PubRank

Thomas Meier

Author PubWeight™ 65.20‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 A randomized placebo-controlled trial of idebenone in Leber's hereditary optic neuropathy. Brain 2011 3.48
2 Histological parameters for the quantitative assessment of muscular dystrophy in the mdx-mouse. Neuromuscul Disord 2004 2.37
3 Mammalian animal models for Duchenne muscular dystrophy. Neuromuscul Disord 2009 2.15
4 High-resolution structure of the rotor ring of a proton-dependent ATP synthase. Nat Struct Mol Biol 2009 1.80
5 Mitochondria-targeted antioxidants protect Friedreich Ataxia fibroblasts from endogenous oxidative stress more effectively than untargeted antioxidants. FASEB J 2003 1.70
6 Catalytic and mechanical cycles in F-ATP synthases. Fourth in the Cycles Review Series. EMBO Rep 2006 1.65
7 The heart in Friedreich ataxia: definition of cardiomyopathy, disease severity, and correlation with neurological symptoms. Circulation 2012 1.50
8 The c15 ring of the Spirulina platensis F-ATP synthase: F1/F0 symmetry mismatch is not obligatory. EMBO Rep 2005 1.48
9 A new type of proton coordination in an F(1)F(o)-ATP synthase rotor ring. PLoS Biol 2010 1.43
10 Microscopic rotary mechanism of ion translocation in the F(o) complex of ATP synthases. Nat Chem Biol 2010 1.39
11 Molecular architecture of the undecameric rotor of a bacterial Na+-ATP synthase. J Mol Biol 2002 1.38
12 The c13 ring from a thermoalkaliphilic ATP synthase reveals an extended diameter due to a special structural region. J Mol Biol 2009 1.23
13 A phase 3, double-blind, placebo-controlled trial of idebenone in friedreich ataxia. Arch Neurol 2010 1.21
14 Structure of the c(10) ring of the yeast mitochondrial ATP synthase in the open conformation. Nat Struct Mol Biol 2012 1.20
15 A cellular model for Friedreich Ataxia reveals small-molecule glutathione peroxidase mimetics as novel treatment strategy. Hum Mol Genet 2002 1.14
16 The oligomeric state of c rings from cyanobacterial F-ATP synthases varies from 13 to 15. J Bacteriol 2007 1.11
17 Long-term blinded placebo-controlled study of SNT-MC17/idebenone in the dystrophin deficient mdx mouse: cardiac protection and improved exercise performance. Eur Heart J 2008 1.11
18 Structural and energetic basis for H+ versus Na+ binding selectivity in ATP synthase Fo rotors. Biochim Biophys Acta 2010 1.07
19 Omigapil ameliorates the pathology of muscle dystrophy caused by laminin-alpha2 deficiency. J Pharmacol Exp Ther 2009 1.06
20 Engineering rotor ring stoichiometries in the ATP synthase. Proc Natl Acad Sci U S A 2012 1.05
21 Sevoflurane inhalation at sedative concentrations provides endothelial protection against ischemia-reperfusion injury in humans. Anesthesiology 2007 1.05
22 An intermediate step in the evolution of ATPases: a hybrid F(0)-V(0) rotor in a bacterial Na(+) F(1)F(0) ATP synthase. FEBS J 2008 1.03
23 On the structure of the proton-binding site in the F(o) rotor of chloroplast ATP synthases. J Mol Biol 2009 1.03
24 The c-ring stoichiometry of ATP synthase is adapted to cell physiological requirements of alkaliphilic Bacillus pseudofirmus OF4. Proc Natl Acad Sci U S A 2013 1.02
25 Idebenone in Friedreich ataxia cardiomyopathy-results from a 6-month phase III study (IONIA). Am Heart J 2011 1.01
26 Effect of calpain and proteasome inhibition on Ca2+-dependent proteolysis and muscle histopathology in the mdx mouse. FASEB J 2008 1.01
27 Idebenone as a novel, therapeutic approach for Duchenne muscular dystrophy: results from a 12 month, double-blind, randomized placebo-controlled trial. Neuromuscul Disord 2011 1.00
28 A new type of Na(+)-driven ATP synthase membrane rotor with a two-carboxylate ion-coupling motif. PLoS Biol 2013 0.98
29 Probing the rotor subunit interface of the ATP synthase from Ilyobacter tartaricus. FEBS J 2008 0.96
30 Observing membrane protein diffusion at subnanometer resolution. J Mol Biol 2003 0.95
31 Activation of muscle-specific receptor tyrosine kinase and binding to dystroglycan are regulated by alternative mRNA splicing of agrin. J Biol Chem 2006 0.95
32 Meta-analysis of the prevalence of Leber hereditary optic neuropathy mtDNA mutations in Europe. Eur J Ophthalmol 2012 0.94
33 Electrical power fuels rotary ATP synthase. Structure 2003 0.92
34 Apoptosis inhibitors and mini-agrin have additive benefits in congenital muscular dystrophy mice. EMBO Mol Med 2011 0.91
35 Membrane embedded location of Na+ or H+ binding sites on the rotor ring of F1F0 ATP synthases. Eur J Biochem 2002 0.89
36 Glucocorticoid-mediated regulation of utrophin levels in human muscle fibers. Neuromuscul Disord 2002 0.89
37 Structural study on the architecture of the bacterial ATP synthase Fo motor. Proc Natl Acad Sci U S A 2012 0.88
38 Cell-free expression and assembly of ATP synthase. J Mol Biol 2011 0.88
39 The c-ring ion binding site of the ATP synthase from Bacillus pseudofirmus OF4 is adapted to alkaliphilic lifestyle. Mol Microbiol 2014 0.87
40 Novel cell-penetrating alpha-keto-amide calpain inhibitors as potential treatment for muscular dystrophy. Bioorg Med Chem Lett 2005 0.86
41 Effects of idebenone on color vision in patients with leber hereditary optic neuropathy. J Neuroophthalmol 2013 0.85
42 Rating disease progression of Friedreich's ataxia by the International Cooperative Ataxia Rating Scale: analysis of a 603-patient database. Brain 2013 0.84
43 ATP synthases: cellular nanomotors characterized by LILBID mass spectrometry. Phys Chem Chem Phys 2010 0.84
44 Midterm outcome of endovascular repair of ruptured isolated iliac artery aneurysms. J Vasc Surg 2010 0.84
45 Fourth generation human immunodeficiency virus (HIV) screening assays with an improved sensitivity for p24 antigen close the second diagnostic window in primary HIV infection. J Clin Virol 2002 0.83
46 Protective effects of Fe-Aox29, a novel antioxidant derived from a molecular combination of Idebenone and vitamin E, in immortalized fibroblasts and fibroblasts from patients with Friedreich Ataxia. Mol Cell Biochem 2007 0.83
47 Time-resolved microspectrofluorometry and fluorescence lifetime imaging of photosensitizers using picosecond pulsed diode lasers in laser scanning microscopes. J Biomed Opt 2003 0.82
48 The function of the Na+-driven flagellum of Vibrio cholerae is determined by osmolality and pH. J Bacteriol 2013 0.82
49 Draft genome sequence of the thermoalkaliphilic Caldalkalibacillus thermarum strain TA2.A1. J Bacteriol 2011 0.82
50 Mutations in a helix-1 motif of the ATP synthase c-subunit of Bacillus pseudofirmus OF4 cause functional deficits and changes in the c-ring stability and mobility on sodium dodecyl sulfate-polyacrylamide gel electrophoresis. Biochemistry 2011 0.81
51 Massive monoclonal expansion of CD4 T-cells specific for a Mycobacterium tuberculosis ESAT-6 peptide. Eur Respir J 2012 0.81
52 A1Ao-ATP synthase of Methanobrevibacter ruminantium couples sodium ions for ATP synthesis under physiological conditions. J Biol Chem 2011 0.80
53 Low-molecular-weight heparin for prevention of restenosis after femoropopliteal percutaneous transluminal angioplasty: a randomized controlled trial. J Vasc Surg 2006 0.79
54 Reengineered glucose oxidase for amperometric glucose determination in diabetes analytics. Biosens Bioelectron 2013 0.78
55 Transcriptional activation of the utrophin promoter B by a constitutively active Ets-transcription factor. Neuromuscul Disord 2003 0.78
56 Effects of glucocorticoids and idebenone on respiratory function in patients with duchenne muscular dystrophy. Pediatr Pulmonol 2012 0.78
57 Detection of glucocorticoid-like activity in traditional Chinese medicine used for the treatment of Duchenne muscular dystrophy. Neuromuscul Disord 2003 0.77
58 Nailfold capillaroscopy: Specific features in Fabry disease. Clin Hemorheol Microcirc 2009 0.77
59 The interaction of lipid modified pseudopeptides with lipid membranes. Org Biomol Chem 2011 0.77
60 Plasma Homocysteine is Not Related to the Severity of Microangiopathy in Secondary Raynaud Phenomenon. Open Rheumatol J 2011 0.75
61 Social structures and social relations--an archaeological and anthropological examination of three early Medieval separate burial sites in Bavaria. Anthropol Anz 2006 0.75
62 Predictive value of duplex ultrasound for restenosis after renal artery stenting. Clin Hemorheol Microcirc 2010 0.75