Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
1
|
ADAMTSL2 mutations in geleophysic dysplasia demonstrate a role for ADAMTS-like proteins in TGF-beta bioavailability regulation.
|
Nat Genet
|
2008
|
1.78
|
2
|
Mutations in the TGFβ binding-protein-like domain 5 of FBN1 are responsible for acromicric and geleophysic dysplasias.
|
Am J Hum Genet
|
2011
|
1.55
|
3
|
Punctin, a novel ADAMTS-like molecule, ADAMTSL-1, in extracellular matrix.
|
J Biol Chem
|
2002
|
1.31
|
4
|
ADAMTS7B, the full-length product of the ADAMTS7 gene, is a chondroitin sulfate proteoglycan containing a mucin domain.
|
J Biol Chem
|
2004
|
1.26
|
5
|
ADAMTS10 protein interacts with fibrillin-1 and promotes its deposition in extracellular matrix of cultured fibroblasts.
|
J Biol Chem
|
2011
|
1.25
|
6
|
Functional analysis of an ADAMTS10 signal peptide mutation in Weill-Marchesani syndrome demonstrates a long-range effect on secretion of the full-length enzyme.
|
Hum Mutat
|
2008
|
1.10
|
7
|
ADAMTS9 is a cell-autonomously acting, anti-angiogenic metalloprotease expressed by microvascular endothelial cells.
|
Am J Pathol
|
2010
|
1.07
|
8
|
ADAMTSL4, a secreted glycoprotein widely distributed in the eye, binds fibrillin-1 microfibrils and accelerates microfibril biogenesis.
|
Invest Ophthalmol Vis Sci
|
2012
|
0.97
|
9
|
A disintegrin-like and metalloprotease domain containing thrombospondin type 1 motif-like 5 (ADAMTSL5) is a novel fibrillin-1-, fibrillin-2-, and heparin-binding member of the ADAMTS superfamily containing a netrin-like module.
|
Matrix Biol
|
2012
|
0.86
|
10
|
Nonselective assembly of fibrillin 1 and fibrillin 2 in the rodent ocular zonule and in cultured cells: implications for Marfan syndrome.
|
Invest Ophthalmol Vis Sci
|
2013
|
0.85
|
11
|
An ADAMTSL2 founder mutation causes Musladin-Lueke Syndrome, a heritable disorder of beagle dogs, featuring stiff skin and joint contractures.
|
PLoS One
|
2010
|
0.83
|
12
|
Time-resolved analysis of the matrix metalloproteinase 10 substrate degradome.
|
Mol Cell Proteomics
|
2013
|
0.81
|
13
|
Hedgehog pathway inhibition in chondrosarcoma using the smoothened inhibitor IPI-926 directly inhibits sarcoma cell growth.
|
Mol Cancer Ther
|
2014
|
0.78
|