Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
1
|
Spinal cord endoplasmic reticulum stress associated with a microsomal accumulation of mutant superoxide dismutase-1 in an ALS model.
|
Proc Natl Acad Sci U S A
|
2006
|
2.10
|
2
|
The inflammatory NADPH oxidase enzyme modulates motor neuron degeneration in amyotrophic lateral sclerosis mice.
|
Proc Natl Acad Sci U S A
|
2006
|
1.90
|
3
|
Increased autophagy in transgenic mice with a G93A mutant SOD1 gene.
|
Brain Res
|
2007
|
1.43
|
4
|
Mutant SOD1 linked to familial amyotrophic lateral sclerosis, but not wild-type SOD1, induces ER stress in COS7 cells and transgenic mice.
|
Biochem Biophys Res Commun
|
2003
|
1.28
|
5
|
Disease progression of human SOD1 (G93A) transgenic ALS model rats.
|
J Neurosci Res
|
2006
|
1.24
|
6
|
Expression of netrin-1 and its receptors DCC and neogenin in rat brain after ischemia.
|
Brain Res
|
2007
|
1.04
|
7
|
Decreased focal inflammatory response by G-CSF may improve stroke outcome after transient middle cerebral artery occlusion in rats.
|
J Neurosci Res
|
2007
|
0.98
|
8
|
Arg(184)His mutant GTP cyclohydrolase I, causing recessive hyperphenylalaninemia, is responsible for dopa-responsive dystonia with parkinsonism: a case report.
|
Mov Disord
|
2004
|
0.97
|
9
|
Disruption of neurovascular unit prior to motor neuron degeneration in amyotrophic lateral sclerosis.
|
J Neurosci Res
|
2011
|
0.96
|
10
|
Alteration of familial ALS-linked mutant SOD1 solubility with disease progression: its modulation by the proteasome and Hsp70.
|
Biochem Biophys Res Commun
|
2006
|
0.95
|
11
|
Potentiation of neurogenesis and angiogenesis by G-CSF after focal cerebral ischemia in rats.
|
Brain Res
|
2007
|
0.95
|
12
|
Two cases of spinocerebellar ataxia accompanied by involvement of the skeletal motor neuron system and bulbar palsy.
|
Intern Med
|
2007
|
0.91
|
13
|
Neuronal NOS and cyclooxygenase-2 contribute to DNA damage in a mouse model of Parkinson disease.
|
Free Radic Biol Med
|
2009
|
0.91
|
14
|
Accumulation of α-synuclein triggered by presynaptic dysfunction.
|
J Neurosci
|
2012
|
0.90
|
15
|
Parkin-mediated protection of dopaminergic neurons in a chronic MPTP-minipump mouse model of Parkinson disease.
|
J Neuropathol Exp Neurol
|
2011
|
0.89
|
16
|
Motor neuron disease in transgenic mice with an H46R mutant SOD1 gene.
|
J Neuropathol Exp Neurol
|
2007
|
0.88
|
17
|
Atorvastatin and pitavastatin improve cognitive function and reduce senile plaque and phosphorylated tau in aged APP mice.
|
Brain Res
|
2010
|
0.87
|
18
|
Histological evidence of redox system breakdown caused by superoxide dismutase 1 (SOD1) aggregation is common to SOD1-mutated motor neurons in humans and animal models.
|
Acta Neuropathol
|
2003
|
0.85
|
19
|
Therapeutic benefits of intrathecal protein therapy in a mouse model of amyotrophic lateral sclerosis.
|
J Neurosci Res
|
2008
|
0.85
|
20
|
Early decrease of mitochondrial DNA repair enzymes in spinal motor neurons of presymptomatic transgenic mice carrying a mutant SOD1 gene.
|
Brain Res
|
2007
|
0.83
|
21
|
PINK1, a gene product of PARK6, accumulates in alpha-synucleinopathy brains.
|
J Neurol Neurosurg Psychiatry
|
2007
|
0.83
|
22
|
Food conditions, competitive regime, and female social relationships in Japanese macaques: within-population variation on Yakushima.
|
Primates
|
2007
|
0.83
|
23
|
Development of a rat model of amyotrophic lateral sclerosis expressing a human SOD1 transgene.
|
Neuropathology
|
2005
|
0.82
|
24
|
Intrathecal injection of epidermal growth factor and fibroblast growth factor 2 promotes proliferation of neural precursor cells in the spinal cords of mice with mutant human SOD1 gene.
|
J Neurosci Res
|
2006
|
0.81
|
25
|
Enhanced accumulation of phosphorylated alpha-synuclein in double transgenic mice expressing mutant beta-amyloid precursor protein and presenilin-1.
|
J Neurosci Res
|
2007
|
0.80
|
26
|
Intrathecal delivery of hepatocyte growth factor from amyotrophic lateral sclerosis onset suppresses disease progression in rat amyotrophic lateral sclerosis model.
|
J Neuropathol Exp Neurol
|
2007
|
0.80
|
27
|
Vascular endothelial growth factor promotes brain tissue regeneration with a novel biomaterial polydimethylsiloxane-tetraethoxysilane.
|
Brain Res
|
2006
|
0.79
|
28
|
G-CSF enhances stem cell proliferation in rat hippocampus after transient middle cerebral artery occlusion.
|
Neurosci Lett
|
2007
|
0.79
|
29
|
[A case of Marchiafava-Bignami disease: serial changes with diffusion-weighted MR imaging].
|
Rinsho Shinkeigaku
|
2002
|
0.79
|
30
|
Motoneuron degeneration after facial nerve avulsion is exacerbated in presymptomatic transgenic rats expressing human mutant Cu/Zn superoxide dismutase.
|
J Neurosci Res
|
2005
|
0.79
|
31
|
Comparisons of acoustic function in SCA31 and other forms of ataxias.
|
Neurol Res
|
2011
|
0.79
|
32
|
Progressive decrease in the level of YAPdeltaCs, prosurvival isoforms of YAP, in the spinal cord of transgenic mouse carrying a mutant SOD1 gene.
|
J Neurosci Res
|
2009
|
0.79
|
33
|
Induction of parkinsonism-related proteins in the spinal motor neurons of transgenic mouse carrying a mutant SOD1 gene.
|
J Neurosci Res
|
2010
|
0.79
|
34
|
Mitochondrial alterations in transgenic mice with an H46R mutant Cu/Zn superoxide dismutase gene.
|
J Neuropathol Exp Neurol
|
2009
|
0.77
|
35
|
Early detachment of neuromuscular junction proteins in ALS mice with SODG93A mutation.
|
Neurol Int
|
2009
|
0.77
|
36
|
Spinal anterior horn has the capacity to self-regenerate in amyotrophic lateral sclerosis model mice.
|
J Neurosci Res
|
2009
|
0.77
|
37
|
Differentiation of PA from early PSP with different patterns of symptoms and CBF reduction.
|
Neurol Res
|
2008
|
0.75
|
38
|
Loss of DARPP-32 and calbindin in multiple system atrophy.
|
J Neural Transm (Vienna)
|
2013
|
0.75
|
39
|
Changes of Nogo-A and receptor NgR in the lumbar spinal cord of ALS model mice.
|
Neurol Res
|
2009
|
0.75
|
40
|
[MR spectroscopy findings of a case of intravascular malignant lymphoma: usefulness for differential diagnosis].
|
Rinsho Shinkeigaku
|
2003
|
0.75
|
41
|
[Toxoplasma encephalitis in a patient receiving cyclosporine monotherapy for Behçet disease].
|
Rinsho Shinkeigaku
|
2005
|
0.75
|