Published in Lancet Neurol on January 01, 2009
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The clinicopathologic spectrum of focal cortical dysplasias: a consensus classification proposed by an ad hoc Task Force of the ILAE Diagnostic Methods Commission. Epilepsia (2010) 6.23
15q13.3 microdeletions increase risk of idiopathic generalized epilepsy. Nat Genet (2009) 6.21
Electrical stimulation of the anterior nucleus of thalamus for treatment of refractory epilepsy. Epilepsia (2010) 5.64
Epilepsy, ataxia, sensorineural deafness, tubulopathy, and KCNJ10 mutations. N Engl J Med (2009) 4.96
Infantile spasms: a U.S. consensus report. Epilepsia (2010) 4.62
Recurrent microdeletions at 15q11.2 and 16p13.11 predispose to idiopathic generalized epilepsies. Brain (2009) 3.96
Dose-dependent risk of malformations with antiepileptic drugs: an analysis of data from the EURAP epilepsy and pregnancy registry. Lancet Neurol (2011) 3.93
The role of inflammation in epilepsy. Nat Rev Neurol (2010) 3.89
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The ketogenic diet for the treatment of childhood epilepsy: a randomised controlled trial. Lancet Neurol (2008) 3.51
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Somatic mutations in cerebral cortical malformations. N Engl J Med (2014) 3.13
Optimal clinical management of children receiving the ketogenic diet: recommendations of the International Ketogenic Diet Study Group. Epilepsia (2008) 2.87
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Hippocampal sclerosis after febrile status epilepticus: the FEBSTAT study. Ann Neurol (2014) 2.57
MRI abnormalities following febrile status epilepticus in children: the FEBSTAT study. Neurology (2012) 2.41
Language reorganization in children with early-onset lesions of the left hemisphere: an fMRI study. Brain (2004) 2.22
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Mutations in TUBG1, DYNC1H1, KIF5C and KIF2A cause malformations of cortical development and microcephaly. Nat Genet (2013) 2.06
Autosomal recessive cortical myoclonic tremor and epilepsy: association with a mutation in the potassium channel associated gene CNTN2. Brain (2013) 2.02
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Mutations in ARFGEF2 implicate vesicle trafficking in neural progenitor proliferation and migration in the human cerebral cortex. Nat Genet (2003) 1.96
Early-onset absence epilepsy caused by mutations in the glucose transporter GLUT1. Ann Neurol (2009) 1.94
Mutations of DEPDC5 cause autosomal dominant focal epilepsies. Nat Genet (2013) 1.91
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Mutations of ARX are associated with striking pleiotropy and consistent genotype-phenotype correlation. Hum Mutat (2004) 1.76
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Updated ILAE evidence review of antiepileptic drug efficacy and effectiveness as initial monotherapy for epileptic seizures and syndromes. Epilepsia (2013) 1.69
Disparities in NIH funding for epilepsy research. Neurology (2011) 1.69
Practice parameter: temporal lobe and localized neocortical resections for epilepsy. Epilepsia (2003) 1.66
Disruption of neural progenitors along the ventricular and subventricular zones in periventricular heterotopia. Hum Mol Genet (2008) 1.62
Clinical and imaging heterogeneity of polymicrogyria: a study of 328 patients. Brain (2010) 1.61
Novel brain expression of ClC-1 chloride channels and enrichment of CLCN1 variants in epilepsy. Neurology (2013) 1.61
Timing of antiepileptic drug withdrawal and long-term seizure outcome after paediatric epilepsy surgery (TimeToStop): a retrospective observational study. Lancet Neurol (2012) 1.60
Molecular mechanisms generating and stabilizing terminal 22q13 deletions in 44 subjects with Phelan/McDermid syndrome. PLoS Genet (2011) 1.60
Mutations in GRIN2A cause idiopathic focal epilepsy with rolandic spikes. Nat Genet (2013) 1.59
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Idiosyncratic adverse reactions to antiepileptic drugs. Epilepsia (2007) 1.56
Abnormal neuroimaging in patients with benign epilepsy with centrotemporal spikes. Epilepsia (2003) 1.56
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Unusual side effects of lamotrigine therapy. J Child Neurol (2003) 1.52
Proposed criteria for referral and evaluation of children for epilepsy surgery: recommendations of the Subcommission for Pediatric Epilepsy Surgery. Epilepsia (2006) 1.52
The core FOXG1 syndrome phenotype consists of postnatal microcephaly, severe mental retardation, absent language, dyskinesia, and corpus callosum hypogenesis. J Med Genet (2011) 1.50
Orange-colored diapers as first sign of Lesch-Nyhan disease in an asymptomatic infant. Pediatr Nephrol (2010) 1.49
Peritrigonal and temporo-occipital heterotopia with corpus callosum and cerebellar dysgenesis. Neurology (2012) 1.48
Genome-wide association analysis of genetic generalized epilepsies implicates susceptibility loci at 1q43, 2p16.1, 2q22.3 and 17q21.32. Hum Mol Genet (2012) 1.48
Sleep-related, low voltage Rolandic and vertex spikes: an EEG marker of benignity in infancy-onset focal epilepsies. Epileptic Disord (2002) 1.46
Identification of new epilepsy treatments: issues in preclinical methodology. Epilepsia (2012) 1.45
Development of new antiepileptic drugs: challenges, incentives, and recent advances. Lancet Neurol (2007) 1.44
Senile myoclonic epilepsy: delineation of a common condition associated with Alzheimer's disease in Down syndrome. Seizure (2010) 1.44
Which seizure-precipitating factors do patients with epilepsy most frequently report? Epilepsy Behav (2005) 1.44
Atypical multifocal Dravet syndrome lacks generalized seizures and may show later cognitive decline. Dev Med Child Neurol (2013) 1.44
Introduction: Recommendations regarding management of patients with Lennox-Gastaut syndrome. Epilepsia (2014) 1.44
Defining the spectrum of international practice in pediatric epilepsy surgery patients. Epilepsia (2007) 1.43
Seizure outcome after extratemporal epilepsy surgery in childhood. Dev Med Child Neurol (2012) 1.43
Psychopathology in children before and after surgery for extratemporal lobe epilepsy. Dev Med Child Neurol (2012) 1.41
An unusual cause of flaccid paralysis and coma: baclofen overdose. J Child Neurol (2013) 1.41
A 7 Mb duplication at 22q13 in a girl with bipolar disorder and hippocampal malformation. Am J Med Genet A (2008) 1.41
Sertraline-induced potentiation of the CYP3A4-dependent neurotoxicity of carbamazepine: an in vitro study. Epilepsia (2015) 1.40
Guidelines for imaging infants and children with recent-onset epilepsy. Epilepsia (2009) 1.40
Pediatric extratemporal epilepsy presenting with a complex auditory aura. Epileptic Disord (2008) 1.40
Acute symptomatic seizures--should we retain the term? Epilepsia (2010) 1.40
Benign familial neonatal-infantile seizures: characterization of a new sodium channelopathy. Ann Neurol (2004) 1.40
De novo loss-of-function mutations in CHD2 cause a fever-sensitive myoclonic epileptic encephalopathy sharing features with Dravet syndrome. Am J Hum Genet (2013) 1.40
Amygdalar neuromelanosis intractable epilepsy without leptomeningeal involvement. J Neurosurg Pediatr (2013) 1.39
Cardiac function and antiepileptic drug treatment in the elderly: a comparison between lamotrigine and sustained-release carbamazepine. Epilepsia (2009) 1.38
Antiepileptic drug-induced pharmacodynamic aggravation of seizures: does valproate have a lower potential? CNS Drugs (2003) 1.38
Polymicrogyria and deletion 22q11.2 syndrome: window to the etiology of a common cortical malformation. Am J Med Genet A (2006) 1.38
Subcortical band heterotopia (SBH) in males: clinical, imaging and genetic findings in comparison with females. Brain (2002) 1.37
Placebo-corrected efficacy of modern antiepileptic drugs for refractory epilepsy: reply to Beyenburg et al., 2009. Epilepsia (2010) 1.37