol, a major chalcone constituent of Angelica keiskei, induces apoptosis in neuroblastoma and leukemia cells. Biol Pharm Bull (2005) 0.84
Successful treatment with infliximab for inflammatory colitis in a patient with X-linked anhidrotic ectodermal dysplasia with immunodeficiency. J Clin Immunol (2011) 0.84
Efficacy of plasma exchange and methylprednisolone pulse therapy on influenza-associated encephalopathy. J Infect (2005) 0.84
Intravenous administration of amino acids during anesthesia stimulates muscle protein synthesis and heat accumulation in the body. Am J Physiol Endocrinol Metab (2005) 0.84
FK-506 extended the therapeutic time window for thrombolysis without increasing the risk of hemorrhagic transformation in an embolic rat stroke model. Brain Res (2007) 0.84
Classification of acute encephalopathy in respiratory syncytial virus infection. J Infect Chemother (2011) 0.84
The ex vivo production of ammonia predicts L-asparaginase biological activity in children with acute lymphoblastic leukemia. Int J Hematol (2009) 0.84
Enhanced bio-ethanol production from cellulosic materials by semi-simultaneous saccharification and fermentation using high temperature resistant Saccharomyces cerevisiae TJ14. J Biosci Bioeng (2012) 0.84
Low-volume muscular endurance and strength training during 3-week forearm immobilization was effective in preventing functional deterioration. Dyn Med (2008) 0.84
A case of Reye syndrome with rotavirus infection accompanied with high cytokines. J Infect (2005) 0.83