| Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
|
1
|
Prevalence of the metabolic syndrome in American adolescents: findings from the Third National Health and Nutrition Examination Survey.
|
Circulation
|
2004
|
4.58
|
|
2
|
Effectiveness and safety of ICL670 in iron-loaded patients with thalassaemia: a randomised, double-blind, placebo-controlled, dose-escalation trial.
|
Lancet
|
2003
|
3.07
|
|
3
|
Complications of beta-thalassemia major in North America.
|
Blood
|
2004
|
2.97
|
|
4
|
Severe hemorrhage in children with newly diagnosed immune thrombocytopenic purpura.
|
Blood
|
2008
|
2.17
|
|
5
|
Relative response of patients with myelodysplastic syndromes and other transfusion-dependent anaemias to deferasirox (ICL670): a 1-yr prospective study.
|
Eur J Haematol
|
2007
|
2.14
|
|
6
|
Clinical effects and safety of rituximab for treatment of refractory pediatric autoimmune diseases.
|
J Pediatr
|
2007
|
1.75
|
|
7
|
Risk factors and mortality associated with an elevated tricuspid regurgitant jet velocity measured by Doppler-echocardiography in thalassemia: a Thalassemia Clinical Research Network report.
|
Blood
|
2011
|
1.61
|
|
8
|
Hemoglobin Jamaica plain--a sickling hemoglobin with reduced oxygen affinity.
|
N Engl J Med
|
2004
|
1.59
|
|
9
|
Urinary hepcidin in congenital chronic anemias.
|
Pediatr Blood Cancer
|
2007
|
1.58
|
|
10
|
Hemolytic anemia and severe rhabdomyolysis caused by compound heterozygous mutations of the gene for erythrocyte/muscle isozyme of aldolase, ALDOA(Arg303X/Cys338Tyr).
|
Blood
|
2003
|
1.57
|
|
11
|
Response to mercaptopurine for refractory autoimmune cytopenias in children.
|
Pediatr Blood Cancer
|
2009
|
1.49
|
|
12
|
Bleeding risks are higher in children versus adults given prophylactic platelet transfusions for treatment-induced hypoproliferative thrombocytopenia.
|
Blood
|
2012
|
1.48
|
|
13
|
Systematic molecular genetic analysis of congenital sideroblastic anemia: evidence for genetic heterogeneity and identification of novel mutations.
|
Pediatr Blood Cancer
|
2010
|
1.43
|
|
14
|
Transfusion complications in thalassemia patients: a report from the Centers for Disease Control and Prevention (CME).
|
Transfusion
|
2013
|
1.43
|
|
15
|
Evaluation of the coagulation system in children with two-ventricle congenital heart disease.
|
Ann Thorac Surg
|
2007
|
1.39
|
|
16
|
X-linked gray platelet syndrome due to a GATA1 Arg216Gln mutation.
|
Blood
|
2007
|
1.38
|
|
17
|
Prospective phase 1/2 study of rituximab in childhood and adolescent chronic immune thrombocytopenic purpura.
|
Blood
|
2005
|
1.37
|
|
18
|
Genetic ablation of the CDP/Cux protein C terminus results in hair cycle defects and reduced male fertility.
|
Mol Cell Biol
|
2002
|
1.28
|
|
19
|
Defective RNA ribose synthesis in fibroblasts from patients with thiamine-responsive megaloblastic anemia (TRMA).
|
Blood
|
2003
|
1.26
|
|
20
|
Safety and efficacy of pegylated interferon alpha-2a and ribavirin for the treatment of hepatitis C in patients with thalassemia.
|
Haematologica
|
2008
|
1.26
|
|
21
|
Reversible severe combined immunodeficiency phenotype secondary to a mutation of the proton-coupled folate transporter.
|
Clin Immunol
|
2009
|
1.26
|
|
22
|
The frequency and management of asparaginase-related thrombosis in paediatric and adult patients with acute lymphoblastic leukaemia treated on Dana-Farber Cancer Institute consortium protocols.
|
Br J Haematol
|
2011
|
1.24
|
|
23
|
Validity, reliability, and responsiveness of a new measure of health-related quality of life in children with immune thrombocytopenic purpura: the Kids' ITP Tools.
|
J Pediatr
|
2007
|
1.18
|
|
24
|
Inflammation and oxidant-stress in beta-thalassemia patients treated with iron chelators deferasirox (ICL670) or deferoxamine: an ancillary study of the Novartis CICL670A0107 trial.
|
Haematologica
|
2008
|
1.18
|
|
25
|
The incidence and implications of anti-heparin-platelet factor 4 antibody formation in a pediatric cardiac surgical population.
|
Anesth Analg
|
2008
|
1.15
|
|
26
|
Iron overload in patients with acute leukemia or MDS undergoing myeloablative stem cell transplantation.
|
Biol Blood Marrow Transplant
|
2010
|
1.13
|
|
27
|
Induced pluripotent stem cells with a mitochondrial DNA deletion.
|
Stem Cells
|
2013
|
1.13
|
|
28
|
Red cell alloimmunization in a diverse population of transfused patients with thalassaemia.
|
Br J Haematol
|
2011
|
1.10
|
|
29
|
Pain as an emergent issue in thalassemia.
|
Am J Hematol
|
2010
|
1.10
|
|
30
|
Deferasirox pharmacokinetics in patients with adequate versus inadequate response.
|
Blood
|
2009
|
1.04
|
|
31
|
Thirty-day readmission rates following hospitalization for pediatric sickle cell crisis at freestanding children's hospitals: risk factors and hospital variation.
|
Pediatr Blood Cancer
|
2011
|
1.03
|
|
32
|
Thiamine-responsive megaloblastic anemia: identification of novel compound heterozygotes and mutation update.
|
J Pediatr
|
2009
|
1.01
|
|
33
|
A phase 1 dose-escalation study: safety, tolerability, and pharmacokinetics of FBS0701, a novel oral iron chelator for the treatment of transfusional iron overload.
|
Haematologica
|
2010
|
1.01
|
|
34
|
Corticosteroids for acute chest syndrome in children with sickle cell disease: variation in use and association with length of stay and readmission.
|
Am J Hematol
|
2010
|
1.00
|
|
35
|
Sildenafil therapy in thalassemia patients with Doppler-defined risk of pulmonary hypertension.
|
Haematologica
|
2013
|
0.99
|
|
36
|
Does iron overload really matter in stem cell transplantation?
|
Am J Hematol
|
2012
|
0.99
|
|
37
|
Symptoms of depression and anxiety in patients with thalassemia: prevalence and correlates in the thalassemia longitudinal cohort.
|
Am J Hematol
|
2010
|
0.98
|
|
38
|
Chelation use and iron burden in North American and British thalassemia patients: a report from the Thalassemia Longitudinal Cohort.
|
Blood
|
2012
|
0.98
|
|
39
|
Coagulation abnormalities in patients with single-ventricle physiology precede the Fontan procedure.
|
J Thorac Cardiovasc Surg
|
2002
|
0.97
|
|
40
|
Male infertility and thiamine-dependent erythroid hypoplasia in mice lacking thiamine transporter Slc19a2.
|
Mol Genet Metab
|
2003
|
0.97
|
|
41
|
Successful use of bivalirudin for cardiac transplantation in a child with heparin-induced thrombocytopenia.
|
J Heart Lung Transplant
|
2006
|
0.94
|
|
42
|
Hormonal contraception and thrombotic risk: a multidisciplinary approach.
|
Pediatrics
|
2011
|
0.94
|
|
43
|
Myocardial immediate early gene activation after cardiopulmonary bypass with cardiac ischemia-reperfusion.
|
Ann Thorac Surg
|
2002
|
0.93
|
|
44
|
Prospective longitudinal study of coagulation profiles in children with hypoplastic left heart syndrome from stage I through Fontan completion.
|
J Thorac Cardiovasc Surg
|
2009
|
0.93
|
|
45
|
Iron chelation adherence to deferoxamine and deferasirox in thalassemia.
|
Am J Hematol
|
2011
|
0.93
|
|
46
|
Applicability of 2009 international consensus terminology and criteria for immune thrombocytopenia to a clinical pediatric population.
|
Pediatr Blood Cancer
|
2011
|
0.93
|
|
47
|
Practical implications of liver and heart iron load assessment by T2*-MRI in children and adults with transfusion-dependent anemias.
|
Am J Hematol
|
2008
|
0.89
|
|
48
|
Transition from pediatric to adult care for sickle cell disease: results of a survey of pediatric providers.
|
Am J Hematol
|
2011
|
0.88
|
|
49
|
Observational cohort study of pediatric inpatients with central venous catheters at "intermediate risk" of thrombosis and eligible for anticoagulant prophylaxis.
|
J Pediatr Oncol Nurs
|
2010
|
0.88
|
|
50
|
Primary care clinicians' knowledge and confidence about newborn screening for sickle cell disease: randomized assessment of educational strategies.
|
J Natl Med Assoc
|
2010
|
0.85
|
|
51
|
One year follow-up of children and adolescents with chronic immune thrombocytopenic purpura (ITP) treated with rituximab.
|
Pediatr Blood Cancer
|
2009
|
0.84
|
|
52
|
Treatment with rituximab in benign and malignant hematologic disorders in children.
|
J Pediatr
|
2007
|
0.84
|
|
53
|
Genetic studies in pediatric ITP: outlook, feasibility, and requirements.
|
Ann Hematol
|
2010
|
0.83
|
|
54
|
MRI guided iron assessment and oral chelator use improve iron status in thalassemia major patients.
|
Am J Hematol
|
2014
|
0.83
|
|
55
|
Renal dysfunction in patients with thalassaemia.
|
Br J Haematol
|
2011
|
0.82
|
|
56
|
Screening and counseling for thalassemia.
|
Blood
|
2006
|
0.80
|
|
57
|
Chronic disseminated intravascular coagulation and childhood-onset skin necrosis resulting from homozygosity for a protein C Gla domain mutation, Arg15Trp.
|
J Pediatr Hematol Oncol
|
2002
|
0.80
|
|
58
|
Inadequate dietary intake in patients with thalassemia.
|
J Acad Nutr Diet
|
2012
|
0.79
|
|
59
|
Trends in anti-D immune globulin for childhood immune thrombocytopenia: usage, response rates, and adverse effects.
|
Am J Hematol
|
2011
|
0.79
|
|
60
|
Relationship among chelator adherence, change in chelators, and quality of life in thalassemia.
|
Qual Life Res
|
2014
|
0.79
|
|
61
|
Prospective reevaluation of the association between thrombotic diathesis and legg-perthes disease.
|
J Bone Joint Surg Am
|
2002
|
0.79
|
|
62
|
Targeted ITP strategies: do they elucidate the biology of ITP and related disorders?
|
Pediatr Blood Cancer
|
2006
|
0.78
|
|
63
|
Preface to Cooley's Anemia: Ninth Symposium.
|
Ann N Y Acad Sci
|
2010
|
0.78
|
|
64
|
Compliance with immunizations in splenectomized individuals with hereditary spherocytosis.
|
Pediatr Blood Cancer
|
2009
|
0.78
|
|
65
|
Response to steroids predicts response to rituximab in pediatric chronic immune thrombocytopenia.
|
Pediatr Blood Cancer
|
2011
|
0.78
|
|
66
|
Human T cell lymphotropic virus type 1 infection among U.S. thalassemia patients.
|
AIDS Res Hum Retroviruses
|
2013
|
0.78
|
|
67
|
Infantile myofibroma or lymphatic malformation: differential diagnosis of neonatal cystic cervicofacial lesions.
|
J Craniofac Surg
|
2010
|
0.78
|
|
68
|
Beliefs about chelation among thalassemia patients.
|
Health Qual Life Outcomes
|
2012
|
0.78
|
|
69
|
Education and employment status of children and adults with thalassemia in North America.
|
Pediatr Blood Cancer
|
2010
|
0.78
|
|
70
|
Guidelines for the Standard Monitoring of Patients With Thalassemia: Report of the Thalassemia Longitudinal Cohort.
|
J Pediatr Hematol Oncol
|
2015
|
0.78
|
|
71
|
Future research in ITP: an ICIS consensus.
|
Ann Hematol
|
2010
|
0.77
|
|
72
|
To treat or not to treat--from guidelines to individualized patient management.
|
Semin Hematol
|
2013
|
0.77
|
|
73
|
Risk factors for thromboembolism in teens: when should I test?
|
Curr Opin Pediatr
|
2002
|
0.77
|
|
74
|
Female monozygotic twins discordant for hemophilia A due to nonrandom X-chromosome inactivation.
|
Am J Hematol
|
2008
|
0.75
|
|
75
|
The use of erythropoietin-stimulating agents versus supportive care in newborns with hereditary spherocytosis: a single centre's experience.
|
Eur J Haematol
|
2014
|
0.75
|
|
76
|
Remission from transfusion-dependence in a patient with congenital dyserythropoietic anemia (CDA) and increased intensity of iron chelation.
|
Pediatr Blood Cancer
|
2009
|
0.75
|
|
77
|
Increased leucocyte apoptosis in transfused β-thalassaemia patients.
|
Br J Haematol
|
2012
|
0.75
|
|
78
|
Novel dominant β-thalassemia: Hb Boston-Kuwait [codon 139/140(+T)].
|
Pediatr Blood Cancer
|
2013
|
0.75
|
|
79
|
Pregnancy outcomes in women with thalassemia in North America and the United Kingdom.
|
Am J Hematol
|
2013
|
0.75
|
|
80
|
Extracorporeal membrane oxygenation as a bridge to cardiac transplantation in a patient with cardiomyopathy and hemophilia A.
|
Intensive Care Med
|
2003
|
0.75
|
|
81
|
Time course of early induction of intracellular adhesion molecule-1 messenger RNA during reperfusion, following cardiopulmonary bypass with hypothermic circulatory arrest in lambs.
|
Pediatr Crit Care Med
|
2003
|
0.75
|
|
82
|
Validation and reliability of a disease-specific quality of life measure (the TranQol) in adults and children with thalassaemia major.
|
Br J Haematol
|
2013
|
0.75
|