Masakatsu Motomura

Author PubWeight™ 36.96‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Autoimmune targets of heart and skeletal muscles in myasthenia gravis. Arch Neurol 2009 2.42
2 Reduction of P/Q-type calcium channels in the postmortem cerebellum of paraneoplastic cerebellar degeneration with Lambert-Eaton myasthenic syndrome. Ann Neurol 2003 2.28
3 The muscle protein Dok-7 is essential for neuromuscular synaptogenesis. Science 2006 2.26
4 Dok-7 mutations underlie a neuromuscular junction synaptopathy. Science 2006 1.88
5 Total tau protein in cerebrospinal fluid and diffusion-weighted MRI as an early diagnostic marker for Creutzfeldt-Jakob disease. Dement Geriatr Cogn Disord 2007 1.72
6 Autoantibodies to low-density lipoprotein receptor-related protein 4 in myasthenia gravis. Ann Neurol 2011 1.69
7 Correlation of bite force with excitation-contraction coupling time of the masseter in myasthenia gravis. Clin Neurophysiol 2010 1.43
8 Myasthenia gravis with anti-MuSK antibody, showing progressive muscular atrophy without blepharoptosis. Intern Med 2005 1.42
9 Contribution of anti-ryanodine receptor antibody to impairment of excitation-contraction coupling in myasthenia gravis. Clin Neurophysiol 2011 1.40
10 Effects of reduced joint mobility on sarcomere length, collagen fibril arrangement in the endomysium, and hyaluronan in rat soleus muscle. J Muscle Res Cell Motil 2004 1.20
11 Characteristics of myasthenia gravis according to onset-age: Japanese nationwide survey. J Neurol Sci 2011 1.15
12 Acetylcholine receptors loss and postsynaptic damage in MuSK antibody-positive myasthenia gravis. Ann Neurol 2005 1.14
13 Early detection of sporadic CJD by diffusion-weighted MRI before the onset of symptoms. J Neurol Neurosurg Psychiatry 2010 0.94
14 [Leptomeningeal infiltlation of primary CNS B-cell lymphoma diagnosed by the biopsy of cauda equina: a case report]. Rinsho Shinkeigaku 2013 0.83
15 [A recalcitrant case of encephalitis with voltage-gated potassium channel antibodies]. Brain Nerve 2010 0.83
16 Anti-Hu paraneoplastic syndrome presenting with brainstem-cerebellar symptoms and Lambert-Eaton myasthenic syndrome. Neuropathology 2003 0.81
17 [A case of thymoma-associated myasthenia gravis with anti-MuSK antibodies]. Rinsho Shinkeigaku 2013 0.81
18 Antibodies against Wnt receptor of muscle-specific tyrosine kinase in myasthenia gravis. J Neuroimmunol 2012 0.80
19 Quality of life in purely ocular myasthenia in Japan. BMC Neurol 2014 0.80
20 Early effect of tacrolimus in improving excitation-contraction coupling in myasthenia gravis. Clin Neurophysiol 2012 0.79
21 Antibodies against the main immunogenic region of the acetylcholine receptor correlate with disease severity in myasthenia gravis. J Neurol Neurosurg Psychiatry 2012 0.79
22 Effect of myasthenic immunoglobulin G on motor end-plate morphology. J Neurol 2003 0.78
23 Anti-ryanodine receptor-positive acetylcholine receptor-negative myasthenia gravis: evidence of impaired excitation-contraction coupling. Muscle Nerve 2011 0.78
24 Anti-citrullinated protein antibody-positive rheumatoid arthritis associated with RS3PE syndrome-like symptoms and an elevated serum vascular endothelial growth factor level in a patient with myasthenia gravis. Intern Med 2014 0.78
25 [A pregnant patient with anti-MuSK antibody positive myasthenia gravis and her infant with transient neonatal myasthenia gravis]. Rinsho Shinkeigaku 2011 0.77
26 Is excitation-contraction coupling impaired in myasthenia gravis? Clin Neurophysiol 2007 0.77
27 Thymic myoid cells as a myasthenogenic antigen and antigen-presenting cells. J Neuroimmunol 2004 0.77
28 Laminin-induced autoimmune myositis in rats. J Neuropathol Exp Neurol 2005 0.77
29 Anti-MuSK Antibody-positive Myasthenia Gravis Mimicking Amyotrophic Lateral Sclerosis. Intern Med 2015 0.76
30 Thymoma with Lambert-Eaton myasthenic syndrome. Ann Thorac Surg 2010 0.76
31 A case of acute sarcoid myositis treated with weekly low-dose methotrexate. Muscle Nerve 2011 0.76
32 [Successful treatment in a patient with a focal form of stiff-person syndrome using plasma exchange and intravenous immunoglobulin therapy]. Rinsho Shinkeigaku 2002 0.76
33 A case of Japanese spotted fever complicated with central nervous system involvement and multiple organ failure. Intern Med 2012 0.76
34 Thyrotoxic myopathy mimicking myasthenic syndrome associated with thymic hyperplasia. Intern Med 2008 0.76
35 Isoniazid-triggered pure red cell aplasia in systemic lupus erythematosus complicated with myasthenia gravis. Rheumatol Int 2009 0.76
36 Macrophagic myofascitis associated with rheumatoid arthritis. Rheumatol Int 2009 0.75
37 Chronological changes in MRI and CSF biochemical markers in Creutzfeldt-Jakob disease patients. Dement Geriatr Cogn Disord 2007 0.75
38 [Autoantibodies detected in acetylcholine receptor antibody-negative myasthenia gravis]. Rinsho Byori 2014 0.75
39 [Japan MG Registry Study: A Sophisti- cated Multi-center Study of Myasthe- nia Gravis A sophisticated multi-center Study of Myasthenia Gravis]. Fukuoka Igaku Zasshi 2015 0.75
40 [A case of Mycobacterium fortuitum meningitis following surgery for meningioma]. Rinsho Shinkeigaku 2006 0.75
41 A case of primary Sjögren's syndrome complicated with inflammatory myopathy and interstitial lung disease. Rheumatol Int 2010 0.75
42 [A case of CIDP with horizontal gaze-evoked nystagmus and ataxia]. Rinsho Shinkeigaku 2002 0.75
43 [A case of myasthenia gravis with anti-MuSK antibodies showing a dramatic improvement with plasma exchange]. Rinsho Shinkeigaku 2005 0.75
44 Transient subacute cerebellar ataxia in a patient with Lambert-Eaton myasthenic syndrome after intracranial aneurysm surgery. Clin Neurol Neurosurg 2008 0.75
45 A case of recurrent optic neuritis associated with cerebral and spinal cord lesions and autoantibodies against myelin oligodendrocyte glycoprotein relapsed after fingolimod therapy. Rinsho Shinkeigaku 2016 0.75
46 [A case of meningeal disseminated sarcoidosis with marked hypoglycorrhachia in the CSF]. Rinsho Shinkeigaku 2013 0.75
47 [Successful treatment of a Lambert-Eaton myasthenic syndrome patient with 3,4-diaminopyridine]. Nihon Naika Gakkai Zasshi 2007 0.75
48 False-positive accumulation of metaiodobenzylguanidine in a case with acute intermittent porphyria. Intern Med 2011 0.75
49 Childhood-onset anti-MuSK antibody positive myasthenia gravis demonstrates a distinct clinical course. Brain Dev 2012 0.75
50 [Paraneoplastic neurological syndromes of neuromuscular junctions]. Nihon Naika Gakkai Zasshi 2008 0.75
51 [Novel autoantibodies in myasthenia gravis]. Nihon Rinsho 2013 0.75
52 Clinical, serologic and magnetic resonance imaging of 3 cases of inflammatory myopathy with abundant macrophages in the Japanese population. Rheumatol Int 2010 0.75
53 [Churg-Strauss syndrome with neurogenic bladder and good recovery after steroid therapy]. Nihon Naika Gakkai Zasshi 2003 0.75
54 IgG4-related disease with cavernous sinus and intra-orbital lesions diagnosed by nasal mucosa biopsy. Rinsho Shinkeigaku 2016 0.75
55 [Lambert-Eaton myasthenic syndrome (LEMS)]. Nihon Rinsho 2015 0.75
56 Myasthenia gravis with diffuse alopecia areata and pemphigus foliaceus. J Neurol 2002 0.75
57 Muscle-specific tyrosine kinase-antibody-positive myasthenic crisis with detailed electrophysiologic studies. Am J Emerg Med 2009 0.75
58 Two cases of refractory polymyositis accompanied with steroid myopathy. Mod Rheumatol 2014 0.75
59 [Adverse effects of therapeutic drugs on neuromuscular junctions]. Nihon Naika Gakkai Zasshi 2007 0.75
60 [The role of autoantibodies in myasthenia gravis]. Nihon Rinsho 2015 0.75
61 Successful treatment of HTLV-1-related overlap syndrome using tacrolimus. Intern Med 2011 0.75
62 Efficacy of tacrolimus in Sjögren's syndrome-associated CNS disease with aquaporin-4 autoantibodies. J Neurol 2009 0.75
63 [Histochemical findings of and fine structural changes in motor endplates in diseases with neuromuscular transmission abnormalities]. Brain Nerve 2011 0.75
64 [Anti-MuSK antibody-positive myasthenia gravis with nephrotic syndrome: a case report]. Rinsho Shinkeigaku 2009 0.75