Published in J Am Diet Assoc on May 01, 2008
Clinical care guidelines for cystic fibrosis-related diabetes: a position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed by the Pediatric Endocrine Society. Diabetes Care (2010) 2.52
Longevity of patients with cystic fibrosis in 2000 to 2010 and beyond: survival analysis of the Cystic Fibrosis Foundation patient registry. Ann Intern Med (2014) 2.15
We can handle this: parents' use of religion in the first year following their child's diagnosis with cystic fibrosis. J Health Care Chaplain (2010) 1.30
Randomized clinical trial of behavioral intervention and nutrition education to improve caloric intake and weight in children with cystic fibrosis. Arch Pediatr Adolesc Med (2009) 1.25
Progress in cystic fibrosis and the CF Therapeutics Development Network. Thorax (2012) 1.12
Trends in the use of routine therapies in cystic fibrosis: 1995-2005. Pediatr Pulmonol (2010) 1.00
Metabolomic profiling reveals biochemical pathways and biomarkers associated with pathogenesis in cystic fibrosis cells. J Biol Chem (2010) 1.00
The cystic fibrosis intestine. Cold Spring Harb Perspect Med (2013) 0.98
Cystic fibrosis growth retardation is not correlated with loss of Cftr in the intestinal epithelium. Am J Physiol Gastrointest Liver Physiol (2011) 0.97
Classification of malnutrition in cystic fibrosis: implications for evaluating and benchmarking clinical practice performance. Am J Clin Nutr (2008) 0.93
Risk factors associated with depressive symptoms in caregivers of children with type 1 diabetes or cystic fibrosis. J Pediatr Psychol (2010) 0.90
Impaired mucosal barrier function in the small intestine of the cystic fibrosis mouse. J Pediatr Gastroenterol Nutr (2011) 0.89
Developmental and psychosocial issues in cystic fibrosis. Child Adolesc Psychiatr Clin N Am (2010) 0.88
Exocrine pancreatic insufficiency in adults: a shared position statement of the Italian Association for the Study of the Pancreas. World J Gastroenterol (2013) 0.88
Mealtime problems predict outcome in clinical trial to improve nutrition in children with CF. Pediatr Pulmonol (2010) 0.88
The effects of an intensive behavior and nutrition intervention compared to standard of care on weight outcomes in CF. Pediatr Pulmonol (2010) 0.88
Medication beliefs mediate between depressive symptoms and medication adherence in cystic fibrosis. Health Psychol (2014) 0.87
Diagnosis and treatment of endocrine comorbidities in patients with cystic fibrosis. Curr Opin Endocrinol Diabetes Obes (2014) 0.87
Nutritional outcomes following gastrostomy in children with cystic fibrosis. Pediatr Pulmonol (2012) 0.86
Genetic modifiers of nutritional status in cystic fibrosis. Am J Clin Nutr (2012) 0.86
Health-related quality of life of Spanish children with cystic fibrosis. Qual Life Res (2012) 0.86
Children and young adults with CF in the USA have better lung function compared with the UK. Thorax (2014) 0.86
Risk factors for the progression of cystic fibrosis lung disease throughout childhood. Ann Am Thorac Soc (2014) 0.85
Comparison of WHO and CDC growth charts in predicting pulmonary outcomes in cystic fibrosis. J Pediatr Gastroenterol Nutr (2015) 0.85
Early Life Growth Trajectories in Cystic Fibrosis are Associated with Pulmonary Function at Age 6 Years. J Pediatr (2015) 0.84
Incorporating genetic potential when evaluating stature in children with cystic fibrosis. J Cyst Fibros (2010) 0.84
Maintenance of nutritional status in patients with cystic fibrosis: new and emerging therapies. Drug Des Devel Ther (2012) 0.84
Comparing the Use of Centers for Disease Control and Prevention and World Health Organization Growth Charts in Children with Cystic Fibrosis through 2 Years of Age. J Pediatr (2015) 0.84
Parental Depression and Pancreatic Enzymes Adherence in Children With Cystic Fibrosis. Pediatrics (2016) 0.84
New stable isotope method to measure protein digestibility and response to pancreatic enzyme intake in cystic fibrosis. Clin Nutr (2013) 0.84
Cost of care for cystic fibrosis: an investigation of cost determinants using national registry data. Eur J Health Econ (2014) 0.84
Qualitative analysis of parent experiences with achieving cystic fibrosis nutrition recommendations. J Cyst Fibros (2011) 0.83
Pubertal height velocity and associations with prepubertal and adult heights in cystic fibrosis. J Pediatr (2013) 0.82
Trends in bone mineral density in young adults with cystic fibrosis over a 15 year period. J Cyst Fibros (2015) 0.82
Changes in Mineral Micronutrient Status During and After Pulmonary Exacerbation in Adults With Cystic Fibrosis. Nutr Clin Pract (2015) 0.82
Disrupted tight junctions in the small intestine of cystic fibrosis mice. Cell Tissue Res (2013) 0.82
Parents' religious coping styles in the first year after their child's cystic fibrosis diagnosis. J Health Care Chaplain (2010) 0.81
Nutritional status is associated with health-related quality of life in children with cystic fibrosis aged 9-19 years. J Cyst Fibros (2013) 0.81
Nutritional Status Improved in Cystic Fibrosis Patients with the G551D Mutation After Treatment with Ivacaftor. Dig Dis Sci (2015) 0.81
Relationship Between Fat-Soluble Vitamin Supplementation and Blood Concentrations in Adolescent and Adult Patients With Cystic Fibrosis. Nutr Clin Pract (2014) 0.81
Body composition and pulmonary function in cystic fibrosis. Front Pediatr (2014) 0.80
Early attained weight and length predict growth faltering better than velocity measures in infants with CF. J Cyst Fibros (2014) 0.80
Protein is an important but undervalued macronutrient in the nutritional care of patients with cystic fibrosis. Curr Opin Clin Nutr Metab Care (2014) 0.79
Adherence to airway clearance therapy in pediatric cystic fibrosis: Socioeconomic factors and respiratory outcomes. Pediatr Pulmonol (2015) 0.79
Altered de novo lipogenesis contributes to low adipose stores in cystic fibrosis mice. Am J Physiol Gastrointest Liver Physiol (2012) 0.79
Oxandrolone Improves Height Velocity and BMI in Patients with Cystic Fibrosis. Int J Pediatr Endocrinol (2010) 0.78
Pancrelipase: an evidence-based review of its use for treating pancreatic exocrine insufficiency. Core Evid (2012) 0.78
A multi-center controlled trial of growth hormone treatment in children with cystic fibrosis. Pediatr Pulmonol (2011) 0.78
Mild CFTR mutations and genetic predisposition to lactase persistence in cystic fibrosis. Eur J Hum Genet (2011) 0.78
Study design considerations for evaluating the efficacy and safety of pancreatic enzyme replacement therapy in patients with cystic fibrosis. Clin Investig (Lond) (2013) 0.78
Efficacy and safety of a unique enteric-coated bicarbonate-buffered pancreatic enzyme replacement therapy in children and adults with cystic fibrosis. Clin Investig (Lond) (2013) 0.77
Young adults with cystic fibrosis have altered trabecular microstructure by ITS-based morphological analysis. Osteoporos Int (2016) 0.77
Nutritional status of adolescents with cystic fibrosis treated at a reference center in the southeast region of Brazil. Ital J Pediatr (2015) 0.77
Insulin secretion abnormalities in exocrine pancreatic sufficient cystic fibrosis patients. J Cyst Fibros (2015) 0.76
Diagnosing exocrine pancreatic insufficiency after surgery: when and which patients to treat. HPB (Oxford) (2009) 0.76
Use of WHO growth curves for patients with cystic fibrosis may provide a false sense of security. J Pediatr Gastroenterol Nutr (2015) 0.75
Impact of CFTR Modulation on Intestinal pH, Motility, and Clinical Outcomes in Patients With Cystic Fibrosis and the G551D Mutation. Clin Transl Gastroenterol (2017) 0.75
Plasma metabolomics in adults with cystic fibrosis during a pulmonary exacerbation: A pilot randomized study of high-dose vitamin D3 administration. Metabolism (2017) 0.75
Dietary intake and nutritional status in a Scandinavian adult cystic fibrosis-population compared with recommendations. Food Nutr Res (2011) 0.75
Sputum glucose and glycemic control in cystic fibrosis-related diabetes: a cross-sectional study. PLoS One (2015) 0.75
Dietetic management of people with cystic fibrosis. J Am Diet Assoc (2008) 0.75
Digestive Enzyme Supplementation in Gastrointestinal Diseases. Curr Drug Metab (2016) 0.75
Measures of body habitus are associated with lung function in adults with cystic fibrosis: a population-based study. J Cyst Fibros (2012) 0.75
Exercise capacity following a percutaneous endoscopic gastrostomy in a young female with cystic fibrosis: a case report. Physiol Rep (2016) 0.75
Web-Based Intervention for Nutritional Management in Cystic Fibrosis: Development, Usability, and Pilot Trial. J Pediatr Psychol (2015) 0.75
Background and Epidemiology. Pediatr Clin North Am (2016) 0.75
Quality of life in children with CF: Psychometrics and relations with stress and mealtime behaviors. Pediatr Pulmonol (2014) 0.75
Body composition and lung function in cystic fibrosis and their association with adiposity and normal-weight obesity. Nutrition (2015) 0.75
Growth deficits in cystic fibrosis mice begin in utero prior to IGF-1 reduction. PLoS One (2017) 0.75
Gastrointestinal Manifestations of Cystic Fibrosis. Gastroenterol Hepatol (N Y) (2016) 0.75
Dynamics of Disease Progression and Gastrostomy Tube Placement in Children and Adolescents with Cystic Fibrosis: Application of Joint Models for Longitudinal and Time-to-Event Data. Intern Med Rev (Wash D C) (2016) 0.75
Sleep-disordered breathing in patients with cystic fibrosis. J Bras Pneumol (2015) 0.75
Nationwide trends of hospitalizations for cystic fibrosis in the United States from 2003 to 2013. Intractable Rare Dis Res (2017) 0.75
Body composition and lung function in children with cystic fibrosis and meconium ileus. Eur J Pediatr (2017) 0.75
Cystic fibrosis and Silver-Russell syndrome due to a partial maternal isodisomy of chromosome 7. Clin Case Rep (2017) 0.75
Lumacaftor/Ivacaftor in Patients Aged 6-11 Years With Cystic Fibrosis Homozygous for F508del-CFTR. Am J Respir Crit Care Med (2016) 0.75
Growth in Prepubertal Children With Cystic Fibrosis Treated With Ivacaftor. Pediatrics (2017) 0.75
Physician staffing patterns and clinical outcomes in critically ill patients: a systematic review. JAMA (2002) 9.89
Cultural competence: a systematic review of health care provider educational interventions. Med Care (2005) 5.09
Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health. Am J Respir Crit Care Med (2007) 4.34
Cystic fibrosis pulmonary guidelines: treatment of pulmonary exacerbations. Am J Respir Crit Care Med (2009) 2.65
Clinical care guidelines for cystic fibrosis-related diabetes: a position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed by the Pediatric Endocrine Society. Diabetes Care (2010) 2.52
Development of the Cochrane Collaboration's CENTRAL Register of controlled clinical trials. Eval Health Prof (2002) 2.48
Surgical strategies for coexisting glaucoma and cataract: an evidence-based update. Ophthalmology (2002) 2.45
A systematic review of the methodological rigor of studies evaluating cultural competence training of health professionals. Acad Med (2005) 2.44
Using existing systematic reviews in complex systematic reviews. Ann Intern Med (2008) 2.36
Evaluation of guideline recommendations on oral medications for type 2 diabetes mellitus: a systematic review. Ann Intern Med (2012) 2.24
Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis. J Pediatr (2009) 2.16
The impact of obesity on outcomes after critical illness: a meta-analysis. Intensive Care Med (2009) 2.01
Clinical review: Prevalence and incidence of endocrine and metabolic disorders in the United States: a comprehensive review. J Clin Endocrinol Metab (2009) 1.93
Increases in thyroid nodule fine-needle aspirations, operations, and diagnoses of thyroid cancer in the United States. Surgery (2013) 1.85
Requirements for efficient correction of ΔF508 CFTR revealed by analyses of evolved sequences. Cell (2012) 1.81
Inhaled nitric oxide in preterm infants: a systematic review. Pediatrics (2011) 1.78
Cystic fibrosis pulmonary guidelines. Chronic medications for maintenance of lung health. Am J Respir Crit Care Med (2013) 1.77
Respiratory microbiology of patients with cystic fibrosis in the United States, 1995 to 2005. Chest (2009) 1.57
Diagnostic errors in the pediatric and neonatal ICU: a systematic review. Pediatr Crit Care Med (2015) 1.47
Medication errors in paediatric care: a systematic review of epidemiology and an evaluation of evidence supporting reduction strategy recommendations. Qual Saf Health Care (2007) 1.46
Arsenic in drinking water and lung cancer: a systematic review. Environ Res (2008) 1.43
Effectiveness of combination therapy with statin and another lipid-modifying agent compared with intensified statin monotherapy: a systematic review. Ann Intern Med (2014) 1.40
Does my dizzy patient have a stroke? A systematic review of bedside diagnosis in acute vestibular syndrome. CMAJ (2011) 1.39
Cruciferous vegetable consumption and lung cancer risk: a systematic review. Cancer Epidemiol Biomarkers Prev (2009) 1.38
Fluid flow induces mechanosensitive ATP release, calcium signalling and Cl- transport in biliary epithelial cells through a PKCzeta-dependent pathway. J Physiol (2008) 1.36
Carotenoids and the risk of developing lung cancer: a systematic review. Am J Clin Nutr (2008) 1.31
Comparative effectiveness of treatments for open-angle glaucoma: a systematic review for the U.S. Preventive Services Task Force. Ann Intern Med (2013) 1.31
Attention-deficit/hyperactivity disorder outcomes for children treated in community-based pediatric settings. Arch Pediatr Adolesc Med (2010) 1.30
The Navigation Guide - evidence-based medicine meets environmental health: systematic review of human evidence for PFOA effects on fetal growth. Environ Health Perspect (2014) 1.28
Community-wide intervention to improve the attention-deficit/hyperactivity disorder assessment and treatment practices of community physicians. Pediatrics (2008) 1.27
Caloric intake and eating behavior in infants and toddlers with cystic fibrosis. Pediatrics (2002) 1.26
Better nutritional status in early childhood is associated with improved clinical outcomes and survival in patients with cystic fibrosis. J Pediatr (2012) 1.26
Cystic fibrosis pulmonary guidelines: airway clearance therapies. Respir Care (2009) 1.25
Family functioning in school-age children with cystic fibrosis: an observational assessment of family interactions in the mealtime environment. J Pediatr Psychol (2005) 1.25
Cost-effectiveness of a novel molecular test for cytologically indeterminate thyroid nodules. J Clin Endocrinol Metab (2011) 1.24
Family functioning in young children with cystic fibrosis: observations of interactions at mealtime. J Dev Behav Pediatr (2004) 1.23
Effectiveness of hospital staff mass-casualty incident training methods: a systematic literature review. Prehosp Disaster Med (2004) 1.20
Effect of technique on intraocular pressure after combined cataract and glaucoma surgery: An evidence-based review. Ophthalmology (2002) 1.20
Identification and functional characterization of TMEM16A, a Ca2+-activated Cl- channel activated by extracellular nucleotides, in biliary epithelium. J Biol Chem (2010) 1.19
Adulthood consumption of preserved and nonpreserved vegetables and the risk of nasopharyngeal carcinoma: a systematic review. Int J Cancer (2006) 1.16
Clinical characteristics of symptomatic vertebral artery dissection: a systematic review. Neurologist (2012) 1.15
Outcome Measurement in ICU Survivorship Research From 1970 to 2013: A Scoping Review of 425 Publications. Crit Care Med (2016) 1.15
The Navigation Guide - evidence-based medicine meets environmental health: integration of animal and human evidence for PFOA effects on fetal growth. Environ Health Perspect (2014) 1.14
Infection prevention and control guideline for cystic fibrosis: 2013 update. Infect Control Hosp Epidemiol (2014) 1.13
The Navigation Guide - evidence-based medicine meets environmental health: systematic review of nonhuman evidence for PFOA effects on fetal growth. Environ Health Perspect (2014) 1.13
Development and pilot test of a process to identify research needs from a systematic review. J Clin Epidemiol (2012) 1.11
Cystic fibrosis pulmonary guidelines: pulmonary complications: hemoptysis and pneumothorax. Am J Respir Crit Care Med (2010) 1.11
Obesity in preschoolers: behavioral correlates and directions for treatment. Obesity (Silver Spring) (2011) 1.07
Interventions to modify health care provider adherence to asthma guidelines: a systematic review. Pediatrics (2013) 1.06
Regulation of purinergic signaling in biliary epithelial cells by exocytosis of SLC17A9-dependent ATP-enriched vesicles. J Biol Chem (2011) 1.05
Purinergic regulation of cholangiocyte secretion: identification of a novel role for P2X receptors. Am J Physiol Gastrointest Liver Physiol (2004) 1.05
Acne therapy: a methodologic review. J Am Acad Dermatol (2002) 1.04
Alcohol consumption and the risk of nasopharyngeal carcinoma: a systematic review. Nutr Cancer (2009) 1.02
Understanding why evidence from randomised clinical trials may not be retrieved from Medline: comparison of indexed and non-indexed records. BMJ (2012) 1.01
Selective toxin sequestrants for the treatment of bacterial infections. J Am Chem Soc (2009) 1.01
Mealtime behaviors in families of infants and toddlers with cystic fibrosis. J Cyst Fibros (2005) 0.99
Differences in home food and activity environments between obese and healthy weight families of preschool children. J Nutr Educ Behav (2013) 0.97
Developing a Treatment Program for Obesity in Preschool Age Children: Preliminary Data. Child Health Care (2010) 0.97
Cystic Fibrosis Foundation pulmonary guideline. pharmacologic approaches to prevention and eradication of initial Pseudomonas aeruginosa infection. Ann Am Thorac Soc (2014) 0.97
Development quality criteria to evaluate nontherapeutic studies of incidence, prevalence, or risk factors of chronic diseases: pilot study of new checklists. J Clin Epidemiol (2010) 0.96
Prevalence of postpartum thyroid dysfunction: a quantitative review. Thyroid (2006) 0.95
Adenosine triphosphate release and purinergic (P2) receptor-mediated secretion in small and large mouse cholangiocytes. Hepatology (2010) 0.94
Extracellular nucleotides stimulate Cl- currents in biliary epithelia through receptor-mediated IP3 and Ca2+ release. Am J Physiol Gastrointest Liver Physiol (2008) 0.94
Vesicular nucleotide transporter-mediated ATP release regulates insulin secretion. Endocrinology (2012) 0.94
Identification and functional characterization of the intermediate-conductance Ca(2+)-activated K(+) channel (IK-1) in biliary epithelium. Am J Physiol Gastrointest Liver Physiol (2009) 0.91
Developmental and psychosocial issues in cystic fibrosis. Child Adolesc Psychiatr Clin N Am (2010) 0.88
Mealtime problems predict outcome in clinical trial to improve nutrition in children with CF. Pediatr Pulmonol (2010) 0.88
Imaging characteristics of symptomatic vertebral artery dissection: a systematic review. Neurologist (2012) 0.88
Developmental and psychosocial issues in cystic fibrosis. Pediatr Clin North Am (2011) 0.88
High priority research needs for gestational diabetes mellitus. J Womens Health (Larchmt) (2012) 0.88
Active cycle of breathing technique for cystic fibrosis. Cochrane Database Syst Rev (2012) 0.87
Brief report: parent perspectives of nutritional status and mealtime behaviors in children with sickle cell disease. J Pediatr Psychol (2004) 0.87
How often is dizziness from primary cardiovascular disease true vertigo? A systematic review. J Gen Intern Med (2008) 0.86
Impaired health-related quality of life in preschoolers with obesity. J Pediatr Psychol (2012) 0.86
Bringing evidence to practice: a team approach to teaching skills required for an informationist role in evidence-based clinical and public health practice. J Med Libr Assoc (2008) 0.84
Mechanosensitive Cl- secretion in biliary epithelium mediated through TMEM16A. Am J Physiol Gastrointest Liver Physiol (2012) 0.84
Molecular characterization of volume-sensitive SK(Ca) channels in human liver cell lines. Am J Physiol Gastrointest Liver Physiol (2002) 0.83
Parent/Child training to increase preteens' calcium, physical activity, and bone density: a controlled trial. Am J Health Promot (2009) 0.83
The association between sleep duration and weight in treatment-seeking preschoolers with obesity. Sleep Med (2012) 0.81
Thinking outside the cell: the role of extracellular adenosine triphosphate in bile formation. Gastroenterology (2007) 0.81
Development of evaluation modules for use in hospital disaster drills. Am J Disaster Med (2008) 0.81
Training to hospital staff to respond to a mass casualty incident. Evid Rep Technol Assess (Summ) (2004) 0.79
Immunosuppressive drug therapy for preventing rejection following lung transplantation in cystic fibrosis. Cochrane Database Syst Rev (2015) 0.77
Development and use of evidence-based clinical practice guidelines for thyroid disease. Endocrinol Metab Clin North Am (2002) 0.77
Efficacy of increasing physical activity to reduce children's visceral fat: a pilot randomized controlled trial. Int J Pediatr Obes (2010) 0.76
Immunosuppressive drug therapy for preventing rejection following lung transplantation in cystic fibrosis. Cochrane Database Syst Rev (2013) 0.76
Critically appraise before you believe: the quality of meta-analyses in critical care medicine. Crit Care Med (2007) 0.75
Should meta-analysts search Embase in addition to Medline? J Clin Epidemiol (2005) 0.75
Methodologic rigor of clinical trials on surgical management of eyes with coexisting cataract and glaucoma. Ophthalmology (2002) 0.75
Web-based Bayesian Communication: the Bayesian z-test. AMIA Annu Symp Proc (2005) 0.75
Active cycle of breathing technique for cystic fibrosis. Cochrane Database Syst Rev (2016) 0.75
Advancing evidence in preterm neonatal medicine. Dev Disabil Res Rev (2010) 0.75
In the shadow of academic medical centers: a systematic review of urban health research in Baltimore City. J Community Health (2010) 0.75