PubRank

Frédérique René

Author PubWeight™ 13.60‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Evidence for defective energy homeostasis in amyotrophic lateral sclerosis: benefit of a high-energy diet in a transgenic mouse model. Proc Natl Acad Sci U S A 2004 2.26
2 Sodium valproate exerts neuroprotective effects in vivo through CREB-binding protein-dependent mechanisms but does not improve survival in an amyotrophic lateral sclerosis mouse model. J Neurosci 2007 1.52
3 Increased peripheral lipid clearance in an animal model of amyotrophic lateral sclerosis. J Lipid Res 2007 1.09
4 A point mutation in the dynein heavy chain gene leads to striatal atrophy and compromises neurite outgrowth of striatal neurons. Hum Mol Genet 2010 1.09
5 Amyotrophic lateral sclerosis: all roads lead to Rome. J Neurochem 2007 0.99
6 Dynein mutations associated with hereditary motor neuropathies impair mitochondrial morphology and function with age. Neurobiol Dis 2013 0.96
7 Investigating the contribution of VAPB/ALS8 loss of function in amyotrophic lateral sclerosis. Hum Mol Genet 2013 0.89
8 Evidence of a dosage effect and a physiological endplate acetylcholinesterase deficiency in the first mouse models mimicking Schwartz-Jampel syndrome neuromyotonia. Hum Mol Genet 2008 0.89
9 Degeneration of serotonergic neurons in amyotrophic lateral sclerosis: a link to spasticity. Brain 2012 0.82
10 A mouse model of Schwartz-Jampel syndrome reveals myelinating Schwann cell dysfunction with persistent axonal depolarization in vitro and distal peripheral nerve hyperexcitability when perlecan is lacking. Am J Pathol 2012 0.82
11 The Onecut transcription factor HNF-6 regulates in motor neurons the formation of the neuromuscular junctions. PLoS One 2012 0.80
12 Neuroendocrinology of neurodegenerative diseases. Insights from transgenic mouse models. Neuroendocrinology 2003 0.78
13 Evaluating Behavior in Mouse Models of the Behavioral Variant of Frontotemporal Dementia: Which Test for Which Symptom? Neurodegener Dis 2015 0.77