Masami Iida

Author PubWeight™ 6.74‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Chemical chaperone therapy: clinical effect in murine G(M1)-gangliosidosis. Ann Neurol 2007 0.93
2 Enzyme enhancement activity of N-octyl-beta-valienamine on beta-glucosidase mutants associated with Gaucher disease. Biochim Biophys Acta 2007 0.89
3 Fibroblast screening for chaperone therapy in beta-galactosidosis. Brain Dev 2006 0.88
4 Microscale preparation of even- and odd-numbered N-acetylheparosan oligosaccharides. Carbohydr Res 2005 0.85
5 Chemical chaperone therapy: chaperone effect on mutant enzyme and cellular pathophysiology in β-galactosidase deficiency. Hum Mutat 2011 0.85
6 Therapeutic chaperone effect of N-octyl 4-epi-β-valienamine on murine G(M1)-gangliosidosis. Mol Genet Metab 2012 0.82
7 Lysosomal accumulation of Trk protein in brain of GM₁ -gangliosidosis mouse and its restoration by chemical chaperone. J Neurochem 2011 0.79
8 Chemical chaperone therapy: luciferase assay for screening of β-galactosidase mutations. Mol Genet Metab 2010 0.75
9 The pharmacological chaperone effect of N-octyl-beta-valienamine on human mutant acid beta-glucosidases. Blood Cells Mol Dis 2009 0.75
10 The effect of N-octyl-β-valienamine on β-glucosidase activity in tissues of normal mice. Brain Dev 2010 0.75