PubRank

Véronique Frémeaux-Bacchi

Author PubWeight™ 80.39‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Complement-binding anti-HLA antibodies and kidney-allograft survival. N Engl J Med 2013 6.31
2 Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies. Kidney Int 2012 3.99
3 Identification of a mutation in complement factor H-related protein 5 in patients of Cypriot origin with glomerulonephritis. Lancet 2010 3.74
4 Atypical hemolytic uremic syndrome. Orphanet J Rare Dis 2011 3.35
5 Primary glomerulonephritis with isolated C3 deposits: a new entity which shares common genetic risk factors with haemolytic uraemic syndrome. J Med Genet 2006 3.24
6 C3 glomerulopathy: a new classification. Nat Rev Nephrol 2010 3.17
7 Anti-Factor H autoantibodies associated with atypical hemolytic uremic syndrome. J Am Soc Nephrol 2004 2.97
8 Recessive mutations in DGKE cause atypical hemolytic-uremic syndrome. Nat Genet 2013 2.91
9 C3 glomerulopathy: consensus report. Kidney Int 2013 2.85
10 Use of eculizumab for atypical haemolytic uraemic syndrome and C3 glomerulopathies. Nat Rev Nephrol 2012 2.62
11 Heterozygous and homozygous factor h deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: report and genetic analysis of 16 cases. J Am Soc Nephrol 2004 2.46
12 The clinical spectrum and therapeutic management of hypocomplementemic urticarial vasculitis: data from a French nationwide study of fifty-seven patients. Arthritis Rheumatol 2015 1.98
13 The interactive Factor H-atypical hemolytic uremic syndrome mutation database and website: update and integration of membrane cofactor protein and Factor I mutations with structural models. Hum Mutat 2007 1.59
14 Clinical features of anti-factor H autoantibody-associated hemolytic uremic syndrome. J Am Soc Nephrol 2010 1.53
15 A clinicopathologic study of thrombotic microangiopathy in IgA nephropathy. J Am Soc Nephrol 2011 1.51
16 New insights into postrenal transplant hemolytic uremic syndrome. Nat Rev Nephrol 2010 1.36
17 Glomerulonephritis with isolated C3 deposits and monoclonal gammopathy: a fortuitous association? Clin J Am Soc Nephrol 2011 1.31
18 Complement alternative pathway acts as a positive feedback amplification of neutrophil activation. Blood 2010 1.31
19 Severe ADAMTS13 deficiency in adult idiopathic thrombotic microangiopathies defines a subset of patients characterized by various autoimmune manifestations, lower platelet count, and mild renal involvement. Medicine (Baltimore) 2004 1.21
20 Efficacy of eculizumab in a patient with factor-H-associated atypical hemolytic uremic syndrome. Pediatr Nephrol 2010 1.20
21 High prevalence of anti-C1q antibodies in biopsy-proven active lupus nephritis. Nephrol Dial Transplant 2006 1.17
22 Factor H, membrane cofactor protein, and factor I mutations in patients with hemolysis, elevated liver enzymes, and low platelet count syndrome. Blood 2008 1.06
23 Atypical haemolytic uraemic syndrome and mutations in complement regulator genes. Springer Semin Immunopathol 2005 1.05
24 A novel non-synonymous polymorphism (p.Arg240His) in C4b-binding protein is associated with atypical hemolytic uremic syndrome and leads to impaired alternative pathway cofactor activity. J Immunol 2008 1.03
25 Heterogeneous pattern of renal disease associated with homozygous factor H deficiency. Hum Pathol 2011 1.00
26 Systemic and kidney toxicity of intraocular administration of vascular endothelial growth factor inhibitors. Am J Kidney Dis 2011 1.00
27 Complement factor H deficiency and posttransplantation glomerulonephritis with isolated C3 deposits. Am J Kidney Dis 2008 0.99
28 Late-onset thrombocytic microangiopathy caused by cblC disease: association with a factor H mutation. Am J Kidney Dis 2005 0.99
29 C3 glomerulopathy. Contrib Nephrol 2013 0.98
30 Pulse cyclophosphamide therapy and clinical remission in atypical hemolytic uremic syndrome with anti-complement factor H autoantibodies. Am J Kidney Dis 2010 0.97
31 Obstetric nephrology: AKI and thrombotic microangiopathies in pregnancy. Clin J Am Soc Nephrol 2012 0.93
32 The interaction between factor H and VWF increases factor H cofactor activity and regulates VWF prothrombotic status. Blood 2013 0.93
33 Haemolytic uraemic syndrome caused by factor H mutation: is single kidney transplantation under intensive plasmatherapy an option? Nephrol Dial Transplant 2009 0.92
34 Atypical hemolytic uremic syndrome: from the rediscovery of complement to targeted therapy. Eur J Intern Med 2013 0.92
35 C3 nephritic factor associated with C3 glomerulopathy in children. Pediatr Nephrol 2013 0.91
36 Ocular involvement in hemolytic uremic syndrome due to factor H deficiency--are there therapeutic consequences? Pediatr Nephrol 2007 0.91
37 Overall neutralization of complement factor H by autoantibodies in the acute phase of the autoimmune form of atypical hemolytic uremic syndrome. J Immunol 2012 0.90
38 Long-term remission of atypical HUS with anti-factor H antibodies after cyclophosphamide pulses. Pediatr Nephrol 2013 0.90
39 Atypical hemolytic uremic syndrome associated with mutations in complement regulator genes. Semin Thromb Hemost 2010 0.88
40 Targeted strategies in the prevention and management of atypical HUS recurrence after kidney transplantation. Transplant Rev (Orlando) 2013 0.87
41 Neurological involvement in a child with atypical hemolytic uremic syndrome. Pediatr Nephrol 2010 0.86
42 Does hemolytic uremic syndrome differ from thrombotic thrombocytopenic purpura? Nat Clin Pract Nephrol 2007 0.86
43 Secondary failure of plasma therapy in factor H deficiency. Pediatr Nephrol 2006 0.85
44 No lupus nephritis in the absence of antiC1q autoantibodies? Nephrol Dial Transplant 2002 0.84
45 Functional evaluation of factor H genetic and acquired abnormalities: application for atypical hemolytic uremic syndrome (aHUS). Methods Mol Biol 2014 0.82
46 Heme interacts with c1q and inhibits the classical complement pathway. J Biol Chem 2011 0.82
47 A case of C3 glomerulonephritis successfully treated with eculizumab. Pediatr Nephrol 2015 0.82
48 Functional analysis of splicing mutations and of an exon 2 polymorphic variant of SERPING1/C1NH. Hum Mutat 2006 0.81
49 Lupus nephritis associated with complete C1s deficiency efficiently treated with rituximab: a case report. Arthritis Care Res (Hoboken) 2010 0.81
50 Functional characterization of the recombinant human C1 inhibitor serpin domain: insights into heparin binding. J Immunol 2010 0.80
51 Efficacy of plasma therapy in atypical hemolytic uremic syndrome with complement factor H mutations. Pediatr Nephrol 2008 0.80
52 Obstetrical Complications and Outcome in Two Families with Hereditary Angioedema due to Mutation in the F12 Gene. Obstet Gynecol Int 2010 0.79
53 Physiological and therapeutic complement regulators in kidney transplantation. Curr Opin Organ Transplant 2013 0.78
54 Anti-factor H autoantibodies assay. Methods Mol Biol 2014 0.77
55 Recurrent Hemolytic and Uremic Syndrome Induced by Escherichia Coli. Medicine (Baltimore) 2016 0.75
56 A nationwide study of acquired C1-inhibitor deficiency in France: Characteristics and treatment responses in 92 patients. Medicine (Baltimore) 2016 0.75
57 Thrombotic microangiopathy: eculizumab for atypical haemolytic uraemic syndrome: what next? Nat Rev Nephrol 2013 0.75
58 Erratum: Post-partum atypical haemolytic-uraemic syndrome treated with eculizumab: terminal complement activity assessment in clinical practice. Clin Kidney J 2013 0.75
59 [Hereditary hemolytic uremic syndromes and thrombotic thrombocytopenic purpura]. Nephrol Ther 2006 0.75
60 C3 nephritic factor can be associated with membranous glomerulonephritis. Pediatr Nephrol 2014 0.75
61 [Combined-heterozygous deficiency of complement C7 in a patient with recurrent meningitis]. Med Klin (Munich) 2006 0.75