A management strategy for fetal immune-mediated atrioventricular block.

Congenital and childhood atrioventricular blocks: pathophysiology and contemporary management. Eur J Pediatr (2016) 0.80

Prevention and treatment in utero of autoimmune-associated congenital heart block. Cardiol Rev (2014) 0.76

Atrioventricular conduction delay in the second trimester measured by fetal magnetocardiography. J Immunol Res (2014) 0.75

Atenolol versus losartan in children and young adults with Marfan's syndrome. N Engl J Med (2014) 5.11

Genetic basis for congenital heart defects: current knowledge: a scientific statement from the American Heart Association Congenital Cardiac Defects Committee, Council on Cardiovascular Disease in the Young: endorsed by the American Academy of Pediatrics. Circulation (2007) 4.34

Comparison of magnetic resonance feature tracking for strain calculation with harmonic phase imaging analysis. JACC Cardiovasc Imaging (2010) 3.50

Constitutively active AMP kinase mutations cause glycogen storage disease mimicking hypertrophic cardiomyopathy. J Clin Invest (2002) 3.33

Extracellular matrix remodeling and organization in developing and diseased aortic valves. Circ Res (2006) 2.91

Calmodulin mutations associated with recurrent cardiac arrest in infants. Circulation (2013) 2.66

Nkx2-5 pathways and congenital heart disease; loss of ventricular myocyte lineage specification leads to progressive cardiomyopathy and complete heart block. Cell (2004) 2.64

AHA/ACCF scientific statement on the evaluation of syncope: from the American Heart Association Councils on Clinical Cardiology, Cardiovascular Nursing, Cardiovascular Disease in the Young, and Stroke, and the Quality of Care and Outcomes Research Interdisciplinary Working Group; and the American College of Cardiology Foundation In Collaboration With the Heart Rhythm Society. J Am Coll Cardiol (2006) 2.38

Inherited arrhythmias: a National Heart, Lung, and Blood Institute and Office of Rare Diseases workshop consensus report about the diagnosis, phenotyping, molecular mechanisms, and therapeutic approaches for primary cardiomyopathies of gene mutations affecting ion channel function. Circulation (2007) 2.33

Hypoplastic left heart syndrome is heritable. J Am Coll Cardiol (2007) 2.24

Bicuspid aortic valve is heritable. J Am Coll Cardiol (2004) 2.18

Hypoplastic left heart syndrome: current considerations and expectations. J Am Coll Cardiol (2012) 2.10

NKX2.5 mutations in patients with congenital heart disease. J Am Coll Cardiol (2003) 2.09

Hypoplastic left heart syndrome links to chromosomes 10q and 6q and is genetically related to bicuspid aortic valve. J Am Coll Cardiol (2009) 1.88

AHA/ACCF Scientific Statement on the evaluation of syncope: from the American Heart Association Councils on Clinical Cardiology, Cardiovascular Nursing, Cardiovascular Disease in the Young, and Stroke, and the Quality of Care and Outcomes Research Interdisciplinary Working Group; and the American College of Cardiology Foundation: in collaboration with the Heart Rhythm Society: endorsed by the American Autonomic Society. Circulation (2006) 1.86

Biochemical analyses of eight NKX2.5 homeodomain missense mutations causing atrioventricular block and cardiac anomalies. Cardiovasc Res (2004) 1.80

Electrocardiographic features in Andersen-Tawil syndrome patients with KCNJ2 mutations: characteristic T-U-wave patterns predict the KCNJ2 genotype. Circulation (2005) 1.77

Circumferential strain analysis identifies strata of cardiomyopathy in Duchenne muscular dystrophy: a cardiac magnetic resonance tagging study. J Am Coll Cardiol (2009) 1.74

Spectrum of heart disease associated with murine and human GATA4 mutation. J Mol Cell Cardiol (2007) 1.71

Polymorphic ventricular tachycardia and KCNJ2 mutations. Heart Rhythm (2004) 1.68

Transcription factors and congenital heart defects. Annu Rev Physiol (2006) 1.66

Clinical, genetic, and biophysical characterization of SCN5A mutations associated with atrioventricular conduction block. Circulation (2002) 1.65

The effects of dexmedetomidine on cardiac electrophysiology in children. Anesth Analg (2008) 1.64

Prenatal diagnosis and in utero treatment of torsades de pointes associated with congenital long QT syndrome. Am J Cardiol (2003) 1.61

KCNJ2 mutation results in Andersen syndrome with sex-specific cardiac and skeletal muscle phenotypes. Am J Hum Genet (2002) 1.60

Risk factors for aortic valve disease in bicuspid aortic valve: a family-based study. Am J Med Genet A (2011) 1.55

Genetic variants in SCN5A promoter are associated with arrhythmia phenotype severity in patients with heterozygous loss-of-function mutation. Heart Rhythm (2012) 1.51

ACC/AHA/AAP recommendations for training in pediatric cardiology. Pediatrics (2005) 1.46

Atrial and ventricular rate response and patterns of heart rate acceleration during maternal-fetal terbutaline treatment of fetal complete heart block. Am J Cardiol (2007) 1.43

A common SCN5A polymorphism modulates the biophysical effects of an SCN5A mutation. J Clin Invest (2003) 1.41

Mouse heart valve structure and function: echocardiographic and morphometric analyses from the fetus through the aged adult. Am J Physiol Heart Circ Physiol (2008) 1.40

Outpatient continuous inotrope infusion as an adjunct to heart failure therapy in Duchenne muscular dystrophy. Neuromuscul Disord (2006) 1.40

Practice advisory for the prevention and management of operating room fires. Anesthesiology (2008) 1.38

Magnetic resonance derived myocardial strain assessment using feature tracking. J Vis Exp (2011) 1.32

Amiodarone therapy for drug-refractory fetal tachycardia. Circulation (2004) 1.29

Evidence in favor of linkage to human chromosomal regions 18q, 5q and 13q for bicuspid aortic valve and associated cardiovascular malformations. Hum Genet (2007) 1.28

The new sequencer on the block: comparison of Life Technology's Proton sequencer to an Illumina HiSeq for whole-exome sequencing. Hum Genet (2013) 1.27

Fetal heart rate predictors of long QT syndrome. Circulation (2012) 1.24

Prevalence and distribution of late gadolinium enhancement in a large population of patients with Duchenne muscular dystrophy: effect of age and left ventricular systolic function. J Cardiovasc Magn Reson (2013) 1.18

Characteristics of children and young adults with Marfan syndrome and aortic root dilation in a randomized trial comparing atenolol and losartan therapy. Am Heart J (2013) 1.14

Analysis of Ellis van Creveld syndrome gene products: implications for cardiovascular development and disease. Hum Mol Genet (2009) 1.13

Developmentally regulated SCN5A splice variant potentiates dysfunction of a novel mutation associated with severe fetal arrhythmia. Heart Rhythm (2011) 1.11

Arrhythmia phenotype during fetal life suggests long-QT syndrome genotype: risk stratification of perinatal long-QT syndrome. Circ Arrhythm Electrophysiol (2013) 1.11

Prenatal head growth and white matter injury in hypoplastic left heart syndrome. Pediatr Res (2008) 1.09

Deletion of ETS-1, a gene in the Jacobsen syndrome critical region, causes ventricular septal defects and abnormal ventricular morphology in mice. Hum Mol Genet (2009) 1.09

Sporadic isolated left ventricular noncompaction: dread disease or not? Pacing Clin Electrophysiol (2007) 1.07

Phenotyping the function of TRPV1-expressing sensory neurons by targeted axonal silencing. J Neurosci (2013) 1.06

Elastin haploinsufficiency results in progressive aortic valve malformation and latent valve disease in a mouse model. Circ Res (2010) 1.02

Detection of progressive cardiac dysfunction by serial evaluation of circumferential strain in patients with Duchenne muscular dystrophy. Am J Cardiol (2010) 1.00

An intronic mutation causes long QT syndrome. J Am Coll Cardiol (2004) 0.97

Intermittent airway obstruction and superior vena cava syndrome in a patient with an undiagnosed mediastinal mass after cesarean delivery. Anesth Analg (2003) 0.97

BMP and FGF regulatory pathways in semilunar valve precursor cells. Dev Dyn (2007) 0.97

Abnormal circumferential strain is present in young Duchenne muscular dystrophy patients. Pediatr Cardiol (2013) 0.96

Patterns of left ventricular remodeling in patients with Duchenne Muscular Dystrophy: a cardiac MRI study of ventricular geometry, global function, and strain. Int J Cardiovasc Imaging (2011) 0.95

The role of mitochondrial genome in essential hypertension in a Chinese Han population. Eur J Hum Genet (2009) 0.95

Abnormalities of diastolic function precede dilated cardiomyopathy associated with Duchenne muscular dystrophy. J Am Soc Echocardiogr (2006) 0.95

Clinical, genetic, and biophysical characterization of a homozygous HERG mutation causing severe neonatal long QT syndrome. Pediatr Res (2003) 0.93

Left ventricular T2 distribution in Duchenne muscular dystrophy. J Cardiovasc Magn Reson (2010) 0.93

Characterization of T gene sequence variants and germline duplications in familial and sporadic chordoma. Hum Genet (2014) 0.92

Trafficking-competent and trafficking-defective KCNJ2 mutations in Andersen syndrome. Hum Mutat (2006) 0.92

Regional circumferential strain is a biomarker for disease severity in duchenne muscular dystrophy heart disease: a cross-sectional study. Pediatr Cardiol (2014) 0.89

Effects of steroids and angiotensin converting enzyme inhibition on circumferential strain in boys with Duchenne muscular dystrophy: a cross-sectional and longitudinal study utilizing cardiovascular magnetic resonance. J Cardiovasc Magn Reson (2011) 0.88

Bidirectional ventricular tachycardia and channelopathy. Am J Cardiol (2003) 0.88

Differentiation of cardiac Purkinje fibers requires precise spatiotemporal regulation of Nkx2-5 expression. Dev Dyn (2006) 0.88

An expanded phenotype of maternal SSA/SSB antibody-associated fetal cardiac disease. J Matern Fetal Neonatal Med (2009) 0.87

Conduction system disease in fetuses evaluated for irregular cardiac rhythm. Fetal Diagn Ther (2006) 0.87

Autonomic dysfunction: a driving force for myocardial fibrosis in young Duchenne muscular dystrophy patients? Pediatr Cardiol (2014) 0.87

Investigation of near ohmic behavior for poly(3,4-ethylenedioxythiophene): a model consistent with systematic variations in polymerization conditions. ACS Appl Mater Interfaces (2010) 0.86

Digital health tools for diabetes. J Ambul Care Manage (2015) 0.86

Defibrillator for primary prevention in congenital heart disease. Pacing Clin Electrophysiol (2004) 0.85

Highly sensitive noninvasive cardiac transplant rejection monitoring using targeted quantification of donor-specific cell-free deoxyribonucleic acid. J Am Coll Cardiol (2013) 0.85

Proximal sano anastomosis aneurysm due to degeneration of bovine pericardial patch. Ann Thorac Surg (2012) 0.84

Genetic analyses in two extended families with deletion 22q11 syndrome: importance of extracardiac manifestations. J Pediatr (2005) 0.84

Utility of tonsillectomy in 2 patients with the syndrome of periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis. Arch Otolaryngol Head Neck Surg (2003) 0.84

Genetic characterization of familial CPVT after 30 years. Biol Res Nurs (2009) 0.83

Bilateral semilunar valve disease in a child with partial deletion of the Williams-Beuren syndrome region is associated with elastin haploinsufficiency. J Heart Valve Dis (2006) 0.83

Aorta Measurements are Heritable and Influenced by Bicuspid Aortic Valve. Front Genet (2011) 0.83

The presence of bicuspid aortic valve does not predict ventricular septal defect type. Am J Med Genet A (2008) 0.83

Spontaneous rupture of atrioventricular valve tensor apparatus as late manifestation of anti-Ro/SSA antibody-mediated cardiac disease. Am J Cardiol (2011) 0.82

Chronic fatigue syndrome and eating disorders: concurrence or coincidence? Int J Adolesc Med Health (2003) 0.81

Single versus weekly courses of antenatal corticosteroids in preterm premature rupture of membranes. Obstet Gynecol (2004) 0.81

Electrocardiographic abnormalities in very young Duchenne muscular dystrophy patients precede the onset of cardiac dysfunction. Neuromuscul Disord (2011) 0.81

Magnetic resonance imaging assessment of cardiac dysfunction in δ-sarcoglycan null mice. Neuromuscul Disord (2010) 0.80

Evaluation of the fetal QT interval using non-invasive fetal ECG technology. Physiol Meas (2016) 0.80

Surveillance and management practices in tracheotomy patients. Laryngoscope (2012) 0.79

Factors associated with success of emergent second-trimester cerclage. Obstet Gynecol (2003) 0.79

In vivo CH3(CH2)11SAu SAM electrodes in the beating heart: in situ analytical studies relevant to pacemakers and interstitial biosensors. Biosens Bioelectron (2003) 0.79

Pediatric adenoidectomy: what is the effect of obstructive symptoms on the likelihood of future surgery? Int J Pediatr Otorhinolaryngol (2006) 0.79

Left ventricular noncompaction in Duchenne muscular dystrophy. J Cardiovasc Magn Reson (2013) 0.79

Looking down the atrioventricular canal. Cardiovasc Res (2010) 0.78

Neonatal long QT syndrome due to a de novo dominant negative hERG mutation. Am J Crit Care (2007) 0.78

Compound heterozygous SCN5A mutations: does the sum of the parts equal the whole? Heart Rhythm (2009) 0.78

ACCF/AHA/AAP recommendations for training in pediatric cardiology. A report of the American College of Cardiology Foundation/American Heart Association/American College of Physicians Task Force on Clinical Competence (ACC/AHA/AAP Writing Committee to Develop Training Recommendations for Pediatric Cardiology). Circulation (2005) 0.78

Determination of standard electrode potential E(o) for chronic platinum and gold electrodes in rat muscle: implications for biosensors and the "anode" of bipolar pacing. Pacing Clin Electrophysiol (2002) 0.77

Thar's tendons in them thar valves! Circ Res (2008) 0.77

TBX5: a developmental key that fits many locks. J Mol Cell Cardiol (2003) 0.77

Complex story of the genetic origins of pediatric heart disease. Circulation (2010) 0.77