Published in Pediatrics on July 01, 1949
Effects of reduced mucus oxygen concentration in airway Pseudomonas infections of cystic fibrosis patients. J Clin Invest (2002) 6.35
Mucus clearance as a primary innate defense mechanism for mammalian airways. J Clin Invest (2002) 5.94
The porcine lung as a potential model for cystic fibrosis. Am J Physiol Lung Cell Mol Physiol (2008) 2.53
Innate immunity in the respiratory epithelium. Am J Respir Cell Mol Biol (2011) 2.04
Effective mucus clearance is essential for respiratory health. Am J Respir Cell Mol Biol (2006) 1.98
Loss of cystic fibrosis transmembrane conductance regulator function produces abnormalities in tracheal development in neonatal pigs and young children. Am J Respir Crit Care Med (2010) 1.94
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis. Am J Pathol (2010) 1.60
Development of chronic bronchitis and emphysema in beta-epithelial Na+ channel-overexpressing mice. Am J Respir Crit Care Med (2007) 1.60
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis. Am J Physiol Cell Physiol (2010) 1.56
Liquid secretion properties of airway submucosal glands. J Physiol (2003) 1.40
Pharmacological correction of a defect in PPAR-gamma signaling ameliorates disease severity in Cftr-deficient mice. Nat Med (2010) 1.36
A new role for bicarbonate secretion in cervico-uterine mucus release. J Physiol (2010) 1.20
CFTR, mucins, and mucus obstruction in cystic fibrosis. Cold Spring Harb Perspect Med (2012) 1.15
Fluid secretion by submucosal glands of the tracheobronchial airways. Respir Physiol Neurobiol (2007) 1.12
Localization of Burkholderia cepacia complex bacteria in cystic fibrosis lungs and interactions with Pseudomonas aeruginosa in hypoxic mucus. Infect Immun (2014) 1.00
Glycaemic regulation and insulin secretion are abnormal in cystic fibrosis pigs despite sparing of islet cell mass. Clin Sci (Lond) (2015) 0.94
Cilia dysfunction in lung disease. Annu Rev Physiol (2014) 0.94
Review of recombinant human deoxyribonuclease (rhDNase) in the management of patients with cystic fibrosis. Biologics (2008) 0.86
Native small airways secrete bicarbonate. Am J Respir Cell Mol Biol (2014) 0.85
Animal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology. Am J Physiol Gastrointest Liver Physiol (2015) 0.84
Hypoxic epithelial necrosis triggers neutrophilic inflammation via IL-1 receptor signaling in cystic fibrosis lung disease. Am J Respir Crit Care Med (2015) 0.79
Rapid identification of enteropathogenic Escherichia coli O127:B8 by the fluorescent antibody technique. AMA J Dis Child (1958) 3.37
A new technique for differentiation of hemoglobin. J Lab Clin Med (1957) 3.30
MECHANISMS OF ISOIMMUNIZATION. I. THE TRANSPLACENTAL PASSAGE OF FETAL ERYTHROCYTES IN HOMOSPECIFIC PREGNANCIES. Blood (1964) 2.83
CATALYTIC PROPERTIES OF TRYPTOPHANASE, A MULTIFUNCTIONAL PYRIDOXAL PHOSPHATE ENZYME. Proc Natl Acad Sci U S A (1964) 2.65
Kernicterus; etiologic study based on an analysis of 55 cases. Pediatrics (1950) 2.53
Studies on the neonatal development of the glucuronide conjugating system. J Clin Invest (1958) 2.48
A new inherited abnormality of hemoglobin and its interaction with sickle cell hemoglobin. Blood (1951) 2.26
Erythrocyte survival studies in childhood. II. Studies in Mediterranean anemia. J Lab Clin Med (1950) 2.21
IMPLICATIONS OF LONG-TERM SURVIVAL IN ACUTE STEM CELL LEUKEMIA OF CHILDHOOD TREATED WITH COMPOSITE CYCLIC THERAPY. Blood (1964) 2.20
Neonatal jaundice. A review. Am J Dis Child (1961) 2.16
IDENTIFICATION OF BLOOD GROUP ANTIGENS BY IMMUNOFLUORESCENCE AND ITS APPLICATION TO THE DETECTION OF THE TRANSPLACENTAL PASSAGE OF ERYTHROCYTES IN MOTHER AND CHILD. Vox Sang (1964) 1.98
Herpes simplex virus as the cause of fulminating visceral disease and hepatitis in infancy; report of eight cases and isolation of the virus in one case. AMA Am J Dis Child (1952) 1.97
Serious Coxsackie infection in infants and children; myocarditis, meningoencephalitis, and hepatitis. AMA J Dis Child (1958) 1.95
Two fast hemoglobin components in Liberian blood samples. Blood (1956) 1.89
PROPERTIES OF CRYSTALLINE TRYPTOPHANASE. J Biol Chem (1965) 1.88
Acute childhood leukemia: a ten-year study. Am J Dis Child (1960) 1.70
An inducible tryptophan synthetase in tryptophan auxotrophs of Escherichia coli. Proc Natl Acad Sci U S A (1962) 1.65
Immunofluorescence in diagnostic bacteriology. II. Identification of group A streptococci in throat smears. Am J Dis Child (1961) 1.55
Megaloblastic anemia of infancy. Adv Pediatr (1953) 1.52
"MYELOKATHEXIS"--A NEW FORM OF CHRONIC GRANULOCYTOPENIA. REPORT OF A CASE. N Engl J Med (1964) 1.44
ABO heterospecific pregnancy and hemolytic disease; a study of normal and pathologic variants. IV. Pathologic variants. AMA Am J Dis Child (1954) 1.38
Primary tumours of the liver in infants and children. Arch Dis Child (1960) 1.30
Further studies on hemoglobin C. II. The hematologic effects of hemoglobin C alone and in combination with sickle cell hemoglobin. Blood (1953) 1.26
ABO hemolytic disease and heterospecific pregnancy. Pediatr Clin North Am (1957) 1.25
Combinations of hemoglobin G, hemoglobin S and thalassemia occurring in one family. Blood (1957) 1.20
FORMATION AND INTERRELATIONSHIPS OF TRYPTOPHANASE AND TRYPTOPHAN SYNTHETASES IN ESCHERICHIA COLI. J Bacteriol (1965) 1.18
Circulatory diseases of the kidneys in infancy and childhood. VI. Thrombosis of renal veins. AMA Am J Dis Child (1951) 1.17
Date on the occurrence of hemoglobin C and other abnormal hemoglobins in some African populations. Am J Hum Genet (1956) 1.17
Sideroblasts: a study of stainable nonhemoglobin iron in marrow normoblasts. Blood (1954) 1.13
Neonatal tuberculosis. AMA Am J Dis Child (1955) 1.11
Identification of blood group antigens and minor cell populations by the fluorescent antibody method. Blood (1960) 1.11
Circulatory diseases of the kidneys in infancy and childhood. I. Symmetrical cortical necrosis. AMA Am J Dis Child (1951) 1.10
Unusual glomerulonephritis in young children probably radiation nephritis. Am J Pathol (1950) 1.10
MEDIASTINAL ORIGIN OF A MELANOTIC PROGONOMA OR RETINAL ANLAGE TUMOR: ULTRASTRUCTURAL EVIDENCE FOR NEURAL CREST ORIGIN. Cancer (1965) 1.09
Familial nonspherocytic hemolytic anemia. Blood (1950) 1.09
A LONG-TERM STUDY OF CEREBROSPINAL LEUKEMIA. J Pediatr (1965) 1.07
The frequency of elevations in the A and fetal hemoglobin fractions in the natives of Liberia and adjacent regions, with data on haptoglobin and transferrin types. Am J Hum Genet (1961) 1.06
Studies in hyperbilirubinemia. II. Clearance of bilirubin from plasma and extravascular space in newborn infants during exchange transfusion. AMA J Dis Child (1957) 1.06
Studies in hyperbilirubinemia. I. Hyperbilirubinemia of the newborn unrelated to isoimmunization. AMA J Dis Child (1957) 1.05
Reciprocal relationship of hemoglobins A2 and F in beta chain thalassemias, a key to the genetic control of hemoglobin F. Blood (1961) 1.03
GENERALIZED UNBALANCED MOSAICISM ATTRIBUTABLE TO DISPERMY AND PROBABLE FERTILIZATION OF A POLAR BODY. Am J Hum Genet (1964) 1.02
Escherichia coli O127:B8, a pathogenic strain causing infantile diarrhea. I. Epidemiology and bacteriology of a prolonged outbreak in a premature nursery. AMA Am J Dis Child (1955) 1.00
Infantile pyknocytosis; a common erythrocyte abnormality of the first trimester. AMA J Dis Child (1959) 1.00
Evidence concerning the inadequacy of mutation as an explanation of the frequency of the sickle cell gene in the Belgian Congo. Blood (1955) 1.00
The distribution of several blood group genes in Liberia, the Ivory Coast and Upper Volta. Am J Phys Anthropol (1960) 0.99
Idiopathic thrombopenic purpura in childhood. N Engl J Med (1951) 0.99
Thalassaemia in Liberia. Br Med J (1959) 0.98
Circulatory diseases of the kidneys in infancy and childhood. IV. Occlusion of the renal artery. AMA Am J Dis Child (1951) 0.97
Abnormal hemoglobins. Prog Hematol (1956) 0.96
Anti-A agglutinins in pooled plasma as a cause of hemolytic anemia. Blood (1956) 0.96
Circulatory diseases of the kidneys in infancy and childhood. AMA Am J Dis Child (1951) 0.96
Further studies on hemoglobin C. I. A description of three additional families segregating for hemoglobin C and sickle cell hemoglobin. Blood (1953) 0.93
Haemoglobin F: its significance in the genetics and evolution of haemoglobin. Nature (1961) 0.92
Functional intestinal obstruction on a congenital neurogenic basis in infancy. Am J Dis Child (1948) 0.90
Escherichia coli 0127:B8, a serotype causing infantile diarrhea. III. The antibody response of infants. J Immunol (1956) 0.89
CHROMOSOME STUDIES IN LEUKEMIA. I. EVIDENCE FOR THE ORIGIN OF LEUKEMIC STEM LINES FROM ANEUPLOID MUTANTS. N Engl J Med (1964) 0.89
Dynamic investigation of perinatal mortality. Am J Obstet Gynecol (1958) 0.88
Multiple inherited erythrocyte abnormalities in an American Negro family: hereditary spherocytosis, sickling and thalassemia. Blood (1959) 0.85
Erythrocyte survival studies in childhood. I. Methods and general observations. J Lab Clin Med (1950) 0.85
RENAL VASCULAR DISEASE. Pediatr Clin North Am (1964) 0.84
Ovarian tumors and cysts in infants and children. Arch Surg (1961) 0.84
Proteins in normal and nephrotic sera with filter paper electrophoretic mobility of albumin. J Lab Clin Med (1961) 0.83
BLOOD GROUP CHIMERISM AS A CLUE TO GENERALIZED TISSUE MOSAICISM. Transfusion (1964) 0.83
The case of imferon--convenience and conscience. Am J Dis Child (1960) 0.83
Torsion of previously normal tube and ovary in children. N Engl J Med (1963) 0.83
Separation of human serum albumins. Nature (1960) 0.82
Thalassemia-hemoglobin C disease; a new syndrome presumably due to the combination of the genes for thalassemia and hemoglobin C. Blood (1954) 0.81
Acute hemolytic anemia due to naphthalene poisoning; a clinical and experimental study. J Am Med Assoc (1949) 0.81
Infantile diarrhea due to Escherichia coli. Ann N Y Acad Sci (1956) 0.80
ENDOREDUPLICATION IN A PATIENT WITH ACUTE MONOCYTIC LEUKAEMIA. Lancet (1963) 0.80
Disseminated visceral lesions associated with extreme eosinophilia; pathologic and clinical observations on a syndrome of young children. Am J Dis Child (1949) 0.80
An epidemic of diarrhea of the newborn cause by Escherichia coli O-111, B4. Pediatrics (1954) 0.79
FURTHER OBSERVATION ON THE ROLE OF ANEUPLOIDY IN ACUTE LEUKEMIA. Cancer Res (1964) 0.79
INTERRELATIONSHIP OF THE VARIOUS SUBGROUPS OF THE BLOOD GROUP A: STUDY WITH IMMUNOFLUORESCENCE. Transfusion (1965) 0.77
Parapertussis pneumonia. J Pediatr (1946) 0.76
The use of the fluorescent antibody technique for the demonstration of erythrocyte antigens. J Lab Clin Med (1959) 0.76
Circulatory diseases of the kidneys in infancy and childhood. V. Ischemic atrophy of the kidneys. AMA Am J Dis Child (1951) 0.75
Circulatory diseases of the kidneys in infancy and childhood. VII. Diffuse hemorrhagic infarction of the kidneys without vascular thrombosis. AMA Am J Dis Child (1951) 0.75
Clinical experience using 6-mercaptopurine in childhood leukemia. Ann N Y Acad Sci (1954) 0.75
Folic acid therapy in macrocytic anemias of infancy. Proc Soc Exp Biol Med (1946) 0.75
Pathogenesis of anemia in infancy and childhood. J Am Med Assoc (1947) 0.75
Ritter's disease. J Pediatr (1948) 0.75
Adrenocortical insufficiency in infants with the adrenogenital syndrome; a clinical and pathologic study of four cases. J Pediatr (1949) 0.75
Circulatory diseases of the kidneys in infancy and childhood. II. Acute glomerular thrombosis. AMA Am J Dis Child (1951) 0.75
Normal and pathologic physiology of the bone marrow. Am J Dis Child (1949) 0.75
Etiology of kernicterus. AMA Am J Dis Child (1950) 0.75
Circulatory diseases of the kidneys in infancy and childhood. III. Arteriolar necrosis (acute malignant hypertension). AMA Am J Dis Child (1951) 0.75
Neurogenic intestinal obstruction in infancy; a clinical and pathologic study. Am J Dis Child (1947) 0.75
[Not Available]. Wien Med Wochenschr (1947) 0.75
Current trends in hematology. Pediatrics (1949) 0.75
Changes in the bone marrow in megaloblastic anemias of infancy before and after folic acid therapy. J Lab Clin Med (1947) 0.75
Megaloblastic anemia in infancy; a common syndrome responding specifically to folic acid therapy. Am J Dis Child (1946) 0.75
Circulatory diseases of the kidneys in infancy and childhood. VIII. Lower nephron nephrosis. AMA Am J Dis Child (1951) 0.75
The Rh factor; practical aspects. Pediatrics (1948) 0.75
Folic acid therapy in the anemias of infancy and childhood. J Am Med Assoc (1946) 0.75
Erythrocyte survival studies in childhood. III. Unusual familial hemolytic anemias associated with intrinsic erythrocyte abnormality. J Lab Clin Med (1950) 0.75