PubRank

Elaine C Davis

Author PubWeight™ 66.26‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 A syndrome of altered cardiovascular, craniofacial, neurocognitive and skeletal development caused by mutations in TGFBR1 or TGFBR2. Nat Genet 2005 9.62
2 Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo. Nature 2002 3.60
3 Mutations in the gene encoding the RER protein FKBP65 cause autosomal-recessive osteogenesis imperfecta. Am J Hum Genet 2010 2.39
4 Integrin-modulating therapy prevents fibrosis and autoimmunity in mouse models of scleroderma. Nature 2013 1.86
5 Autosomal dominant cutis laxa with severe lung disease: synthesis and matrix deposition of mutant tropoelastin. J Invest Dermatol 2005 1.82
6 Fibrillin-1 interactions with fibulins depend on the first hybrid domain and provide an adaptor function to tropoelastin. J Biol Chem 2007 1.56
7 GLUT10 is required for the development of the cardiovascular system and the notochord and connects mitochondrial function to TGFβ signaling. Hum Mol Genet 2011 1.52
8 Lack of fibulin-3 causes early aging and herniation, but not macular degeneration in mice. Hum Mol Genet 2007 1.50
9 Elastic fiber formation: a dynamic view of extracellular matrix assembly using timer reporters. J Cell Physiol 2006 1.47
10 Fibulin-4 deficiency results in ascending aortic aneurysms: a potential link between abnormal smooth muscle cell phenotype and aneurysm progression. Circ Res 2009 1.46
11 Extracellular matrix proteases contribute to progression of pelvic organ prolapse in mice and humans. J Clin Invest 2011 1.44
12 Loss-of-function mutations in ATP6V0A2 impair vesicular trafficking, tropoelastin secretion and cell survival. Hum Mol Genet 2009 1.40
13 Altered vascular remodeling in fibulin-5-deficient mice reveals a role of fibulin-5 in smooth muscle cell proliferation and migration. Proc Natl Acad Sci U S A 2005 1.37
14 Mutations in LTBP4 cause a syndrome of impaired pulmonary, gastrointestinal, genitourinary, musculoskeletal, and dermal development. Am J Hum Genet 2009 1.34
15 Fibulin-5 mutations: mechanisms of impaired elastic fiber formation in recessive cutis laxa. Hum Mol Genet 2006 1.31
16 Mutations in FKBP10, which result in Bruck syndrome and recessive forms of osteogenesis imperfecta, inhibit the hydroxylation of telopeptide lysines in bone collagen. Hum Mol Genet 2012 1.29
17 Domains in tropoelastin that mediate elastin deposition in vitro and in vivo. J Biol Chem 2003 1.27
18 Discrete contributions of elastic fiber components to arterial development and mechanical compliance. Arterioscler Thromb Vasc Biol 2009 1.18
19 Dual functions for LTBP in lung development: LTBP-4 independently modulates elastogenesis and TGF-beta activity. J Cell Physiol 2009 1.14
20 Molecular analysis of fibulin-5 function during de novo synthesis of elastic fibers. Mol Cell Biol 2006 1.13
21 Failure of pelvic organ support in mice deficient in fibulin-3. Am J Pathol 2008 1.13
22 Elastic fiber macro-assembly is a hierarchical, cell motion-mediated process. J Cell Physiol 2006 1.09
23 Unraveling the mechanism of elastic fiber assembly: The roles of short fibulins. Int J Biochem Cell Biol 2010 1.08
24 Autophagy and skeletal muscles in sepsis. PLoS One 2012 1.05
25 Characterization of human thioredoxin-like 2. A novel microtubule-binding thioredoxin expressed predominantly in the cilia of lung airway epithelium and spermatid manchette and axoneme. J Biol Chem 2003 1.01
26 Fibrillins, fibulins, and matrix-associated glycoprotein modulate the kinetics and morphology of in vitro self-assembly of a recombinant elastin-like polypeptide. Biochemistry 2008 1.01
27 Fibulin-5 functions as an endogenous angiogenesis inhibitor. Lab Invest 2007 1.00
28 Mechanisms of emphysema in autosomal dominant cutis laxa. Matrix Biol 2010 0.99
29 Transforming growth factor-β signaling in myogenic cells regulates vascular morphogenesis, differentiation, and matrix synthesis. Arterioscler Thromb Vasc Biol 2011 0.96
30 Developmental regulation and coordinate reexpression of FKBP65 with extracellular matrix proteins after lung injury suggest a specialized function for this endoplasmic reticulum immunophilin. Cell Stress Chaperones 2005 0.96
31 Analysis of dermal elastic fibers in the absence of fibulin-5 reveals potential roles for fibulin-5 in elastic fiber assembly. Matrix Biol 2009 0.95
32 CEACAM1: a key regulator of vascular permeability. J Cell Sci 2010 0.94
33 Fibulin-2 and fibulin-5 cooperatively function to form the internal elastic lamina and protect from vascular injury. Arterioscler Thromb Vasc Biol 2009 0.93
34 Comprehensive clinical and molecular analysis of 12 families with type 1 recessive cutis laxa. Hum Mutat 2012 0.93
35 Fibrillin-3 expression in human development. Matrix Biol 2010 0.92
36 Micropatterned cell sheets with defined cell and extracellular matrix orientation exhibit anisotropic mechanical properties. J Biomech 2011 0.91
37 Normal wound healing in mice deficient for fibulin-5, an elastin binding protein essential for dermal elastic fiber assembly. J Invest Dermatol 2006 0.91
38 The phosphatase PTP-PEST/PTPN12 regulates endothelial cell migration and adhesion, but not permeability, and controls vascular development and embryonic viability. J Biol Chem 2012 0.91
39 Elastin haploinsufficiency impedes the progression of arterial calcification in MGP-deficient mice. J Bone Miner Res 2014 0.89
40 Function of latent TGFβ binding protein 4 and fibulin 5 in elastogenesis and lung development. J Cell Physiol 2015 0.87
41 Control of lung development by latent TGF-β binding proteins. J Cell Physiol 2011 0.87
42 Genomic organization of mouse and human 65 kDa FK506-binding protein genes and evolution of the FKBP multigene family. Genomics 2002 0.83
43 In vitro elastogenesis: instructing human vascular smooth muscle cells to generate an elastic fiber-containing extracellular matrix scaffold. Biomed Mater 2015 0.81
44 Novel mechanism of aortic aneurysm development in mice associated with smoking and leukocytes. Arterioscler Thromb Vasc Biol 2012 0.81
45 Alternative splicing and tissue-specific elastin misassembly act as biological modifiers of human elastin gene frameshift mutations associated with dominant cutis laxa. J Biol Chem 2012 0.81
46 FKBP10/FKBP65 expression in high-grade ovarian serous carcinoma and its association with patient outcome. Int J Oncol 2013 0.80
47 Vascular response to intra-arterial injury in the thrombospondin-1 null mouse. J Mol Cell Cardiol 2007 0.79
48 VGLL3 expression is associated with a tumor suppressor phenotype in epithelial ovarian cancer. Mol Oncol 2013 0.79
49 Airway hyperresponsiveness is associated with airway remodeling but not inflammation in aging Cav1-/- mice. Respir Res 2013 0.78
50 Analysis of obstetric complications and uterine connective tissue in tenascin-X-deficient humans and mice. Cell Tissue Res 2008 0.77
51 Characterization of an unusual tropoelastin with truncated C-terminus in the frog. Matrix Biol 2009 0.76
52 An electrochemical method for functionalization of a 316L stainless steel surface being used as a stent in coronary surgery: irreversible immobilization of fibronectin for the enhancement of endothelial cell attachment. Biotechnol Lett 2012 0.75