Published in Amyloid on March 01, 2010
Peripheral sympathetic nerve dysfunction in adolescent Japanese girls following immunization with the human papillomavirus vaccine. Intern Med (2014) 4.78
A primer of amyloid nomenclature. Amyloid (2007) 2.70
Native state kinetic stabilization as a strategy to ameliorate protein misfolding diseases: a focus on the transthyretin amyloidoses. Acc Chem Res (2005) 2.25
Amyloid: toward terminology clarification. Report from the Nomenclature Committee of the International Society of Amyloidosis. Amyloid (2005) 2.14
Epicardial electrogram of the right ventricular outflow tract in patients with the Brugada syndrome: using the epicardial lead. J Am Coll Cardiol (2002) 2.01
Amyloid fibril protein nomenclature: 2010 recommendations from the nomenclature committee of the International Society of Amyloidosis. Amyloid (2010) 1.91
The pathophysiological mechanism underlying Brugada syndrome: depolarization versus repolarization. J Mol Cell Cardiol (2010) 1.78
Functional characterization of a trafficking-defective HCN4 mutation, D553N, associated with cardiac arrhythmia. J Biol Chem (2004) 1.75
Clinical significance of macroscopic T-wave alternans after sodium channel blocker administration in patients with Brugada syndrome. J Cardiovasc Electrophysiol (2007) 1.55
Longer repolarization in the epicardium at the right ventricular outflow tract causes type 1 electrocardiogram in patients with Brugada syndrome. J Am Coll Cardiol (2008) 1.54
Fragmented QRS is associated with torsades de pointes in patients with acquired long QT syndrome. Heart Rhythm (2010) 1.52
Spontaneous electrocardiogram alterations predict ventricular fibrillation in Brugada syndrome. Heart Rhythm (2011) 1.51
Continuous improvements in "chain of survival" increased survival after out-of-hospital cardiac arrests: a large-scale population-based study. Circulation (2009) 1.51
Native state stabilization by NSAIDs inhibits transthyretin amyloidogenesis from the most common familial disease variants. Lab Invest (2004) 1.50
Use of a whole blood rapid panel test for heart-type fatty acid-binding protein in patients with acute chest pain: comparison with rapid troponin T and myoglobin tests. Am J Med (2003) 1.44
Successful pregnancy and lactation outcome in a patient with Gaucher disease receiving enzyme replacement therapy, and the subsequent distribution and excretion of imiglucerase in human breast milk. Clin Ther (2010) 1.43
Surgical treatment of traumatic thoracic aorta rupture: a 7-year experience. Jpn J Thorac Cardiovasc Surg (2003) 1.42
Myasthenia gravis with anti-MuSK antibody, showing progressive muscular atrophy without blepharoptosis. Intern Med (2005) 1.42
Long-term follow-up of systemic reactive AA amyloidosis secondary to rheumatoid arthritis: successful treatment with intermediate-dose corticosteroid. Intern Med (2002) 1.39
An unusual case of Klippel-Trénaunay-Weber syndrome presenting with portosystemic encephalopathy. Intern Med (2008) 1.37
D18G transthyretin is monomeric, aggregation prone, and not detectable in plasma and cerebrospinal fluid: a prescription for central nervous system amyloidosis? Biochemistry (2003) 1.36
Atrial fibrillation in patients with Brugada syndrome relationships of gene mutation, electrophysiology, and clinical backgrounds. J Am Coll Cardiol (2008) 1.33
Rheumatoid meningitis: an autopsy report and review of the literature. Clin Rheumatol (2003) 1.33
Carvedilol decreases elevated oxidative stress in human failing myocardium. Circulation (2002) 1.32
Follow-up of three patients with a large in-frame deletion of exons 45-55 in the Duchenne muscular dystrophy (DMD) gene. J Clin Neurosci (2008) 1.30
The Lycopodium alkaloids. Alkaloids Chem Biol (2005) 1.30
Relationship between arrhythmogenesis and disease activity in cardiac sarcoidosis. Heart Rhythm (2007) 1.23
Significance of lymphatic invasion and cancer invasion-related proteins on lymph node metastasis in gastric cancer. J Gastroenterol Hepatol (2009) 1.22
Outcome and characteristics of out-of-hospital cardiac arrest according to location of arrest: A report from a large-scale, population-based study in Osaka, Japan. Resuscitation (2006) 1.21
Age-specific differences in outcomes after out-of-hospital cardiac arrests. Pediatrics (2011) 1.20
Diflunisal stabilizes familial amyloid polyneuropathy-associated transthyretin variant tetramers in serum against dissociation required for amyloidogenesis. Neurosci Res (2006) 1.20
Liver Transplantation for Hereditary Transthyretin Amyloidosis: After 20 Years Still the Best Therapeutic Alternative? Transplantation (2015) 1.13
Energetic characteristics of the new transthyretin variant A25T may explain its atypical central nervous system pathology. Lab Invest (2003) 1.10
Exome sequencing reveals a homozygous SYT14 mutation in adult-onset, autosomal-recessive spinocerebellar ataxia with psychomotor retardation. Am J Hum Genet (2011) 1.10
Clinical and genetic features of familial Mediterranean fever in Japan. J Rheumatol (2009) 1.09
Novel pathogenic mutations and copy number variations in the VPS13A gene in patients with chorea-acanthocytosis. Am J Med Genet B Neuropsychiatr Genet (2011) 1.08
Alkaloids from the seeds of Peganum harmala showing antiplasmodial and vasorelaxant activities. J Nat Med (2008) 1.07
Expression of secretory phospholipase A2s in human atherosclerosis development. Atherosclerosis (2007) 1.07
Noninvasive metabolomic profiling as an adjunct to morphology for noninvasive embryo assessment in women undergoing single embryo transfer. Fertil Steril (2009) 1.06
Dystonia, mental deterioration, and dyschromatosis symmetrica hereditaria in a family with ADAR1 mutation. Mov Disord (2006) 1.06
Adult or late-onset triple A syndrome: case report and literature review. J Neurol Sci (2010) 1.05
Genotype-phenotype correlations in early onset ataxia with ocular motor apraxia and hypoalbuminaemia. Brain (2011) 1.04
Myocardial apoptosis associated with the expression of proinflammatory cytokines during the course of myocardial infarction. Mod Pathol (2006) 1.04
Erythrocarpines A-E, new cytotoxic limonoids from Chisocheton erythrocarpus. Bioorg Med Chem (2007) 1.04
Familial Mediterranean fever in Japan. Medicine (Baltimore) (2012) 1.04
Induction of AApoAII amyloidosis by various heterogeneous amyloid fibrils. FEBS Lett (2004) 1.03
Relationship between oxidative stress and systolic dysfunction in patients with hypertrophic cardiomyopathy. J Card Fail (2005) 1.01
Significance of the level of monocyte chemoattractant protein-1 in human atherosclerosis. Circ J (2004) 1.00
Distinct U wave changes in patients with catecholaminergic polymorphic ventricular tachycardia (CPVT). Int Heart J (2006) 0.99
Alogliptin ameliorates postprandial lipemia and postprandial endothelial dysfunction in non-diabetic subjects: a preliminary report. Cardiovasc Diabetol (2013) 0.99
Amyloid fibrils containing fragmented ATTR may be the standard fibril composition in ATTR amyloidosis. Amyloid (2013) 0.98
Identification of high-risk syncope related to ventricular fibrillation in patients with Brugada syndrome. Heart Rhythm (2011) 0.97
Increase in incidence of elderly-onset patients with myasthenia gravis in Nagano Prefecture, Japan. Intern Med (2005) 0.97
Low-dose isoproterenol for repetitive ventricular arrhythmia in patients with Brugada syndrome. Eur Heart J (2006) 0.96
Analysis of an insertion mutation in a cohort of 94 patients with spinocerebellar ataxia type 31 from Nagano, Japan. Neurogenetics (2010) 0.96
Effects of periocular administration of triamcinolone acetonide on leukocyte-endothelium interactions in the ischemic retina. Invest Ophthalmol Vis Sci (2007) 0.95
Studies on the constituents from the fruits of Phaleria macrocarpa. J Nat Med (2007) 0.95
Successful treatment with rituximab in a patient with stiff-person syndrome complicated by dysthyroid ophthalmopathy. Intern Med (2010) 0.95
Spinal nerve root hypertrophy on MRI: clinical significance in the diagnosis of chronic inflammatory demyelinating polyradiculoneuropathy. Intern Med (2008) 0.94
Vasorelaxant effect of FR900359 from Ardisia crenata on rat aortic artery. J Nat Med (2012) 0.92
Extensive loss of arterial medial smooth muscle cells and mural extracellular matrix in cerebral autosomal recessive arteriopathy with subcortical infarcts and leukoencephalopathy (CARASIL). Neuropathology (2007) 0.92
Nankakurine A, a novel C16N2-type alkaloid from Lycopodium hamiltonii. Org Lett (2004) 0.91
Cytokine reducing effect of azelnidipine in human peripheral blood mononuclear cells. Biol Pharm Bull (2010) 0.91
4-Hydroxy-2-nonenal induces calcium overload via the generation of reactive oxygen species in isolated rat cardiac myocytes. J Card Fail (2009) 0.91
High prevalence of wild-type transthyretin deposition in patients with idiopathic carpal tunnel syndrome: a common cause of carpal tunnel syndrome in the elderly. Hum Pathol (2011) 0.91
Simple and useful tests for discriminating between acute aortic dissection of the ascending aorta and acute myocardial infarction in the emergency setting. Circ J (2005) 0.90
Ezetimibe improves postprandial hyperlipemia and its induced endothelial dysfunction. Atherosclerosis (2011) 0.90
Cerebral hemorrhage in Fabry's disease. J Hum Genet (2010) 0.89
Intravenous immunoglobulin (IVIg) with methylprednisolone pulse therapy for motor impairment of neuralgic amyotrophy: clinical observations in 10 cases. Intern Med (2012) 0.89
The Daphniphyllum alkaloids. Alkaloids Chem Biol (2003) 0.89
Alstiphyllanines E-H, picraline and ajmaline-type alkaloids from Alstonia macrophylla inhibiting sodium glucose cotransporter. Bioorg Med Chem (2010) 0.89
Differential association of visceral adipose tissue with coronary plaque characteristics in patients with and without diabetes mellitus. Cardiovasc Diabetol (2014) 0.88
Early cardiac involvement in senile systemic amyloidosis: a case report. Amyloid (2008) 0.88
Safety and efficacy of long-term diflunisal administration in hereditary transthyretin (ATTR) amyloidosis. Amyloid (2015) 0.88
Clinical evaluation of point-of-care-testing of heart-type fatty acid-binding protein (H-FABP) for the diagnosis of acute myocardial infarction. J Immunoassay Immunochem (2006) 0.88
Pneumatosis cystoides intestinalis in neuropsychiatric systemic lupus erythematosus with diabetes mellitus: case report and literature review. Mod Rheumatol (2011) 0.88
Alstilobanines A-E, new indole alkaloids from Alstonia angustiloba. Bioorg Med Chem (2008) 0.87
Evidence of active endocarditis, caused by Gemella morbillorum, related to acute embolic stroke. Int J Cardiol (2006) 0.87
Circular dichroism calculation for natural products. J Nat Med (2013) 0.87
Multiple analyses of G-protein coupled receptor (GPCR) expression in the development of gefitinib-resistance in transforming non-small-cell lung cancer. PLoS One (2012) 0.87
The Diflunisal Trial: study accrual and drug tolerance. Amyloid (2012) 0.87
Clinical and radiological findings of a cerebrotendinous xanthomatosis patient with a novel p.A335V mutation in the CYP27A1 gene. Intern Med (2014) 0.87
A cross-sectional study of glucose regulation in young adults with very low birth weight: impact of male gender on hyperglycaemia. BMJ Open (2012) 0.87
Retrospective analyses of clinical features and therapeutic outcomes in thymectomized patients with myasthenia gravis at Shinshu University. Intern Med (2004) 0.87
Justidrusamides A-D, new 2-aminobenzyl alcohol derivatives from Justicia gendarussa. J Nat Med (2014) 0.87
Adult onset X-linked chronic granulomatous disease in a woman patient caused by a de novo mutation in paternal-origin CYBB gene and skewed inactivation of normal maternal X chromosome. Intern Med (2008) 0.86
Location of out-of-hospital cardiac arrests in Takatsuki City: where should automated external defibrillator be placed. Circ J (2006) 0.86
Ten years of experience with liver transplantation for familial amyloid polyneuropathy in Japan: outcomes of living donor liver transplantations. Intern Med (2005) 0.86
Fragmented QRS: What Is The Meaning? Indian Pacing Electrophysiol J (2012) 0.86
Risk of alveolar hemorrhage in patients with primary pulmonary hypertension--anticoagulation and epoprostenol therapy. Circ J (2005) 0.85