Published in Blood on September 20, 2010
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Small vessels, big trouble in the kidneys and beyond: hematopoietic stem cell transplantation-associated thrombotic microangiopathy. Blood (2011) 1.43
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Perforin is a critical physiologic regulator of T-cell activation. Blood (2011) 1.32
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Munc18b/STXBP2 is required for platelet secretion. Blood (2012) 1.30
Private cord blood banking: experiences and views of pediatric hematopoietic cell transplantation physicians. Pediatrics (2009) 1.29
Gene expression profiling of peripheral blood mononuclear cells from children with active hemophagocytic lymphohistiocytosis. Blood (2011) 1.29
Genetic variation in the leptin receptor gene and obesity in survivors of childhood acute lymphoblastic leukemia: a report from the Childhood Cancer Survivor Study. J Clin Oncol (2004) 1.28
Frequency and spectrum of central nervous system involvement in 193 children with haemophagocytic lymphohistiocytosis. Br J Haematol (2007) 1.27
Alpha-lipoic acid decreases hepatic lipogenesis through adenosine monophosphate-activated protein kinase (AMPK)-dependent and AMPK-independent pathways. Hepatology (2008) 1.27
Interplay of adaptive th2 immunity with eotaxin-3/c-C chemokine receptor 3 in eosinophilic esophagitis. J Pediatr Gastroenterol Nutr (2007) 1.26
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Successful bone marrow transplantation for IPEX syndrome after reduced-intensity conditioning. Blood (2006) 1.23
Abnormalities in the alternative pathway of complement in children with hematopoietic stem cell transplant-associated thrombotic microangiopathy. Blood (2013) 1.22
Primary immunodeficiencies predisposed to Epstein-Barr virus-driven haematological diseases. Br J Haematol (2013) 1.20
Salvage therapy of refractory hemophagocytic lymphohistiocytosis with alemtuzumab. Pediatr Blood Cancer (2012) 1.20
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Aberrant maturation of mutant perforin underlies the clinical diversity of hemophagocytic lymphohistiocytosis. J Clin Invest (2005) 1.18
Hypoxia modulates early events in T cell receptor-mediated activation in human T lymphocytes via Kv1.3 channels. J Physiol (2005) 1.17
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A deletion mutation in the betaA1/A3 crystallin gene ( CRYBA1/A3) is associated with autosomal dominant congenital nuclear cataract in a Chinese family. Hum Genet (2003) 1.16
Perforin deficiency impairs a critical immunoregulatory loop involving murine CD8(+) T cells and dendritic cells. Blood (2013) 1.14
Statistical issues in longitudinal data analysis for treatment efficacy studies in the biomedical sciences. Mol Ther (2010) 1.14
Numerical chromosomal changes and risk of development of myelodysplastic syndrome--acute myeloid leukemia in patients with Fanconi anemia. Cancer Genet Cytogenet (2010) 1.13
Rapid detection of intracellular SH2D1A protein in cytotoxic lymphocytes from patients with X-linked lymphoproliferative disease and their family members. Blood (2005) 1.13
Wiskott-Aldrich syndrome: diagnosis, clinical and laboratory manifestations, and treatment. Biol Blood Marrow Transplant (2009) 1.12
The FA pathway counteracts oxidative stress through selective protection of antioxidant defense gene promoters. Blood (2012) 1.12
Pregnancy after hematopoietic cell transplantation: a report from the late effects working committee of the Center for International Blood and Marrow Transplant Research (CIBMTR). Biol Blood Marrow Transplant (2010) 1.11
Individual physician practice variation in hematopoietic cell transplantation. J Clin Oncol (2008) 1.11
Allogeneic hematopoietic cell transplantation for XIAP deficiency: an international survey reveals poor outcomes. Blood (2012) 1.11