PubRank

Douglas R Keene

Author PubWeight™ 113.40‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Hfq: a bacterial Sm-like protein that mediates RNA-RNA interaction. Mol Cell 2002 5.26
2 Latent transforming growth factor beta-binding protein 1 interacts with fibrillin and is a microfibril-associated protein. J Biol Chem 2002 3.92
3 Evidence for a critical contribution of haploinsufficiency in the complex pathogenesis of Marfan syndrome. J Clin Invest 2004 3.01
4 Type 2 alveolar cells are stem cells in adult lung. J Clin Invest 2013 2.93
5 Regulation of tendon differentiation by scleraxis distinguishes force-transmitting tendons from muscle-anchoring tendons. Development 2007 2.92
6 Bone marrow transplantation for recessive dystrophic epidermolysis bullosa. N Engl J Med 2010 2.82
7 Stable nonviral genetic correction of inherited human skin disease. Nat Med 2002 2.20
8 Fibrillins 1 and 2 perform partially overlapping functions during aortic development. J Biol Chem 2005 2.19
9 Lack of collagen XVIII/endostatin results in eye abnormalities. EMBO J 2002 2.13
10 A comparative analysis of the fibulin protein family. Biochemical characterization, binding interactions, and tissue localization. J Biol Chem 2007 2.12
11 Streptococcal Scl1 and Scl2 proteins form collagen-like triple helices. J Biol Chem 2002 1.95
12 The prodomain of BMP-7 targets the BMP-7 complex to the extracellular matrix. J Biol Chem 2005 1.91
13 Injection of genetically engineered fibroblasts corrects regenerated human epidermolysis bullosa skin tissue. J Clin Invest 2003 1.83
14 Targeting of bone morphogenetic protein growth factor complexes to fibrillin. J Biol Chem 2008 1.80
15 A 'Collagen Hug' model for Staphylococcus aureus CNA binding to collagen. EMBO J 2005 1.78
16 Conversion of mechanical force into TGF-β-mediated biochemical signals. Curr Biol 2011 1.74
17 Molecular imaging of activated von Willebrand factor to detect high-risk atherosclerotic phenotype. JACC Cardiovasc Imaging 2010 1.71
18 Restoration of type VII collagen expression and function in dystrophic epidermolysis bullosa. Nat Genet 2002 1.67
19 Injection of recombinant human type VII collagen restores collagen function in dystrophic epidermolysis bullosa. Nat Med 2004 1.62
20 Fibrillins can co-assemble in fibrils, but fibrillin fibril composition displays cell-specific differences. J Biol Chem 2002 1.61
21 Injection of recombinant human type VII collagen corrects the disease phenotype in a murine model of dystrophic epidermolysis bullosa. Mol Ther 2008 1.54
22 Postnatal induction of transforming growth factor beta signaling in fibroblasts of mice recapitulates clinical, histologic, and biochemical features of scleroderma. Arthritis Rheum 2007 1.51
23 Differential expression of fibrillin-3 adds to microfibril variety in human and avian, but not rodent, connective tissues. Genomics 2004 1.49
24 Use of Bmp1/Tll1 doubly homozygous null mice and proteomics to identify and validate in vivo substrates of bone morphogenetic protein 1/tolloid-like metalloproteinases. Mol Cell Biol 2003 1.46
25 PhiC31 integrase-mediated nonviral genetic correction of junctional epidermolysis bullosa. Hum Gene Ther 2003 1.45
26 Versican interacts with fibrillin-1 and links extracellular microfibrils to other connective tissue networks. J Biol Chem 2001 1.41
27 Intravenously injected human fibroblasts home to skin wounds, deliver type VII collagen, and promote wound healing. Mol Ther 2007 1.41
28 The effect of matrix composition of 3D constructs on embryonic stem cell differentiation. Biomaterials 2005 1.40
29 Fine tuning of growth factor signals depends on fibrillin microfibril networks. Birth Defects Res C Embryo Today 2004 1.37
30 Normal and gene-corrected dystrophic epidermolysis bullosa fibroblasts alone can produce type VII collagen at the basement membrane zone. J Invest Dermatol 2003 1.37
31 Intradermal injection of lentiviral vectors corrects regenerated human dystrophic epidermolysis bullosa skin tissue in vivo. Mol Ther 2004 1.36
32 Collagen XVIII/endostatin is essential for vision and retinal pigment epithelial function. EMBO J 2003 1.34
33 PCOLCE2 encodes a functional procollagen C-proteinase enhancer (PCPE2) that is a collagen-binding protein differing in distribution of expression and post-translational modification from the previously described PCPE1. J Biol Chem 2002 1.32
34 Proteinases of the bone morphogenetic protein-1 family convert procollagen VII to mature anchoring fibril collagen. J Biol Chem 2002 1.32
35 Punctin, a novel ADAMTS-like molecule, ADAMTSL-1, in extracellular matrix. J Biol Chem 2002 1.31
36 Collagen XXVIII, a novel von Willebrand factor A domain-containing protein with many imperfections in the collagenous domain. J Biol Chem 2005 1.31
37 A streptococcal collagen-like protein interacts with the alpha2beta1 integrin and induces intracellular signaling. J Biol Chem 2005 1.27
38 Assessment of prokaryotic collagen-like sequences derived from streptococcal Scl1 and Scl2 proteins as a source of recombinant GXY polymers. Appl Microbiol Biotechnol 2006 1.26
39 HOXA13 Is essential for placental vascular patterning and labyrinth endothelial specification. PLoS Genet 2008 1.25
40 Mammalian tolloid metalloproteinase, and not matrix metalloprotease 2 or membrane type 1 metalloprotease, processes laminin-5 in keratinocytes and skin. J Biol Chem 2002 1.25
41 ADAMTS10 protein interacts with fibrillin-1 and promotes its deposition in extracellular matrix of cultured fibroblasts. J Biol Chem 2011 1.25
42 Identification of the first prokaryotic collagen sequence motif that mediates binding to human collagen receptors, integrins alpha2beta1 and alpha11beta1. J Biol Chem 2008 1.22
43 The atypical homeodomain transcription factor Mohawk controls tendon morphogenesis. Mol Cell Biol 2010 1.21
44 Effects of fibrillin-1 degradation on microfibril ultrastructure. J Biol Chem 2006 1.18
45 Laminin-10 is crucial for hair morphogenesis. EMBO J 2003 1.17
46 Cleavage and oligomerization of gliomedin, a transmembrane collagen required for node of ranvier formation. J Biol Chem 2007 1.16
47 A novel binding site in collagen type III for integrins alpha1beta1 and alpha2beta1. J Biol Chem 2005 1.15
48 A correlative method for imaging identical regions of samples by micro-CT, light microscopy, and electron microscopy: imaging adipose tissue in a model system. J Histochem Cytochem 2012 1.15
49 Bacillus anthracis internalization by human fibroblasts and epithelial cells. Cell Microbiol 2007 1.14
50 The Scl1 protein of M6-type group A Streptococcus binds the human complement regulatory protein, factor H, and inhibits the alternative pathway of complement. Mol Microbiol 2007 1.14
51 Collagen XII interacts with avian tenascin-X through its NC3 domain. J Biol Chem 2006 1.10
52 Binding of the low-density lipoprotein by streptococcal collagen-like protein Scl1 of Streptococcus pyogenes. Mol Microbiol 2006 1.10
53 A fibronectin-independent mechanism of collagen fibrillogenesis in adult liver remodeling. Gastroenterology 2011 1.09
54 Potential dissemination of Bacillus anthracis utilizing human lung epithelial cells. Cell Microbiol 2007 1.08
55 Generalized connective tissue disease in Crtap-/- mouse. PLoS One 2010 1.07
56 Prolyl 3-hydroxylase 1 null mice display abnormalities in fibrillar collagen-rich tissues such as tendons, skin, and bones. J Biol Chem 2010 1.06
57 Microenvironmental regulation by fibrillin-1. PLoS Genet 2012 1.05
58 Zebrafish collagen XII is present in embryonic connective tissue sheaths (fascia) and basement membranes. Matrix Biol 2008 1.04
59 ADAMTSL-6 is a novel extracellular matrix protein that binds to fibrillin-1 and promotes fibrillin-1 fibril formation. J Biol Chem 2009 1.03
60 A novel marker of tissue junctions, collagen XXII. J Biol Chem 2004 1.03
61 Microfibril structure masks fibrillin-2 in postnatal tissues. J Biol Chem 2010 1.03
62 In vivo studies of mutant fibrillin-1 microfibrils. J Biol Chem 2010 1.03
63 Y-position cysteine substitution in type I collagen (alpha1(I) R888C/p.R1066C) is associated with osteogenesis imperfecta/Ehlers-Danlos syndrome phenotype. Hum Mutat 2007 0.98
64 Collagen XII and XIV, new partners of cartilage oligomeric matrix protein in the skin extracellular matrix suprastructure. J Biol Chem 2012 0.97
65 Induction of epidermolysis bullosa acquisita in mice by passive transfer of autoantibodies from patients. J Invest Dermatol 2006 0.97
66 Mutation in cyclophilin B that causes hyperelastosis cutis in American Quarter Horse does not affect peptidylprolyl cis-trans isomerase activity but shows altered cyclophilin B-protein interactions and affects collagen folding. J Biol Chem 2012 0.97
67 Secretion of cartilage oligomeric matrix protein is affected by the signal peptide. J Biol Chem 2005 0.94
68 Nano-structure of the laminin γ-1 short arm reveals an extended and curved multidomain assembly. Matrix Biol 2010 0.93
69 Keratinocytes from induced pluripotent stem cells in junctional epidermolysis bullosa. J Invest Dermatol 2012 0.92
70 Identification, content, and distribution of type VI collagen in bovine tendons. Cell Tissue Res 2006 0.91
71 Posttranslational modifications in type I collagen from different tissues extracted from wild type and prolyl 3-hydroxylase 1 null mice. J Biol Chem 2013 0.88
72 Y-position collagen II mutation disrupts cartilage formation and skeletal development in a transgenic mouse model of spondyloepiphyseal dysplasia. J Bone Miner Res 2002 0.88
73 Expression of PSACH-associated mutant COMP in tendon fibroblasts leads to increased apoptotic cell death irrespective of the secretory characteristics of mutant COMP. Matrix Biol 2007 0.87
74 Versican and fibrillin-1 form a major hyaluronan-binding complex in the ciliary body. Invest Ophthalmol Vis Sci 2008 0.86
75 Nonselective assembly of fibrillin 1 and fibrillin 2 in the rodent ocular zonule and in cultured cells: implications for Marfan syndrome. Invest Ophthalmol Vis Sci 2013 0.85
76 Mouse AMACO, a kidney and skin basement membrane associated molecule that mediates RGD-dependent cell attachment. Matrix Biol 2009 0.85
77 Sequential and coordinated actions of c-Myc and N-Myc control appendicular skeletal development. PLoS One 2011 0.83
78 MEGF9: a novel transmembrane protein with a strong and developmentally regulated expression in the nervous system. Biochem J 2007 0.83
79 Disruption of a Sox9-β-catenin circuit by mutant Fgfr3 in thanatophoric dysplasia type II. Hum Mol Genet 2012 0.82
80 Observations of skin grafts derived from keratinocytes expressing selectively engineered mutant laminin-332 molecules. J Invest Dermatol 2010 0.81
81 Keratinocyte-targeted expression of human laminin γ2 rescues skin blistering and early lethality of laminin γ2 deficient mice. PLoS One 2012 0.76