PubRank

Luc Dupuis

Author PubWeight™ 37.70‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Muscle Nogo-A expression is a prognostic marker in lower motor neuron syndromes. Ann Neurol 2007 2.37
2 Nogo-A, -B, and -C are found on the cell surface and interact together in many different cell types. J Biol Chem 2005 1.61
3 Sodium valproate exerts neuroprotective effects in vivo through CREB-binding protein-dependent mechanisms but does not improve survival in an amyotrophic lateral sclerosis mouse model. J Neurosci 2007 1.52
4 Gene profiling of skeletal muscle in an amyotrophic lateral sclerosis mouse model. Physiol Genomics 2007 1.31
5 Cytoplasmic dynein in neurodegeneration. Pharmacol Ther 2011 1.25
6 Impaired glucose tolerance in patients with amyotrophic lateral sclerosis. Amyotroph Lateral Scler 2010 1.20
7 Mechanisms, models and biomarkers in amyotrophic lateral sclerosis. Amyotroph Lateral Scler Frontotemporal Degener 2013 1.16
8 Nogo expression in muscle correlates with amyotrophic lateral sclerosis severity. Ann Neurol 2005 1.11
9 Increased peripheral lipid clearance in an animal model of amyotrophic lateral sclerosis. J Lipid Res 2007 1.09
10 The neurite outgrowth inhibitor Nogo-A promotes denervation in an amyotrophic lateral sclerosis model. EMBO Rep 2006 1.09
11 A point mutation in the dynein heavy chain gene leads to striatal atrophy and compromises neurite outgrowth of striatal neurons. Hum Mol Genet 2010 1.09
12 CNS-targeted viral delivery of G-CSF in an animal model for ALS: improved efficacy and preservation of the neuromuscular unit. Mol Ther 2010 1.08
13 Amyotrophic lateral sclerosis: all roads lead to Rome. J Neurochem 2007 0.99
14 Dynein mutations associated with hereditary motor neuropathies impair mitochondrial morphology and function with age. Neurobiol Dis 2013 0.96
15 PGC-1α is a male-specific disease modifier of human and experimental amyotrophic lateral sclerosis. Hum Mol Genet 2013 0.96
16 BBS-induced ciliary defect enhances adipogenesis, causing paradoxical higher-insulin sensitivity, glucose usage, and decreased inflammatory response. Cell Metab 2012 0.93
17 Oxidative stress in skeletal muscle stimulates early expression of Rad in a mouse model of amyotrophic lateral sclerosis. Free Radic Biol Med 2010 0.93
18 Investigating the contribution of VAPB/ALS8 loss of function in amyotrophic lateral sclerosis. Hum Mol Genet 2013 0.89
19 P-glycoprotein expression and function are increased in an animal model of amyotrophic lateral sclerosis. Neurosci Lett 2010 0.88
20 Muscle gene expression is a marker of amyotrophic lateral sclerosis severity. Neurodegener Dis 2011 0.88
21 The metabolic hypothesis in amyotrophic lateral sclerosis: insights from mutant Cu/Zn-superoxide dismutase mice. Biomed Pharmacother 2005 0.87
22 Tissue specificity and regulation of the N-terminal diversity of reticulon 3. Biochem J 2005 0.86
23 Mutations in cytoplasmic dynein lead to a Huntington's disease-like defect in energy metabolism of brown and white adipose tissues. Biochim Biophys Acta 2010 0.85
24 G-CSF protects motoneurons against axotomy-induced apoptotic death in neonatal mice. BMC Neurosci 2010 0.85
25 Degeneration of serotonergic neurons in amyotrophic lateral sclerosis: a link to spasticity. Brain 2012 0.82
26 Fumaric acid esters stimulate astrocytic VEGF expression through HIF-1α and Nrf2. PLoS One 2013 0.82
27 Mitochondrial dysfunction in amyotrophic lateral sclerosis also affects skeletal muscle. Muscle Nerve 2006 0.81
28 VAPB/ALS8 MSP ligands regulate striated muscle energy metabolism critical for adult survival in caenorhabditis elegans. PLoS Genet 2013 0.81
29 Percutaneous endoscopic gastrostomy in amyotrophic lateral sclerosis: a prospective observational study. J Neurol 2015 0.81
30 Adipose Tissue Distribution Predicts Survival in Amyotrophic Lateral Sclerosis. PLoS One 2013 0.80
31 Reticulons as markers of neurological diseases: focus on amyotrophic lateral sclerosis. Neurodegener Dis 2005 0.80
32 Antibody-bound beta-amyloid precursor protein stimulates the production of tumor necrosis factor-alpha and monocyte chemoattractant protein-1 by cortical neurons. Neurobiol Dis 2005 0.79
33 Systemic down-regulation of delta-9 desaturase promotes muscle oxidative metabolism and accelerates muscle function recovery following nerve injury. PLoS One 2013 0.79
34 Early activation of antioxidant mechanisms in muscle of mutant Cu/Zn-superoxide dismutase-linked amyotrophic lateral sclerosis mice. Ann N Y Acad Sci 2003 0.78
35 A mutation in the dynein heavy chain gene compensates for energy deficit of mutant SOD1 mice and increases potentially neuroprotective IGF-1. Mol Neurodegener 2011 0.78
36 Neuroendocrinology of neurodegenerative diseases. Insights from transgenic mouse models. Neuroendocrinology 2003 0.78
37 Progranulin bridges energy homeostasis and fronto-temporal dementia. Cell Metab 2012 0.76
38 Full-length PGC-1α salvages the phenotype of a mouse model of human neuropathy through mitochondrial proliferation. Hum Mol Genet 2013 0.75
39 [Cellular prion protein: more than what beyond spongiform encephalopathies]. Med Sci (Paris) 2003 0.75
40 [Nutritional management in amyotrophic lateral sclerosis: A medical and ethical stake]. Presse Med 2011 0.75